pyrroles has been researched along with Porphyria in 83 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 78 (93.98) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 3 (3.61) | 29.6817 |
2010's | 1 (1.20) | 24.3611 |
2020's | 1 (1.20) | 2.80 |
Authors | Studies |
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Mulder, RT; Rucklidge, JJ; Sarris, J; Warren, B | 1 |
Guillén, C; Llombart, B; Martorell-Calatayud, A; Nagore, E; Requena, C; Sanmartín, O; Sanz-Motilva, V; Serra-Guillén, C; Traves, V | 1 |
ACKNER, B; COOPER, JE; GRAY, CH; KELLY, M; NICHOLSON, DC | 1 |
HAEGER-ARONSEN, B | 2 |
RIMINGTON, C; ZIEGLER, G | 1 |
GRINSTEIN, M; RIVAS, EA; TIGIER, HA | 1 |
TOWNSEND, JD | 1 |
CHISOLM, JJ | 1 |
BRONOW, RS; REDEKER, AG; STERLING, RE | 1 |
COLLINS, G; GADDIS, EM; HELLMAN, ES; HUNTER, GW; TSCHUDY, DP; WELLAND, FH | 1 |
COLLINS, A; HELLMAN, ES; HUNTER, GW; TSCHUDY, DP; WELLAND, FH | 1 |
BOSSENMAIER, I; TADDEINI, L; WATSON, CJ | 1 |
THIELE, S; WITH, TK | 1 |
DOWDLE, EB; EALES, L; SAUNDERS, SJ; SWEENEY, GD | 1 |
MARKLE, V; PAZDER, LH; TAYLOR, JD | 1 |
DRUYAN, R; HAEGER-ARONSEN, B; WALDENSTROEM, J | 1 |
ARATO, G; BUDA, V; KELENYI, G; ORBAN, S | 1 |
Boers, GH; The, GK; van de Kerkhof, R; van der Meer, JW | 1 |
Kamsteeg, J | 1 |
Both, SP | 1 |
Fillippini, L; Siegenthaler, W | 1 |
Gorchein, A | 2 |
Tishler, PV; Winston, SH | 1 |
Graham, DJ; Moore, MR | 1 |
Lamola, AA | 1 |
Brodie, MJ; Goldberg, A; Graham, DJ; McColl, KE; Moore, MR | 1 |
Gorchein, A; Rogers, AT | 1 |
Duhan, HA; Gendler, PL; Rapoport, H | 1 |
Irvine, DG | 3 |
Formgren, B; Wetterberg, L | 1 |
McDonagh, AF | 1 |
Brodie, MJ; Goldberg, A; Graham, DJ; Moore, MR; Thompson, GG | 1 |
Dean, G | 1 |
Irvine, DG; Wetterberg, L | 1 |
Iwanow, ED | 1 |
Iarlykova, EI; Krasiukova, LI; Lorie, IuI | 1 |
Berk, PD; Schalch, D; Tschudy, DP; Waxman, AD | 1 |
Asmal, AC; Joubert, SM; Vinik, AI | 1 |
Eales, L; Sears, WG | 1 |
Stein, JA; Tschudy, DP | 1 |
Doss, M; Marver, HS; Meyer, UA; Rees, AC; Strand, LJ | 1 |
Roomi, MW | 1 |
McEwen, J; Paterson, C | 1 |
Berlin, NI; Bloomer, JR; Jones, EA | 1 |
Flyger, V; Levin, EY | 1 |
Bossenmaier, I; Cardinal, R; Miyagi, K; Watson, CJ | 1 |
Mezey, E; Nair, PP; Quartner, J | 1 |
Padmanaban, G; Rao, MR; Sarma, PS | 1 |
Vaisrub, S | 1 |
Bonkowsky, HL; Bossenmaier, I; Cardinal, R; Collins, A; Doherty, J; Tschudy, DP; Watson, CJ | 1 |
Bannerman, RM; Kreimer-Birnbaum, M; Mosovich, LL | 1 |
Brown, H; Deleña, S | 1 |
Goreczky, L; Róth, I | 1 |
Hänninen, P | 1 |
Bossenmaier, I; Cardinal, R; Watson, CJ | 1 |
Chatterjea, JB; Chatterji, AK | 1 |
Gibson, SL; Goldberg, A | 1 |
Eichhorn, F; Fischl, J; Major, C; Ruttenberg, A | 1 |
Carr, AA; Sanders, JL | 1 |
Galambos, JT; Olansky, S; Vogler, WR | 1 |
Gross, SR; Hutton, JJ | 1 |
Kaback, MM; Levin, EY; Romeo, G | 1 |
Glenn, BL; Levin, EY; Romeo, G | 1 |
