pyrrolidonecarboxylic acid and Anemia, Hemolytic

pyrrolidonecarboxylic acid has been researched along with Anemia, Hemolytic in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19903 (42.86)18.7374
1990's1 (14.29)18.2507
2000's1 (14.29)29.6817
2010's1 (14.29)24.3611
2020's1 (14.29)2.80

Authors

AuthorsStudies
Ekuni, S; Hirayama, K; Kanno, H; Katayama, Y; Kondo, H; Nagasaka, M; Nakahara, E; Osumi, K; Shimojima Yamamoto, K1
Aloulou, H; Ben Ameur, S; Hachicha, M; Kaabachi, N; Kamoun, T; Nasrallah, F1
Gradowska, W; Jurecka, A; Pajdowska, M; Pronicka, E; Sykut-Cegielska, J; Taybert, J1
Crist, WM; Prchal, JT; Roper, M; Wellner, VP1
Guthrie, R; Naylor, EW; Orfanos, AP1
Board, P; Carlsson, B; Dahl, N; Gali, R; Larsson, A; Mannervik, B; Pigg, M; Ristoff, E1
Meister, A1

Reviews

1 review(s) available for pyrrolidonecarboxylic acid and Anemia, Hemolytic

ArticleYear
The gamma-glutamyl cycle. Diseases associated with specific enzyme deficiencies.
    Annals of internal medicine, 1974, Volume: 81, Issue:2

    Topics: Acyltransferases; Adult; Amidohydrolases; Amino Acid Metabolism, Inborn Errors; Amino Acids; Anemia, Hemolytic; Cell Membrane Permeability; Child, Preschool; Cysteine; Erythrocytes; Female; gamma-Glutamyltransferase; Glutamates; Glutathione; Glycine; Humans; Infant; Infant, Newborn; Kidney; Male; Peptide Synthases; Proline; Pyrrolidonecarboxylic Acid

1974

Other Studies

6 other study(ies) available for pyrrolidonecarboxylic acid and Anemia, Hemolytic

ArticleYear
Severe Hemolytic Anemia and Metabolic Acidosis at Birth with Glutathione Synthetase Deficiency and Progressive Neurological Symptoms on Follow-Up.
    The American journal of case reports, 2023, Apr-13, Volume: 24

    Topics: Acidosis; Anemia, Hemolytic; Child, Preschool; Follow-Up Studies; Glutathione Synthase; Humans; Infant; Infant, Newborn; Male; Pyrrolidonecarboxylic Acid

2023
Hemolytic anemia and metabolic acidosis: think about glutathione synthetase deficiency.
    Fetal and pediatric pathology, 2015, Volume: 34, Issue:1

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Anemia, Hemolytic; Antioxidants; Erythrocytes; Fatal Outcome; Fever; Fibroblasts; Glutathione Synthase; Humans; Infant; Klebsiella Infections; Male; Pyrrolidonecarboxylic Acid; Sepsis; Skin; Treatment Outcome; Tunisia

2015
Trial of erythropoietin treatment in a boy with glutathione synthetase deficiency.
    Journal of inherited metabolic disease, 2005, Volume: 28, Issue:6

    Topics: Anemia, Hemolytic; Child, Preschool; Erythrocytes; Erythropoietin; Fibroblasts; Gas Chromatography-Mass Spectrometry; Glutathione Synthase; Heterozygote; Humans; Male; Mass Spectrometry; Metabolism, Inborn Errors; Oxidants; Pyrrolidonecarboxylic Acid

2005
Hemolytic anemia, recurrent metabolic acidosis, and incomplete albinism associated with glutathione synthetase deficiency.
    Blood, 1983, Volume: 62, Issue:4

    Topics: Acidosis; Albinism; Anemia, Hemolytic; Cells, Cultured; Erythrocytes; Fibroblasts; Glucosephosphate Dehydrogenase; Glutathione Synthase; Granulocytes; Humans; Infant; Male; Peptide Synthases; Pyrrolidonecarboxylic Acid

1983
Ultramicromethod for estimation of total glutathione in dried blood spots on filter paper.
    Analytical biochemistry, 1980, May-01, Volume: 104, Issue:1

    Topics: Adult; Anemia, Hemolytic; Child; Drug Stability; Female; Glutathione; Humans; Infant; Infant, Newborn; Male; Microchemistry; Oxidation-Reduction; Pyrrolidonecarboxylic Acid; Spectrophotometry

1980
Missense mutations in the human glutathione synthetase gene result in severe metabolic acidosis, 5-oxoprolinuria, hemolytic anemia and neurological dysfunction.
    Human molecular genetics, 1997, Volume: 6, Issue:7

    Topics: Acidosis; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Anemia, Hemolytic; Animals; Blotting, Southern; Child, Preschool; Glutathione Synthase; Humans; Infant, Newborn; Molecular Sequence Data; Mutation; Nervous System Diseases; Phenotype; Point Mutation; Polymerase Chain Reaction; Pyrrolidonecarboxylic Acid; Rats; Recombinant Proteins; Restriction Mapping; Sequence Analysis, DNA; Sequence Homology, Amino Acid; Xenopus

1997