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propionyl-coenzyme a and Propionic Acidemia

propionyl-coenzyme a has been researched along with Propionic Acidemia in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (25.00)24.3611
2020's3 (75.00)2.80

Authors

AuthorsStudies
Barry, MA; He, W; Wang, Y; Xie, EJ; Zhang, GF1
Armstrong, AJ; Chapman, KA; Collado, MS; Figler, RA; Hamilton, CA; Henke, BR; Hoang, SA; Johns, BA; Olson, MW; Pourtaheri, TD; Reardon, JE; Summar, MM; Wamhoff, BR1
Armstrong, AJ; Collado, MS; Dillberger, JE; Figler, RA; Henke, BR; Hoang, SA; Johns, BA; Olson, MW; Pourtaheri, TD; Reardon, JE; Roper, TD; Taylor, JM; Wamhoff, BR1
Brunengraber, H; Chapman, KA; Cline, GW; Han, Y; Hess, JP; Tochtrop, GP; Wilson, KA; Zhang, GF; Zhang, M1

Other Studies

4 other study(ies) available for propionyl-coenzyme a and Propionic Acidemia

ArticleYear
Metabolic perturbations mediated by propionyl-CoA accumulation in organs of mouse model of propionic acidemia.
    Molecular genetics and metabolism, 2021, Volume: 134, Issue:3

    Topics: Acyl Coenzyme A; Animal Feed; Animals; Disease Models, Animal; Heart; Liver; Lung; Male; Metabolic Flux Analysis; Metabolomics; Methylmalonyl-CoA Decarboxylase; Mice; Propionates; Propionic Acidemia

2021
A novel small molecule approach for the treatment of propionic and methylmalonic acidemias.
    Molecular genetics and metabolism, 2021, Volume: 133, Issue:1

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Citrates; Hepatocytes; Humans; Methylmalonyl-CoA Decarboxylase; Methylmalonyl-CoA Mutase; Propionic Acidemia; Small Molecule Libraries

2021
Identification of 2,2-Dimethylbutanoic Acid (HST5040), a Clinical Development Candidate for the Treatment of Propionic Acidemia and Methylmalonic Acidemia.
    Journal of medicinal chemistry, 2021, 04-22, Volume: 64, Issue:8

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Animals; Area Under Curve; Butyrates; Cells, Cultured; Dogs; Drug Evaluation, Preclinical; Half-Life; Hepatocytes; Humans; Mice; Models, Biological; Propionic Acidemia; Rats; ROC Curve; Structure-Activity Relationship

2021
Inter-relations between 3-hydroxypropionate and propionate metabolism in rat liver: relevance to disorders of propionyl-CoA metabolism.
    American journal of physiology. Endocrinology and metabolism, 2017, 10-01, Volume: 313, Issue:4

    Topics: Acyl Coenzyme A; Ammonium Compounds; Animals; Carbon Isotopes; Citrates; Citric Acid Cycle; Lactic Acid; Liver; Liver Transplantation; Male; Oxidation-Reduction; Propionates; Propionic Acidemia; Proteolysis; Rats; Rats, Sprague-Dawley

2017