Gerald, PS; Kang, ES | 1 |
Bock, KD; Hocevar, V; Merguet, P; Rausch-Stroomann, JG; Schley, G; Schröder, E; Schümann, HJ | 1 |
Samuels, S; Veliz, G | 1 |
Doss, M; Schmidt, A | 1 |
Beattie, AD; Beveridge, GW; Goldberg, A; Hope, E; Hunter, JA; Khan, SA; Smith, AW | 1 |
Neuberger, A | 1 |
Goldberg, A | 1 |
Hocevar, V; Rausch-Stroomann, JG | 1 |
Lovelace, RE; Zimmerman, EA | 1 |
Belcher, RV; Lockwood, WH; Rimington, C | 1 |
Aoki, K | 1 |
Aguadé, JP; Castells, A; Indacochea, A; Rodés, J | 1 |
Killough, JH; Mahood, WH | 1 |
Gable, JJ; Lacefield, DJ | 1 |
McMillin, JM; Watson, CJ; Zimmerman, TS | 1 |
5 review(s) available for pyrroles and Porphyria
Article | Year |
---|---|
Pyroluria: Fact or Fiction?
Topics: Adult; Child; Female; Humans; Male; Porphyrias; Pyrroles; Schizophrenia; Vitamin B 6; Vitamin B 6 Deficiency; Zinc | 2021 |
PEDIATRIC ASPECTS OF THE PORPHYRIAS.
Topics: Blood Chemical Analysis; Child; Erythropoiesis; Feces; Genetics, Medical; Glycine; Humans; Liver Diseases; Porphyrias; Porphyrins; Pyrroles | 1964 |
Thermal and photochemical reactions of bilirubin IX-alpha.
Topics: Animals; Bilirubin; Darkness; Free Radicals; Homozygote; Hot Temperature; Isomerases; Light; Molecular Conformation; Oxidation-Reduction; Oxygen; Photochemistry; Porphyrias; Porphyrins; Pyrroles; Rats; Spectrophotometry; Spectrophotometry, Ultraviolet | 1975 |
Kryptopyrrole and other monopyrroles in molecular neurobiology.
Topics: Animals; Anticonvulsants; Behavior, Animal; Bile Pigments; Blood-Brain Barrier; Chemical Phenomena; Chemistry; Chromatography; Electrophysiology; Humans; Mental Disorders; Molecular Conformation; Nervous System; Oxidation-Reduction; Porphyrias; Pyrroles; Rats | 1974 |
Acute intermittent porphyria. A clinical and biochemical study of 46 patients.
Topics: Acute Disease; Adolescent; Adult; Blood Volume Determination; Cholesterol; Electroencephalography; Female; Follow-Up Studies; Glucose; Humans; Levulinic Acids; Liver; Liver Function Tests; Male; Middle Aged; Neurologic Examination; Porphyrias; Propionates; Pyrroles; Thyroid Function Tests | 1970 |
78 other study(ies) available for pyrroles and Porphyria
Article | Year |
---|---|
Sunitinib-induced pseudoporphyria.
Topics: Aged; Aged, 80 and over; Antineoplastic Agents; Biopsy; Diagnosis, Differential; Drug Eruptions; Gastrointestinal Stromal Tumors; Humans; Indoles; Kidney Neoplasms; Male; Middle Aged; Porphyrias; Pyrroles; Sunitinib | 2015 |
Excretion of porphobilinogen and 5-aminolaevulinic acid in acute porphyria.
Topics: Amino Acids; Humans; Porphobilinogen; Porphyria, Acute Intermittent; Porphyrias; Pyrroles | 1961 |
Porphyria induced in the rabbit by diethyl 1,4-dihydro-2,4,6-trimethylpyridine-3,5-dicarboxylate. I. Excretion of 5-aminolaevulic acid, porphobilinogen, coproporphyrin and protoporphyrin.
