proline has been researched along with Cystinosis in 10 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 9 (90.00) | 18.7374 |
1990's | 1 (10.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Meister, A; Wellner, D | 1 |
D'Apice, AJ; Hooke, D; Kincaid-Smith, P; Walker, RG; Walter, NM; Whitworth, JA | 1 |
Milner, RD; Wirdnam, PK | 1 |
Segal, S; States, B | 1 |
Greco, GM; Magli, A | 1 |
Benson, L; Foreman, JW | 1 |
Ampola, MG | 1 |
Kroll, S; Toussaint, W; Zebisch, P | 2 |
Gjessing, LR; Seip, M; Vellan, EJ | 1 |
3 review(s) available for proline and Cystinosis
Article | Year |
---|---|
A survey of inborn errors of amino acid metabolism and transport in man.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Amino Acids, Branched-Chain; Biological Transport; Cystinosis; Female; Glutathione; Glycine; Homocystinuria; Humans; Hydroxyproline; Infant; Infant, Newborn; Lysine; Maple Syrup Urine Disease; Phenylalanine; Proline; Serine; Tyrosine; Urea; Valine | 1981 |
[Eye manifestations of amino acid disorders].
Topics: Alanine; Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Child; Cystinosis; Cystinuria; Eye Diseases; Eye Manifestations; Glycine; Hartnup Disease; Hepatolenticular Degeneration; Homocystinuria; Humans; Lysine; Oculocerebrorenal Syndrome; Oxidoreductases; Phenylketonurias; Proline; Pyruvates | 1978 |
Phenylketonuria and other disorders of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; Cystinosis; Cystinuria; Diet Therapy; Dietary Proteins; Family; Female; Hartnup Disease; Histidine; Homocystinuria; Humans; Hyperglycemia; Infant; Infant, Newborn; Lysine; Maple Syrup Urine Disease; Ornithine; Phenylketonurias; Pregnancy; Proline; Tyrosine | 1973 |
7 other study(ies) available for proline and Cystinosis
Article | Year |
---|---|
Repeated renal failure with use of captopril in a cystinotic renal allograft recipient.
Topics: Acute Kidney Injury; Captopril; Child; Cystinosis; Female; Humans; Kidney Transplantation; Proline; Recurrence | 1982 |
The pancreatic beta cell fraction in children with errors of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Cystinosis; Homocystinuria; Humans; Infant; Infant, Newborn; Islets of Langerhans; Maple Syrup Urine Disease; Methionine; Phenylketonurias; Proline; Tyrosine | 1982 |
Effect of cysteamine on amino acid pools of cultured fibroblasts and the uptake of L-proline.
Topics: Amino Acids; Biological Transport; Cell Line; Cysteamine; Cystinosis; Fibroblasts; Humans; Proline | 1982 |
Effect of cystine loading and cystine dimethylester on renal brushborder membrane transport.
Topics: Animals; Biological Transport; Cells, Cultured; Cystine; Cystinosis; Fanconi Syndrome; Kidney Tubules; Male; Microvilli; Proline; Rats; Rats, Inbred Strains | 1990 |
[Hereditary amino acid metabolism disorders. Indications for early diagnosis].
Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Cystathionine; Cystinosis; Diagnosis, Differential; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Infant; Infant, Newborn; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine | 1972 |
[Diagnosis of inborn amino acid metabolism errors. Important symptoms and laboratory methods].
Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Clinical Laboratory Techniques; Cystathionine; Cystinosis; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine | 1972 |
Hair amino acids in cystinosis, homocystinuria, Fölling's disease and tyrosinosis.
Topics: Amino Acids; Autoanalysis; Citrulline; Cystine; Cystinosis; Female; Hair; Homocysteine; Homocystinuria; Humans; In Vitro Techniques; Male; Metabolic Diseases; Methionine; Methods; Phenylalanine; Phenylketonurias; Proline; Tyrosine | 1969 |