pyrrolidonecarboxylic acid has been researched along with Anemia, Hemolytic in 7 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (42.86) | 18.7374 |
1990's | 1 (14.29) | 18.2507 |
2000's | 1 (14.29) | 29.6817 |
2010's | 1 (14.29) | 24.3611 |
2020's | 1 (14.29) | 2.80 |
Authors | Studies |
---|---|
Ekuni, S; Hirayama, K; Kanno, H; Katayama, Y; Kondo, H; Nagasaka, M; Nakahara, E; Osumi, K; Shimojima Yamamoto, K | 1 |
Aloulou, H; Ben Ameur, S; Hachicha, M; Kaabachi, N; Kamoun, T; Nasrallah, F | 1 |
Gradowska, W; Jurecka, A; Pajdowska, M; Pronicka, E; Sykut-Cegielska, J; Taybert, J | 1 |
Crist, WM; Prchal, JT; Roper, M; Wellner, VP | 1 |
Guthrie, R; Naylor, EW; Orfanos, AP | 1 |
Board, P; Carlsson, B; Dahl, N; Gali, R; Larsson, A; Mannervik, B; Pigg, M; Ristoff, E | 1 |
Meister, A | 1 |
1 review(s) available for pyrrolidonecarboxylic acid and Anemia, Hemolytic
Article | Year |
---|---|
The gamma-glutamyl cycle. Diseases associated with specific enzyme deficiencies.
Topics: Acyltransferases; Adult; Amidohydrolases; Amino Acid Metabolism, Inborn Errors; Amino Acids; Anemia, Hemolytic; Cell Membrane Permeability; Child, Preschool; Cysteine; Erythrocytes; Female; gamma-Glutamyltransferase; Glutamates; Glutathione; Glycine; Humans; Infant; Infant, Newborn; Kidney; Male; Peptide Synthases; Proline; Pyrrolidonecarboxylic Acid | 1974 |
6 other study(ies) available for pyrrolidonecarboxylic acid and Anemia, Hemolytic
Article | Year |
---|---|
Severe Hemolytic Anemia and Metabolic Acidosis at Birth with Glutathione Synthetase Deficiency and Progressive Neurological Symptoms on Follow-Up.
Topics: Acidosis; Anemia, Hemolytic; Child, Preschool; Follow-Up Studies; Glutathione Synthase; Humans; Infant; Infant, Newborn; Male; Pyrrolidonecarboxylic Acid | 2023 |
Hemolytic anemia and metabolic acidosis: think about glutathione synthetase deficiency.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Anemia, Hemolytic; Antioxidants; Erythrocytes; Fatal Outcome; Fever; Fibroblasts; Glutathione Synthase; Humans; Infant; Klebsiella Infections; Male; Pyrrolidonecarboxylic Acid; Sepsis; Skin; Treatment Outcome; Tunisia | 2015 |
Trial of erythropoietin treatment in a boy with glutathione synthetase deficiency.
Topics: Anemia, Hemolytic; Child, Preschool; Erythrocytes; Erythropoietin; Fibroblasts; Gas Chromatography-Mass Spectrometry; Glutathione Synthase; Heterozygote; Humans; Male; Mass Spectrometry; Metabolism, Inborn Errors; Oxidants; Pyrrolidonecarboxylic Acid | 2005 |
Hemolytic anemia, recurrent metabolic acidosis, and incomplete albinism associated with glutathione synthetase deficiency.
Topics: Acidosis; Albinism; Anemia, Hemolytic; Cells, Cultured; Erythrocytes; Fibroblasts; Glucosephosphate Dehydrogenase; Glutathione Synthase; Granulocytes; Humans; Infant; Male; Peptide Synthases; Pyrrolidonecarboxylic Acid | 1983 |
Ultramicromethod for estimation of total glutathione in dried blood spots on filter paper.
Topics: Adult; Anemia, Hemolytic; Child; Drug Stability; Female; Glutathione; Humans; Infant; Infant, Newborn; Male; Microchemistry; Oxidation-Reduction; Pyrrolidonecarboxylic Acid; Spectrophotometry | 1980 |
Missense mutations in the human glutathione synthetase gene result in severe metabolic acidosis, 5-oxoprolinuria, hemolytic anemia and neurological dysfunction.
Topics: Acidosis; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Anemia, Hemolytic; Animals; Blotting, Southern; Child, Preschool; Glutathione Synthase; Humans; Infant, Newborn; Molecular Sequence Data; Mutation; Nervous System Diseases; Phenotype; Point Mutation; Polymerase Chain Reaction; Pyrrolidonecarboxylic Acid; Rats; Recombinant Proteins; Restriction Mapping; Sequence Analysis, DNA; Sequence Homology, Amino Acid; Xenopus | 1997 |