proline has been researched along with Amyloidosis in 22 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (13.64) | 18.7374 |
1990's | 5 (22.73) | 18.2507 |
2000's | 8 (36.36) | 29.6817 |
2010's | 4 (18.18) | 24.3611 |
2020's | 2 (9.09) | 2.80 |
Authors | Studies |
---|---|
Berk, JL; Burks, EJ; Chen, H; Chiu, A; Choate, LA; Connors, LH; Cuddy, SAM; Cui, H; Dasari, S; Gibson, VM; Hu, Y; Joshi, T; Klimtchuk, ES; McPhail, ED; Nedelkov, D; Prokaeva, T; Sanchorawala, V; Siddiqi, O; Spencer, B | 1 |
Cappelli, C; Delbarba, A; Di Lodovico, E; Facchetti, F; Facondo, P; Ferlin, A; Fisogni, S; Izzi, C; Maffezzoni, F; Pezzaioli, LC; Scolari, F | 1 |
Kelly, JW; Morgan, GJ; Usher, GA | 1 |
Hilvert, D; Torbeev, VY | 1 |
Bellotti, V; Chen, W; Clatworthy, IR; Gillmore, JD; Giorgetti, S; Hawkins, PN; Mangione, PP; Marchese, L; Marcoux, J; Monti, M; Pepys, MB; Porcari, M; Porcari, R; Pucci, P; Raimondi, S; Relini, A; Robinson, CV; Serpell, LC; Stoppini, M; Taylor, GW; Tennent, GA; Wood, SP | 1 |
Frosch, MP; Greenberg, SM; Nakagawa, K; Sheikh, SI; Snuderl, M | 1 |
Barbiroli, A; Bellotti, V; Bolognesi, M; Bonomi, F; Colombo, M; Giorgetti, S; Grandori, R; Raimondi, S; Ricagno, S; Santambrogio, C | 1 |
Fernandes, R; Palha, JA; Saraiva, MJ; Sousa, MM; Taboada, A; Vieira, P | 1 |
PERKOFF, GT | 1 |
Coriu, D; Dispenzieri, A; Murphy, CL; Solomon, A; Stevens, FJ; Wang, S; Weiss, DT | 1 |
Arbustini, E; Bellotti, V; Bergonzi, C; Calabresi, L; Donadei, S; Giorgetti, S; Gregorini, G; Marciano, S; Merlini, G; Obici, L; Palladini, G; Perfetti, V; Scolari, F; Verga, L | 1 |
Affeldt, JA; Aldave, AJ; Gutmark, JG; Klintworth, GK; Meallet, MA; Rao, NA; Small, KW; Udar, N; Yellore, VS | 1 |
Colón, W; Kelly, JW; Lai, Z; McCutchen, SL; Miroy, GJ | 1 |
Higuchi, K; Naiki, H; Nakakuki, K; Shimada, A; Takeda, T | 1 |
Ferlini, A; Forabosco, A; Gobbi, P; Mencucci, R; Michelucci, R; Plasmati, R; Salvi, F; Salvi, G; Santangelo, M; Volpe, R | 1 |
Damas, AM; Merlini, G; Saraiva, MJ; Sebastião, MP | 1 |
Fast, J; Håkansson, M; Linse, S; Svensson, A | 1 |
Fersht, AR; Galani, D; Perrett, S | 1 |
Buxbaum, JN; Jacobson, DR; Kane, I; McFarlin, DE | 1 |
Almeida, MR; Altland, K; Costa, PP; Gawinowicz, M; Moreira, P; Rauh, S; Saraiva, MJ | 1 |
Braun, HJ | 1 |
Kissane, JM | 1 |
3 review(s) available for proline and Amyloidosis
Article | Year |
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FAMILIAL ASPECTS OF DIFFUSE RENAL DISEASES.
Topics: Amyloidosis; Angiokeratoma; Blood; Congenital Abnormalities; Deafness; Genetics, Medical; Hematuria; Humans; Hydroxyproline; Kidney; Kidney Diseases; Nephritis; Paralyses, Familial Periodic; Polycystic Kidney Diseases; Proline; Skin Neoplasms; Urticaria | 1964 |
[Properties of the amyloid and views on the pathogenesis of amyloidosis].
Topics: Amino Acid Sequence; Amyloid; Amyloidosis; Animals; Antigens; Birefringence; Caseins; Glycosaminoglycans; Humans; Hydroxyproline; Lipids; Molecular Conformation; Proline; Solubility; Staining and Labeling; Tryptophan | 1972 |
Hereditary disorders of the kidney. II. Hereditary nephropathies.
