retinol and Cystic Fibrosis

retinol has been researched along with Cystic Fibrosis in 117 studies

Research

Studies (117)

TimeframeStudies, this research(%)All Research%
pre-199032 (27.35)18.7374
1990's26 (22.22)18.2507
2000's26 (22.22)29.6817
2010's25 (21.37)24.3611
2020's8 (6.84)2.80

Authors

AuthorsStudies
Hurwitz, JL; Sealy, RE; Surman, SL; Vogel, P1
Bach, T; Chin, LH; Farrell, PM; Lai, HJ; Murali, S; Sander, D1
Hendrix, SJ; Sankararaman, S; Schindler, T1
Grzybowska-Chlebowczyk, U; Pyziak-Skupień, A; Wielkoszyński, T; Woś, H; Wysocka-Wojakiewicz, P1
Bauraind, O; Lebecque, P; Mulder, A; Rebia, I; Thimmesch, M1
Balfour-Lynn, IM; Bentley, S; Carr, SB; Schembri, L; Warraich, S1
Bartlett, LE; Bridges, G; Cogen, JD; Faino, A; Green, N; Hergenroeder, GE; McNamara, S; Nichols, DP; Ramos, KJ1
Biffi, A; Bulfamante, AMC; Claut, L; Colombo, C; Cuomo, M; Norsa, L; Zazzeron, L1
Eryilmaz-Polat, S; Inal-Ince, D; Kahraman, A; Karakaya, J; Livanelioglu, A; Mutlu, A; Ozcelik, U; Tekerlek, H1
Bonifant, CM; Chang, AB; de Vries, JJ; Marchant, JM; Shevill, E1
Acuña Quirós, MD; Bousoño-García, C; Díaz Martín, JJ; Garagorri Otero, JM; González Jiménez, D; Heredia González, S; Lázaro Almarza, A; Rivas-Crespo, MF; Sojo Aguirre, A1
Ambroszkiewicz, J; Chelchowska, M; Gajewska, J; Laskowska-Klita, T; Sands, D1
Bertolaso, C; Dougherty, KA; Groleau, V; Latham, NE; Maqbool, A; Mascarenhas, M; Schall, JI; Stallings, VA1
Angurana, SK; Attri, SV; Bhalla, AK; Sharma, G; Singh, M; Tageja, M; Yadav, K1
Coakley, J; Gaskin, K; Jaffe, A; Katz, T; Lochhead, A; Rana, M; Whitehead, B; Wong-See, D1
Bonifant, CM; Chang, AB; Shevill, E2
Filbrun, AG; Nasr, SZ; Safi, KH1
Bączek, T; Kamińska, B; Kaźmierska, K; Olędzka, I; Plenis, A1
Arets, HG; Broos, N; Houwen, RH; Stellato, RK; van der Ent, CK; Woestenenk, JW2
De Spirt, S; Joachim, C; Langhans, CD; Mall, MA; Mattern, A; Nesaretnam, K; Siems, W; Sommerburg, O; Stahl, W1
Rivas-Crespo, MF1
Houwen, RH; Woestenenk, JW1
Breuer, O; Cohen-Cymberknoh, M; Kerem, E; Shamali, M; Shoseyov, D; Wilschanski, M1
Alzaben, AS; Brown, N; Chung, TT; Goodvin, M; Hubert, G; Jackson, K; Lien, D; Mager, DR; Prosser, C; Salgado, J; Tabak, J; Weinkauf, J1
Maqbool, A; Stallings, VA1
TSAO, M; WEICK, G1
Beaune, P; Bonnefont, JP; de Villartay, P; Feuillet-Fieux, MN; Kelly, M; Lacour, B; Lenoir, G; Loriot, MA; Nguyen-Khoa, T; Sermet, I; Verrier, P1
Allen, J; Blumenthal, C; Gaskin, K; Suttle, C; Whatham, A1
BINKLEY, EL; DANIELSON, WH; PALMER, HD1
Cheng, MP; Lands, LC; Ovetchkine, P; Paquette, K; Quach, C; Théoret, Y1
Patel, AS; Sathe, MN1
DANIELSON, WH; PALMER, HD1
Brotherwood, M; Chaparro, C; Cortes, D; Gupta, S; Ho, T; Keshavjee, S; Robert, R; Stephenson, A; Tullis, E; Verjee, Z1
Clancy, G; Elnazir, B; Feehan, S; Greally, P; Leen, G; Roddy, MF1
Almgren, MM; Braga, SF1
Agostoni, C; Alicandro, G; Bianchi, ML; Biffi, A; Cirilli, N; Colombo, C; Faelli, N; Gagliardini, R; Galli, C; Loi, S; Magazzù, G; Palmas, T; Risé, P; Santini, B; Tirelli, AS; Valmarana, L; Vieni, G1
Brei, C; Krawinkel, MB; Naehrlich, L; Simon, A1
Lloyd-Still, JD1
Bérubé, D; Bureau, N; Champagne, J; Chemtob, S; Lepage, G; Ronco, N; Roy, CC; Yesair, DW1
Aksnes, L; Dorlöchter, L; Fluge, G1
Balfour-Lynn, IM; Buchdahl, R; Bush, A; Jaffé, A1
Fitzgerald, DA; Garg, ML; Lee, AK; Wood, LG1
KLUTHE, R; MERTZ, DP; SARRE, H1
KONZERT, W1
BLAKE, RM; GOLDBLOOM, RB1
Díaz, E; Fielbaum, O; Gattas, V; Herrera, O; Hunter, B; Marín, VB; Velandia, S1
Batch, JA; Bell, SC; Buntain, HM; Francis, PW; Greer, RM; Lewindon, PJ; Potter, JM; Wainwright, CE; Wong, JC1
Brotherwood, M; Chaparro, C; Corey, M; Durie, P; Robert, R; Stephenson, A; Tullis, E; Verjee, Z1
Minarowska, A; Mrugacz, M; Tobolczyk, J1
Albert, DM; Mootha, VV; Patel, SM; Villalobos, R; Wamsley, S; Wood, MG1
Douglas, JA; Farrell, PM; Koscik, RL; Kosorok, MR; Lai, HJ; Laxova, A; Rock, MJ; Splaingard, ML; Zaremba, KM1
Armstrong, DS; Bines, JE; Carzino, R; Grimwood, K; Truby, HD1
Sethuraman, U1
Aird, FK; Greene, SA; Macdonald, TM; Mukhopadhyay, S; Ogston, SA1
Graham-Maar, RC; Schall, JI; Stallings, VA; Stettler, N; Zemel, BS1
Basu, AP; Devlin, AM; Kumar, P; O'Brien, CJ1
Graham-Maar, RC; Maqbool, A; Schall, JI; Stallings, VA; Zemel, BS1
Bdolach-Abram, T; Bentur, L; Hakim, F; Kerem, E; Rivlin, J; Stankiewicz, H; Wilschanski, M1
De Beer, J; Huyghebaert, N; Remon, JP; Vervaet, C1
ANDERSEN, DH1
Chang, AB; O'Neil, C; Shevill, E1
Bennett, MJ; Medwadowski, BF1
Russell, RM; Solomons, NW1
Barg, DC; Fulton, AB; Hansen, RM; Shwachman, H; Underwood, BA1
Desquilbet, N; Navarro, J1
Bruce, G; Clarke, PC; Congden, PJ; Kelleher, J; Littlewood, JM; Losowsky, MS; Rothburn, MM1
Bartens, C; Elmadfa, I; Jakob, E; König, J1
Faure, HS; Favier, AE; Hadjian, AJ; Portal, BC; Richard, MJ1
Azoulay, C; Blanchard, B; Ganière-Monteil, C; Kergueris, MF; Larousse, C; Pineau, A1
Borowitz, D; Harris, M; Wegman, T1
Hahn, T; Kerasin, E; Tabachnik, E; Trifon, S; Vaisman, N; Voet, H1
Peters, SA; Rolles, CJ1
Shmerling, DH; van't Hof, MA; Winklhofer-Roob, BM1
Edmund, C; Koch, C; Lanng, S; Michaelsen, KF; Morkeberg, JC; Prause, JU1
D'Orazio, C; Lancellotti, L; Lippi, U; Mastella, G; Mazzi, G1
Carr, SB; Dinwiddie, R1
Agil, A; Colin, AA; Duggan, C; Higgins, L; Rifai, N1
Champagne, J; Lacaille, F; Lenaerts, C; Lepage, G; Paradis, K; Rasquin-Weber, A; Ronco, N; Roy, CC; Sénéchal, L1
Diczfalusy, U; Hultcrantz, R; Lindblad, A; Strandvik, B; Thorell, A1
Charavel, A; Huet, F; Maingueneau, C; Nivelon, JL; Semama, D1
Eichler, I; Elmadfa, I; Renner, S; Rust, P1
Ansari, EA; Conway, SP; Etherington, C; Littlewood, JM; Morton, A; Moya, E; Sahni, K1
Collins, CE; Garg, ML; Henry, RL; O'Loughlin, EV; Quaggiotto, P; Wood, L1
Accurso, FJ; Feranchak, AP; Hammond, KB; Sokol, RJ; Sontag, MK; Wagener, JS1
Hofley, PM; Kawchak, DA; Scanlin, TF; Sowell, AL; Stallings, VA; Zemel, BS1
Congdon, NG; Ng, EW; Sommer, A1
Biró, L; Greiner, E; Holics, K; Lugassi, A; Madarasi, A; Mozsáry, E1
Galli-Tsinopoulou, A; Nousia-Arvanitakis, S; Roubies, N; Stangos, N; Tentzidou, K; Tsinopoulos, I; Xefteri, M1
Jacob, RA; Rieger, C; Rothberg, R; Sandstead, HH; Solomons, NW1
Denning, CR; Palin, D; Underwood, BA1
Ekvall, S; Mitchell, A1
Hansen, LG; Sharp, H; Warwick, WJ1
Abernathy, RS1
Knöpfle, G; Odenthal, A; Rotthauwe, HW1
Bremer, DL; Leguire, LE; McGregor, ML; Pappa, KS; Rogers, GL1
Campbell, IA; Goodchild, MC; James, DR; Owen, G1
Lacaille, F; Lamarre, A; Lepage, G; Ronco, N; Roy, CC; Smith, LJ1
Bremer, DL; Kachmer, ML; Leguire, LE; Pappa, KS; Rogers, GL1
Brooks, HL; Driebe, WT; Schemmer, GG1
Ahmed, F; Ellis, J; Jackson, AA; Murphy, J; Wootton, S1
Eid, NS; Samiec, TD; Shoemaker, LR1
Brimlow, G; Hiller, EJ; Marenah, C; Neugebauer, MA; Tyrrell, JC; Vernon, SA1
Brimlow, G; Hiller, EJ; Marenah, C; Neugebauer, MA; Rayner, RJ; Tyrrell, JC; Vernon, SA1
Abman, SH; Accurso, FJ; Hammond, KB; Narkewicz, M; Reardon, MC; Sokol, RJ; Stall, C1
Biggemann, B; Bremer, HJ; Griese, M; Laryea, MD; Reinhardt, D; Schuster, A1
Bui, MH1
Goodchild, MC1
Dodge, JA1
Watari, N1
Underwood, BA1
Denning, CR; Underwood, BA2
Denning, CR; Goodman, DS; Smith, FR; Underwood, BA; Varma, A1
Petersen, RA; Petersen, VS; Robb, RM1
Norman, A; Strandvik, B; Zetterström, R1

