sirolimus and Pityriasis-Rubra-Pilaris

sirolimus has been researched along with Pityriasis-Rubra-Pilaris* in 1 studies

Reviews

1 review(s) available for sirolimus and Pityriasis-Rubra-Pilaris

ArticleYear
Keratosis pilaris rubra successfully treated with topical sirolimus: Report of a case and review of the literature.
    Pediatric dermatology, 2022, Volume: 39, Issue:3

    Keratosis pilaris rubra (KPR) is a subtype of keratosis pilaris (KP) presenting with numerous "grainlike" follicular papules in a background of confluent erythema most often affecting the face and upper extremities with persistence beyond puberty. Treatment has remained challenging with inconsistent benefit from topical therapies such as emollients, keratolytics, corticosteroids, and retinoids, though case reports documenting success with pulsed dye laser therapy have been found. We present a case of KPR in a 15-year-old boy who was successfully treated with topical sirolimus 1% cream.

    Topics: Abnormalities, Multiple; Adolescent; Darier Disease; Emollients; Exanthema; Eyebrows; Humans; Immunosuppressive Agents; Male; Pityriasis Rubra Pilaris; Sirolimus

2022