Topics: Adolescent; Adult; Aldosterone; Amyloidosis; Bone Resorption; Child; Child, Preschool; Female; Glomerulonephritis; Humans; Infant; Juxtaglomerular Apparatus; Kidney; Kidney Calculi; Kidney Diseases; Kidney Neoplasms; Laurence-Moon Syndrome; Lipodystrophy; Male; Metabolic Diseases; Middle Aged; Muscular Atrophy; Nail-Patella Syndrome; Nephritis; Nephrotic Syndrome; Potassium; Proline; Renal Tubular Transport, Inborn Errors | 1973 |
19 other study(ies) available for proline and Amyloidosis
Article | Year |
---|---|
A novel substitution of proline (P32L) destabilises β2-microglobulin inducing hereditary systemic amyloidosis.
Topics: Amyloid; Amyloidosis; Amyloidosis, Familial; beta 2-Microglobulin; Humans; Proline | 2022 |
Testicular Involvement is a Hallmark of Apo A-I Leu75Pro Mutation Amyloidosis.
Topics: Adolescent; Adult; Aged; Aged, 80 and over; Amino Acid Substitution; Amyloidosis; Apolipoprotein A-I; Cohort Studies; Databases, Factual; Genetic Predisposition to Disease; Humans; Italy; Leucine; Male; Middle Aged; Mutation, Missense; Proline; Retrospective Studies; Testicular Diseases; Testis; Young Adult | 2020 |
Incomplete Refolding of Antibody Light Chains to Non-Native, Protease-Sensitive Conformations Leads to Aggregation: A Mechanism of Amyloidogenesis in Patients?
Topics: Alanine; Amyloid; Amyloidosis; Circular Dichroism; Endopeptidases; Humans; Immunoglobulin Light Chains; Kinetics; Models, Molecular; Proline; Protein Aggregates; Protein Conformation; Protein Folding; Thermodynamics | 2017 |
Both the cis-trans equilibrium and isomerization dynamics of a single proline amide modulate β2-microglobulin amyloid assembly.
Topics: Amides; Amyloidosis; beta 2-Microglobulin; Chromatography, Gel; Chromatography, High Pressure Liquid; Circular Dichroism; Dialysis; Humans; Isomerism; Magnetic Resonance Spectroscopy; Models, Molecular; Molecular Structure; Proline; Protein Conformation; Solubility | 2013 |
Proteolytic cleavage of Ser52Pro variant transthyretin triggers its amyloid fibrillogenesis.
Topics: Amino Acid Sequence; Amyloid; Amyloidosis; Crystallography, X-Ray; Humans; Hydrogen Bonding; Molecular Conformation; Molecular Sequence Data; Phenotype; Prealbumin; Proline; Proteolysis; Serine | 2014 |
A new Thr49Pro transthyretin gene mutation associated with leptomeningeal amyloidosis.
Topics: Amyloidosis; DNA Mutational Analysis; Humans; Magnetic Resonance Imaging; Male; Meninges; Middle Aged; Mutation; Prealbumin; Proline; Threonine | 2008 |
The effects of an ideal beta-turn on beta-2 microglobulin fold stability.
Topics: Alzheimer Disease; Amino Acid Substitution; Amyloid; Amyloidosis; beta 2-Microglobulin; Crystallography, X-Ray; Humans; Mutation; Proline; Protein Folding; Protein Stability; Protein Structure, Secondary | 2011 |
Evidence for early cytotoxic aggregates in transgenic mice for human transthyretin Leu55Pro.
Topics: Amyloid; Amyloid Neuropathies, Familial; Amyloidosis; Animals; Coloring Agents; Congo Red; Genetic Vectors; Humans; Immunohistochemistry; Intestine, Small; Leucine; Mice; Mice, Inbred C57BL; Mice, Knockout; Mice, Transgenic; Microscopy, Immunoelectron; Mutation; Oxidative Stress; Prealbumin; Proline; RNA, Messenger; Skin | 2002 |
Hepatic amyloidosis resulting from deposition of the apolipoprotein A-I variant Leu75Pro.
Topics: Amino Acid Sequence; Amino Acid Substitution; Amyloidosis; Apolipoprotein A-I; DNA; Female; Genetic Variation; Humans; Leucine; Liver; Liver Diseases; Mass Spectrometry; Middle Aged; Molecular Sequence Data; Mutation; Plasma; Polymorphism, Restriction Fragment Length; Proline; Sequence Homology, Amino Acid | 2003 |
Liver biopsy discloses a new apolipoprotein A-I hereditary amyloidosis in several unrelated Italian families.