Reviews

16 review(s) available for retinol and Cystic Fibrosis

ArticleYear
Update on the management of vitamins and minerals in cystic fibrosis.
    Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition, 2022, Volume: 37, Issue:5

    Topics: Cystic Fibrosis; Dietary Supplements; Humans; Micronutrients; Minerals; Vitamin A; Vitamins

2022
Vitamin A and beta (β)-carotene supplementation for cystic fibrosis.
    The Cochrane database of systematic reviews, 2018, 08-09, Volume: 8

    Topics: beta Carotene; Cystic Fibrosis; Humans; Provitamins; Randomized Controlled Trials as Topic; Vitamin A; Vitamin A Deficiency; Vitamins

2018
Vitamin A supplementation for cystic fibrosis.
    The Cochrane database of systematic reviews, 2014, May-14, Issue:5

    Topics: Cystic Fibrosis; Humans; Vitamin A; Vitamin A Deficiency; Vitamins

2014
Hypervitaminosis A causing hypercalcemia in cystic fibrosis. Case report and focused review.
    Annals of the American Thoracic Society, 2014, Volume: 11, Issue:8

    Topics: Calcium; Child, Preschool; Cystic Fibrosis; Female; Humans; Hypercalcemia; Hypervitaminosis A; Vitamin A

2014
Update on fat-soluble vitamins in cystic fibrosis.
    Current opinion in pulmonary medicine, 2008, Volume: 14, Issue:6

    Topics: Cystic Fibrosis; Humans; Vitamin A; Vitamin D; Vitamin E; Vitamin K; Vitamins

2008
Update in pediatrics: focus on fat-soluble vitamins.
    Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition, 2010, Volume: 25, Issue:4

    Topics: Avitaminosis; Child; Cholestasis; Cystic Fibrosis; Humans; Pediatrics; Vitamin A; Vitamin D; Vitamin E; Vitamin K; Vitamins

2010
Vitamin A supplementation for cystic fibrosis.
    The Cochrane database of systematic reviews, 2012, Aug-15, Issue:8

    Topics: Cystic Fibrosis; Humans; Vitamin A; Vitamin A Deficiency; Vitamins

2012
Complementary therapies in cystic fibrosis: nutritional supplements and herbal products.
    Journal of pharmacy practice, 2013, Volume: 26, Issue:1

    Topics: Antioxidants; Ascorbic Acid; Curcumin; Cystic Fibrosis; Dietary Supplements; Docosahexaenoic Acids; Fatty Acids, Omega-3; Garlic; Humans; Panax; Phytotherapy; Vitamin A; Vitamin E; Zinc

2013
[CELIAC DISEASE AND PANCREATIC FIBROSIS].
    Hippokrates, 1963, Nov-30, Volume: 34

    Topics: Celiac Disease; Child; Cystic Fibrosis; Diagnosis, Differential; Enzymes; Humans; Infant; Infant, Newborn; Physical Therapy Modalities; Prognosis; Vitamin A; Vitamins

1963
Vitamins.
    Pediatrics in review, 2006, Volume: 27, Issue:2

    Topics: Ascorbic Acid; Ascorbic Acid Deficiency; Avitaminosis; Breast Feeding; Child, Preschool; Cystic Fibrosis; Female; Humans; Hypervitaminosis A; Infant; Infant, Newborn; Male; Rickets; Vitamin A; Vitamin A Deficiency; Vitamin B Complex; Vitamin D; Vitamin E; Vitamin K; Vitamins

2006
Vitamin A supplementation for cystic fibrosis.
    The Cochrane database of systematic reviews, 2008, Jan-23, Issue:1

