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propionyl-coenzyme a and Electron Transport Chain Deficiencies, Mitochondrial

propionyl-coenzyme a has been researched along with Electron Transport Chain Deficiencies, Mitochondrial in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hinz, A; Hoffmann, GF; Hörster, F; Kölker, S; Mayatepek, E; Okun, JG; Sauer, S; Schwab, M; Smeitink, JA; Wolf, NI1
Brandt, U; Dröse, S; Hoffmann, GF; Kölker, S; Nijtmans, LG; Okun, JG; Rodenburg, RJ; Sauer, SW; Schwab, MA; Smeitink, JA; Ter Laak, H; van den Heuvel, LP1

Other Studies

2 other study(ies) available for propionyl-coenzyme a and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain.
    The Journal of biological chemistry, 2003, Nov-28, Volume: 278, Issue:48

    Topics: Acyl Coenzyme A; Adenosine Triphosphate; Aging; Amino Acid Metabolism, Inborn Errors; Animals; Cattle; Citrates; Citric Acid Cycle; Dose-Response Relationship, Drug; Electron Transport; Female; Hydrogen-Ion Concentration; Male; Malonates; Methylmalonic Acid; Mice; Mice, Inbred C57BL; Mitochondria; Mitochondrial Diseases; Muscles; Myocardium; Oxygen; Phosphorylation; Pyruvates; Spectrophotometry; Time Factors

2003
Secondary mitochondrial dysfunction in propionic aciduria: a pathogenic role for endogenous mitochondrial toxins.
    The Biochemical journal, 2006, Aug-15, Volume: 398, Issue:1

    Topics: Acetyl Coenzyme A; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Animals; Cattle; Energy Metabolism; Fatty Acids; Female; Fibroblasts; Humans; Infant, Newborn; Male; Mitochondrial Diseases; Oxidative Phosphorylation; Propionates; Pyruvate Dehydrogenase Complex; Quadriceps Muscle; Skin; Swine; Toxins, Biological

2006