pregnanetriol has been researched along with Congenital Adrenal Hyperplasia in 161 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 141 (87.58) | 18.7374 |
1990's | 7 (4.35) | 18.2507 |
2000's | 4 (2.48) | 29.6817 |
2010's | 8 (4.97) | 24.3611 |
2020's | 1 (0.62) | 2.80 |
Authors | Studies |
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Hamajima, T; Hasegawa, Y; Itonaga, T; Izawa, M | 1 |
Beuschlein, F; Greifenstein, A; Krone, N; Reincke, M; Reisch, N; Rottenkolber, M; Schmidt, H; Schwarz, HP | 1 |
Fukami, M; Hasegawa, T; Hayashi, M; Homma, K; Kataoka, Y; Kato, F; Ogata, T; Oiso, Y; Sasano, H; Sugimura, Y; Tanaka, H | 1 |
Boettcher, C; Hartmann, MF; Kamrath, C; Wudy, SA | 1 |
Boettcher, C; Hartmann, MF; Kamrath, C; Wudy, SA; Zimmer, KP | 1 |
Arlt, W; Hughes, BA; Jones, CM; Krone, N; Mallappa, A; Merke, DP; Nikolaou, N; O'Neil, DM; Reisch, N; Ross, RJ; Storbeck, KH; Tomlinson, JW; Whitaker, MJ | 1 |
Dörr, HG; Kiess, W; Körner, A; Kratzsch, J; Rascher, W; Simm, D; Völkl, TM | 1 |
Dörr, HG; Kiess, W; Körner, A; Kratzsch, J; Simm, D; Völkl, TM | 1 |
Dauber, A; Kellogg, M; Majzoub, JA | 1 |
Fukami, M; Hasegawa, T; Homma, K; Ikeda, K; Koyama, Y; Miwa, M; Murata, M; Ogata, T | 1 |
Chan, AO; Taylor, NF | 1 |
BELL, M; VARLEY, H | 1 |
BONGIOVANNI, A | 1 |
DION, FR; HAYLES, AB; MATTOX, VR; SALASSA, RM | 1 |
DAVID, MA; FAREDIN, I; JULESZ, M; SZARVAS, F; TOTH, I | 1 |
BONGIOVANNI, AM; EBERLEIN, WR; ROOT, AW | 1 |
CONCOLINO, G; RASCIO, L; SCIARRA, F; SORCINI, G | 1 |
BROSSWITZ, E; LOHMEYER, H | 1 |
Anzo, M; Hamajima, T; Hasegawa, T; Homma, K; Jinno, K; Matsuo, N; Ohashi, T; Takahashi, T; Takahashi, Y; Takeshita, E; Toyoura, T; Watanabe, K | 1 |
Toma, Y; Yanaihara, T | 1 |
Aceto, T; Caprano, VJ; MacGILLIVRAY, MH; Munschauer, RW; Raiti, S | 1 |
Bacchus, H | 1 |
Finkelstein, M; Halperin, G | 1 |
Kusunoki, T; Matsumoto, K; Mizutani, S; Seki, T | 1 |
Faredin, I; Tóth, I | 1 |
Lacroix, A; McKenna, TJ; Moore, GW; Rabin, D | 1 |
LaFranchi, S | 1 |
Prader, A; Tassinari, D; Zachmann, M | 1 |
Levine, LS; Mininberg, DT; New, MI | 1 |
Joannou, GE | 1 |
Drayer, NM; Nagel, GT; van der Ploeg, KR; Volmer, M; Wolthers, BG | 1 |
Czira, G; Kecskés, L | 1 |
Bougneres, P; Couzinet, B; Elkik, F; Gourmelen, M; Schaison, G | 1 |
Jansen, M; van den Brande, JL; Wit, JM | 1 |
Ishida, H; Kinoshita, K; Minowada, S; Niijima, T | 1 |
Hendricks, SA; Kaplan, SA; Lavin, N; Lippe, BM; Mayes, DM | 1 |
Gutai, JP; Lee, PA; Migeon, CJ; Urban, MD | 1 |
Frisch, H; Parth, K; Schober, E; Swoboda, W | 1 |
Granoff, AB | 1 |
Lim, YJ; Montalto, J; Warne, GL; Yong, AB | 1 |
Fardella, CE; Lin, D; Mahachoklertwattana, P; Miller, WL; Zhang, LH | 1 |
Joannou, GE; Reeder, AY | 1 |
Saisho, S; Shimozawa, K; Toyoura, T; Yang, Y; Yata, J | 1 |
Phillipov, G | 1 |
Dörr, HG; Frenzel, S | 1 |
Bierich, JR; Gupta, D | 1 |
Ferrante, L | 1 |
Barrett, GN; Clayton, GW; Holcombe, JH; Keenan, BS; Kirkland, RT; McNeel, R | 1 |
Hammond, CB; Riddick, DH | 2 |
Brandt-Erichsen, D; Donelan, L; Schoen, EJ; Solomon, IL | 1 |
