proline and Cystic Fibrosis

proline has been researched along with Cystic Fibrosis in 13 studies

Research

Studies (13)

TimeframeStudies, this research(%)All Research%
pre-19902 (15.38)18.7374
1990's4 (30.77)18.2507
2000's2 (15.38)29.6817
2010's2 (15.38)24.3611
2020's3 (23.08)2.80

Authors

AuthorsStudies
Almond, LM; Beringer, PM; Chung, PS; Hong, E; Rao, AP1
Altenbach, RJ; Balut, C; Bogdan, A; Fan, Y; Gao, W; Gfesser, GA; Greszler, S; Koenig, JR; Kym, P; Liu, B; Manelli, A; Scanio, MJC; Schrimpf, M; Searle, XB; Singh, A; Swensen, AM; Tse, C; Vortherms, T; Wang, X; Yong, H; Zhao, G1
Alton, EWFW; Blalock, JE; Brown, S; Bush, A; Davies, JC; Gaggar, A; Hilliard, TN; Jackson, PL; Lloyd, CM; Mc Fie, M; Patel, DF; Pyle, CJ; Regamey, N; Short, C; Snelgrove, RJ; Tan, HL; Thursfield, R; Turnbull, AR1
Cutello, S; Di Dio, G; La Rosa, M; Leonardi, S; Parisi, GF; Rotolo, N1
Britz-McKibbin, P; Finan, TM; Gavina, JM; White, CE1
GOULD, BS; SHWACHMAN, H1
Dötsch, J; Korbmacher, C; Kraus, C; Naehrlich, L; Rauh, R; Reis, A1
Blalock, JE; Clancy, JP; Gaggar, A; Jackson, PL; McQuaid, DB; Noerager, BD; O'Reilly, PJ; Rowe, SM1
Ishihara, H; Sheppard, DN; Travis, SM; Welsh, MJ1
Akcakaya, N; Apak, M; Camcioglu, Y; Cokugras, H; Gokgoz, N; Kayserili, H; Kirdar, B; Onay, T; Topaloglu, O; Tsui, LC; Zielenski, J1
Bonduelle, M; Dab, I; Liebaers, I; Lissens, W; Malfroot, A1
Hodson, ME; Pitt, TL; Taylor, RF1
Ammitzbøll, T; Espersen, F; Pedersen, SS; Schiøler, H1

Other Studies

13 other study(ies) available for proline and Cystic Fibrosis

ArticleYear
Physiologically-Based Pharmacokinetic-Led Guidance for Patients With Cystic Fibrosis Taking Elexacaftor-Tezacaftor-Ivacaftor With Nirmatrelvir-Ritonavir for the Treatment of COVID-19.
    Clinical pharmacology and therapeutics, 2022, Volume: 111, Issue:6

    Topics: Aminophenols; Benzodioxoles; Chloride Channel Agonists; COVID-19 Drug Treatment; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytochrome P-450 CYP3A; Drug Combinations; Drug Interactions; Humans; Indoles; Lactams; Leucine; Mutation; Nitriles; Proline; Pyrazoles; Pyridines; Pyrrolidines; Quinolines; Quinolones; Ritonavir

2022
Discovery and SAR of 4-aminopyrrolidine-2-carboxylic acid correctors of CFTR for the treatment of cystic fibrosis.
    Bioorganic & medicinal chemistry letters, 2022, 09-15, Volume: 72

    Topics: Benzodioxoles; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Mutation; Proline; Structure-Activity Relationship

2022
Abnormal pro-gly-pro pathway and airway neutrophilia in pediatric cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2020, Volume: 19, Issue:1

    Topics: Airway Remodeling; Bronchoalveolar Lavage Fluid; Bronchoscopy; Chemotaxis, Leukocyte; Child; Cystic Fibrosis; Female; Humans; Infant, Newborn; Inflammation; Leukocyte Elastase; Male; Matrix Metalloproteinase 9; Neutrophils; Oligopeptides; Proline; Prolyl Oligopeptidases; Sputum

2020
Phenotypic expression of the p.Leu1077Pro CFTR mutation in Sicilian cystic fibrosis patients.
    BMC research notes, 2013, Nov-13, Volume: 6

    Topics: Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Gene Expression Regulation; Genotype; Heterozygote; Humans; Leucine; Male; Mutation; Phenotype; Proline; Pseudomonas aeruginosa; Pseudomonas Infections; Sicily; Young Adult