Topics: Amino Acids; Animals; Coproporphyrins; Porphobilinogen; Porphyrias; Porphyrins; Protoporphyrins; Pyridines; Pyrroles; Rabbits | 1961 |
EXPERIMENTAL PORPHYRIA IN RATS INDUCED BY CHLORINATED BENZENES.
Topics: Amino Acids; Benzene; Catalase; Chlorine; Levulinic Acids; Liver; Pharmacology; Porphyrias; Porphyrins; Pyrroles; Rats; Research; Toxicology; Urine | 1963 |
[EXPERIMENTAL PORPHYRIA].
Topics: Animals; Hypnotics and Sedatives; Levulinic Acids; Metabolism; Pharmacology; Porphyrias; Pyrroles; Rabbits; Rats; Research; Toxicology | 1963 |
AN EVALUATION OF A RECENT MODIFICATION OF THE WATSON-SCHWARTZ TEST FOR PORPHOBILINOGEN.
Topics: Clinical Laboratory Techniques; Humans; Indicators and Reagents; Porphobilinogen; Porphyrias; Porphyrins; Pyrroles; Urine | 1964 |
EFFECT OF GRISEOFLUVIN IN ACUTE INTERMITTENT PORPHYRIA.
Topics: Alanine Transaminase; Clinical Enzyme Tests; Griseofulvin; Liver Function Tests; Porphyria, Acute Intermittent; Porphyrias; Porphyrins; Pyrroles; Toxicology; Urine | 1964 |
FACTORS AFFECTING THE EXCRETION OF PORPHYRIN PRECURSORS BY PATIENTS WITH ACUTE INTERMITTENT PORPHYRIA. I. THE EFFECT OF DIET.
Topics: Amino Acids; Biological Transport; Diet; Dietary Carbohydrates; Dietary Fats; Dietary Proteins; Humans; Levulinic Acids; Metabolism; Porphyria, Acute Intermittent; Porphyrias; Porphyrins; Pyrroles; Urine | 1964 |
FACTORS AFFECTING THE EXCRETION OF PORPHYRIN PRECURSORS BY PATIENTS WITH ACUTE INTERMITTENT PORPHYRIA. II. THE EFFECT OF ETHINYL ESTRADIOL.
Topics: Amino Acids; Diabetes Mellitus; Ethinyl Estradiol; Humans; Levulinic Acids; Medroxyprogesterone; Metabolism; Pharmacology; Porphyria, Acute Intermittent; Porphyrias; Porphyrins; Pyrroles; Urine | 1964 |
PRESENT STATUS OF THE EHRLICH ALDEHYDE REACTION FOR URINARY PORPHOBILINOGEN.
Topics: Acetates; Alcohols; Aldehydes; Chloroform; Chromatography; Humans; Hydrochloric Acid; Indicators and Reagents; Porphobilinogen; Porphyrias; Porphyrins; Pyrroles; Urine | 1964 |
ACUTE INTERMITTENT PORPHYRIA; DIAGNOSIS FOUR YEARS POST MORTEM BY CHEMICAL STUDIES IN RELATIVES.
Topics: Diagnosis, Differential; Genetics, Medical; Humans; Levulinic Acids; Necrosis; Pancreas; Paralysis; Porphyria, Acute Intermittent; Porphyrias; Porphyrins; Pyrroles; Urine | 1964 |
EXPERIMENTAL DISTURBANCE OF PORPHYRIN METABOLISM AND OF LIVER CATALASE ACTIVITY IN GUINEA PIGS AND RABBITS.
Topics: Amino Acids; Catalase; Enzyme Inhibitors; Feces; Griseofulvin; Guinea Pigs; Hexachlorocyclohexane; Lead Poisoning; Levulinic Acids; Liver; Porphyrias; Porphyrins; Pyrroles; Rabbits; Research; Toxicology; Triazoles; Urine | 1964 |
EFFECTS OF CHLOROQUINE ON PATIENTS WITH CUTANEOUS PORPHYRIA OF THE "SYMPTOMATIC" TYPE.
Topics: Amino Acids; Aspartate Aminotransferases; Chemical and Drug Induced Liver Injury; Chloroquine; Classification; Clinical Enzyme Tests; Fluids and Secretions; Glucosephosphate Dehydrogenase Deficiency; Glucosephosphates; Hepatitis; Humans; Levulinic Acids; Liver; Metabolism; Pathology; Porphyrias; Porphyrins; Pyrroles; Toxicology; Urine | 1965 |
PORPHOBILINOGEN AND DELTA-AMINOLEVULINIC ACID EXCRETION IN MULTIPLE SCLEROSIS.
