proline and Hyperoxaluria, Primary

proline has been researched along with Hyperoxaluria, Primary in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (50.00)18.2507
2000's0 (0.00)29.6817
2010's1 (50.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Holmes, RP; Johnson, LC; Jönsson, TJ; Lowther, WT; Parsonage, D; Summitt, CB1
Danpure, CJ; Leiper, JM; Oatey, PB1

Other Studies

2 other study(ies) available for proline and Hyperoxaluria, Primary

ArticleYear
Proline dehydrogenase 2 (PRODH2) is a hydroxyproline dehydrogenase (HYPDH) and molecular target for treating primary hyperoxaluria.
    The Biochemical journal, 2015, Mar-01, Volume: 466, Issue:2

    Topics: Biocatalysis; Catalytic Domain; Enzyme Inhibitors; Flavin-Adenine Dinucleotide; Flavoproteins; Furans; Humans; Hydroxyproline; Hyperoxaluria, Primary; Ligands; Models, Molecular; Mutant Proteins; Peptide Fragments; Proline; Proline Oxidase; Protein Conformation; Recombinant Proteins; Substrate Specificity; Terminology as Topic; Ubiquinone

2015
Inhibition of alanine:glyoxylate aminotransferase 1 dimerization is a prerequisite for its peroxisome-to-mitochondrion mistargeting in primary hyperoxaluria type 1.
    The Journal of cell biology, 1996, Volume: 135, Issue:4

    Topics: Alanine Transaminase; Animals; Arginine; Biological Transport; COS Cells; Dimerization; Glycine; Humans; Hyperoxaluria, Primary; Leucine; Liver; Microbodies; Mitochondria; Point Mutation; Polymorphism, Genetic; Proline; Transaminases

1996