Bongiovanni, AM; Genel, M; Goldman, AS; Rosenfield, RL; Schneider, G | 1 |
David, R; Youssefnejadian, E | 1 |
Burr, IM; Jennings, AS; Liddle, GW; McKenna, TJ | 1 |
Baron, MC; Girard, F; Gourmelen, M; Pham-Huu-Trung, MT; Raux, MC | 1 |
Bohrn, E; Brunel, R; Parth, K; Swoboda, W; Zimprich, H | 1 |
Christensen, T; Petersen, KE | 1 |
Brown, DR; Steffes, MW; Ulstrom, RA; Wong, ET | 1 |
Chowers, I; Finkelstein, M; Maschler, I; Muller, A; Shaefer, J; Slavin, S; Weidenfeld, J | 1 |
Prader, A; Zachmann, M | 1 |
Bailey, CC; Komrower, GM; Palmer, M | 1 |
Blizzard, RM; Huseman, CA; Johanson, A; Varma, MM | 1 |
Manouguian, G; Stubbe, P | 1 |
Hansen, JW; Loriaux, DL | 1 |
Juricskay, Z; Kecskés, L; Németh, M; Temesi, M; Tényi, I | 1 |
Hughes, IA; Winter, JS | 1 |
Shibata, Y | 1 |
Franceschetti, F; Magini, A; Messeri, G; Pazzagli, M; Pinzani, P | 1 |
Goldsmith, MA; Miller, WL; Solish, SB; Voutilainen, R | 1 |
Itoh, N; Kumamoto, Y; Maruta, H; Mikuma, N; Nanbu, A; Tachiki, H; Takagi, Y; Tsunekawa, T | 1 |
Homoki, J; Solyom, J; Teller, WM | 1 |
Connelly, JF; Davies, HE; Montalto, J; Pitt, JJ; Warne, GL; Yong, AB | 1 |
Chrousos, GP; Cutler, GB; Loriaux, DL; Winterer, J | 1 |
Hikita, Y | 1 |
Fuse, H; Ito, H; Kataumi, Z; Kawamura, K; Shimazaki, J; Sumiya, H | 1 |
Frisch, H; Nowotny, P; Vierhapper, H; Waldhäusl, W | 1 |
Kellie, AE; Samarajeewa, P | 1 |
Canlorbe, P; Chaussain, JL; Job, JC; Munck, A | 1 |
Davis, JC; Fliegner, JR; Jeffcoate, TN; Russell, SH; Wade, AP | 1 |
Bertrand, J; Cathro, DM; Coyle, MG | 1 |
Nichols, J | 1 |
Prlpva, VG | 1 |
Gson, GG; Nichols, J | 1 |
Dorfman, RI; Forchielli, E; Rivera, R | 1 |
Cyran, J; Göbel, P | 1 |
Cacciari, E; Cicognani, A; Dallera, L; Miano, A; Tassoni, P | 1 |
Schindler, H | 1 |
Gabrilove, JL; Garmendia, F; Nicolis, GL | 1 |
Golubev, VA | 1 |
Berger, H; Glatzl, J; Gleispach, H; Rössler, H | 2 |
Balachandran, R; Sanghvi, A; Serenko, A; Wight, C | 1 |
Metcalf, MG | 1 |
Hall, K; Hökfelt, B | 1 |
Nagano, T | 1 |
Brough, AJ; Camacho, AM; Kowarski, A; Migeon, CJ | 1 |
Drayer, NM; Galal, OM; Rudd, BT | 1 |
Steinbeck, AW; Thomas, FJ | 2 |
Dingman, JF; Lim, NY; Mimica, N | 1 |
Acerbi, L; Faglia, G; Farrari, C; Gattinoni, L; Neri, V; Travaglini, P | 1 |
New, MI; Seaman, MP | 1 |
Cohen, MM; Edwards, JA; Schussler, GC; Vance, VK | 1 |
Curtius, HC; Murset, G; Prader, A; Vollmin, JA; Zachmann, M | 1 |
Brimblecombe, FS; Eades, SM; Rossiter, MA | 1 |
Matsumoto, Y | 1 |
Bode, HH; Crawford, JD; Hayek, A | 1 |
Curtius, HC; New, MI; Prader, A; Völlmin, JA; Zachmann, M | 1 |
Gregorová, I; Horký, K; Kuchel, O; Stárka, L | 1 |
Levine, LS; New, MI; Peterson, RE; Pitt, P | 1 |
Atherden, SM; Barnes, ND | 1 |
Grychtolik, H; Gudowski, G; Ijaiya, K; Tacke, A | 1 |
Bayard, F; Beitins, IZ; Kowarski, A; Migeon, CJ | 1 |
Newns, GH | 1 |
Bailey, CC; Komrower, GM | 1 |
Berger, H; Glatzl, J; Gleispach, H; Rössler, H; Tschager, E | 1 |
Coyotupa, J; Kaplan, SA; LaFranchi, SH; Lavin, N; Lippe, BM; Parlow, A | 1 |
Gleispach, H | 1 |