Topics: Amino Acids; Aminolevulinic Acid; Demyelinating Diseases; Diagnosis, Differential; Fluids and Secretions; Humans; Levulinic Acids; Multiple Sclerosis; Neoplasms; Poliomyelitis; Porphobilinogen; Porphyrias; Porphyrins; Pyrroles; Urine | 1965 |
RENAL MECHANISM FOR EXCRETION OF PORPHYRIN PRECURSORS IN PATIENTS WITH ACUTE INTERMITTENT PORPHYRIA AND CHRONIC LEAD POISONING.
Topics: Amino Acids; Biomedical Research; Blood; Creatine; Creatinine; Fluids and Secretions; Humans; Kidney; Lead Poisoning; Levulinic Acids; Porphyria, Acute Intermittent; Porphyrias; Porphyrins; Pyrroles; Tryptophan; Tyrosine; Urine | 1965 |
[On the excretion of 5-aminolevulinic acid and porphobilinogen in latent porphyria].
Topics: Amino Acids; Aminolevulinic Acid; Humans; Porphobilinogen; Porphyrias; Porphyrins; Pyrroles | 1961 |
[Hemopyrrollactamuria (HPU); from spots to pseudo-disease].
Topics: Humans; Metabolic Diseases; Porphyrias; Pyrroles; Schizophrenia | 2003 |
[Hemopyrrollactamuria (HPU); from spots to pseudo-disease].
Topics: Diagnosis, Differential; Humans; Metabolic Diseases; Porphyrias; Pyrroles | 2003 |
[Hemopyrrollactamuria (HPU); from spots to pseudo-disease].
Topics: Dietary Supplements; Humans; Metabolic Diseases; Porphyrias; Pyrroles | 2003 |
[Qualitative demonstration of porphobilinogen in the urine in the framework of diagnosis of porphyria].
Topics: Humans; Porphyrias; Porphyrins; Pyrroles | 1967 |
Determination of delta-aminolaevulinic acid in biological fluids by gas-liquid chromatography with electron-capture detection.
Topics: Aminocaproic Acid; Aminolevulinic Acid; Body Fluids; Chromatography, Gas; Chromatography, Thin Layer; Electrons; Humans; Levulinic Acids; Porphyrias; Pyrroles; Spectrum Analysis | 1984 |
Simple screening test for qualitative detection of increased delta-aminolevulinic acid in urine.
Topics: Acute Disease; Aminolevulinic Acid; Benzaldehydes; Colorimetry; Humans; Levulinic Acids; Porphobilinogen Synthase; Porphyrias; Pyrroles | 1984 |
Monopyrroles in porphyria, psychosis and lead exposure.
Topics: 5-Aminolevulinate Synthetase; Acute Disease; Aminolevulinic Acid; Animals; Heme Oxygenase (Decyclizing); Humans; Lead Poisoning; Leukocytes; Liver; Male; Porphyrias; Porphyrins; Psychotic Disorders; Pyrroles; Rats | 1980 |
Fluorescence methods in the diagnosis and management of diseases of tetrapyrrole metabolism.
Topics: Bilirubin; Diagnosis, Differential; Humans; Infant, Newborn; Jaundice, Neonatal; Metabolic Diseases; Porphyrias; Protoporphyrins; Pyrroles; Spectrometry, Fluorescence; Tetrapyrroles | 1981 |
Urine concentration of 3-ethyl-5-hydroxy-4,5-dimethyl-delta 3-pyrrolin-2-one ('mauve factor') is not causally related to schizophrenia or to acute intermittent porphyria.
Topics: Acute Disease; Adult; Chromatography, Gas; Female; Humans; Porphyrias; Pyrroles; Schizophrenia | 1980 |
Quantitation of 3-ethyl-5-hydroxy-4,5-dimethyl-delta 3-pyrrolin-2-one in the urine of patients with acute intermittent porphyria.
Topics: Acute Disease; Adult; Aminolevulinic Acid; Chromatography, Gas; Female; Heme; Humans; Porphobilinogen; Porphyrias; Pyrroles | 1979 |
The 'mauve factor' of schizophrenia and porphyria, 5-hydroxyhaemopyrrole lactam, has low pharmacological potency on guinea-pig ileum.
