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propofol and Glycogen Storage Disease Type II

propofol has been researched along with Glycogen Storage Disease Type II in 1 studies

Propofol: An intravenous anesthetic agent which has the advantage of a very rapid onset after infusion or bolus injection plus a very short recovery period of a couple of minutes. (From Smith and Reynard, Textbook of Pharmacology, 1992, 1st ed, p206). Propofol has been used as ANTICONVULSANTS and ANTIEMETICS.
propofol : A phenol resulting from the formal substitution of the hydrogen at the 2 position of 1,3-diisopropylbenzene by a hydroxy group.

Glycogen Storage Disease Type II: An autosomal recessively inherited glycogen storage disease caused by GLUCAN 1,4-ALPHA-GLUCOSIDASE deficiency. Large amounts of GLYCOGEN accumulate in the LYSOSOMES of skeletal muscle (MUSCLE, SKELETAL); HEART; LIVER; SPINAL CORD; and BRAIN. Three forms have been described: infantile, childhood, and adult. The infantile form is fatal in infancy and presents with hypotonia and a hypertrophic cardiomyopathy (CARDIOMYOPATHY, HYPERTROPHIC). The childhood form usually presents in the second year of life with proximal weakness and respiratory symptoms. The adult form consists of a slowly progressive proximal myopathy. (From Muscle Nerve 1995;3:S61-9; Menkes, Textbook of Child Neurology, 5th ed, pp73-4)

Research Excerpts

ExcerptRelevanceReference
"Deaths resulting from arrhythmia appeared to correlate with left ventricular mass indices >350 g x m(-2)."1.34Cardiac arrhythmias following anesthesia induction in infantile-onset Pompe disease: a case series. ( Corzo, D; Dearmey, SM; Kishnani, PS; Li, JS; Mackey, JF; Morgan, C; Ross, AK; Wang, LY; Worden, M, 2007)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Wang, LY1
Ross, AK1
Li, JS1
Dearmey, SM1
Mackey, JF1
Worden, M1
Corzo, D1
Morgan, C1
Kishnani, PS1

Other Studies

1 other study available for propofol and Glycogen Storage Disease Type II

ArticleYear
Cardiac arrhythmias following anesthesia induction in infantile-onset Pompe disease: a case series.
    Paediatric anaesthesia, 2007, Volume: 17, Issue:8

    Topics: alpha-Glucosidases; Anesthesia, General; Anesthetics, Intravenous; Arrhythmias, Cardiac; Clinical Tr

2007