Bidlingmaier, F; Knorr, D | 1 |
Bongiovanni, AM; Kirkland, R; Parks, JS; Ranke, M; Tenore, A; Vaidya, V | 1 |
Mallin, SR; Walker, FA | 1 |
Bergadá, C; Dahl, V; Rivarola, MA | 1 |
Knorr, D | 2 |
Bergier, G; Varette-Dauvergne, Y; Zakarian, S; Zographos, G | 1 |
Bierich, JR; Gupta, D; Huenges, R; Rager, K | 1 |
Basmaciogullari, A; Bouthreuil, E; Marti-Henneberg, C; Rappaport, R | 1 |
Gabrilove, JL; Nicolis, GL; Sohval, AR | 1 |
Frasier, SD; Horton, R; Weiss, BA | 1 |
Serrera Contreras, JL | 1 |
Holzmann, K; Mickan, H; Wittenbecher, G | 1 |
New, MI | 1 |
Teller, WM | 1 |
Farquhar, JW; Mitchell, FL; Shackleton, CH | 1 |
Bicknell, EJ | 1 |
Kotchen, TA; Strickland, AL | 1 |
Hrnciar, J; Izakovic, V; Stárka, L | 1 |
Bongiovanni, AM; Eberlein, WR; Moshang, T | 1 |
Herrera Pombo, JL; Ramos, F; Rodríguez Miñón, JL; Vivanco, F | 1 |
Merkatz, IR; New, MI; Peterson, RE; Seaman, MP | 1 |
Christy, NP; Janoski, AH; Kelly, WG; Roginsky, MS | 1 |
Torigoe, T | 1 |
Bertrand, J; Haour, F; Loras, B | 1 |
Lohmeyer, H | 1 |
Miyakawa, I; Mori, N | 1 |
Hill, JG; Qazi, QH; Thompson, MW | 1 |
Riley, WJ | 1 |
Bardin, CW; Lipsett, MB; Strott, CA; Yoshimi, T | 1 |
Karl, HJ; Raith, L; Rauhut, D | 1 |
Cornu, G; Rappaport, R; Royer, P | 1 |
Addy, D; Littlewood, J | 1 |
Kelley, VC; Limbeck, GA; Ruvalcaba, RH | 1 |
Frasier, SD; Horton, R; Ulstrom, RA | 1 |
Szamatowicz, M | 1 |
Kogut, MD | 1 |
Brachfeldová, J; Hostomská, L | 1 |
Isurugi, K; Kinoshita, K; Kumamoto, Y; Takayasu, H | 1 |
Rosenbloom, AL; Smith, DW | 1 |
Degenhart, HJ; Visser, HK | 1 |
Curtius, HC | 1 |
6 review(s) available for pregnanetriol and Congenital Adrenal Hyperplasia
Article | Year |
---|---|
Monitoring of therapy in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Bone Development; Catecholamines; Glucocorticoids; Humans; Mineralocorticoids; Monitoring, Physiologic; Pregnanetriol; Saliva; Testosterone | 2010 |
[Pregnanediol (P2), pregnanetriol (P3)].
Topics: Adrenal Hyperplasia, Congenital; Biomarkers; Chromatography, Gas; Cushing Syndrome; Female; Humans; Hypertension; Luteinization; Male; Ovarian Function Tests; Ovulation Detection; Placental Function Tests; Pregnancy; Pregnanediol; Pregnanetriol; Reference Values; Specimen Handling | 2005 |
[The clinical value of amniotic fluid studies (literature review)].
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Carbon Dioxide; Chromosome Aberrations; Chromosome Disorders; Congenital Abnormalities; Down Syndrome; Embryonic and Fetal Development; Erythroblastosis, Fetal; Estriol; Female; Fetal Diseases; Humans; Mucopolysaccharidoses; Oxygen; Pregnancy; Pregnanetriol; Rh-Hr Blood-Group System; Sex Chromatin; Sex Determination Analysis | 1971 |
Congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Bone Development; Child; Cortisone; Female; Glucocorticoids; Growth; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Menstruation; Mixed Function Oxygenases; Pregnanetriol; Sodium Chloride; Spermatogenesis; Virilism | 1974 |
[Intersexuality in childhood].