2013
Determination of 4-hydroxyproline-2-epimerase activity by capillary electrophoresis: A stereoselective platform for inhibitor screening of amino acid isomerases.
    Electrophoresis, 2010, Volume: 31, Issue:16

    Topics: Amino Acid Isomerases; Bacterial Proteins; Cystic Fibrosis; Electrophoresis, Capillary; Enzyme Inhibitors; Humans; Hydroxyproline; Kinetics; Proline; Pseudomonas aeruginosa; Sensitivity and Specificity

2010
Studies in cystic fibrosis; determination of plasma proline following protein feeding as a diagnostic test for pancreatic insufficiency.
    A.M.A. journal of diseases of children, 1956, Volume: 91, Issue:6

    Topics: Blood; Cystic Fibrosis; Diagnostic Tests, Routine; Disease; Exocrine Pancreatic Insufficiency; Humans; Pancreas; Pancreatic Diseases; Proline

1956
Functional characterization of a novel CFTR mutation P67S identified in a patient with atypical cystic fibrosis.
    Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology, 2007, Volume: 19, Issue:5-6

    Topics: Action Potentials; Adolescent; Amino Acid Substitution; Base Sequence; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Humans; Molecular Sequence Data; Proline; Serine

2007
A novel proteolytic cascade generates an extracellular matrix-derived chemoattractant in chronic neutrophilic inflammation.
    Journal of immunology (Baltimore, Md. : 1950), 2008, Apr-15, Volume: 180, Issue:8

    Topics: Animals; Chemotactic Factors; Chemotaxis, Leukocyte; Chronic Disease; Cystic Fibrosis; Extracellular Matrix; Extracellular Matrix Proteins; Humans; Inflammation; Matrix Metalloproteinase 8; Matrix Metalloproteinase 9; Mice; Neutrophil Activation; Neutrophils; Oligopeptides; Proline; Prolyl Oligopeptidases; Receptors, Interleukin-8A; Receptors, Interleukin-8B; Serine Endopeptidases; Sputum

2008
Contribution of proline residues in the membrane-spanning domains of cystic fibrosis transmembrane conductance regulator to chloride channel function.
    The Journal of biological chemistry, 1996, Jun-21, Volume: 271, Issue:25

    Topics: Adenosine Triphosphate; Amino Acid Sequence; Chloride Channels; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Electrophysiology; HeLa Cells; Humans; Membrane Potentials; Models, Structural; Point Mutation; Proline; Protein Structure, Secondary; Recombinant Proteins

1996
Analysis of the CFTR gene in Turkish cystic fibrosis patients: identification of three novel mutations (3172delAC, P1013L and M1028I).
    Human genetics, 1998, Volume: 102, Issue:2

    Topics: Adenine; Amino Acid Substitution; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytosine; Frameshift Mutation; Humans; Isoleucine; Leucine; Methionine; Mutation; Polymorphism, Genetic; Proline; Sequence Deletion; Turkey

1998
A serine to proline substitution (S1255P) in the second nucleotide binding fold of the cystic fibrosis gene.
    Human molecular genetics, 1992, Volume: 1, Issue:6

    Topics: Adenosine Triphosphate; Base Sequence; Binding Sites; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Exons; Gene Frequency; Humans; Infant, Newborn; Male; Membrane Proteins; Point Mutation; Polymerase Chain Reaction; Proline; Serine

1992
Auxotrophy of Pseudomonas aeruginosa in cystic fibrosis.
    FEMS microbiology letters, 1992, May-01, Volume: 71, Issue:3

    Topics: Amino Acids; Arginine; Bronchiectasis; Cystic Fibrosis; Humans; Methionine; Proline; Pseudomonas aeruginosa; Sputum; Thiamine

1992
Excretion of urinary collagen metabolites correlates to severity of pulmonary disease in cystic fibrosis.
    Acta paediatrica Scandinavica, 1988, Volume: 77, Issue:6

    Topics: Adolescent; Adult; Bronchitis; Cystic Fibrosis; Female; Forced Expiratory Volume; Humans; Hydroxylysine; Hydroxyproline; Male; Pneumonia; Proline; Pseudomonas aeruginosa; Pseudomonas Infections

1988