Page last updated: 2024-10-20

propionic acid and Diseases, Metabolic

propionic acid has been researched along with Diseases, Metabolic in 4 studies

propionic acid : A short-chain saturated fatty acid comprising ethane attached to the carbon of a carboxy group.

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19901 (25.00)18.7374
1990's1 (25.00)18.2507
2000's2 (50.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Tuchman, M1
Caldovic, L1
Daikhin, Y1
Horyn, O1
Nissim, I2
Korson, M1
Burton, B1
Yudkoff, M1
Millington, DS1
Roe, CR1
Maltby, DA1
Shigematsu, Y1
Nakai, A1
Liu, YY1
Kikawa, Y1
Sudo, M1
Fujioka, M1
Yorifuji, T1
Muroi, J1
Uematsu, A1
Nakahata, T1
Egawa, H1
Tanaka, K1

Clinical Trials (1)

Trial Overview

TrialPhaseEnrollmentStudy TypeStart DateStatus
Increasing Ureagenesis in Inborn Errors of Metabolism With N-Carbamylglutamate[NCT01341379]Phase 20 participants (Actual)Interventional2010-12-31Withdrawn (stopped due to Lack of funding)
[information is prepared from clinicaltrials.gov, extracted Sep-2024]

Trials

1 trial available for propionic acid and Diseases, Metabolic

ArticleYear
N-carbamylglutamate markedly enhances ureagenesis in N-acetylglutamate deficiency and propionic acidemia as measured by isotopic incorporation and blood biomarkers.
    Pediatric research, 2008, Volume: 64, Issue:2

    Topics: Acetyl Coenzyme A; Adult; Amino Acids; Ammonia; Biomarkers; Carbon Dioxide; Carbon Isotopes; Child;

2008

Other Studies

3 other studies available for propionic acid and Diseases, Metabolic

ArticleYear
Application of high resolution fast atom bombardment and constant B/E ratio linked scanning to the identification and analysis of acylcarnitines in metabolic disease.
    Biomedical mass spectrometry, 1984, Volume: 11, Issue:5

    Topics: Acetylcarnitine; Acidosis; Carnitine; Humans; Magnetic Resonance Spectroscopy; Malonates; Mass Spect

1984
Free carnitine and short-chain acylcarnitines in cerebrospinal fluid of patients with disorders of propionate metabolism determined by fast atom bombardment and tandem mass spectrometry.
    Acta paediatrica Japonica : Overseas edition, 1994, Volume: 36, Issue:1

    Topics: Adolescent; Carnitine; Female; Humans; Infant; Mass Spectrometry; Metabolic Diseases; Propionates; S

1994
Living-related liver transplantation for neonatal-onset propionic acidemia.
    The Journal of pediatrics, 2000, Volume: 137, Issue:4

    Topics: Carboxy-Lyases; Female; Humans; Infant; Liver Transplantation; Metabolic Diseases; Methylmalonyl-CoA

2000