Page last updated: 2024-08-23

s-adenosylmethionine and Hyperammonemia

s-adenosylmethionine has been researched along with Hyperammonemia in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's3 (27.27)29.6817
2010's5 (45.45)24.3611
2020's3 (27.27)2.80

Authors

AuthorsStudies
Houten, SM; Ranea-Robles, P; van Vlies, N; Vaz, FM; Yu, C1
Aldehaimi, A; Almannai, M; Almontashiri, NAM; Peake, RWA1
Chen, Y; Lin, Q; Liu, G; Qiu, X; Zeng, Y; Zhu, W1
Couce, ML; de Castro, MJ; López, M; Rite, S; Roca, I; Sánchez-Pintos, P1
Bueno, MA; Castiñeiras, DE; Cocho, JA; Couce, ML; Delgado-Pecellín, C; Diogo, L; Fraga, JM; García-Villoria, J; Leão-Teles, E; Martins, E; Ribes, A; Rocha, H; Sánchez-Pintos, P; Santos, H1
Bo, R; Hasegawa, Y; Ishige, N; Kobayashi, H; Nakamura, M; Takahashi, T; Yamada, K; Yamaguchi, S1
Abdella, MM; Hamed, SA1
Fukao, T; Fukuda, S; Hasegawa, Y; Kobayashi, H; Purevsuren, J; Takahashi, T; Takayanagi, M; Yamada, K; Yamaguchi, S1
Eyer, F; Felgenhauer, N; Gempel, K; Gerbitz, KD; Steimer, W; Zilker, T1
Chakrapani, A; Gray, G; Hendriksz, C; Macdonald, A; Pierre, G; Preece, MA1
Cheillan, D; Dessein, AF; Dobbelaere, D; Fontaine, M; Joncquel-Chevalier Curt, M; Mention-Mulliez, K; Porchet, N; Soto-Ares, G; Vamecq, J; Voicu, PM1

Reviews

1 review(s) available for s-adenosylmethionine and Hyperammonemia

ArticleYear
Creatine biosynthesis and transport in health and disease.
    Biochimie, 2015, Volume: 119

    Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Amino Acid Transport Systems, Basic; AMP-Activated Protein Kinases; Animals; Biological Transport, Active; Brain Diseases, Metabolic, Inborn; Creatine; Developmental Disabilities; Energy Metabolism; Guanidinoacetate N-Methyltransferase; Gyrate Atrophy; Humans; Hyperammonemia; Intellectual Disability; Language Development Disorders; Mental Retardation, X-Linked; Methylation; Mitochondrial Membrane Transport Proteins; Movement Disorders; Mutation; Nerve Tissue Proteins; Ornithine; Plasma Membrane Neurotransmitter Transport Proteins; Prenatal Diagnosis; S-Adenosylmethionine; Speech Disorders; Urea Cycle Disorders, Inborn

2015

Trials

1 trial(s) available for s-adenosylmethionine and Hyperammonemia

ArticleYear
The risk of asymptomatic hyperammonemia in children with idiopathic epilepsy treated with valproate: relationship to blood carnitine status.
    Epilepsy research, 2009, Volume: 86, Issue:1

    Topics: Adolescent; Ammonia; Anticonvulsants; Carnitine; Child; Epilepsy; Female; Humans; Hyperammonemia; Male; Prospective Studies; Valproic Acid; Vitamin B Complex

2009

Other Studies

9 other study(ies) available for s-adenosylmethionine and Hyperammonemia

ArticleYear
Slc22a5 haploinsufficiency does not aggravate the phenotype of the long-chain acyl-CoA dehydrogenase KO mouse.
    Journal of inherited metabolic disease, 2020, Volume: 43, Issue:3

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Cardiomyopathies; Carnitine; Disease Models, Animal; Fatty Acids; Female; Haploinsufficiency; Hyperammonemia; Lipid Metabolism; Liver; Male; Mice; Mice, Knockout; Muscular Diseases; Myocardium; Phenotype; Solute Carrier Family 22 Member 5