Topics: Aged; Amyloidosis; Apolipoprotein A-I; Biopsy; DNA; Female; Heterozygote; Humans; Italy; Leucine; Liver; Male; Microscopy, Immunoelectron; Middle Aged; Mutation; Pedigree; Proline | 2004 |
Lattice corneal dystrophy associated with the Ala546Asp and Pro551Gln missense changes in the TGFBI gene.
Topics: Adult; Alanine; Amyloid; Amyloidosis; Aspartic Acid; Cornea; Corneal Dystrophies, Hereditary; DNA Mutational Analysis; Exons; Extracellular Matrix Proteins; Female; Glutamine; Haplotypes; Humans; Mutation, Missense; Pedigree; Proline; Transforming Growth Factor beta | 2004 |
Comparison of lethal and nonlethal transthyretin variants and their relationship to amyloid disease.
Topics: Amino Acid Sequence; Amyloidosis; Base Sequence; DNA Primers; Electrophoresis, Polyacrylamide Gel; Genes, Lethal; Genetic Variation; Humans; Hydrogen-Ion Concentration; Kinetics; Leucine; Lysosomes; Macromolecular Substances; Models, Molecular; Molecular Sequence Data; Mutagenesis, Site-Directed; Point Mutation; Prealbumin; Proline; Protein Denaturation; Protein Structure, Secondary; Recombinant Proteins; Structure-Activity Relationship | 1995 |
Genetic analysis of murine senile amyloidosis.
Topics: Aging; Amyloidosis; Animals; Dementia; DNA; Genotype; Glutamine; Mice; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Proline; Protein Precursors; Serum Amyloid A Protein; Spectrometry, Fluorescence | 1993 |
Transthyretin-related TTR hereditary amyloidosis of the vitreous body. Clinical and molecular characterization in two Italian families.
Topics: Adult; Aged; Alanine; Amyloidosis; Eye Diseases; Female; Humans; Lens Diseases; Male; Middle Aged; Mutation; Pedigree; Prealbumin; Proline; Ultrasonography; Vitreous Body | 1993 |
The molecular interaction of 4'-iodo-4'-deoxydoxorubicin with Leu-55Pro transthyretin 'amyloid-like' oligomer leading to disaggregation.
Topics: Amino Acid Substitution; Amyloidosis; Benzothiazoles; Crystallization; Doxorubicin; Humans; Iodine; Leucine; Models, Molecular; Prealbumin; Proline; Protein Binding; Protein Structure, Secondary; Thiazoles; X-Ray Diffraction | 2000 |
An extended hydrophobic core induces EF-hand swapping.
Topics: Amino Acid Substitution; Amyloidosis; Apoproteins; Binding Sites; Calbindins; Calcium; Chromatography, Gel; Crystallography, X-Ray; Dimerization; EF Hand Motifs; Kinetics; Methionine; Models, Molecular; Mutation; Proline; Protein Structure, Quaternary; Protein Structure, Tertiary; S100 Calcium Binding Protein G; Structure-Activity Relationship; Thermodynamics | 2001 |
Folding of the yeast prion protein Ure2: kinetic evidence for folding and unfolding intermediates.
Topics: Amyloidosis; Dimerization; Fluorescence; Glutathione Peroxidase; Guanidine; Isomerism; Kinetics; Models, Biological; Mutation; Prions; Proline; Protein Denaturation; Protein Folding; Protein Renaturation; Protein Structure, Tertiary; Saccharomyces cerevisiae; Saccharomyces cerevisiae Proteins; Solutions; Thermodynamics; Water | 2002 |
Transthyretin Pro55, a variant associated with early-onset, aggressive, diffuse amyloidosis with cardiac and neurologic involvement.
Topics: Amyloidosis; Base Sequence; Cardiomyopathies; Cell Line, Transformed; Female; Humans; Male; Molecular Sequence Data; Mutation; Nucleic Acid Conformation; Pedigree; Peripheral Nervous System Diseases; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Prealbumin; Proline | 1992 |
Characterization of a basic transthyretin variant--TTR Arg 102--in the German population.
Topics: Amyloidosis; Arginine; Base Sequence; Exons; Female; Genetic Testing; Genetic Variation; Germany; Humans; Molecular Sequence Data; Mutation; Peptide Mapping; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Prealbumin; Pregnancy; Proline | 1991 |