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Androgen-Insensitivity Syndrome; Child; Child, Preschool; Chorionic Gonadotropin; Diagnosis, Differential; Disorders of Sex Development; Female; Genetic Counseling; Genitalia, Female; Genitalia, Male; Humans; Hypospadias; Infant; Klinefelter Syndrome; Male; Mosaicism; Pregnanetriol; Progesterone; Psychosexual Development; Sex Chromosome Aberrations; Transsexualism; Turner Syndrome; Virilism | 1974 |
Congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Glucocorticoids; Gonadal Steroid Hormones; Humans; Metabolism, Inborn Errors; Mineralocorticoids; Pregnanetriol | 1968 |
4 trial(s) available for pregnanetriol and Congenital Adrenal Hyperplasia
Article | Year |
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Pregnenolone, 17-OH-pregnenolone, and testosterone in plasma of patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Clinical Trials as Topic; Female; Humans; Hydrocortisone; Hyperplasia; Infant; Male; Pregnanetriol; Pregnenolone; Progesterone Reductase; Steroid Hydroxylases; Testosterone | 1976 |
Effect of hydrocortisone dose schedule on adrenal steroid secretion in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Child; Cortodoxone; Drug Administration Schedule; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pregnanetriol | 1985 |
Single dose dexamethasone in treatment of congenital adrenocortical hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Circadian Rhythm; Clinical Trials as Topic; Cortisone; Dexamethasone; Female; Humans; Hydrocortisone; Hyperplasia; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol | 1971 |
Effect of aminoglutethimide on urinary steroid excretion in patients with congenital adrenal hyperplasia due to incomplete 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropic Hormone; Adult; Aminoglutethimide; Androsterone; Aniline Compounds; Anticonvulsants; Chemistry, Clinical; Clinical Trials as Topic; Dehydroepiandrosterone; Depression, Chemical; Dexamethasone; Etiocholanolone; Female; Humans; Metabolism, Inborn Errors; Metyrapone; Mixed Function Oxygenases; Pregnanetriol; Pyridones | 1972 |
151 other study(ies) available for pregnanetriol and Congenital Adrenal Hyperplasia
Article | Year |
---|---|
First Morning Pregnanetriol and 17-Hydroxyprogesterone Correlated Significantly in 21-Hydroxylase Deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Humans; Pregnanetriol; Prospective Studies; Young Adult | 2021 |
Testicular adrenal rest tumors develop independently of long-term disease control: a longitudinal analysis of 50 adult men with congenital adrenal hyperplasia due to classic 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Child; Child, Preschool; Cross-Sectional Studies; Follow-Up Studies; Glucocorticoids; Humans; Infant; Infertility, Male; Longitudinal Studies; Male; Pregnanetriol; Retrospective Studies; Testicular Neoplasms; Ultrasonography | 2013 |
A 68-year-old phenotypically male patient with 21-hydroxylase deficiency and concomitant adrenocortical neoplasm producing testosterone and cortisol.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Aged; Androstenedione; Base Sequence; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydrocortisone; Immunohistochemistry; Japan; Magnetic Resonance Imaging; Male; Molecular Sequence Data; Pregnanetriol; Sequence Analysis, DNA; Testosterone | 2013 |
Reduced activity of 11β-hydroxylase accounts for elevated 17α-hydroxyprogesterone in preterms.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Chromatography, Gas; Cortodoxone; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Infant, Premature; Male; Mass Spectrometry; Metabolome; Pregnanetriol; Retrospective Studies; Steroid 11-beta-Hydroxylase; Steroid 17-alpha-Hydroxylase | 2014 |
Diagnosis of 21-hydroxylase deficiency by urinary metabolite ratios using gas chromatography-mass spectrometry analysis: Reference values for neonates and infants.
Topics: Adrenal Hyperplasia, Congenital; Cohort Studies; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Male; Metabolomics; Pregnanetriol; Reference Values; Steroids; Tetrahydrocortisone | 2016 |
Modified-Release and Conventional Glucocorticoids and Diurnal Androgen Excretion in Congenital Adrenal Hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androsterone; Circadian Rhythm; Cortodoxone; Delayed-Action Preparations; Dexamethasone; Female; Gas Chromatography-Mass Spectrometry; Glucocorticoids; Humans; Hydrocortisone; Male; Middle Aged; Prednisolone; Pregnanetriol; Young Adult | 2017 |
Does an altered leptin axis play a role in obesity among children and adolescents with classical congenital adrenal hyperplasia due to 21-hydroxylase deficiency?
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Cross-Sectional Studies; Female; Humans; Insulin Resistance; Leptin; Male; Models, Statistical; Obesity; Overweight; Pregnanetriol; Prospective Studies; Receptors, Leptin; Risk Factors; Steroid 21-Hydroxylase; Testosterone; Young Adult | 2009 |
Adiponectin levels are high in children with classic congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adiponectin; Adolescent; Adrenal Hyperplasia, Congenital; Body Mass Index; Bone Development; Child; Child, Preschool; Cross-Sectional Studies; Dehydroepiandrosterone Sulfate; Female; Glucocorticoids; Humans; Male; Mineralocorticoids; Obesity; Pregnanetriol; Prospective Studies; Saliva; Skinfold Thickness; Steroid 21-Hydroxylase; Testosterone; Young Adult | 2009 |
Two-step biochemical differential diagnosis of classic 21-hydroxylase deficiency and cytochrome P450 oxidoreductase deficiency in Japanese infants by GC-MS measurement of urinary pregnanetriolone/ tetrahydroxycortisone ratio and 11β-hydroxyandrosterone.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androsterone; Biomarkers; Case-Control Studies; Diagnosis, Differential; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Male; NADPH-Ferrihemoprotein Reductase; Pregnanetriol; Steroid 17-alpha-Hydroxylase; Steroid 21-Hydroxylase; Tetrahydrocortisone | 2012 |
New strategies for detecting steroid metabolic disorders--paneling vs profiling.
Topics: Adrenal Hyperplasia, Congenital; Androsterone; Female; Humans; Male; NADPH-Ferrihemoprotein Reductase; Pregnanetriol; Steroid 21-Hydroxylase; Tetrahydrocortisone | 2012 |
The estimation of pregnanetriol and 17-hydroxypregnanolone in urine in congenital adrenal hyperplasia.
Topics: Adrenal Cortex; Adrenal Hyperplasia, Congenital; Humans; Pregnanediol; Pregnanetriol; Pregnanolone | 1960 |
The value of urinary pregnanetriol levels in the diagnosis and treatment of the adrenogenital syndrome.
Topics: Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Body Fluids; Pregnanediol; Pregnanetriol | 1959 |
URINARY STEROID PATTERNS AND LOSS OF SALT IN CONGENITAL ADRENAL HYPERPLASIA.
Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Aldosterone; Biomedical Research; Blood; Child; Creatine; Creatinine; Diet, Sodium-Restricted; Humans; Infant; Infant, Newborn; Natriuresis; Pregnanediol; Pregnanetriol; Sodium; Sodium, Dietary; Steroids | 1964 |
PREGNANETRIOL STUDIES IN HIRSUTISM AND OTHER ENDOCRINE DISEASES.
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenogenital Syndrome; Cushing Syndrome; Endocrine System Diseases; Hirsutism; Hypertrichosis; Metabolism; Obesity; Pregnanetriol; Progestins; Urine | 1964 |
MEASUREMENT OF PREGNANETRIOL IN PLASMA.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Blood; Body Fluids; Child; Cortisone; Drug Therapy; Humans; Hydrocortisone; Infant; Infant, Newborn; Pregnanetriol; Progestins; Urine | 1964 |
[PLASMATIC ESTROGENS IN BILATERAL HYPERPLASIA OF THE ADRENAL CORTEX. COMPARATIVE STUDY IN CONGENITAL ADRENOGENITAL SYNDROME AND CUSHING'S SYNDROME].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adrenogenital Syndrome; Blood; Cushing Syndrome; Estrogens; Humans; Hyperplasia; Pharmacology; Pregnanetriol; Triamcinolone; Urine | 1964 |
[PREGNANETRIOLONE. SYNTHESIS, QUANTITATIVE DETERMINATION AND ITS IMPORTANCE IN ADRENOGENITAL SYNDROME AND IN FEMALE STERILITY].
Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Chromatography; Cortisone; Female; Humans; Infertility, Female; Metabolism; Pregnanetriol | 1964 |
Elevated urine pregnanetriolone definitively establishes the diagnosis of classical 21-hydroxylase deficiency in term and preterm neonates.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Case-Control Studies; Diagnosis, Differential; Female; Gestational Age; Humans; Infant, Newborn; Infant, Premature; Male; Pregnanetriol; Sensitivity and Specificity | 2004 |
Congenital virilizing adrenal hyperplasia without acceleration of growth or bone maturation.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Infant; Pregnanetriol | 1966 |
A method for measurement of total 17-OH, 21-methyl steroids in the urine and its application to clinical problems.
Topics: 17-Hydroxycorticosteroids; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Carbon Tetrachloride; Chemistry Techniques, Analytical; Chromatography, Paper; Corticosterone; Cortisone; Glucuronidase; Humans; Pregnanetriol | 1967 |
Biosynthesis of pregnanetriolone and pregnanetetrol in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Carbon Isotopes; Chromatography, Thin Layer; Female; Humans; Hydroxyprogesterones; Hyperplasia; Pregnanediol; Pregnanetriol; Tritium | 1967 |
Urinary steroids in fifteen cases of congenital virilizing adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Estrogens; Female; Gonadotropins; Humans; Hydroxyprogesterones; Hyperplasia; Male; Pregnanetriol; Virilism | 1967 |
Metabolism and concentration of androgenic steroids in abdominal skin of hirsute women with androgenital syndrome.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Abdominal Muscles; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenediol; Androstenedione; Dehydroepiandrosterone; Female; Hirsutism; Humans; Male; Middle Aged; Pregnanetriol; Skin; Sulfates; Testosterone | 1984 |
Gonadal dysfunction in adult men with congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Dexamethasone; Follicle Stimulating Hormone; Humans; Leydig Cells; Luteinizing Hormone; Male; Pregnanetriol; Pregnenolone; Progesterone; Testis; Testosterone | 1980 |
Plasma adrenocorticotrophic hormone in congenital adrenal hyperplasia. Importance in long-term management.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Female; Fludrocortisone; Glucocorticoids; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Long-Term Care; Male; Natriuresis; Pregnanetriol | 1980 |
Clinical and biochemical variability of congenital adrenal hyperplasia due to 11 beta-hydroxylase deficiency. A study of 25 patients.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Cortodoxone; Female; Humans; Hydrocortisone; Infant, Newborn; Male; Pregnanediones; Pregnanetriol; Steroid Hydroxylases | 1983 |
Current concepts in congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Cholesterol Side-Chain Cleavage Enzyme; Corticosterone; Female; Humans; Hydroxyprogesterones; Infant, Newborn; Male; Pregnanetriol; Progesterone Reductase; Steroid Hydroxylases | 1982 |
Identification of 15 beta-hydroxylated C21 steroids in the neo-natal period: the role of 3 alpha,15 beta,17 alpha-trihydroxy-5 beta-pregnan-20-one in the perinatal diagnosis of congenital adrenal hyperplasia (CAH) due to a 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxypregnenolone; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Penicillium; Pregnancy; Pregnanetriol; Pregnenes; Steroid Hydroxylases | 1981 |
The diagnosis of 21-hydroxylase deficiency in a prematurely born infant on the basis of the urinary steroid excretion pattern.