    Topics: Cystic Fibrosis; Humans; Vitamin A; Vitamin A Deficiency; Vitamins

2008
The interaction of vitamin A and zinc: implications for human nutrition.
    The American journal of clinical nutrition, 1980, Volume: 33, Issue:9

    Topics: Adolescent; Animals; Child; Cystic Fibrosis; Dark Adaptation; Humans; Infant; Liver Diseases; Male; Oxidation-Reduction; Protein-Energy Malnutrition; Retinol-Binding Proteins; Vision Disorders; Vitamin A; Vitamin A Deficiency; Zinc

1980
Vitamin therapy in cystic fibrosis--a review and rationale.
    Journal of clinical pharmacy and therapeutics, 1993, Volume: 18, Issue:1

    Topics: Ascorbic Acid; Cystic Fibrosis; Humans; Vitamin A; Vitamin B Complex; Vitamin D; Vitamin E; Vitamins

1993
Vitamin A in cystic fibrosis: case report and review of the literature.
    Journal of pediatric gastroenterology and nutrition, 1990, Volume: 10, Issue:2

    Topics: Biological Availability; Cystic Fibrosis; Humans; Hypervitaminosis A; Infant; Male; Vitamin A; Vitamin A Deficiency

1990
The nutritional state and nutrition.
    Acta paediatrica Scandinavica. Supplement, 1985, Volume: 317

    Topics: Age Determination by Skeleton; Body Height; Body Weight; Child; Cystic Fibrosis; Energy Intake; Fatty Acids, Essential; Humans; Infant, Low Birth Weight; Infant, Newborn; Iron; Nutritional Physiological Phenomena; Puberty, Delayed; Vitamin A; Vitamin D; Vitamin E; Vitamin K; Zinc

1985
The determination of vitamin A and some aspects of its distribution, mobilization and transport in health and disease.
    World review of nutrition and dietetics, 1974, Volume: 19

    Topics: Adolescent; Adult; Biological Transport; Carrier Proteins; Child; Cystic Fibrosis; Female; Humans; Infant; Infant, Newborn; Liver; Lymph; Male; Middle Aged; Pregnancy; Spectrometry, Fluorescence; Spectrophotometry; Spectrophotometry, Ultraviolet; Vitamin A

1974

Trials

10 trial(s) available for retinol and Cystic Fibrosis

ArticleYear
Fat-soluble vitamins in cystic fibrosis and pancreatic insufficiency: efficacy of a nutrition intervention.
    Journal of pediatric gastroenterology and nutrition, 2014, Volume: 58, Issue:4

    Topics: Adolescent; alpha-Tocopherol; Child; Child, Preschool; Cystic Fibrosis; Diet Records; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Humans; Lipids; Male; Surveys and Questionnaires; Vitamin A; Vitamin D; Vitamin K

2014
Supplementation with red palm oil increases β-carotene and vitamin A blood levels in patients with cystic fibrosis.
    Mediators of inflammation, 2015, Volume: 2015

    Topics: Adolescent; Adult; beta Carotene; Carotenoids; Child; Cystic Fibrosis; Dietary Supplements; Female; Humans; Lycopene; Male; Palm Oil; Plant Oils; Vitamin A; Young Adult

2015
A randomized placebo-controlled study on high-dose oral algal docosahexaenoic acid supplementation in children with cystic fibrosis.
    Prostaglandins, leukotrienes, and essential fatty acids, 2013, Volume: 88, Issue:2

    Topics: Administration, Oral; alpha-Tocopherol; Body Composition; Bone Density; C-Reactive Protein; Child; Cystic Fibrosis; Docosahexaenoic Acids; Female; Humans; Interleukin-8; Male; Tumor Necrosis Factor-alpha; Vitamin A

2013
Effect of an organized lipid matrix on lipid absorption and clinical outcomes in patients with cystic fibrosis.
    The Journal of pediatrics, 2002, Volume: 141, Issue:2

    Topics: Adolescent; Adult; Anthropometry; Area Under Curve; beta Carotene; Canada; Child; Child Welfare; Cystic Fibrosis; Dietary Fats; Diterpenes; Double-Blind Method; Eicosanoids; Energy Intake; Fatty Acids; Female; Follow-Up Studies; Forced Expiratory Volume; Humans; Intestinal Absorption; Liver; Male; Malondialdehyde; Patient Compliance; Retinol-Binding Proteins; Retinyl Esters; Time Factors; Treatment Outcome; Triglycerides; Vitamin A; Vitamins

2002
Improved antioxidant and fatty acid status of patients with cystic fibrosis after antioxidant supplementation is linked to improved lung function.
    The American journal of clinical nutrition, 2003, Volume: 77, Issue:1

    Topics: Antioxidants; Ascorbic Acid; Child; Cystic Fibrosis; Diet Records; Dinoprostone; Double-Blind Method; Fatty Acids; Female; Humans; Isoprostanes; Male; Oxidative Stress; Respiratory Function Tests; Selenomethionine; Vitamin A; Vitamin E

2003
Retinol binding protein status in relation to ocular surface changes in patients with cystic fibrosis treated with daily vitamin A supplements.
    European journal of pediatrics, 2005, Volume: 164, Issue:4

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Female; Humans; Lung Volume Measurements; Male; Nutritional Status; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Vitamin A; Xerophthalmia

2005
Ursodeoxycholic acid improves the hepatic metabolism of essential fatty acids and retinol in children with cystic fibrosis.
    The Journal of pediatrics, 1997, Volume: 130, Issue:1

    Topics: Adolescent; Child; Cholagogues and Choleretics; Cross-Over Studies; Cystic Fibrosis; Double-Blind Method; Fatty Acids, Essential; Female; Humans; Lipid Metabolism; Liver; Liver Function Tests; Male; Ursodeoxycholic Acid; Vitamin A; Vitamins

1997
Effects of long-term oral beta-carotene supplementation on lipid peroxidation in patients with cystic fibrosis.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1998, Volume: 68, Issue:2

    Topics: Adolescent; Antioxidants; Ascorbic Acid; beta Carotene; Carotenoids; Child; Cystic Fibrosis; Humans; Lipid Peroxidation; Lycopene; Malondialdehyde; Vitamin A; Vitamin E

1998
Absorption of vitamin A in patients with cystic fibrosis. Absorption is best with emulsified vitamin A alcohol.
    Clinical pediatrics, 1976, Volume: 15, Issue:9

    Topics: Adolescent; Adult; Child; Child, Preschool; Clinical Trials as Topic; Cystic Fibrosis; Emulsions; Ethanol; Female; Humans; Infant; Intestinal Absorption; Male; Palmitates; Vitamin A; Vitamin A Deficiency

1976
Taurine decreases fecal fatty acid and sterol excretion in cystic fibrosis. A randomized double-blind trial.
    American journal of diseases of children (1960), 1991, Volume: 145, Issue:12

    Topics: Adolescent; Adult; Body Height; Body Weight; Celiac Disease; Child; Cystic Fibrosis; Double-Blind Method; Fatty Acids; Feces; Female; Forced Expiratory Flow Rates; Humans; Male; Nutritional Status; Sterols; Taurine; Vital Capacity; Vitamin A

1991

Other Studies

91 other study(ies) available for retinol and Cystic Fibrosis

ArticleYear
Might Routine Vitamin A Monitoring in Cystic Fibrosis Patients Reduce Virus-Mediated Lung Pathology?
    Frontiers in immunology, 2021, Volume: 12

    Topics: Animals; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Dietary Supplements; Disease Models, Animal; Fatty Acid-Binding Proteins; Humans; Lung; Mice; Mice, Inbred CFTR; Mice, Transgenic; Promoter Regions, Genetic; Respirovirus Infections; Sendai virus; Vitamin A

