sorbitol has been researched along with Hepatolenticular Degeneration in 1 studies
D-glucitol : The D-enantiomer of glucitol (also known as D-sorbitol).
Hepatolenticular Degeneration: A rare autosomal recessive disease characterized by the deposition of copper in the BRAIN; LIVER; CORNEA; and other organs. It is caused by defects in the ATP7B gene encoding copper-transporting ATPase 2 (EC 3.6.3.4), also known as the Wilson disease protein. The overload of copper inevitably leads to progressive liver and neurological dysfunction such as LIVER CIRRHOSIS; TREMOR; ATAXIA and intellectual deterioration. Hepatic dysfunction may precede neurologic dysfunction by several years.
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 1 (100.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Shimada, H | 1 |
| Takahashi, M | 1 |
| Shimada, A | 1 |
| Okawara, T | 1 |
| Yasutake, A | 1 |
| Imamura, Y | 1 |
| Kiyozumi, M | 1 |
1 other study available for sorbitol and Hepatolenticular Degeneration
| Article | Year |
|---|---|
Protection from spontaneous hepatocellular damage by N-benzyl-d-glucamine dithiocarbamate in Long-Evans Cinnamon rats, an animal model of Wilson's disease.
Topics: Animals; Body Weight; Chelating Agents; Copper; Disease Models, Animal; Dose-Response Relationship, | 2005 |