Topics: Adrenal Hyperplasia, Congenital; Aging; Androstanes; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydrocortisone; Infant, Newborn; Infant, Premature; Male; Pregnanes; Pregnanetriol; Pregnanolone; Pregnenes; Steroid Hydroxylases; Steroids; Tetrahydrocortisone | 1982 |
Steroid spectrum in human urine as revealed by gas chromatography V. Identification and quantitation of 3 alpha, 20 alpha-dihydroxy-5-beta pregnan-11-one (11-keto-pregnanediol) during different stages of development in children with C/21 hydroxylase defic
Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Aging; Child; Child, Preschool; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Male; Pregnanediol; Pregnanetriol; Puberty; Steroid Hydroxylases | 1981 |
Angiotensin and adrenal steroidogenesis: study of 21-hydroxylase-deficient congenital adrenal hyperplasia.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Angiotensin II; Diet, Sodium-Restricted; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pregnanetriol; Renin; Steroid Hydroxylases | 1980 |
Reinstitution of mineralocorticoid therapy in congenital adrenal hyperplasia. Effects on control and growth.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Growth; Humans; Hydrocortisone; Male; Mineralocorticoids; Pregnanetriol; Renin | 1981 |
Dissociation of plasma renin activity and plasma aldosterone level during dexamethasone suppression test in non-salt-losers with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Dexamethasone; Female; Humans; Male; Pregnanetriol; Renin | 1980 |
Urinary and serum steroid concentrations in the management of congenital adrenal hyperplasia. Lack of physiologic correlations.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Child; Child, Preschool; Dose-Response Relationship, Drug; Female; Hormones; Humans; Infant; Male; Pregnanetriol | 1982 |
Plasma progesterone, 17-hydroxyprogesterone, androstenedione and testosterone in prepubertal, pubertal and adult subjects with congenital virilizing adrenal hyperplasia as indicators of adrenal suppression.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydroxyprogesterones; Infant; Male; Pregnanetriol; Progesterone; Puberty; Sex Factors; Testosterone | 1980 |
Circadian patterns of plasma cortisol, 17-hydroxyprogesterone, and testosterone in congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Prednisone; Pregnanetriol; Testosterone | 1981 |
Treatment of menstrual irregularities with dexamethasone in congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Dexamethasone; Female; Gonadal Steroid Hormones; Humans; Hydroxyprogesterones; Menstruation Disturbances; Pregnanetriol; Testosterone | 1981 |
Urinary 17 alpha-hydroxyprogesterone in management of 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Case-Control Studies; Child; Child, Preschool; Chromatography, Gas; Circadian Rhythm; Enzyme-Linked Immunosorbent Assay; Female; Glucocorticoids; Humans; Hydroxyprogesterones; Infant; Male; Predictive Value of Tests; Pregnanetriol; Radioimmunoassay | 1995 |
Deletion of amino acids Asp487-Ser488-Phe489 in human cytochrome P450c17 causes severe 17 alpha-hydroxylase deficiency.
Topics: 17-Hydroxycorticosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Aldehyde-Lyases; Amino Acid Sequence; Base Sequence; Blotting, Southern; Blotting, Western; Cytochrome P-450 Enzyme System; DNA; Female; Homozygote; Humans; Hypertension; Hypokalemia; Molecular Sequence Data; Mutagenesis, Site-Directed; Polymerase Chain Reaction; Pregnanediol; Pregnanetriol; Sequence Deletion | 1993 |
15 beta-hydroxysteroids (Part IV). Steroids of the human perinatal period: the synthesis of 3 alpha,15 beta,17 alpha-trihydroxy-5 alpha-pregnan-20-one and its A/B-ring configurational isomers.
Topics: Adrenal Hyperplasia, Congenital; Gas Chromatography-Mass Spectrometry; Humans; Hydroxysteroids; Infant, Newborn; Magnetic Resonance Spectroscopy; Molecular Structure; Pregnanetriol; Stereoisomerism | 1995 |
Urinary pregnanetriol-3-glucuronide in children: age-related change and application to the management of 21-hydroxylase deficiency.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Child; Child, Preschool; Enzyme-Linked Immunosorbent Assay; Female; Humans; Infant; Infant, Newborn; Male; Pregnanetriol; Reference Values | 1996 |
Effect of hypercortisolism and ACTH on the metabolism of cortisol.
Topics: ACTH Syndrome, Ectopic; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Cushing Syndrome; Female; Humans; Hydrocortisone; Male; Middle Aged; Pregnanetriol | 1998 |
[Problems of delayed diagnosis of an uncomplicated adrenogenital syndrome (AGS) with 21-hydroxylase defect in a 7-year-old boy].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Anti-Inflammatory Agents; Child; Follicle Stimulating Hormone; Gonadotropin-Releasing Hormone; Humans; Hydrocortisone; Luteinizing Hormone; Luteolytic Agents; Male; Pregnanetriol; Puberty, Precocious; Testosterone; Time Factors; Triptorelin Pamoate | 1998 |
[Prenatal diagnosis of the congenital adrenogenital syndrome].
Topics: Adrenal Hyperplasia, Congenital; Dehydroepiandrosterone; Estriol; Female; Humans; Hydroxyprogesterones; Pregnancy; Pregnanetriol; Prenatal Diagnosis | 1975 |
[Complex biochemical aspects in virilizing adrenal gland syndromes].