2021
Vitamins A, D, E status as related to supplementation and lung disease markers in young children with cystic fibrosis.
    Pediatric pulmonology, 2022, Volume: 57, Issue:4

    Topics: alpha-Tocopherol; Child; Child, Preschool; Cystic Fibrosis; Dietary Supplements; Humans; Infant; Infant, Newborn; Interleukin-10; Interleukin-8; Vitamin A; Vitamin D; Vitamin E; Vitamins

2022
Vitamin Status in Children with Cystic Fibrosis Transmembrane Conductance Regulator Gene Mutation.
    Nutrients, 2022, Nov-04, Volume: 14, Issue:21

    Topics: Child, Preschool; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Humans; Male; Mutation; Neonatal Screening; Vitamin A; Vitamin D; Vitamins

2022
[How I treat … vitamin D intoxication in a child with cystic fibrosis].
    Revue medicale de Liege, 2023, Volume: 78, Issue:4

    Topics: Calcium; Child; Cystic Fibrosis; Humans; Vitamin A; Vitamin D; Vitamins

2023
Impact of elexacaftor/tezacaftor/ivacaftor on fat-soluble vitamin levels in children with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2023, Volume: 22, Issue:5

    Topics: Aminophenols; Benzodioxoles; Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Mutation; Vitamin A; Vitamins

2023
The impact of elexacaftor/tezacaftor/ivacaftor on fat-soluble vitamin levels in people with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2023, Volume: 22, Issue:6

    Topics: Aminophenols; Benzodioxoles; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Mutation; Retrospective Studies; Vitamin A; Vitamin D; Vitamin E; Vitamins

2023
Night Blindness in Cystic Fibrosis: The Key Role of Vitamin A in the Digestive System.
    Nutrients, 2019, Aug-13, Volume: 11, Issue:8

    Topics: Child; Cystic Fibrosis; Dietary Supplements; Female; Humans; Intestinal Absorption; Night Blindness; Night Vision; Nutritional Status; Parenteral Nutrition, Home; Recurrence; Short Bowel Syndrome; Treatment Outcome; Vitamin A; Vitamin A Deficiency

2019
Motor repertoire is age-inadequate in infants with cystic fibrosis.
    Pediatric research, 2021, Volume: 89, Issue:5

    Topics: Age Factors; Case-Control Studies; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Genetic Association Studies; Genotype; Hospitalization; Humans; Infant; Male; Motor Skills; Movement; Mutation; Phenotype; Severity of Illness Index; Video Recording; Vitamin A

2021
High serum retinol and lung function in young patients with cystic fibrosis.
    Journal of pediatric gastroenterology and nutrition, 2013, Volume: 56, Issue:6

    Topics: Adolescent; Adult; Antioxidants; Body Mass Index; Child; Cohort Studies; Cross-Sectional Studies; Cystic Fibrosis; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Forced Expiratory Volume; Humans; Lung; Male; Odds Ratio; Oxidative Stress; Prospective Studies; Thinness; Up-Regulation; Vitamin A; Young Adult

2013
Bone turnover markers, osteoprotegerin and RANKL cytokines in children with cystic fibrosis.
    Advances in medical sciences, 2013, Volume: 58, Issue:2

    Topics: Acid Phosphatase; Biomarkers; Bone Density; Bone Resorption; Calcium; Child; Child, Preschool; Collagen Type I; Cystic Fibrosis; Female; Humans; Isoenzymes; Male; Osteocalcin; Osteoprotegerin; Peptides; Phosphates; RANK Ligand; Tartrate-Resistant Acid Phosphatase; Vitamin A; Vitamin E

2013
Evaluation of micronutrient profile of North Indian children with cystic fibrosis: a case-control study.
    Pediatric research, 2014, Volume: 75, Issue:6

    Topics: Avitaminosis; Case-Control Studies; Child; Child Nutritional Physiological Phenomena; Child, Preschool; Chromatography, High Pressure Liquid; Copper; Cystic Fibrosis; Humans; India; Infant; Iron; Micronutrients; Nutritional Status; Spectrophotometry, Atomic; Vitamin A; Vitamin D; Vitamin E; Zinc

2014
Fat-soluble vitamin deficiency in children and adolescents with cystic fibrosis.
    Journal of clinical pathology, 2014, Volume: 67, Issue:7

    Topics: Adolescent; Age Factors; Avitaminosis; Biomarkers; Child; Child, Preschool; Cystic Fibrosis; Exocrine Pancreatic Insufficiency; Female; Humans; Male; New South Wales; Prevalence; Prothrombin Time; Retrospective Studies; Solubility; Vitamin A; Vitamin A Deficiency; Vitamin D; Vitamin D Deficiency; Vitamin E; Vitamin E Deficiency; Vitamin K; Vitamin K Deficiency; Vitamins

2014
Capillary electromigration techniques as tools for assessing the status of vitamins A, C and E in patients with cystic fibrosis.
    Journal of pharmaceutical and biomedical analysis, 2015, Volume: 102

    Topics: Adolescent; Ascorbic Acid; Case-Control Studies; Child; Child, Preschool; Chromatography, Micellar Electrokinetic Capillary; Cystic Fibrosis; Female; Humans; Infant; Male; Nutritional Status; Vitamin A; Vitamin E

2015
Serum retinol levels and pulmonary function in children and adolescents with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2015, Volume: 14, Issue:3

    Topics: Adolescent; Biomarkers; Child; Cross-Sectional Studies; Cystic Fibrosis; Female; Follow-Up Studies; Forced Expiratory Volume; Humans; Lung; Male; Respiratory Function Tests; Retrospective Studies; Vitamin A

2015
Vitamin A intake and serum retinol levels in children and adolescents with cystic fibrosis.
    Clinical nutrition (Edinburgh, Scotland), 2016, Volume: 35, Issue:3

    Topics: Adolescent; Adolescent Development; Adolescent Nutritional Physiological Phenomena; Child; Child Development; Child Nutritional Physiological Phenomena; Child, Preschool; Cohort Studies; Cross-Sectional Studies; Cystic Fibrosis; Dietary Supplements; Follow-Up Studies; Humans; Incidence; Intestinal Absorption; Malabsorption Syndromes; Netherlands; Nutrition Assessment; Patient Compliance; Retrospective Studies; Vitamin A; Vitamin A Deficiency

2016
Serum retinol and pulmonary function in young people with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2016, Volume: 15, Issue:2

    Topics: Cystic Fibrosis; Female; Forced Expiratory Volume; Humans; Lung; Male; Up-Regulation; Vitamin A

2016
Serum retinol levels and pulmonary function in children and adolescents with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2016, Volume: 15, Issue:2

    Topics: Cystic Fibrosis; Female; Forced Expiratory Volume; Humans; Lung; Male; Vitamin A

2016
Treatment of cystic fibrosis in low-income countries.
    The Lancet. Respiratory medicine, 2016, Volume: 4, Issue:2

    Topics: Anti-Bacterial Agents; Carrier State; Chest Wall Oscillation; Cystic Fibrosis; Delivery of Health Care; Developing Countries; Enzyme Replacement Therapy; Humans; Patient Compliance; Pseudomonas Infections; Respiratory Therapy; Vitamin A; Vitamin D; Vitamin E; Vitamins

2016
Bone Mineral Density and Fat-Soluble Vitamin Status in Adults with Cystic Fibrosis Undergoing Lung Transplantation: A Pilot Study.
    Canadian journal of dietetic practice and research : a publication of Dietitians of Canada = Revue canadienne de la pratique et de la recherche en dietetique : une publication des Dietetistes du Canada, 2016, Volume: 77, Issue:4

