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pyridoxal phosphate and Glycogen Storage Disease

pyridoxal phosphate has been researched along with Glycogen Storage Disease in 1 studies

Pyridoxal Phosphate: This is the active form of VITAMIN B 6 serving as a coenzyme for synthesis of amino acids, neurotransmitters (serotonin, norepinephrine), sphingolipids, aminolevulinic acid. During transamination of amino acids, pyridoxal phosphate is transiently converted into pyridoxamine phosphate (PYRIDOXAMINE).
pyridoxal 5'-phosphate : The monophosphate ester obtained by condensation of phosphoric acid with the primary hydroxy group of pyridoxal.

Glycogen Storage Disease: A group of inherited metabolic disorders involving the enzymes responsible for the synthesis and degradation of glycogen. In some patients, prominent liver involvement is presented. In others, more generalized storage of glycogen occurs, sometimes with prominent cardiac involvement.

Research Excerpts

ExcerptRelevanceReference
"Pyridoxal phosphate is a covalently bound cofactor of glycogen phosphorylase."1.27Low muscle levels of pyridoxine in McArdle's syndrome. ( Cook, JD; Dempsey, WB; Feit, H; Haller, RG; Knochel, JP, 1983)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19901 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Haller, RG1
Dempsey, WB1
Feit, H1
Cook, JD1
Knochel, JP1

Other Studies

1 other study available for pyridoxal phosphate and Glycogen Storage Disease

ArticleYear
Low muscle levels of pyridoxine in McArdle's syndrome.
    The American journal of medicine, 1983, Volume: 74, Issue:2

    Topics: Adolescent; Adult; Animals; Female; Glycogen Storage Disease; Glycogen Storage Disease Type V; Human

1983