Topics: Animals; Dose-Response Relationship, Drug; Electric Stimulation; Guinea Pigs; Humans; Ileum; Muscle Contraction; Porphyrias; Pyrroles; Rats; Schizophrenia | 1979 |
Hemopyrrole and kryptopyrrole are absent from the urine of schizophrenics and normal persons.
Topics: Chromatography, Gas; Humans; Mass Spectrometry; Methods; Porphyrias; Pyrroles; Schizophrenia | 1978 |
Pyrroles in neuropsychiatric and porphyric disorders: confirmation of a metabolite structure by synthesis.
Topics: Chromatography, Gel; Humans; Mental Disorders; Nervous System Diseases; Porphyrias; Pyrroles | 1978 |
Hydroxy-hemopyrrolenone, not kryptopyrrole, in the urine of schizophrenics and porphyrics.
Topics: Humans; Isomerism; Porphyrias; Pyrroles; Schizophrenia | 1978 |
Pharmacological and biochemical properties of kryptopyrrole and its oxidation products possibly related to acute intermittent porphyria.
Topics: Acute Disease; Animals; Behavior, Animal; Body Temperature; Humans; Male; Mice; Porphyrias; Pyrroles; Reaction Time | 1976 |
The porphyrinogenic effects of kryptopyrrole in the rat and the occurrence of urinary kryptopyrrole in human hereditary hepatic porphyria.
Topics: Aminolevulinic Acid; Animals; Humans; Male; Porphyrias; Porphyrins; Pyrroles; Rats | 1976 |
Screening tests for porphyria.
Topics: Feces; Humans; Porphyrias; Porphyrins; Propionates; Pyrroles | 1971 |
Kryptopyrrole-like substance in acute intermittent porphyria.
Topics: Acute Disease; Humans; Porphyrias; Pyrroles | 1972 |
Diagnostic tests in the porphyrias.
Topics: Feces; Fluorescence; Humans; Porphyrias; Pyrroles | 1967 |
[The role of delta-aminolevulinicacid-dehydrase (ALA-D) in the erythrocytes in the study of porphyrin biosynthesis].
Topics: Erythrocytes; Hepatitis; Hepatolenticular Degeneration; Humans; Hydro-Lyases; Kidney Diseases; Lead Poisoning; Levulinic Acids; Liver Cirrhosis; Nephritis; Porphyrias; Porphyrins; Pyelonephritis; Pyrroles | 1968 |
[On determination of porphobilinogen in urine].
Topics: Adult; Female; Humans; Porphyrias; Porphyrins; Pyrroles | 1966 |
Isolated adrenocorticotrophic hormone deficiency in acute intermittent porphyria.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Acute Disease; Adrenocorticotropic Hormone; Adult; Blood Glucose; Diet; Diet Therapy; Dietary Carbohydrates; Glucose Tolerance Test; Growth Hormone; Humans; Insulin; Lactates; Male; Metyrapone; Pituitary-Adrenal Function Tests; Porphyrias; Porphyrins; Pyrroles; Pyruvates | 1969 |
A neurological disorder in porphyria cutanea tarda.
Topics: Adult; Aspartate Aminotransferases; Bilirubin; Blood Proteins; Female; Glucose; Humans; Iron; Levulinic Acids; Liver Cirrhosis; Male; Middle Aged; Peripheral Nervous System Diseases; Porphyrias; Porphyrins; Propionates; Pyrroles; Serum Albumin | 1970 |
Urinary dipyrrylmethenes in patients with porphyria. A preliminary study of the brown pigments in the urine of a case of acute intermittent porphyria.
Topics: Acute Disease; Adult; Bilirubin; Chromatography, Thin Layer; Humans; Male; Pigments, Biological; Porphobilinogen; Porphyrias; Porphyrins; Pyrroles; Urobilin | 1974 |
Intermittent acute porphyria--demonstration of a genetic defect in porphobilinogen metabolism.
Topics: 5-Aminolevulinate Synthetase; Acute Disease; Adolescent; Adult; Erythrocytes; Feces; Female; Humans; Levulinic Acids; Lyases; Male; Pedigree; Porphobilinogen; Porphyrias; Porphyrins; Propionates; Pyrroles | 1972 |
Separation of aminoketones in biological fluids by thin-layer chromatography.