    Topics: Adult; Anthropometry; Biomarkers; Bone Density; Cystic Fibrosis; Female; Humans; Lumbar Vertebrae; Lung Diseases; Lung Transplantation; Male; Middle Aged; Osteoporosis; Parathyroid Hormone; Pilot Projects; Protein Precursors; Prothrombin; Vitamin A; Vitamin D; Vitamin E; Vitamin K; Vitamins; Young Adult

2016
A comparison of vitamin A absorption in normal children and children with cystic fibrosis of the pancreas using oily and water soluble preparation.
    University Hospital bulletin, 1947, Volume: 13, Issue:11

    Topics: Child; Cystic Fibrosis; Cysts; Dermatitis, Seborrheic; Humans; Pancreas; Pancreatic Cyst; Vitamin A; Vitamins; Water

1947
Glutathione S-transferases related to P. aeruginosa lung infection in cystic fibrosis children: preliminary study.
    Clinical biochemistry, 2009, Volume: 42, Issue:1-2

    Topics: Adolescent; Ascorbic Acid; Child; Child, Preschool; Chromatography, High Pressure Liquid; Cystic Fibrosis; Erythrocytes; Female; Genotype; Glutathione; Glutathione Transferase; Humans; Male; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Pseudomonas aeruginosa; Pseudomonas Infections; Vitamin A; Vitamin E; Young Adult

2009
ERGs in children with pancreatic enzyme insufficient and pancreatic enzyme sufficient cystic fibrosis.
    Documenta ophthalmologica. Advances in ophthalmology, 2009, Volume: 119, Issue:1

    Topics: Adolescent; beta Carotene; Child; Child, Preschool; Cystic Fibrosis; Electroretinography; Enzymes; Female; Humans; Male; Pancreas; Retina; Retinol-Binding Proteins; Vitamin A

2009
The absorption of different forms of vitamin A in cystic fibrosis of the pancreas.
    Rocky Mountain medical journal, 1947, Volume: 44, Issue:8

    Topics: Cystic Fibrosis; Cysts; Humans; Pancreas; Pancreatic Cyst; Vitamin A; Vitamins

1947
Voriconazole inhibition of vitamin A metabolism: are adverse events increased in cystic fibrosis patients?
    Pediatric pulmonology, 2010, Volume: 45, Issue:7

    Topics: Adolescent; Antifungal Agents; Child; Cohort Studies; Cystic Fibrosis; Dietary Supplements; Female; Humans; Male; Photosensitivity Disorders; Pulmonary Aspergillosis; Pyrimidines; Retrospective Studies; Treatment Outcome; Triazoles; Vision Disorders; Vitamin A; Voriconazole

2010
Absorption of vitamin A following enteral use of prostigmine in cystic fibrosis of pancreas.
    American journal of clinical pathology, 1946, Volume: 16

    Topics: Cystic Fibrosis; Humans; Neostigmine; Pancreas; Vitamin A; Vitamins

1946
Increased serum vitamin A and E levels after lung transplantation.
    Transplantation, 2011, Sep-15, Volume: 92, Issue:5

    Topics: Adult; Cystic Fibrosis; Female; Humans; Lung Transplantation; Male; Middle Aged; Respiratory Insufficiency; Risk Factors; Vitamin A; Vitamin E

2011
Night blindness in a teenager with cystic fibrosis.
    Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition, 2011, Volume: 26, Issue:6

    Topics: Adolescent; Cystic Fibrosis; Dietary Supplements; Humans; Male; Night Blindness; Treatment Outcome; Vitamin A; Vitamin A Deficiency

2011
Individualized vitamin A supplementation for patients with cystic fibrosis.
    Clinical nutrition (Edinburgh, Scotland), 2013, Volume: 32, Issue:5

    Topics: Adolescent; Adult; Airway Obstruction; Child; Child, Preschool; Cohort Studies; Cystic Fibrosis; Diet; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Germany; Humans; Hypervitaminosis A; Lung; Male; Pancreas, Exocrine; Precision Medicine; Recommended Dietary Allowances; Severity of Illness Index; Vitamin A; Vitamin A Deficiency; Young Adult

2013
Essential fatty acid deficiency and nutritional supplementation in cystic fibrosis.
    The Journal of pediatrics, 2002, Volume: 141, Issue:2

    Topics: beta Carotene; Cystic Fibrosis; Dietary Fats; Dietary Supplements; Diterpenes; Eicosanoids; Energy Intake; Fatty Acids, Essential; Forced Expiratory Volume; Humans; Intestinal Absorption; Malondialdehyde; Retinol-Binding Proteins; Retinyl Esters; Triglycerides; Vitamin A; Vitamins

2002
Faecal elastase-1 and fat-soluble vitamin profiles in patients with cystic fibrosis in Western Norway.
    European journal of nutrition, 2002, Volume: 41, Issue:4

    Topics: Adolescent; Adult; Calcifediol; Child; Child, Preschool; Cystic Fibrosis; Dietary Supplements; Feces; Female; Humans; Malabsorption Syndromes; Male; Norway; Pancreas; Pancreatic Elastase; Reference Values; Solubility; Vitamin A; Vitamin E; Vitamins

2002
Are annual blood tests in preschool cystic fibrosis patients worthwhile?
    Archives of disease in childhood, 2002, Volume: 87, Issue:6

    Topics: Child, Preschool; Cystic Fibrosis; Female; Glucose; Humans; Infant; Iron; Male; Retrospective Studies; Vitamin A; Vitamin E

2002
[Severe adult mucoviscidosis with protein diarrhea].
    Medizinische Klinik, 1962, Nov-02, Volume: 57

    Topics: Cystic Fibrosis; Diarrhea; Diet; Diet Therapy; Humans; Metabolic Diseases; Pancreatic Juice; Proteins; Vitamin A; Vitamin K; Vitamins

1962
ASSESSMENT OF THREE METHODS FOR MEASURING INTESTINAL FAT ABSORPTION IN INFANTS AND CHILDREN.
    Pediatrics, 1964, Volume: 34

    Topics: Arthritis; Arthritis, Rheumatoid; Butter; Child; Congenital Abnormalities; Cystic Fibrosis; Dietary Fats; Feces; Giardiasis; Glutens; Humans; Infant; Intestinal Absorption; Intestines; Iodine Isotopes; Lipid Metabolism; Lipids; Radiometry; Spectrophotometry; Triolein; Vitamin A

1964
Energy expenditure, nutrition status, and body composition in children with cystic fibrosis.
    Nutrition (Burbank, Los Angeles County, Calif.), 2004, Volume: 20, Issue:2

    Topics: Adolescent; Anthropometry; Basal Metabolism; Body Composition; Calorimetry, Indirect; Case-Control Studies; Child; Child, Preschool; Cystic Fibrosis; Energy Intake; Energy Metabolism; Exercise; Female; Humans; Male; Mental Recall; Micronutrients; Nutritional Requirements; Nutritional Status; Tocopherols; Vitamin A

2004
Vitamin A levels in patients with CF are influenced by the inflammatory response.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2004, Volume: 3, Issue:3

    Topics: Adolescent; Adult; Age Factors; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Inflammation; Male; Middle Aged; Severity of Illness Index; Vitamin A

2004
Increased vitamin A and E levels in adult cystic fibrosis patients after lung transplantation.
    Transplantation, 2005, Mar-15, Volume: 79, Issue:5

    Topics: Adult; Cystic Fibrosis; Female; Humans; Lung Transplantation; Male; Retinol-Binding Proteins; Vitamin A; Vitamin E

2005
Advanced keratomalacia with descemetocele in an infant with cystic fibrosis.
    Archives of ophthalmology (Chicago, Ill. : 1960), 2005, Volume: 123, Issue:7

