Page last updated: 2024-11-04

stearic acid and Adrenoleukodystrophy

stearic acid has been researched along with Adrenoleukodystrophy in 3 studies

octadecanoic acid : A C18 straight-chain saturated fatty acid component of many animal and vegetable lipids. As well as in the diet, it is used in hardening soaps, softening plastics and in making cosmetics, candles and plastics.

Adrenoleukodystrophy: An X-linked recessive disorder characterized by the accumulation of saturated very long chain fatty acids in the LYSOSOMES of ADRENAL CORTEX and the white matter of CENTRAL NERVOUS SYSTEM. This disease occurs almost exclusively in the males. Clinical features include the childhood onset of ATAXIA; NEUROBEHAVIORAL MANIFESTATIONS; HYPERPIGMENTATION; ADRENAL INSUFFICIENCY; SEIZURES; MUSCLE SPASTICITY; and DEMENTIA. The slowly progressive adult form is called adrenomyeloneuropathy. The defective gene ABCD1 is located at Xq28, and encodes the adrenoleukodystrophy protein (ATP-BINDING CASSETTE TRANSPORTERS).

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's3 (100.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Sargent, JR1
Coupland, K1
Wilson, R1
Singh, H1
Usher, S1
Johnson, D1
Poulos, A1
Koike, R1
Tsuji, S1
Ohno, T1
Suzuki, Y1
Orii, T1
Miyatake, T1

Other Studies

3 other studies available for stearic acid and Adrenoleukodystrophy

ArticleYear
Nervonic acid and demyelinating disease.
    Medical hypotheses, 1994, Volume: 42, Issue:4

    Topics: Adrenoleukodystrophy; Fatty Acids, Monounsaturated; Fibroblasts; Humans; Multiple Sclerosis; Myelin

1994
Metabolism of branched chain fatty acids in peroxisomal disorders.
    Journal of inherited metabolic disease, 1990, Volume: 13, Issue:3

    Topics: Adrenoleukodystrophy; Cells, Cultured; Chondrodysplasia Punctata; Fatty Acids; Fibroblasts; Heptanoi

1990
Physiological significance of fatty acid elongation system in adrenoleukodystrophy.
    Journal of the neurological sciences, 1991, Volume: 103, Issue:2

    Topics: Adrenoleukodystrophy; Fatty Acids; Fatty Acids, Unsaturated; Fibroblasts; Humans; Oxidation-Reductio

1991