pyrrolidonecarboxylic acid and Nervous System Diseases

pyrrolidonecarboxylic acid has been researched along with Nervous System Diseases in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19903 (75.00)18.7374
1990's1 (25.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Prusiner, SB1
Jellum, E; Marstein, S; Nesbakken, R; Perry, TL1
Board, P; Carlsson, B; Dahl, N; Gali, R; Larsson, A; Mannervik, B; Pigg, M; Ristoff, E1
Beutler, E1

Reviews

1 review(s) available for pyrrolidonecarboxylic acid and Nervous System Diseases

ArticleYear
Disorders of glutamate metabolism and neurological dysfunction.
    Annual review of medicine, 1981, Volume: 32

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; gamma-Aminobutyric Acid; Glutamates; Glutamine; Glutathione; Histidine; Humans; Ketoglutaric Acids; Nervous System Diseases; Proline; Pyrrolidonecarboxylic Acid

1981

Other Studies

3 other study(ies) available for pyrrolidonecarboxylic acid and Nervous System Diseases

ArticleYear
Biochemical investigations of biopsied brain tissue and autopsied organs from a patient with pyroglutamic acidemia (5-oxoprolinemia).
    Clinica chimica acta; international journal of clinical chemistry, 1981, Apr-09, Volume: 111, Issue:2-3

    Topics: Adult; Amino Acids; Brain; Glutathione; Glutathione Synthase; Humans; Male; Nervous System Diseases; Pyrrolidinones; Pyrrolidonecarboxylic Acid

1981
Missense mutations in the human glutathione synthetase gene result in severe metabolic acidosis, 5-oxoprolinuria, hemolytic anemia and neurological dysfunction.
    Human molecular genetics, 1997, Volume: 6, Issue:7

    Topics: Acidosis; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Anemia, Hemolytic; Animals; Blotting, Southern; Child, Preschool; Glutathione Synthase; Humans; Infant, Newborn; Molecular Sequence Data; Mutation; Nervous System Diseases; Phenotype; Point Mutation; Polymerase Chain Reaction; Pyrrolidonecarboxylic Acid; Rats; Recombinant Proteins; Restriction Mapping; Sequence Analysis, DNA; Sequence Homology, Amino Acid; Xenopus

1997
Editorial: Glutathione deficiency, pyroglutamic acidemia and amino acid transport.
    The New England journal of medicine, 1976, Aug-19, Volume: 295, Issue:8

    Topics: Amino Acids; Anemia, Hemolytic, Congenital Nonspherocytic; Biological Transport, Active; Erythrocytes; gamma-Glutamyltransferase; Glutathione; Humans; Nervous System Diseases; Peptide Synthases; Pyroglutamate Hydrolase; Pyrrolidinones; Pyrrolidonecarboxylic Acid

1976