    Topics: Corneal Diseases; Cystic Fibrosis; Descemet Membrane; Diterpenes; Female; Hernia; Humans; Infant; Keratoplasty, Penetrating; Retinyl Esters; Vitamin A; Xerophthalmia

2005
Preventing early, prolonged vitamin E deficiency: an opportunity for better cognitive outcomes via early diagnosis through neonatal screening.
    The Journal of pediatrics, 2005, Volume: 147, Issue:3 Suppl

    Topics: Adolescent; Age Factors; alpha-Tocopherol; Analysis of Variance; Case-Control Studies; Child; Child Nutrition Disorders; Child, Preschool; Cognition Disorders; Cystic Fibrosis; Early Diagnosis; Humans; Infant; Infant, Newborn; Neonatal Screening; Randomized Controlled Trials as Topic; Risk Factors; Severity of Illness Index; Vitamin A; Vitamin E Deficiency; Wisconsin

2005
Vitamin A and E deficiency and lung disease in infants with cystic fibrosis.
    Journal of paediatrics and child health, 2005, Volume: 41, Issue:12

    Topics: alpha-Tocopherol; Cross-Sectional Studies; Cystic Fibrosis; Energy Intake; Female; Humans; Infant; Infant, Newborn; Lung Diseases; Male; Neonatal Screening; Vitamin A; Vitamin A Deficiency; Vitamin E Deficiency

2005
Vitamin A and lung function in CF.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2006, Volume: 5, Issue:2

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Dietary Supplements; Female; Humans; Male; Respiration; Respiratory Function Tests; Vitamin A; Vitamin D; Vitamin E

2006
Elevated vitamin A intake and serum retinol in preadolescent children with cystic fibrosis.
    The American journal of clinical nutrition, 2006, Volume: 84, Issue:1

    Topics: Child; Child Nutritional Physiological Phenomena; Cross-Sectional Studies; Cystic Fibrosis; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Humans; Male; Nutrition Policy; Nutrition Surveys; United States; Vitamin A; Vitamin A Deficiency; Vitamins

2006
Cystic fibrosis presenting with bilateral facial palsy.
    European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society, 2007, Volume: 11, Issue:4

    Topics: Cystic Fibrosis; Dietary Supplements; Facial Paralysis; Humans; Infant; Male; Vitamin A; Vitamin A Deficiency

2007
Vitamin A intake and elevated serum retinol levels in children and young adults with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2008, Volume: 7, Issue:2

    Topics: Administration, Oral; Adolescent; Adult; Child; Chromatography, High Pressure Liquid; Cystic Fibrosis; Dietary Supplements; Dose-Response Relationship, Drug; Exocrine Pancreatic Insufficiency; Female; Follow-Up Studies; Humans; Male; Treatment Outcome; Vitamin A; Vitamins

2008
Vitamins A and E and pulmonary exacerbations in patients with cystic fibrosis.
    Journal of pediatric gastroenterology and nutrition, 2007, Volume: 45, Issue:3

    Topics: Adolescent; Adult; Antioxidants; Biomarkers; Child; Child, Preschool; Cystic Fibrosis; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Humans; Infant; Lung Diseases; Male; Nutritional Status; Oxidation-Reduction; Oxidative Stress; Respiratory Function Tests; Retrospective Studies; Vitamin A; Vitamin E

2007
Compounding of vitamin A, D3, E and K3 supplements for cystic fibrosis patients: formulation and stability study.
    Journal of clinical pharmacy and therapeutics, 2007, Volume: 32, Issue:5

    Topics: Capsules; Cholecalciferol; Chromatography, High Pressure Liquid; Cystic Fibrosis; Drug Combinations; Drug Compounding; Drug Stability; Drug Storage; Humans; Spectrophotometry; Taste; Vitamin A; Vitamin E; Vitamin K 3; Vitamins

2007
Effect of diet during pregnancy upon the incidence of congenital hereditary diaphragmatic hernia in the rat; failure to produce cystic fibrosis of the pancreas by maternal vitamin A deficiency.
    The American journal of pathology, 1949, Volume: 25, Issue:1

    Topics: Animals; Congenital Abnormalities; Cystic Fibrosis; Diet; Female; Hernia, Diaphragmatic; Hernias, Diaphragmatic, Congenital; Incidence; Pregnancy; Rats; Vitamin A; Vitamin A Deficiency

1949
Vitamin A, vitamin E, and lipids in serum of children with cystic fibrosis or congenital heart defects compared with normal children.
    The American journal of clinical nutrition, 1967, Volume: 20, Issue:5

    Topics: Child; Cholesterol; Cystic Fibrosis; Fatty Acids; Heart Defects, Congenital; Humans; Vitamin A; Vitamin E

1967
Scotopic thresholds and plasma retinol in cystic fibrosis.
    Investigative ophthalmology & visual science, 1982, Volume: 23, Issue:3

    Topics: Adolescent; Adult; Child; Child, Preschool; Cystic Fibrosis; Dark Adaptation; Humans; Psychophysiology; Rhodopsin; Vision, Ocular; Vitamin A

1982
Depressed plasma Vitamin A and retinol-binding protein in cystic fibrosis correlations with zinc deficiency.
    The American journal of clinical nutrition, 1981, Volume: 34, Issue:7

    Topics: Adolescent; Child; Child, Preschool; Cystic Fibrosis; Humans; Infant; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Vitamin A; Zinc

1981
Vitamin status in treated patients with cystic fibrosis.
    Archives of disease in childhood, 1981, Volume: 56, Issue:9

    Topics: Adolescent; Ascorbic Acid; Child; Child, Preschool; Cystic Fibrosis; Female; Folic Acid; Humans; Infant; Male; Riboflavin; Vitamin A; Vitamin B Complex; Vitamin D; Vitamin E; Vitamins

1981
Nutritional status and the immune system: fat-soluble vitamins and other nutrients.
    Bibliotheca nutritio et dieta, 1994, Issue:51

    Topics: Adolescent; Adult; Antioxidants; beta Carotene; Carotenoids; Child; Child, Preschool; Cystic Fibrosis; Humans; Infant; Nutritional Status; Solubility; Vitamin A

1994
Altered antioxidant status and increased lipid peroxidation in children with cystic fibrosis.
    The American journal of clinical nutrition, 1995, Volume: 61, Issue:4

    Topics: Adolescent; Adult; beta Carotene; Carotenoids; Child; Cholesterol; Cystic Fibrosis; Fatty Acids, Unsaturated; Female; Glutathione Peroxidase; Humans; Lipid Metabolism; Lipid Peroxidation; Malabsorption Syndromes; Male; Oxidative Stress; Reactive Oxygen Species; Selenium; Superoxide Dismutase; Thiobarbituric Acid Reactive Substances; Vitamin A; Vitamin E; Vitamins; Zinc

1995
[Determination of plasma retinol and alpha-tocopherol by HPLC].
    Annales de biologie clinique, 1994, Volume: 52, Issue:7-8

    Topics: Adolescent; Adult; Child; Child, Preschool; Chromatography, High Pressure Liquid; Cystic Fibrosis; Humans; Infant; Infant, Newborn; Vitamin A; Vitamin E

1994
Preventive care for patients with chronic illness. Multivitamin use in patients with cystic fibrosis.
    Clinical pediatrics, 1994, Volume: 33, Issue:12

    Topics: Child; Child, Preschool; Cystic Fibrosis; Humans; Patient Compliance; Surveys and Questionnaires; Vitamin A; Vitamin E; Vitamins

