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pyridoxal phosphate and Anemia, Sideroblastic

pyridoxal phosphate has been researched along with Anemia, Sideroblastic in 38 studies

Pyridoxal Phosphate: This is the active form of VITAMIN B 6 serving as a coenzyme for synthesis of amino acids, neurotransmitters (serotonin, norepinephrine), sphingolipids, aminolevulinic acid. During transamination of amino acids, pyridoxal phosphate is transiently converted into pyridoxamine phosphate (PYRIDOXAMINE).
pyridoxal 5'-phosphate : The monophosphate ester obtained by condensation of phosphoric acid with the primary hydroxy group of pyridoxal.

Anemia, Sideroblastic: Anemia characterized by the presence of erythroblasts containing excessive deposits of iron in the marrow.

Research

Studies (38)

TimeframeStudies, this research(%)All Research%
pre-199031 (81.58)18.7374
1990's4 (10.53)18.2507
2000's1 (2.63)29.6817
2010's2 (5.26)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Lee, JS1
Gu, J1
Yoo, HJ1
Koh, Y1
Kim, HK1
Fratz-Berilla, EJ1
Breydo, L1
Gouya, L1
Puy, H1
Uversky, VN1
Ferreira, GC1
Astner, I1
Schulze, JO1
van den Heuvel, J1
Jahn, D1
Schubert, WD1
Heinz, DW1
Bonjour, JP1
Aoki, Y4
Smith, GP1
Samson, D1
Peters, TJ1
Manabe, Y1
Seto, S1
Furusho, K1
May, A2
de Souza, P1
Barnes, K1
Kaaba, S1
Jacobs, A1
Pasanen, AV1
Salmi, M1
Tenhunen, R1
Vuopio, P1
Meier, PJ1
Fehr, J1
Meyer, UA1
Buchanan, GR1
Bottomley, SS3
Nitschke, R1
Takeda, Y1
Sawada, H1
Sawai, H1
Toi-Matsuda, T1
Tashima, M1
Okuma, M1
Watanabe, S1
Ohmori, S1
Kondo, M1
Fitzsimons, E1
Chillar, RK1
Johnson, CS1
Beutler, E1
Penchas, S1
Zlotnick, A1
Cohen, R1
Cohen, MM1
Solomon, LR1
Hillman, RS2
Muranaka, S1
Nakabayashi, K1
Ueda, Y2
Pierce, HI1
McGuffin, RG1
Hansen, OP1
Drivsholm, A1
Hardt, F1
Cartwright, GE1
Deiss, A1
Andersen, K1
Kaad, PH1
Murakami, R1
Takumi, T1
Gouji, J1
Nakamura, H1
Kondou, M1
Tanaka, M2
Self, J1
Child, JA1
Mallinson, CN1
Jonasson, J1
Gahrton, G1
Lindsten, J1
Simonsson-Lindemalm, C1
Zech, L1
Takaku, F1
Yano, Y1
Nakao, K1
Wada, O1
Anderson, BB2
Mollin, DL1
Murakami, M1
Muranaka, M1
Sekimura, T1
Izuka, K1
Yokoari, R1
Okumura, H1
Mason, DY1
Emerson, PM1
Frimpter, GW1
Andelman, RJ1
George, WF1
White, JM1
Brain, MC1
Ali, MA1
Peart, MB1
Fulford-Jones, CE1
Hines, JD1
Cowan, DH1
Weintraub, LR1
French, SW1

Reviews

4 reviews available for pyridoxal phosphate and Anemia, Sideroblastic

ArticleYear
Vitamins and alcoholism. III. Vitamin B6.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1980, Volume: 50, Issue:2

    Topics: Alcoholism; Anemia, Sideroblastic; Animals; Aspartate Aminotransferases; False Positive Reactions; F

1980
Sideroblastic anaemia.
    Bailliere's clinical haematology, 1994, Volume: 7, Issue:4

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Biological Transport; Chloramphenicol; Copper;