2020
Hyperammonemia, Lactic Acidosis, and Arrhythmia in a Newborn.
    Clinical chemistry, 2021, 01-08, Volume: 67, Issue:1

    Topics: Acidosis, Lactic; Arrhythmias, Cardiac; Carnitine; Female; Humans; Hyperammonemia; Infant, Newborn; Lipid Metabolism, Inborn Errors; Membrane Transport Proteins; Mutation

2021
Gene spectrum and clinical traits of 10 patients with primary carnitine deficiency.
    Molecular genetics & genomic medicine, 2021, Volume: 9, Issue:2

    Topics: Adult; Cardiomyopathies; Carnitine; Female; Gene Frequency; Humans; Hyperammonemia; Infant; Male; Muscular Diseases; Mutation; Phenotype; Solute Carrier Family 22 Member 5

2021
Similarities between acylcarnitine profiles in large for gestational age newborns and obesity.
    Scientific reports, 2017, 11-24, Volume: 7, Issue:1

    Topics: Cardiomyopathies; Carnitine; Female; Gestational Age; Humans; Hyperammonemia; Infant, Newborn; Infant, Small for Gestational Age; Male; Muscular Diseases; Obesity; Pregnancy

2017
Newborn screening for medium-chain acyl-CoA dehydrogenase deficiency: regional experience and high incidence of carnitine deficiency.
    Orphanet journal of rare diseases, 2013, Jul-10, Volume: 8

    Topics: Acyl-CoA Dehydrogenase; Cardiomyopathies; Carnitine; Dietary Supplements; Female; Genetic Association Studies; Genotype; Homozygote; Humans; Hyperammonemia; Incidence; Infant, Newborn; Lipid Metabolism, Inborn Errors; Male; Muscular Diseases; Neonatal Screening; Phenotype; Prevalence; Spain; Vitamin B Complex

2013
Elevation of pivaloylcarnitine by sivelestat sodium in two children.
    Molecular genetics and metabolism, 2015, Volume: 116, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Cardiomyopathies; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glycine; Humans; Hyperammonemia; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Muscular Diseases; Neonatal Screening; Serine Proteinase Inhibitors; Sulfonamides; Tandem Mass Spectrometry

2015
Intracellular in vitro probe acylcarnitine assay for identifying deficiencies of carnitine transporter and carnitine palmitoyltransferase-1.
    Analytical and bioanalytical chemistry, 2013, Volume: 405, Issue:4

    Topics: Biological Transport; Cardiomyopathies; Carnitine; Carnitine Acyltransferases; Carnitine O-Palmitoyltransferase; Cells, Cultured; Fatty Acids; Fibroblasts; Humans; Hyperammonemia; Hypoglycemia; Lipid Metabolism, Inborn Errors; Mitochondria; Muscular Diseases; Oxidation-Reduction; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry

2013
Acute valproate poisoning: pharmacokinetics, alteration in fatty acid metabolism, and changes during therapy.
    Journal of clinical psychopharmacology, 2005, Volume: 25, Issue:4

    Topics: Anticonvulsants; Brain Edema; Carnitine; Drug Overdose; Fatty Acids; Female; Humans; Hyperammonemia; Male; Mitochondria; Oxidation-Reduction; Pancreatitis; Renal Dialysis; Valproic Acid

2005
Prospective treatment in carnitine-acylcarnitine translocase deficiency.
    Journal of inherited metabolic disease, 2007, Volume: 30, Issue:5

    Topics: Carnitine; Carnitine Acyltransferases; Dicarboxylic Acids; Diet, Fat-Restricted; Dietary Supplements; Fatty Acids; Humans; Hyperammonemia; Hypoglycemia; Infant; Male; Membrane Transport Proteins; Metabolism, Inborn Errors; Oxidation-Reduction; Pedigree; Phenotype; Severity of Illness Index; Treatment Outcome

2007