propionic acid has been researched along with Acidemia Propionic in 8 studies
propionic acid : A short-chain saturated fatty acid comprising ethane attached to the carbon of a carboxy group.
| Excerpt | Relevance | Reference |
|---|---|---|
| "Propionic acidemia is caused by lack of propionyl-CoA carboxylase activity." | 7.96 | Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats. ( Amaral, AU; Castilho, RF; Cecatto, C; Roginski, AC; Wajner, A; Wajner, M; Wajner, SM, 2020) |
| "In this report we summarize our experience in prenatal diagnosis of propionic acidemia (PA) since 1987." | 7.72 | Prenatal diagnosis of propionic acidemia. ( Desviat, LR; Merinero, B; Pérez, B; Pérez-Cerdá, C; Rodríguez-Pombo, P; Ugarte, M, 2004) |
| "Propionic acidemia is caused by lack of propionyl-CoA carboxylase activity." | 3.96 | Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats. ( Amaral, AU; Castilho, RF; Cecatto, C; Roginski, AC; Wajner, A; Wajner, M; Wajner, SM, 2020) |
| "Propionate, 3-hydroxypropionate (3HP), methylcitrate, related compounds, and ammonium accumulate in body fluids of patients with disorders of propionyl-CoA metabolism, such as propionic acidemia." | 3.85 | Inter-relations between 3-hydroxypropionate and propionate metabolism in rat liver: relevance to disorders of propionyl-CoA metabolism. ( Brunengraber, H; Chapman, KA; Cline, GW; Han, Y; Hess, JP; Tochtrop, GP; Wilson, KA; Zhang, GF; Zhang, M, 2017) |
| "In this report we summarize our experience in prenatal diagnosis of propionic acidemia (PA) since 1987." | 3.72 | Prenatal diagnosis of propionic acidemia. ( Desviat, LR; Merinero, B; Pérez, B; Pérez-Cerdá, C; Rodríguez-Pombo, P; Ugarte, M, 2004) |
| "Propionic acid (PPA) is a ubiquitous short-chain fatty acid, which is a major fermentation product of the enteric microbiome." | 1.43 | Modulation of mitochondrial function by the microbiome metabolite propionic acid in autism and control cell lines. ( Bennuri, SC; Chacko, J; Delhey, L; Frye, RE; Kahler, SG; MacFabe, DF; Melnyk, S; Rose, S; Slattery, JC; Tippett, M; Wynne, R, 2016) |
| "Propionic acidaemia (PA) is an autosomal recessive disease that results from deficiency of propionyl-CoA carboxylase (PCC)." | 1.35 | Unusual presentation of propionic acidaemia as isolated cardiomyopathy. ( Addonizio, LJ; Barshop, BA; Chung, WK; Lee, TM, 2009) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 4 (50.00) | 29.6817 |
| 2010's | 3 (37.50) | 24.3611 |
| 2020's | 1 (12.50) | 2.80 |
| Authors | Studies |
|---|---|
| Roginski, AC | 1 |
| Wajner, A | 1 |
| Cecatto, C | 1 |
| Wajner, SM | 1 |
| Castilho, RF | 1 |
| Wajner, M | 1 |
| Amaral, AU | 1 |
| Wilson, KA | 1 |
| Han, Y | 1 |
| Zhang, M | 1 |
| Hess, JP | 1 |
| Chapman, KA | 1 |
| Cline, GW | 1 |
| Tochtrop, GP | 1 |
| Brunengraber, H | 1 |
| Zhang, GF | 1 |
| Frye, RE | 1 |
| Rose, S | 1 |
| Chacko, J | 1 |
| Wynne, R | 1 |
| Bennuri, SC | 1 |
| Slattery, JC | 1 |
| Tippett, M | 1 |
| Delhey, L | 1 |
| Melnyk, S | 1 |
| Kahler, SG | 1 |
| MacFabe, DF | 1 |
| Witters, P | 1 |
| Debbold, E | 1 |
| Crivelly, K | 1 |
| Vande Kerckhove, K | 1 |
| Corthouts, K | 1 |
| Debbold, B | 1 |
| Andersson, H | 1 |
| Vannieuwenborg, L | 1 |
| Geuens, S | 1 |
| Baumgartner, M | 1 |
| Kozicz, T | 1 |
| Settles, L | 1 |
| Morava, E | 1 |
| Lee, TM | 1 |
| Addonizio, LJ | 1 |
| Barshop, BA | 1 |
| Chung, WK | 1 |
| Al-Hassnan, ZN | 1 |
| Boyadjiev, SA | 1 |
| Praphanphoj, V | 1 |
| Hamosh, A | 1 |
| Braverman, NE | 1 |
| Thomas, GH | 1 |
| Geraghty, MT | 1 |
| Yorifuji, T | 1 |
| Kawai, M | 1 |
| Mamada, M | 1 |
| Kurokawa, K | 1 |
| Egawa, H | 1 |
| Shigematsu, Y | 1 |
| Kohno, Y | 1 |
| Tanaka, K | 1 |
| Nakahata, T | 1 |
| Pérez-Cerdá, C | 1 |
| Pérez, B | 1 |
| Merinero, B | 1 |
| Desviat, LR | 1 |
| Rodríguez-Pombo, P | 1 |
| Ugarte, M | 1 |
8 other studies available for propionic acid and Acidemia Propionic
| Article | Year |
|---|---|
Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats.
Topics: Animals; Calcium; Cardiomyopathies; Cell Fractionation; Cell Line; Energy Metabolism; Humans; Male; | 2020 |
Inter-relations between 3-hydroxypropionate and propionate metabolism in rat liver: relevance to disorders of propionyl-CoA metabolism.
Topics: Acyl Coenzyme A; Ammonium Compounds; Animals; Carbon Isotopes; Citrates; Citric Acid Cycle; Lactic A | 2017 |
Modulation of mitochondrial function by the microbiome metabolite propionic acid in autism and control cell lines.
Topics: Autism Spectrum Disorder; Case-Control Studies; Cell Line; Child; Gastrointestinal Microbiome; Human | 2016 |
Autism in patients with propionic acidemia.
Topics: Adolescent; Adult; Animals; Autism Spectrum Disorder; Child; Female; Humans; Infant, Newborn; Leucin | 2016 |
Unusual presentation of propionic acidaemia as isolated cardiomyopathy.
Topics: Adolescent; Base Sequence; Cardiomyopathies; Heart Transplantation; Humans; Male; Methylmalonyl-CoA | 2009 |
The relationship of plasma glutamine to ammonium and of glycine to acid-base balance in propionic acidaemia.
Topics: Acid-Base Equilibrium; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biomarkers; Diet, Protein | 2003 |
Living-donor liver transplantation for propionic acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Child Development; Child, Preschool; Female; Humans; In | 2004 |
Prenatal diagnosis of propionic acidemia.
Topics: Amniotic Fluid; Cells, Cultured; Chorionic Villi; Chromones; DNA Mutational Analysis; Female; Humans | 2004 |