1994
Sideroblasts, siderocytes, and sideroblastic anemia.
    The New England journal of medicine, 1975, Jan-23, Volume: 292, Issue:4

    Topics: 5-Aminolevulinate Synthetase; Anemia, Hemolytic; Anemia, Sideroblastic; Animals; Bloodletting; Bone

1975
Vitamin B6-dependency syndromes. New horizons in nutrition.
    The American journal of clinical nutrition, 1969, Volume: 22, Issue:6

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Aminobutyrates; Anemia, Sideroblastic; Animals; Child;

1969

Other Studies

34 other studies available for pyridoxal phosphate and Anemia, Sideroblastic

ArticleYear
A Novel
    Annals of clinical and laboratory science, 2017, Volume: 47, Issue:3

    Topics: 5-Aminolevulinate Synthetase; Adolescent; Anemia, Sideroblastic; Female; Genetic Diseases, X-Linked;

2017
Isoniazid inhibits human erythroid 5-aminolevulinate synthase: Molecular mechanism and tolerance study with four X-linked protoporphyria patients.
    Biochimica et biophysica acta. Molecular basis of disease, 2017, Volume: 1863, Issue:2

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Enzyme Inhibitors; Genetic Diseases, X-Linked;

2017
Crystal structure of 5-aminolevulinate synthase, the first enzyme of heme biosynthesis, and its link to XLSA in humans.
    The EMBO journal, 2005, Sep-21, Volume: 24, Issue:18

    Topics: 5-Aminolevulinate Synthetase; Acyl Coenzyme A; Amino Acid Sequence; Anemia, Sideroblastic; Binding S

2005
Multiple enzymatic defects in mitochondria in hematological cells of patients with primary sideroblastic anemia.
    The Journal of clinical investigation, 1980, Volume: 66, Issue:1

    Topics: 5-Aminolevulinate Synthetase; Adenosine Triphosphatases; Anemia, Sideroblastic; Blood Cells; Citrate

1980
A fluorimetric method for the measurement of pyridoxal and pyridoxal phosphate in human plasma and leucocytes, and its application to patients with sideroblastic marrows.
    Journal of clinical pathology, 1983, Volume: 36, Issue:6

    Topics: Anemia, Sideroblastic; Chromatography, Ion Exchange; Fluorometry; Humans; Neutrophils; Pyridoxal; Py

1983
A study of a female with congenital sideroblastic anemia.
    American journal of hematology, 1982, Volume: 12, Issue:1

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Erythroblasts; Female; Granulocytes; Humans; In

1982
Erythroblast iron metabolism in sideroblastic marrows.
    British journal of haematology, 1982, Volume: 52, Issue:4

    Topics: Adult; Aged; Aminolevulinic Acid; Anemia, Sideroblastic; Bone Marrow; Cytoplasm; Erythroblasts; Eryt

1982
Haema synthesis during pyridoxine therapy in two families with different types of hereditary sideroblastic anaemia.
    Annals of clinical research, 1982, Volume: 14, Issue:2

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Coproporphyrins; Erythrocytes; Female; Heme; Hu

1982
Pyridoxine-responsive primary acquired sideroblastic anaemia. In vitro and in vivo effects of vitamin B6 on decreased 5-aminolaevulinate synthase activity.
    Scandinavian journal of haematology, 1982, Volume: 29, Issue:5

    Topics: 5-Aminolevulinate Synthetase; Adult; Aged; Anemia, Sideroblastic; Erythroblasts; Female; Humans; Mal

1982
Bone marrow delta-aminolaevulinate synthase deficiency in a female with congenital sideroblastic anemia.
    Blood, 1980, Volume: 55, Issue:1

    Topics: 5-Aminolevulinate Synthetase; Administration, Oral; Anemia, Sideroblastic; Bone Marrow; Child, Presc