1994
Increased neutrophil chemiluminescence production in patients with cystic fibrosis.
    Metabolism: clinical and experimental, 1994, Volume: 43, Issue:6

    Topics: Adolescent; Child; Child, Preschool; Cystic Fibrosis; Humans; Hydrogen Peroxide; Luminescent Measurements; Neutrophils; Reactive Oxygen Species; Superoxides; Tetradecanoylphorbol Acetate; Vitamin A; Vitamin E

1994
Response to oral beta-carotene supplementation in patients with cystic fibrosis: a 16-month follow-up study.
    Acta paediatrica (Oslo, Norway : 1992), 1995, Volume: 84, Issue:10

    Topics: Adjuvants, Immunologic; Adolescent; Antioxidants; beta Carotene; Carotenoids; Child; Cholesterol; Cystic Fibrosis; Diterpenes; Female; Follow-Up Studies; Food, Fortified; Humans; Male; Regression Analysis; Retinyl Esters; Statistics, Nonparametric; Vitamin A; Vitamin E

1995
Ocular findings in cystic fibrosis patients receiving vitamin A supplementation.
    Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie, 1995, Volume: 233, Issue:11

    Topics: Adolescent; Adult; Color Vision Defects; Conjunctiva; Contrast Sensitivity; Cystic Fibrosis; Dark Adaptation; Female; Humans; Incidence; Keratoconjunctivitis Sicca; Male; Night Blindness; Vitamin A; Vitamin A Deficiency; Xerophthalmia

1995
Deficiency of vitamins E and A in cystic fibrosis is independent of pancreatic function and current enzyme and vitamin supplementation.
    European journal of pediatrics, 1996, Volume: 155, Issue:4

    Topics: Adolescent; Adult; Child; Child, Preschool; Combined Modality Therapy; Cystic Fibrosis; Dose-Response Relationship, Drug; Drug Administration Schedule; Exocrine Pancreatic Insufficiency; Female; Humans; Infant; Male; Pancreatic Extracts; Vitamin A; Vitamin A Deficiency; Vitamin E; Vitamin E Deficiency

1996
Annual review or continuous assessment?
    Journal of the Royal Society of Medicine, 1996, Volume: 89 Suppl 27

    Topics: Bacterial Infections; Child; Cystic Fibrosis; Forced Expiratory Volume; Hematologic Diseases; Humans; Liver Diseases; Lung Diseases; Lung Diseases, Fungal; Nutritional Status; Physical Therapy Modalities; Vital Capacity; Vitamin A

1996
Vitamin A status in acute exacerbations of cystic fibrosis.
    The American journal of clinical nutrition, 1996, Volume: 64, Issue:4

    Topics: Acute Disease; Adult; C-Reactive Protein; Cohort Studies; Cystic Fibrosis; Female; Humans; Lung Diseases; Male; Nutritional Status; Prospective Studies; Regression Analysis; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Vitamin A

1996
Vitamin A concentration in the liver decreases with age in patients with cystic fibrosis.
    Journal of pediatric gastroenterology and nutrition, 1997, Volume: 24, Issue:3

    Topics: Adolescent; Adult; Aging; Biopsy; Child; Cystic Fibrosis; Diterpenes; Female; Humans; Liver; Male; Reference Values; Retinol-Binding Proteins; Retinyl Esters; Vitamin A

1997
Vitamin A deficiency and nocturnal vision in teenagers with cystic fibrosis.
    European journal of pediatrics, 1997, Volume: 156, Issue:12

    Topics: Adaptation, Physiological; Adolescent; Child; Cystic Fibrosis; Darkness; Humans; Linear Models; Prospective Studies; Vision, Ocular; Vitamin A; Vitamin A Deficiency

1997
Ocular signs and symptoms and vitamin A status in patients with cystic fibrosis treated with daily vitamin A supplements.
    The British journal of ophthalmology, 1999, Volume: 83, Issue:6

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Dark Adaptation; Dietary Supplements; Female; Humans; Male; Vitamin A; Vitamin A Deficiency

1999
Elevated plasma levels of F2 alpha isoprostane in cystic fibrosis.
    Lipids, 1999, Volume: 34, Issue:6

    Topics: Adolescent; Adult; Aged; beta Carotene; Case-Control Studies; Child; Cross-Sectional Studies; Cystic Fibrosis; Dinoprost; Erythrocyte Membrane; F2-Isoprostanes; Fatty Acids; Humans; Middle Aged; Vitamin A; Vitamin E

1999
Prospective, long-term study of fat-soluble vitamin status in children with cystic fibrosis identified by newborn screen.
    The Journal of pediatrics, 1999, Volume: 135, Issue:5

    Topics: Child; Child, Preschool; Cystic Fibrosis; Follow-Up Studies; Gastrointestinal Agents; Humans; Infant; Infant, Newborn; Neonatal Screening; Pancrelipase; Prospective Studies; Time Factors; Vitamin A; Vitamin A Deficiency; Vitamin D; Vitamin D Deficiency; Vitamin E; Vitamin E Deficiency; Vitamins

1999
Longitudinal analysis shows serum carotenoid concentrations are low in children with cystic fibrosis.
    Journal of the American Dietetic Association, 1999, Volume: 99, Issue:12

    Topics: beta Carotene; Carotenoids; Child; Chromatography, High Pressure Liquid; Cryptoxanthins; Cystic Fibrosis; Dietary Fats; Exocrine Pancreatic Insufficiency; Female; Humans; Longitudinal Studies; Lutein; Lycopene; Male; Prospective Studies; Vitamin A; Xanthophylls

1999
Acute sixth nerve palsy in vitamin A treatment of xerophthalmia.
    The British journal of ophthalmology, 2000, Volume: 84, Issue:8

    Topics: Abducens Nerve Diseases; Cystic Fibrosis; Humans; Infant; Male; Treatment Outcome; Vitamin A; Vitamin A Deficiency; Xerophthalmia

2000
Antioxidant status in patients with cystic fibrosis.
    Annals of nutrition & metabolism, 2000, Volume: 44, Issue:5-6

    Topics: Antioxidants; Ascorbic Acid; Catalase; Child; Cystic Fibrosis; Female; Glutathione Peroxidase; Humans; Lipid Peroxidation; Male; Malondialdehyde; Nutritional Status; Superoxide Dismutase; Vitamin A; Vitamin E

2000
Role of electroretinography in the assessment of retinal function as an indicator of vitamin A status.
    Documenta ophthalmologica. Advances in ophthalmology, 2000, Volume: 101, Issue:3

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Dietary Supplements; Electroretinography; Female; Humans; Male; Retina; Vitamin A; Vitamin A Deficiency; Zinc

2000
Zinc status and vitamin A transport in cystic fibrosis.
    The American journal of clinical nutrition, 1978, Volume: 31, Issue:4

    Topics: Adolescent; Child; Cystic Fibrosis; Hair; Humans; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Serum Albumin; Vitamin A; Zinc

1978
The effect of oral zinc supplementation on plasma levels of vitamin A and retinol-binding protein in cystic fibrosis.
    The American journal of clinical nutrition, 1979, Volume: 32, Issue:6

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Diet; Growth; Hair; Humans; Placebos; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Taste; Time Factors; Vitamin A; Zinc

1979
The effect of supplemental vitamin E on vitamin A serum levels in cystic fibrosis.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1978, Volume: 48, Issue:4

    Topics: Adolescent; Child; Child, Preschool; Creatine; Creatinine; Cystic Fibrosis; Drug Therapy, Combination; Female; Humans; Male; Vitamin A; Vitamin E

1978
Bulging fontanelle as presenting sign in cystic fibrosis. Vitamin A metabolism and effect on cerebrospinal fluid pressure.
    American journal of diseases of children (1960), 1976, Volume: 130, Issue:12

