proline and Muscular Dystrophies

proline has been researched along with Muscular Dystrophies in 9 studies

Research

Studies (9)

TimeframeStudies, this research(%)All Research%
pre-19905 (55.56)18.7374
1990's2 (22.22)18.2507
2000's1 (11.11)29.6817
2010's1 (11.11)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Balch, F; Carlson, CG; Henley, S; Kurz, J; Miles, M; Plummer, R; Rhodes, JA; Shinn, GL; Siegel, AS; Zimmerman, A1
Allard, B; Berthier, C; Couchoux, H; Jacquemond, V; Legrand, C1
Ionasescu, R; Ionasescu, V; Massimini, G; Sandra, A2
Brown, CA; Ellis, JA; Kendrick-Jones, J; Yates, JR1
Aksmanovic, VM; Bagshaw, J; Coomber, E; Ellis, JA; Kendrick-Jones, J; McMahon, R; Morrison, PJ; Whittaker, JL; Yates, JR1
Burmeister, L; Ionasescu, R; Ionasescu, V; Lara-Braud, C; Zellweger, H1
Conway, TW; Ionasescu, V; Zellweger, H1
Kibrick, AC; Milhorat, AT1

Other Studies

9 other study(ies) available for proline and Muscular Dystrophies

ArticleYear
The influence of passive stretch and NF-κB inhibitors on the morphology of dystrophic muscle fibers.
    Anatomical record (Hoboken, N.J. : 2007), 2011, Volume: 294, Issue:1

    Topics: Animals; Cell Membrane; Mice; Mice, Inbred C57BL; Mice, Inbred mdx; Muscle Fibers, Skeletal; Muscle Stretching Exercises; Muscular Dystrophies; NF-kappa B; Proline; Thiocarbamates; Ursodeoxycholic Acid

2011
Loss of caveolin-3 induced by the dystrophy-associated P104L mutation impairs L-type calcium channel function in mouse skeletal muscle cells.
    The Journal of physiology, 2007, May-01, Volume: 580, Issue:Pt.3

    Topics: Animals; Calcium Channels, L-Type; Caveolin 3; Cells, Cultured; Electric Conductivity; Embryo, Mammalian; Leucine; Mice; Muscle Cells; Muscle Fibers, Skeletal; Muscle, Skeletal; Muscular Dystrophies; Mutation; Proline; Tissue Distribution

2007
Collagen synthesis by Duchenne myogenic clones: pathogenic implications for the disease.
    American journal of medical genetics, 1982, Volume: 11, Issue:3

    Topics: Child, Preschool; Clone Cells; Collagen; Creatine Kinase; Humans; Hydroxyproline; Isoenzymes; Male; Muscles; Muscular Dystrophies; Myofibrils; Proline

1982
Collagen synthesis by Duchenne myogenic clones: pathogenic implications for the disease.
    Birth defects original article series, 1982, Volume: 18, Issue:3B

    Topics: Cells, Cultured; Child, Preschool; Clone Cells; Collagen; Creatine Kinase; DNA; Humans; Hydroxyproline; Male; Muscle Proteins; Muscles; Muscular Dystrophies; Proline

1982
Changes at P183 of emerin weaken its protein-protein interactions resulting in X-linked Emery-Dreifuss muscular dystrophy.
    Human genetics, 1999, Volume: 104, Issue:3

    Topics: Adult; Amino Acid Substitution; Cell Line, Transformed; DNA Mutational Analysis; Genetic Linkage; Genotype; Humans; Immunoblotting; Male; Membrane Proteins; Membranes; Muscular Dystrophies; Muscular Dystrophy, Emery-Dreifuss; Mutation; Nuclear Proteins; Phenotype; Phosphorylation; Proline; Protein Binding; Thymopoietins; X Chromosome

1999
Genotype-phenotype analysis in X-linked Emery-Dreifuss muscular dystrophy and identification of a missense mutation associated with a milder phenotype.
    Neuromuscular disorders : NMD, 1999, Volume: 9, Issue:3

    Topics: Amino Acid Substitution; DNA; DNA Mutational Analysis; Family Health; Female; Genetic Linkage; Genotype; Humans; Male; Membrane Proteins; Muscular Dystrophies; Muscular Dystrophy, Emery-Dreifuss; Mutation, Missense; Nuclear Proteins; Pedigree; Phenotype; Proline; Threonine; Thymopoietins; X Chromosome

1999
Fibroblast cultures in Duchenne muscular dystrophy. Alterations in synthesis and secretion of collagen and noncollagen proteins.
    Acta neurologica Scandinavica, 1977, Volume: 55, Issue:5

    Topics: Cells, Cultured; Collagen; Culture Media; Electrophoresis, Polyacrylamide Gel; Female; Fibroblasts; Humans; Male; Muscle Proteins; Muscular Dystrophies; Proline; Protein Biosynthesis; Proteins

1977
Ribosomal protein synthesis in Duchenne muscular dystrophy.
    Archives of biochemistry and biophysics, 1971, Volume: 144, Issue:1

    Topics: Amino Acids; Carbon Isotopes; Cell Fractionation; Centrifugation, Density Gradient; Chemical Precipitation; Child; Collagen; Glycine; Humans; Infant; Macromolecular Substances; Male; Muscle Proteins; Muscles; Muscular Dystrophies; Proline; Ribosomes; Ultracentrifugation

1971
Glycylprolylhydroxyproline: methods for its quantitative determination in urine and blood serum.
    Biochemical medicine, 1970, Volume: 4, Issue:2

    Topics: Adult; Carbon Isotopes; Chemical Phenomena; Chemistry; Chromatography, Ion Exchange; Chromatography, Paper; Electrophoresis, Paper; Female; Glycine; Humans; Hydroxyproline; Male; Methods; Middle Aged; Muscular Dystrophies; Peptides; Piperazines; Proline

1970