Topics: Acetone; Animals; Chick Embryo; Chromatography, Thin Layer; Ketones; Levulinic Acids; Liver; Methods; Porphyrias; Pyrroles | 1972 |
Drugs and false-positive screening tests for porphyria.
Topics: Adult; Anesthetics, Local; Azo Compounds; False Positive Reactions; Female; Humans; Phenazopyridine; Porphyrias; Porphyrins; Pyridines; Pyrroles; Urinary Tract Infections | 1972 |
The measurement of the synthetic rate of bilirubin from hepatic hemes in patients with acute intermittent porphyria.
Topics: Acute Disease; Adult; Amino Acids; Bilirubin; Carbon Isotopes; Female; Heme; Humans; Levulinic Acids; Liver; Male; Porphyrias; Propionates; Pyrroles; Spectrophotometry; Tritium | 1971 |
Uroporphyrinogen 3 cosynthetase activity in the fox squirrel (Sciurus niger).
Topics: Animals; Blood Cell Count; Disease Models, Animal; Hemoglobins; Isomerases; Kidney; Liver; Myocardium; Porphyrias; Porphyrins; Propionates; Pyrroles; Reticulocytes; Sciuridae; Spleen | 1971 |
The serum porphobilinogen and hepatic porphobilinogen deaminase in normal and porphyric individuals.
Topics: Adult; Aged; Animals; Feces; Female; Humans; Lead Poisoning; Levulinic Acids; Liver; Lyases; Male; Mice; Middle Aged; Neurologic Manifestations; Porphyrias; Porphyrins; Propionates; Pyrroles; Remission, Spontaneous | 1971 |
The effect of vitamin E on porphyrinuria induced by ethanol in the rat.
Topics: 5-Aminolevulinate Synthetase; Acyltransferases; Amines; Animals; Cytochromes; Ethanol; Fasting; Hydro-Lyases; Levulinic Acids; Male; Microsomes, Liver; Porphyrias; Porphyrins; Propionates; Pyrroles; Rats; Succinates; Sucrose; Vitamin E | 1971 |
Porphyrin synthesis in drug induced hepatic porphyria.
Topics: 5-Aminolevulinate Synthetase; Acetamides; Allyl Compounds; Amino Acids; Animals; Dicarboxylic Acids; Esters; Heme; Hydro-Lyases; Iron; Iron Isotopes; Levulinic Acids; Liver; Male; Mice; Porphyrias; Porphyrins; Propionates; Pyridines; Pyrroles; Rats | 1971 |
ALA-S and a lack.
Topics: 5-Aminolevulinate Synthetase; Acyltransferases; Bilirubin; Humans; Lyases; Porphyrias; Porphyrins; Propionates; Pyrroles | 1971 |
Repression of the overproduction of porphyrin precursors in acute intermittent porphyria by intravenous infusions of hematin.
Topics: Adult; Amino Acids; Female; Heme; Humans; Injections, Intravenous; Levulinic Acids; Porphyrias; Porphyrins; Propionates; Pyrroles; Time Factors | 1971 |
Acute intermittent porphyria. A clinical, biochemical and family study.
Topics: Acetone; Acute Disease; Adenosine Monophosphate; Child, Preschool; Glycine; Humans; Injections, Intramuscular; Levulinic Acids; Liver; Male; Pedigree; Porphyrias; Porphyrins; Propionates; Pyrroles | 1971 |
Effect of glycine loading on Delta-Aminolevulinic acid (ALA) and porphobilinogen (PBG) excretion during starvation.
Topics: Adolescent; Adult; Amino Acids; Body Weight; Female; Glycine; Humans; Hydro-Lyases; Levulinic Acids; Male; Middle Aged; Obesity; Porphyrias; Porphyrins; Propionates; Pyrroles; Starvation | 1969 |
[Regulatory disturbances in acute intermittent porphyria and lead poisoning].
Topics: Enzyme Induction; Growth Hormone; Humans; Hydro-Lyases; Hypothalamo-Hypophyseal System; Lead Poisoning; Levulinic Acids; Melanocyte-Stimulating Hormones; Porphyrias; Propionates; Pyrroles; Thyrotropin; Vasopressins; Water-Electrolyte Balance | 1969 |
[A family study of porphyrias].
