Page last updated: 2024-11-04

sevoflurane and Glycogen Storage Disease Type II

sevoflurane has been researched along with Glycogen Storage Disease Type II in 2 studies

Sevoflurane: A non-explosive inhalation anesthetic used in the induction and maintenance of general anesthesia. It does not cause respiratory irritation and may also prevent PLATELET AGGREGATION.
sevoflurane : An ether compound having fluoromethyl and 1,1,1,3,3,3-hexafluoroisopropyl as the two alkyl groups.

Glycogen Storage Disease Type II: An autosomal recessively inherited glycogen storage disease caused by GLUCAN 1,4-ALPHA-GLUCOSIDASE deficiency. Large amounts of GLYCOGEN accumulate in the LYSOSOMES of skeletal muscle (MUSCLE, SKELETAL); HEART; LIVER; SPINAL CORD; and BRAIN. Three forms have been described: infantile, childhood, and adult. The infantile form is fatal in infancy and presents with hypotonia and a hypertrophic cardiomyopathy (CARDIOMYOPATHY, HYPERTROPHIC). The childhood form usually presents in the second year of life with proximal weakness and respiratory symptoms. The adult form consists of a slowly progressive proximal myopathy. (From Muscle Nerve 1995;3:S61-9; Menkes, Textbook of Child Neurology, 5th ed, pp73-4)

Research Excerpts

ExcerptRelevanceReference
"Pompe or glycogen storage disease type II is a genetic disorder affecting the cardiac and skeletal muscle."1.34[Anesthetic management for a child with pompe disease]. ( Hiroki, K; Miwa, T; Sato, Y; Yamaguchi, K, 2007)
"Deaths resulting from arrhythmia appeared to correlate with left ventricular mass indices >350 g x m(-2)."1.34Cardiac arrhythmias following anesthesia induction in infantile-onset Pompe disease: a case series. ( Corzo, D; Dearmey, SM; Kishnani, PS; Li, JS; Mackey, JF; Morgan, C; Ross, AK; Wang, LY; Worden, M, 2007)

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Sato, Y1
Yamaguchi, K1
Miwa, T1
Hiroki, K1
Wang, LY1
Ross, AK1
Li, JS1
Dearmey, SM1
Mackey, JF1
Worden, M1
Corzo, D1
Morgan, C1
Kishnani, PS1

Other Studies

2 other studies available for sevoflurane and Glycogen Storage Disease Type II

ArticleYear
[Anesthetic management for a child with pompe disease].
    Masui. The Japanese journal of anesthesiology, 2007, Volume: 56, Issue:3

    Topics: Anesthesia, General; Child, Preschool; Clubfoot; Glycogen Storage Disease Type II; Humans; Intubatio

2007
Cardiac arrhythmias following anesthesia induction in infantile-onset Pompe disease: a case series.
    Paediatric anaesthesia, 2007, Volume: 17, Issue:8

    Topics: alpha-Glucosidases; Anesthesia, General; Anesthetics, Intravenous; Arrhythmias, Cardiac; Clinical Tr

2007