    Topics: Child, Preschool; Cystic Fibrosis; Diagnosis, Differential; Humans; Intracranial Pressure; Malabsorption Syndromes; Male; Skull; Vitamin A; Vitamin A Deficiency

1976
[Serum concentrations of vitamin A, carotene, retinol-binding protein and prealbumin in patients with cystic fibrosis (author's transl)].
    Zeitschrift fur Kinderheilkunde, 1975, Volume: 119, Issue:4

    Topics: Adolescent; Adult; Age Factors; Blood Proteins; Carotenoids; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Infant, Newborn; Male; Prealbumin; Protein Binding; Serum Albumin; Vitamin A

1975
Electro-oculogram in vitamin A deficiency associated with cystic fibrosis. Short communication.
    Ophthalmic paediatrics and genetics, 1992, Volume: 13, Issue:3

    Topics: Adolescent; Cystic Fibrosis; Dark Adaptation; Electrooculography; Humans; Light; Male; Photoreceptor Cells; Visual Acuity; Vitamin A; Vitamin A Deficiency

1992
Vitamin A absorption in cystic fibrosis: risk of hypervitaminosis A.
    Gut, 1992, Volume: 33, Issue:5

    Topics: Adolescent; Adult; Carotenoids; Cystic Fibrosis; Female; Humans; Hypervitaminosis A; Intestinal Absorption; Male; Retinol-Binding Proteins; Retinol-Binding Proteins, Plasma; Risk Factors; Vitamin A

1992
Loss of contrast sensitivity in cystic fibrosis.
    American journal of ophthalmology, 1991, Apr-15, Volume: 111, Issue:4

    Topics: Adolescent; Contrast Sensitivity; Cystic Fibrosis; Humans; Male; Retinal Diseases; Vitamin A; Vitamin A Deficiency

1991
Xerophthalmia and cystic fibrosis.
    Archives of ophthalmology (Chicago, Ill. : 1960), 1990, Volume: 108, Issue:3

    Topics: Cystic Fibrosis; Diterpenes; Female; Humans; Infant; Malabsorption Syndromes; Male; Retinyl Esters; Vitamin A; Vitamin A Deficiency; Xerophthalmia

1990
Excessive faecal losses of vitamin A (retinol) in cystic fibrosis.
    Archives of disease in childhood, 1990, Volume: 65, Issue:6

    Topics: Adolescent; Adult; Child; Chromatography, High Pressure Liquid; Cystic Fibrosis; Dietary Fats; Feces; Female; Humans; Intestinal Absorption; Lipid Metabolism; Male; Vitamin A

1990
Nyctalopia and conjunctival xerosis indicating vitamin A deficiency in cystic fibrosis.
    Eye (London, England), 1989, Volume: 3 ( Pt 3)

    Topics: Adolescent; Adult; Chi-Square Distribution; Child; Conjunctival Diseases; Cystic Fibrosis; Dark Adaptation; Humans; Ichthyosis; Liver Function Tests; Night Blindness; Vitamin A; Vitamin A Deficiency

1989
Night blindness and conjunctival xerosis caused by vitamin A deficiency in patients with cystic fibrosis.
    Archives of disease in childhood, 1989, Volume: 64, Issue:8

    Topics: Adolescent; Child; Cystic Fibrosis; Female; Humans; Male; Night Blindness; Retinol-Binding Proteins; Vitamin A; Vitamin A Deficiency; Vitamin E; Xerophthalmia

1989
Fat-soluble-vitamin status during the first year of life in infants with cystic fibrosis identified by screening of newborns.
    The American journal of clinical nutrition, 1989, Volume: 50, Issue:5

    Topics: Child, Preschool; Cystic Fibrosis; Female; Humans; Hydroxycholecalciferols; Infant; Infant Nutrition Disorders; Infant, Newborn; Lipids; Male; Neonatal Screening; Nutritional Status; Solubility; Vitamin A; Vitamin E; Vitamin K; Vitamins

1989
Status of plasma and erythrocyte fatty acids and vitamin A and E in young children with cystic fibrosis.
    Scandinavian journal of gastroenterology. Supplement, 1988, Volume: 143

    Topics: Child; Child, Preschool; Cystic Fibrosis; Erythrocytes; Fatty Acids; Humans; Phospholipids; Vitamin A; Vitamin E

1988
Vitamin A, provitamin A and vitamin E serum concentrations in cystic fibrosis patients.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1988, Volume: 58, Issue:3

    Topics: Adolescent; Adult; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Vitamin A; Vitamin E

1988
Practical management of nutrition and gastrointestinal tract in cystic fibrosis.
    Journal of the Royal Society of Medicine, 1986, Volume: 79 Suppl 12

    Topics: Adolescent; Adult; Child; Child, Preschool; Cystic Fibrosis; Diabetes Mellitus; Diet; Humans; Infant; Infant Nutritional Physiological Phenomena; Infant, Newborn; Nutrition Disorders; Pancreatic Extracts; Rectal Prolapse; Vitamin A; Vitamin D; Vitamin E

1986
Intracisternal inclusion bodies induced in animals: their transformation and significance.
    Journal of electron microscopy, 1974, Volume: 23, Issue:4

    Topics: Alloxan; Animals; Chiroptera; Cold Temperature; Cystic Fibrosis; Dogs; Endoplasmic Reticulum; Hexachlorocyclohexane; Hypothermia, Induced; Inclusion Bodies; Rats; Vitamin A; Vitamin E

1974
Blood and liver concentrations of vitamins A and E in children with cystic fibrosis of the pancreas.
    Pediatric research, 1972, Volume: 6, Issue:1

    Topics: Adolescent; Adult; Carotenoids; Child; Child, Preschool; Cholesterol; Cystic Fibrosis; Female; Humans; Infant; Lipid Metabolism; Liver; Male; Muscles; Serum Albumin; Vitamin A; Vitamin E

1972
Depressed plasma retinol-binding protein levels in cystic fibrosis.
    The Journal of laboratory and clinical medicine, 1972, Volume: 80, Issue:3

    Topics: Adolescent; Adult; Age Factors; Biological Transport; Blood Proteins; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Liver Function Tests; Male; Protein Binding; Serum Albumin; Sex Factors; Vitamin A

1972
Correlations between plasma and liver concentrations of vitamins A and E in children with cystic fibrosis.
    Bulletin of the New York Academy of Medicine, 1971, Volume: 47, Issue:1

    Topics: Adolescent; Adult; Child; Cystic Fibrosis; Humans; Liver; Vitamin A; Vitamin E

1971
Vitamin A deficiency with xerophthalmia and night blindness in cystic fibrosis.
    American journal of diseases of children (1960), 1968, Volume: 116, Issue:6

    Topics: Adolescent; Chlortetracycline; Conjunctiva; Cystic Fibrosis; Dark Adaptation; Diet Therapy; Female; Humans; Microscopy, Electron; Night Blindness; Pancreatic Extracts; Vitamin A; Vitamin A Deficiency; Vitamins; Xerophthalmia

1968
Test-meal in the diagnosis of malabsorption in infancy. Tolerance tests using simultaneous oral administration of glucose, D-xylose, cream and vitamin A.
    Acta paediatrica Scandinavica, 1971, Volume: 60, Issue:2

    Topics: Age Factors; Blood Glucose; Body Height; Body Weight; Carbon Isotopes; Celiac Disease; Cholestasis; Cystic Fibrosis; Female; Glucose; Humans; Infant; Lipids; Malabsorption Syndromes; Male; Time Factors; Triglycerides; Vitamin A; Xylose

1971