propionic acid has been researched along with Cardiomyopathies, Primary in 2 studies
propionic acid : A short-chain saturated fatty acid comprising ethane attached to the carbon of a carboxy group.
Excerpt | Relevance | Reference |
---|---|---|
"Propionic acidemia is caused by lack of propionyl-CoA carboxylase activity." | 7.96 | Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats. ( Amaral, AU; Castilho, RF; Cecatto, C; Roginski, AC; Wajner, A; Wajner, M; Wajner, SM, 2020) |
"Propionic acidemia is caused by lack of propionyl-CoA carboxylase activity." | 3.96 | Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats. ( Amaral, AU; Castilho, RF; Cecatto, C; Roginski, AC; Wajner, A; Wajner, M; Wajner, SM, 2020) |
"Propionic acidaemia (PA) is an autosomal recessive disease that results from deficiency of propionyl-CoA carboxylase (PCC)." | 1.35 | Unusual presentation of propionic acidaemia as isolated cardiomyopathy. ( Addonizio, LJ; Barshop, BA; Chung, WK; Lee, TM, 2009) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 1 (50.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 1 (50.00) | 2.80 |
Authors | Studies |
---|---|
Roginski, AC | 1 |
Wajner, A | 1 |
Cecatto, C | 1 |
Wajner, SM | 1 |
Castilho, RF | 1 |
Wajner, M | 1 |
Amaral, AU | 1 |
Lee, TM | 1 |
Addonizio, LJ | 1 |
Barshop, BA | 1 |
Chung, WK | 1 |
2 other studies available for propionic acid and Cardiomyopathies, Primary
Article | Year |
---|---|
Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats.
Topics: Animals; Calcium; Cardiomyopathies; Cell Fractionation; Cell Line; Energy Metabolism; Humans; Male; | 2020 |
Unusual presentation of propionic acidaemia as isolated cardiomyopathy.
Topics: Adolescent; Base Sequence; Cardiomyopathies; Heart Transplantation; Humans; Male; Methylmalonyl-CoA | 2009 |