Topics: Adult; Consanguinity; Drug Tolerance; Female; Humans; Levulinic Acids; Male; Middle Aged; Pedigree; Porphyrias; Propionates; Pyrroles | 1969 |
Formation of porphyrin isomers from porphobilinogen by various hemolysates of red cells from bovine and human subjects with erythropoietic (uro-) porphyria.
Topics: Aminohydrolases; Animals; Cattle; Erythrocytes; Erythropoiesis; Humans; Hydrogen-Ion Concentration; Isomerases; Porphyrias; Porphyrins; Potassium Chloride; Propionates; Pyrroles; Stereoisomerism; Temperature | 1969 |
Porphyrins and porphyrias: new horizons.
Topics: Anemia, Sideroblastic; Heme; India; Metabolic Diseases; Metabolism, Inborn Errors; Porphyrias; Porphyrins; Pyrroles | 1969 |
Defects in haem synthesis in mammalian tissues in experimental lead poisoning and experimental porphyria.
Topics: Amides; Animals; Bone Marrow; Brain; Female; Heme; Hydro-Lyases; Kidney; Lead Poisoning; Levulinic Acids; Ligases; Liver; Porphyrias; Porphyrins; Pyrroles; Rabbits | 1970 |
Conventional and preparative electrophoretic separation of some urinary porphyrins and porphyrin precursors.
Topics: Amino Acids; Buffers; Cellulose; Chromatography; Electrophoresis; Humans; Hydrogen-Ion Concentration; Levulinic Acids; Membranes, Artificial; Methods; Porphyrias; Porphyrins; Pyrroles; Quaternary Ammonium Compounds; Talc; Time Factors | 1970 |
Medical College of Georgia Medical Grand Rounds. Acute intermittent porphyria.
Topics: Acute Disease; Adult; Diagnosis, Differential; Female; Humans; Porphyrias; Porphyrins; Propionates; Pyrroles | 1970 |
Biochemical effects of chloroquine therapy in porphyria cutanea tarda.
Topics: Ascites; Body Temperature; Chemical and Drug Induced Liver Injury; Chloroquine; Chromatography; Feces; Female; Hematologic Diseases; Humans; Iron; Levulinic Acids; Liver Function Tests; Male; Middle Aged; Porphyrias; Porphyrins; Propionates; Pyrroles; Time Factors | 1970 |
Chemical induction of hepatic porphyria in inbred strains of mice.
Topics: Acyltransferases; Amino Acids; Animals; Chemical and Drug Induced Liver Injury; Feedback; Female; Genotype; Hydro-Lyases; Inbreeding; Levulinic Acids; Liver; Liver Diseases; Lyases; Mice; Porphyrias; Porphyrins; Propionates; Pyridines; Pyrroles; Succinates | 1970 |
Uroporphyrinogen 3 cosynthetase activity in fibroblasts from patients with congenital erythropoietic porphyria.
Topics: Adult; Child, Preschool; Female; Fibroblasts; Humans; Isomerases; Male; Porphyrias; Porphyrins; Propionates; Pyrroles | 1970 |
Uroporphyrinogen 3 cosynthetase in asymptomatic carriers of congenital erythpoietic porphyria.
Topics: Adolescent; Adult; Aging; Animals; Cattle; Erythrocyte Aging; Erythrocytes; Erythropoiesis; Female; Heterozygote; Humans; Isomerases; Male; Middle Aged; Porphyrias; Porphyrins; Propionates; Pyrroles | 1970 |
Hereditary tyrosinemia and abnormal pyrrole metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Fructose; Humans; Infant; Levulinic Acids; Liver Cirrhosis; Methionine; Oxidoreductases; Porphyrias; Porphyrins; Pyrroles; Renal Tubular Transport, Inborn Errors; Tyrosine | 1970 |
[Hypertension and tachycardia in acute intermittent porphyria].
Topics: Adult; Aldosterone; Amino Acids; Anemia; Blood Pressure; Catecholamines; Depression, Chemical; Electrocardiography; Female; Heart Rate; Humans; Hypertension; Kidney Function Tests; Levulinic Acids; Middle Aged; Porphyrias; Porphyrins; Propranolol; Pyrroles; Renin; Sympatholytics; Tachycardia; Vanilmandelic Acid | 1970 |
Diagnosis of a case of acute intermittent porphyria with the aid of thin-layer chromatography-thin-layer electrophoresis of urine.
