pyridoxine has been researched along with Cystinuria in 12 studies
4,5-bis(hydroxymethyl)-2-methylpyridin-3-ol: structure in first source
vitamin B6 : Any member of the group of pyridines that exhibit biological activity against vitamin B6 deficiency. Vitamin B6 deficiency is associated with microcytic anemia, electroencephalographic abnormalities, dermatitis with cheilosis (scaling on the lips and cracks at the corners of the mouth) and glossitis (swollen tongue), depression and confusion, and weakened immune function. Vitamin B6 consists of the vitamers pyridoxine, pyridoxal, and pyridoxamine and their respective 5'-phosphate esters (and includes their corresponding ionized and salt forms).
Cystinuria: An inherited disorder due to defective reabsorption of CYSTINE and other BASIC AMINO ACIDS by the PROXIMAL RENAL TUBULES. This form of aminoaciduria is characterized by the abnormally high urinary levels of cystine; LYSINE; ARGININE; and ORNITHINE. Mutations involve the amino acid transport protein gene SLC3A1.
| Excerpt | Relevance | Reference |
|---|---|---|
| "The metabolic response of patients with homocystinuria due to cystabhionine synthase deficiency to oral loads of homocysteine indicates: that even severely affected patients with homocystinuria have pools of cystine in their tissues; that control of sulfur amino acid metabolism favors increased concentrations of methionine rather than homocystine in the plasma; and that even patients who apparently are not B-6-responsive respond differently to the loads of homocysteine when challenged during B-6-treatment compared with their response before B-6 treatment." | 7.65 | Homocysteine and cysteine loads in patients with homocystinuria due to cystathionine synthase deficiency: effects of vitamin B-6. ( Gaull, GE; Longhi, RC; Rassin, DK; Sternowsky, HJ; Sturman, JA, 1977) |
| "The metabolic response of patients with homocystinuria due to cystabhionine synthase deficiency to oral loads of homocysteine indicates: that even severely affected patients with homocystinuria have pools of cystine in their tissues; that control of sulfur amino acid metabolism favors increased concentrations of methionine rather than homocystine in the plasma; and that even patients who apparently are not B-6-responsive respond differently to the loads of homocysteine when challenged during B-6-treatment compared with their response before B-6 treatment." | 3.65 | Homocysteine and cysteine loads in patients with homocystinuria due to cystathionine synthase deficiency: effects of vitamin B-6. ( Gaull, GE; Longhi, RC; Rassin, DK; Sternowsky, HJ; Sturman, JA, 1977) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 11 (91.67) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 1 (8.33) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Tanzer, F | 1 |
| Firat, M | 1 |
| Alagoz, M | 1 |
| Erdogan, H | 1 |
| Rassin, DK | 1 |
| Longhi, RC | 1 |
| Sternowsky, HJ | 1 |
| Sturman, JA | 1 |
| Gaull, GE | 1 |
| Amram, S | 1 |
| Palcoux, JB | 1 |
| Malpuech, G | 1 |
| Plazonnet, MJ | 1 |
| Storme, B | 1 |
| Meyer, M | 1 |
| Werner, T | 1 |
| Weinmann, HM | 1 |
| Houpt, JB | 1 |
| Ogryzlo, MA | 1 |
| Hunt, M | 1 |
| Kodama, H | 1 |
| Ikegami, T | 1 |
| Yao, K | 1 |
| Oura, T | 1 |
| Seashore, MR | 1 |
| Durant, JL | 1 |
| Rosenberg, LE | 1 |
| Fawcett, NP | 1 |
| Nyhan, WL | 1 |
| Keiser, HR | 1 |
| Henkin, RI | 1 |
| Bartter, FC | 1 |
| Sjoerdsma, A | 1 |
| Gibbs, DA | 1 |
| Watts, RW | 1 |
| Frimpter, GW | 1 |
| Berlow, S | 1 |
1 review available for pyridoxine and Cystinuria
| Article | Year |
|---|---|
[10 years of penicillamine].
Topics: Cystinuria; Drug Eruptions; Gold; Hepatolenticular Degeneration; Humans; Lead Poisoning; Leukopenia; | 1966 |
11 other studies available for pyridoxine and Cystinuria
| Article | Year |
|---|---|
Gyrate atrophy of the choroid and retina with hyperornithinemia, cystinuria and lysinuria responsive to vitamin B6.
Topics: Biomarkers; Child; Cystinuria; Female; Gyrate Atrophy; Humans; Lysine; Night Blindness; Ornithine; P | 2011 |
Homocysteine and cysteine loads in patients with homocystinuria due to cystathionine synthase deficiency: effects of vitamin B-6.
Topics: Cystathionine beta-Synthase; Cysteine; Cystine; Cystinuria; Disulfides; Female; Homocysteine; Homocy | 1977 |
[Pyridoxin-resistant homocystinuria. Apropos of a case with early thromboembolic complications].
Topics: Child, Preschool; Cystinuria; Drug Resistance; Humans; Intracranial Embolism and Thrombosis; Male; P | 1986 |
Tryptophan metabolism in man (with special reference to rheumatoid arthritis and scleroderma).
Topics: Arthritis, Rheumatoid; Aspirin; Cystinuria; Drug Synergism; Edetic Acid; Humans; Kynurenic Acid; Kyn | 1973 |
Effect of pyridoxine treatment of a homocystinuric patient on the urinary excretion of some sulfur-containing amino acids.
Topics: Alanine; Amino Acids, Sulfur; Cystinuria; Disulfides; Homocysteine; Homocystine; Homocystinuria; Hum | 1974 |
Studies of the mechanism of pyridoxine-responsive homocystinuria.
Topics: Adolescent; Cells, Cultured; Cystine; Cystinuria; Fibroblasts; Homocystine; Homocystinuria; Humans; | 1972 |
Cystinuria and dermatomyositis.
Topics: Adolescent; Amino Acids; Chromatography, Paper; Cystinuria; Dermatomyositis; Electromyography; Femal | 1970 |
Loss of taste during therapy with penicillamine.
Topics: Adolescent; Adult; Cystinuria; Female; Food; Humans; Hydrochloric Acid; Male; Middle Aged; Penicilla | 1968 |
Studies on the effect of D-penicillamine and N-acetyl-D-penicillamine on the excretion of some tryptophan metabolites in patients with cystinuria.
Topics: Adolescent; Adult; Child; Cystinuria; Female; Humans; Kynurenine; Male; ortho-Aminobenzoates; Penici | 1969 |
Cystathioninuria in a patient with cystinuria.
Topics: Adult; Amino Acids; Cystinuria; Female; Glycine; Heterozygote; Humans; Hydro-Lyases; Methionine; Pyr | 1969 |
Studies in cystathioninemia.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Chromatography, Paper; Cystinuria; Humans; Intelle | 1966 |