pyrrolidonecarboxylic acid and Cystine Diathesis

pyrrolidonecarboxylic acid has been researched along with Cystine Diathesis in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (33.33)18.2507
2000's1 (33.33)29.6817
2010's1 (33.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bachhawat, AK; Kumar, A1
Emma, F; Mannucci, L; Pastore, A; Piemonte, F; Rizzo, C; Rizzoni, G1
Dionisi-Vici, C; Federici, G; Greco, M; Pastore, A; Ribes, A; Rizzo, C; Rizzoni, G1

Other Studies

3 other study(ies) available for pyrrolidonecarboxylic acid and Cystine Diathesis

ArticleYear
A futile cycle, formed between two ATP-dependant gamma-glutamyl cycle enzymes, gamma-glutamyl cysteine synthetase and 5-oxoprolinase: the cause of cellular ATP depletion in nephrotic cystinosis?
    Journal of biosciences, 2010, Volume: 35, Issue:1

    Topics: Adenosine Triphosphate; Amino Acid Transport Systems, Neutral; Animals; Cysteine; Cystinosis; Disease Models, Animal; Glutamate-Cysteine Ligase; Glutamic Acid; Humans; Mice; Models, Biological; Pyroglutamate Hydrolase; Pyrrolidonecarboxylic Acid

2010
Impaired activity of the gamma-glutamyl cycle in nephropathic cystinosis fibroblasts.
    Pediatric research, 2006, Volume: 59, Issue:2

    Topics: Adenosine Triphosphate; Citrate (si)-Synthase; Cystinosis; Electron Transport; Electron Transport Complex IV; Fibroblasts; Glutamic Acid; Glutathione; Humans; Oxidative Stress; Pyrrolidonecarboxylic Acid

2006
Pyroglutamic aciduria and nephropathic cystinosis.
    Journal of inherited metabolic disease, 1999, Volume: 22, Issue:3

    Topics: 3-Hydroxybutyric Acid; Case-Control Studies; Child, Preschool; Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Infant; Ketoglutaric Acids; Lactates; Malates; Pyrrolidonecarboxylic Acid; Succinates

1999