Topics: Acute Disease; Amino Acids; Chromatography, Thin Layer; Color; Electrophoresis; Humans; Indicators and Reagents; Levulinic Acids; Porphyrias; Propionates; Pyrroles | 1971 |
[Quantitative determination of delta-aminolevulinic acid and porphobilinogen in urine, using ion exchange chromatography columns].
Topics: Chemistry, Clinical; Chromatography, Ion Exchange; Humans; Levulinic Acids; Methods; Porphyrias; Propionates; Pyrroles; Renal Aminoacidurias | 1971 |
Hereditary coproporphyria. Photosensitivity, jaundice and neuropsychiatric manifestations associated with pregnancy.
Topics: Adolescent; Amino Acids; Epilepsy; Feces; Female; Fetal Death; Humans; Hypertension; Jaundice; Levulinic Acids; Liver Function Tests; Neurologic Manifestations; Photosensitivity Disorders; Porphyrias; Porphyrins; Postpartum Period; Pregnancy; Pregnancy Complications; Pyrroles; Skin Manifestations | 1971 |
Biochemical basis and regulatory mechanisms of porphyrin synthesis.
Topics: Acute Disease; Amino Acids; Animals; Enzyme Repression; Erythrocytes; Erythrocytes, Abnormal; Erythropoiesis; Guinea Pigs; Humans; Hydro-Lyases; Levulinic Acids; Porphyrias; Porphyrins; Pyrroles; Rats | 1968 |
Diagnosis and treatment of the porphyrias.
Topics: Acute Disease; Amino Acids; Erythropoiesis; Feces; Female; Humans; Levulinic Acids; Liver Diseases; Male; Photosensitivity Disorders; Porphyrias; Porphyrins; Pyrroles; Skin Diseases; Skin Manifestations | 1968 |
[On the problem of treatment of acute intermittent porphyria with ovulation inhibitors. (Studies of delta-aminolevulinic acid, porphobilinogen and total porphyrin excretion)].
Topics: Adult; Amino Acids; Contraceptives, Oral; Female; Humans; Levulinic Acids; Middle Aged; Porphyrias; Porphyrins; Propionates; Pyrroles | 1968 |
The etiology of the neuropathy in acute intermittent porphyria.
Topics: Adult; Biopsy; Electromyography; Female; Humans; Levulinic Acids; Male; Peripheral Nerves; Porphyrias; Propionates; Pyrroles | 1968 |
The excretion of porphyrin-peptide conjugates in porphyria variegata.
Topics: Adolescent; Adult; Aged; Bilirubin; Child; Child, Preschool; Chromatography, Paper; Cysteine; Feces; Female; Hematoporphyrins; Humans; Infant; Lysine; Male; Middle Aged; Peptides; Phenylalanine; Porphyrias; Porphyrins; Pyrroles | 1968 |
[Study of urinary prophyrin and its precursors in children. 2. Variation of urinary prophyrin and its precursors in various types of pediatric diseases].
Topics: Anemia, Aplastic; Animals; Child; Child, Preschool; Chromatography; Female; Humans; Ion Exchange Resins; Lead Poisoning; Male; Porphyrias; Porphyrins; Pyrroles; Rabbits | 1968 |
A case of biochemically unclassifiable hepatic porphyria.
Topics: Adult; Biopsy; Female; Humans; Liver Cirrhosis; Porphyrias; Porphyrins; Pyrroles; Skin Manifestations | 1969 |
Acute intermittent porphyria. A clinical and laboratory study of a large family.
Topics: Humans; Kidney Function Tests; Porphyrias; Porphyrins; Pyrroles; Urine | 1966 |
Methods and pitfalls in the diagnosis of acute intermittent porphyria.
Topics: Humans; In Vitro Techniques; Porphyrias; Porphyrins; Pyrroles; Urine | 1966 |
Onset of manifestations of hepatic porphyria in relation to the influence of female sex hormones.
Topics: Adult; Aged; Alkaline Phosphatase; Bilirubin; Blood; Estrogens; Female; Humans; In Vitro Techniques; Liver Diseases; Male; Menstruation Disturbances; Middle Aged; Neurologic Manifestations; Porphyrias; Porphyrins; Pregnancy; Pregnancy Complications; Pyrroles; Skin Manifestations; Sulfobromophthalein | 1966 |