1980
Acquired hypochromic and microcytic sideroblastic anaemia responsive to pyridoxine with low value of free erythrocyte protoporphyrin: a possible subgroup of idiopathic acquired sideroblastic anaemia (IASA).
    British journal of haematology, 1995, Volume: 90, Issue:1

    Topics: Adult; Anemia, Hypochromic; Anemia, Sideroblastic; Erythrocytes; Female; Humans; Protoporphyrins; Py

1995
Erythrocyte pyridoxine kinase levels in patients with sideroblastic anemia.
    The New England journal of medicine, 1976, Oct-14, Volume: 295, Issue:16

    Topics: Alcoholic Intoxication; Alcoholism; Anemia, Sideroblastic; Aspartate Aminotransferases; Black People

1976
Pyridoxal-5-phosphate-resistant sideroblastic anaemia with trisomy 8 mosaicism in the bone marrow.
    Acta haematologica, 1977, Volume: 57, Issue:6

    Topics: Adult; Anemia, Sideroblastic; Bone Marrow; Bone Marrow Cells; Chromosomes, Human, 6-12 and X; Drug R

1977
Vitamin B6 metabolism in idiopathic sideroblastic anaemia and related disorders.
    British journal of haematology, 1979, Volume: 42, Issue:2

    Topics: Adolescent; Adult; Aged; Anemia, Sideroblastic; Aspartate Aminotransferases; Erythrocyte Aging; Eryt

1979
delta-Aminolevulinic acid synthetase in erythroblasts of patients with pyridoxine-responsive anemia. Hypercatabolism caused by the increased susceptibility to the controlling protease.
    The Journal of clinical investigation, 1979, Volume: 64, Issue:5

    Topics: 5-Aminolevulinate Synthetase; Anemia, Hypochromic; Anemia, Sideroblastic; Bone Marrow; Bone Marrow C

1979
Clinical studies in alcoholic sideroblastosis.
    Archives of internal medicine, 1976, Volume: 136, Issue:3

    Topics: Adult; Aged; Alcoholism; Anemia, Sideroblastic; Chronic Disease; Diet; Erythropoiesis; Ethanol; Foli

1976
[Treatment of primary acquired sideroblastic anemia with pyridoxal-5-phosphate. Recent experience].
    Ugeskrift for laeger, 1976, Nov-22, Volume: 138, Issue:48

    Topics: Administration, Oral; Aged; Anemia, Sideroblastic; Female; Folic Acid; Humans; Male; Pyridoxal Phosp

1976
Congenital sideroblastic anaemia with intrauterine symptoms and early lethal outcome.
    Acta paediatrica (Oslo, Norway : 1992), 1992, Volume: 81, Issue:8

    Topics: Anemia; Anemia, Sideroblastic; Blood Transfusion; Blood Transfusion, Intrauterine; Female; Fetal Dis

1992
Sideroblastic anemia showing unique response to pyridoxine.
    The American journal of pediatric hematology/oncology, 1991,Fall, Volume: 13, Issue:3

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Erythroblasts; Heme; Humans; Infant; Iron; Male

1991
Unusual anaemias of old age.
    Lancet (London, England), 1973, Mar-17, Volume: 1, Issue:7803

    Topics: Age Factors; Aged; Anemia; Anemia, Hypochromic; Anemia, Sideroblastic; Blood Transfusion; Female; He

1973
Delta-aminolevulinic acid synthetase activity in normal human bone marrow and in patients with idiopathic sideroblastic anemia.
    Enzyme, 1973, Volume: 16, Issue:1

    Topics: 5-Aminolevulinate Synthetase; Aged; Anemia, Sideroblastic; Bone Marrow; Carbon Radioisotopes; Chroma

1973
Sideroblastic anaemia and jejunal diverticulosis.
    Guy's Hospital reports, 1973, Volume: 122, Issue:3-4

    Topics: Anemia, Sideroblastic; Blood Transfusion; Bone Marrow; Diverticulum; Erythropoiesis; Female; Headach

