pyrenemethyl laurate has been researched along with Wolman Disease in 2 studies
*Wolman Disease: The severe infantile form of inherited lysosomal lipid storage diseases due to deficiency of acid lipase (STEROL ESTERASE). It is characterized by the accumulation of neutral lipids, particularly CHOLESTEROL ESTERS in leukocytes, fibroblasts, and hepatocytes. It is also known as Wolman's xanthomatosis and is an allelic variant of CHOLESTEROL ESTER STORAGE DISEASE. [MeSH]
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (50.00) | 18.7374 |
| 1990's | 1 (50.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Dagan, A; Gatt, S; Nègre-Salvayre, A; Salvayre, R | 1 |
| Dagan, A; Gatt, S; Nègre, A | 1 |
2 other study(ies) available for pyrenemethyl laurate and Wolman Disease
| Article | Year |
|---|---|
Use of pyrenemethyl laurate for fluorescence-based determination of lipase activity in intact living lymphoblastoid cells and for the diagnosis of acid lipase deficiency.
Topics: Biological Transport; Endocytosis; Fluorescent Dyes; Humans; In Vitro Techniques; Laurates; Lipase; Low Density Lipoprotein Receptor-Related Protein-1; Lymphocytes; Microscopy, Fluorescence; Pyrenes; Receptors, Cell Surface; Receptors, Lipoprotein; Wolman Disease | 1993 |
Pyrene-methyl lauryl ester, a new fluorescent substrate for lipases: use for diagnosis of acid lipase deficiency in Wolman's and cholesteryl ester storage diseases.
Topics: Cell Line; Cells, Cultured; Cholesterol Ester Storage Disease; Clinical Enzyme Tests; Fluorescent Dyes; Genetic Carrier Screening; Humans; Kinetics; Laurates; Lauric Acids; Leukocytes; Lipase; Lymphocytes; Pyrenes; Reference Values; Wolman Disease | 1989 |