1973
Trisomy 8 in acute myeloblastic leukemia and sideroachrestic anemia.
    Blood, 1974, Volume: 43, Issue:4

    Topics: Aged; Anemia, Myelophthisic; Anemia, Sideroblastic; Bone Marrow Examination; Cells, Cultured; Chromo

1974
-Aminolevulinic acid synthetase activity of human bone marrow erythroid cells in various hematological disorders.
    The Tohoku journal of experimental medicine, 1972, Volume: 107, Issue:3

    Topics: 5-Aminolevulinate Synthetase; Anemia, Hypochromic; Anemia, Sideroblastic; Bone Marrow; Bone Marrow C

1972
Red-cell metabolism of pyridoxine in sideroblastic anaemias and related anaemias.
    British journal of haematology, 1972, Volume: 23

    Topics: Adenosine Triphosphate; Adult; Aged; Anemia, Hypochromic; Anemia, Sideroblastic; Biological Assay; E

1972
[Pyridoxine-responsive anemia. Report of a case in a child].
    [Rinsho ketsueki] The Japanese journal of clinical hematology, 1972, Volume: 13, Issue:4

    Topics: Anemia, Sideroblastic; Child; Humans; Male; Pyridoxal Phosphate; Vitamin B Complex

1972
[A case of pyridoxine responsive anemia].
    [Rinsho ketsueki] The Japanese journal of clinical hematology, 1972, Volume: 13, Issue:4

    Topics: Adolescent; Anemia, Sideroblastic; Humans; Male; Pyridoxal Phosphate

1972
Primary acquired sideroblastic anaemia: response to treatment with pyridoxal-5-phosphate.
    British medical journal, 1973, Feb-17, Volume: 1, Issue:5850

    Topics: Aged; Anemia, Sideroblastic; Ascorbic Acid; Female; Folic Acid; Hemoglobinometry; Humans; Pyridoxal

1973
Bone marrow delta-aminolevulinic acid synthetase activity in experimental sideroblastic anemia.
    The Journal of laboratory and clinical medicine, 1974, Volume: 84, Issue:1

    Topics: 5-Aminolevulinate Synthetase; Anemia, Sideroblastic; Animals; Bone Marrow; Bone Marrow Cells; Cyclos

1974
Alpha- and beta- peptide chain synthesis in sideroblastic anaemia.
    British journal of haematology, 1969, Volume: 17, Issue:6

    Topics: Amino Acids; Anemia, Sideroblastic; Heme; Hemoglobins; Humans; In Vitro Techniques; Leucine; Levulin

1969
The measurement of serum pyridoxal by a microbiological assay using Lactobacillus casei.
    Journal of clinical pathology, 1970, Volume: 23, Issue:3

    Topics: Adolescent; Adult; Age Factors; Aged; Anemia, Sideroblastic; Arthritis, Rheumatoid; Biological Assay

1970
Studies on the pathogenesis of alcohol-induced sideroblastic bone-marrow abnormalities.
    The New England journal of medicine, 1970, Aug-27, Volume: 283, Issue:9

    Topics: Adult; Alcoholism; Anemia, Sideroblastic; Bone Marrow; Bone Marrow Examination; Erythrocytes; Ethano

1970
The continuing saga of the sideroblast.
    The New England journal of medicine, 1970, Aug-27, Volume: 283, Issue:9

    Topics: Alcoholism; Anemia, Sideroblastic; Bone Marrow; Ethanol; Folic Acid Deficiency; Heme; Humans; Iron;

1970
Alcohol-induced vitamin-B 6-responsive anemia.
    The New England journal of medicine, 1970, Nov-19, Volume: 283, Issue:21

    Topics: Alcoholism; Anemia, Sideroblastic; Animals; Ethanol; Humans; Liver; Male; Phosphotransferases; Pyrid

1970