Topics: Adrenal Hyperplasia, Congenital; Androsterone; Dehydroepiandrosterone; Etiocholanolone; Female; Humans; Male; Pregnanetriol; Pregnatrienes; Virilism | 1976 |
Plasma androgens in congenital adrenal hyperplasia: androstenedione concentration as an index of adrenal androgen suppression.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; Glucocorticoids; Humans; Male; Pregnanetriol; Testosterone | 1979 |
Long-term steroid therapy in patients with adrenogenital syndrome.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Age Determination by Skeleton; Age Factors; Body Height; Child; Child, Preschool; Cortisone; Dexamethasone; Female; Fertility; Genitalia, Female; Humans; Karyotyping; Male; Menarche; Methylprednisolone; Pregnanetriol; Seizures; Sex Determination Analysis; Time Factors | 1975 |
Adrenal virilism due to 21-hydroxylase deficiency in the postmenarchial female.
Topics: 17-Ketosteroids; Adolescent; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Dexamethasone; Female; Hirsutism; Humans; Hydroxysteroids; Menarche; Metabolism, Inborn Errors; Mixed Function Oxygenases; Prednisone; Pregnancy; Pregnanetriol; Time Factors; Virilism | 1975 |
Blood testosterone values in patients with congenital virilizing adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Age Determination by Skeleton; Body Height; Child; Child, Preschool; Female; Glucocorticoids; Humans; Male; Pregnanetriol; Testosterone; Virilism | 1975 |
Persistent testicular delta5-isomerase-3beta-hydroxysteroid dehydrogenase (delta5-3beta-HSD) deficiency in the delta5-3beta-HSD form of congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Chorionic Gonadotropin; Dexamethasone; Gonadotropins, Pituitary; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Isomerases; Male; Pregnanetriol; Puberty; Sodium; Testis; Testosterone | 1975 |
Early diagnosis of congenital adrenal hyperplasia by measurement of 17-hydroxyprogesterone.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Female; Fetal Blood; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Pregnanetriol; Umbilical Veins | 1975 |
Plasma aldosterone concentrations related to 17alpha-hydroxyprogesterone in congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Child; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Ketosteroids; Male; Pregnanetriol | 1976 |
Congenital adrenal hyperplasia: simultaneous determination of plasma aldosterone and 17-hydroxyprogesterone.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Child; Child, Preschool; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Male; Prednisolone; Pregnanetriol; Radioimmunoassay | 1978 |
17-Hydroxyprogesterone in normal children and congenital adrenal hyperplasia. Measurement in serum by radioimmunoassay after thin-layer chromatography.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Chromatography, Thin Layer; Female; Humans; Hydroxyprogesterones; Infant; Male; Pregnanetriol; Radioimmunoassay; Reference Values | 1979 |
Urinary 17 alpha-hydroxyprogesterone in diagnosis and management of congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Child, Preschool; Creatinine; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Infant, Newborn, Diseases; Male; Middle Aged; Pregnanetriol | 1979 |
A case of adrenogenital syndrome with aberrant 11beta-hydroxylation.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Amenorrhea; Corticosterone; Female; Hirsutism; Humans; Hydrocortisone; Hydroxyprogesterones; Hypertension; Pregnanetriol; Pregnenediones; Steroid Hydroxylases; Syndrome; Testosterone; Thyrotropin; Transcortin | 1977 |
Unusual heterozygotes of congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Female; Heterozygote; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Mixed Function Oxygenases; Pedigree; Pregnanes; Pregnanetriol; Testosterone | 1978 |
Management of congenital adrenal hyperplasia. Urinary steroid estimations--review of their value.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Body Height; Child; Child, Preschool; Female; Fludrocortisone; Humans; Infant; Male; Prednisone; Pregnanetriol; Retrospective Studies | 1978 |
Treatment of congenital virilizing adrenal hyperplasia patients with single and multiple daily doses of prednisone.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Child; Child, Preschool; Drug Administration Schedule; Female; Humans; Hydroxyprogesterones; Male; Prednisone; Pregnanetriol; Progesterone; Testosterone | 1977 |
[Pseudohypoaldsteronism. A further case report (author's transl)].
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Diagnosis, Differential; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium Chloride | 1977 |
Variable efficacy of glucocorticoids in congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Child; Cortisone; Depression, Chemical; Dexamethasone; Female; Glucocorticoids; Humans; Hydrocortisone; Male; Prednisone; Pregnanetriol; Steroid Hydroxylases | 1976 |
Significance of 3alpha, 17 alpha-dihydroxy-5beta-pregnane-20-one in the diagnosis of congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adult; Cholestanes; Chromatography, Gas; Female; Humans; Hydrolysis; Male; Pregnanediol; Pregnanetriol | 1975 |
The application of a serum 17OH-progesterone radioimmunoassay to the diagnosis and management of congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Fetal Blood; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Pregnanetriol; Radioimmunoassay; Renin; Sodium Chloride; Steroid Hydroxylases | 1976 |
[Determination of urinary 17 alpha-hydroxyprogesterone excretion using ELISA--evaluation of normal subjects and patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Child; Child, Preschool; Circadian Rhythm; Enzyme-Linked Immunosorbent Assay; Female; Humans; Hydroxyprogesterones; Infant; Infant, Low Birth Weight; Infant, Newborn; Male; Pregnanetriol; Reference Values | 1991 |
A chemiluminescent method for the measurement of pregnanetriol-3 alpha-glucuronide in human diluted urine.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Female; Humans; Hydroxyprogesterones; Immunoassay; Luminescent Measurements; Male; Middle Aged; Pregnanetriol; Quality Control | 1989 |
Molecular characterization of a Leydig cell tumor presenting as congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child, Preschool; Cosyntropin; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Humans; Hydrocortisone; Hydroxyprogesterones; Leydig Cell Tumor; Male; Pregnanetriol; Testicular Neoplasms; Testosterone | 1989 |
[A clinical study of congenital adrenal hyperplasia].
Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Body Height; Bone Development; Child, Preschool; Cyproterone; Cyproterone Acetate; Dexamethasone; Female; Follicle Stimulating Hormone; Humans; Hydrocortisone; Infant; Infant, Newborn; Luteinizing Hormone; Male; Obesity; Pregnanetriol | 1989 |
Detection of late onset steroid 21-hydroxylase deficiency by capillary gas chromatographic profiling of urinary steroids in children and adolescents.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Infant; Male; Pregnanes; Pregnanetriol; Pregnanolone; Puberty, Precocious; Steroid Hydroxylases; Tetrahydrocortisol; Virilism | 1988 |
Diagnosis of 21-hydroxylase deficiency in newborn infants by GC-MS of urinary steroids.
Topics: Adrenal Hyperplasia, Congenital; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant, Newborn; Male; Pregnanetriol; Progestins; Steroid Hydroxylases | 1988 |
[Reevaluation of recalled infants by neonatal mass screening for congenital adrenal hyperplasia due to 21-hydroxylase deficiency. Diagnostic value of pregnanetriolone in a single urine specimen using glass capillary gas chromatography].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Chromatography, Gas; Cortodoxone; Female; Follow-Up Studies; Humans; Hydroxyprogesterones; Male; Mass Screening; Pregnancy; Pregnanetriol; Steroid Hydroxylases | 1985 |
[A case of congenital adrenogenital syndrome].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Middle Aged; Pregnanetriol; Steroid Hydroxylases | 1985 |
Capillary gas chromatography as a tool for characterization of urinary steroid excretion in patients with congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Male; Middle Aged; Pregnanetriol; Steroids; Tetrahydrocortisone | 1985 |
The radioimmunoassay of pregnanetriol 3 alpha-glucuronide.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Antibody Specificity; Child; Female; Haptens; Humans; Hydrocortisone; Immune Sera; Male; Menstruation; Pregnanetriol; Radioimmunoassay; Serum Albumin, Bovine | 1985 |
[Treatment of virilizing adrenal hyperplasia in adolescents. Use and side-effects of dexamethasone].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androgens; Child; Dexamethasone; Female; Humans; Hydroxyprogesterones; Male; Pregnanetriol; Virilism | 1985 |
Diagnosis of the adrenogenital syndrome before birth.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Female; Fetal Diseases; Humans; Infant, Newborn; Pregnancy; Pregnanetriol | 1965 |
Antenatal diagnosis of adrenocortical hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Estriol; Female; Fetal Diseases; Gestational Age; Humans; Infant, Newborn; Pregnancy; Pregnanetriol | 1969 |
Antenatal diagnosis of adrenocortical hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adult; Amniotic Fluid; Estradiol; Estriol; Estrogens; Estrone; Female; Fetal Diseases; Humans; Pregnancy; Pregnanetriol | 1969 |
[On the method of determination of pregnanetriol].
Topics: Abortion, Habitual; Adrenal Gland Diseases; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Female; Humans; Methods; Microchemistry; Pregnancy; Pregnanetriol | 1969 |
Antenatal diagnosis of the adrenogenital syndrome.
Topics: Adrenal Hyperplasia, Congenital; Amniotic Fluid; Estriol; Female; Fetal Diseases; Humans; Infant, Newborn; Infant, Newborn, Diseases; Pregnancy; Pregnanetriol | 1969 |
A modified method for the analysis of urinary 17-ketosteroids, pregnanediol and pregnanetriol by gas liquid chromatography in normal subjects and subjects with various endocrine disorders.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Disorders of Sex Development; Etiocholanolone; Female; Hirsutism; Humans; Klinefelter Syndrome; Male; Polycystic Ovary Syndrome; Pregnanediol; Pregnanetriol; Testicular Neoplasms; Turner Syndrome | 1967 |
[Gas chromatography determination of urinary pregnanediol and -triol and its significance for the differentiation of adrenal hirsutism in women].
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Chemistry, Clinical; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Diagnosis, Differential; Female; Glucocorticoids; Hirsutism; Humans; Pregnanediol; Pregnanetriol | 1969 |
[Various aspects of steroidogenesis in congenital adrenogenital syndrome with or without salt loss (determination of the urinary excretion of aldosterone, androsterone, etiocholanolone, dehydroisoandrosterone, 17-hydroxy-11-desoxycorticosterone, pregnaned
Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Androsterone; Child; Child, Preschool; Dehydroepiandrosterone; Desoxycorticosterone; Etiocholanolone; Female; Humans; Infant; Kidney; Male; Mineralocorticoids; Pregnanediol; Pregnanetriol; Progestins; Sodium; Water-Electrolyte Balance | 1969 |
[Suprarenal virilism].
Topics: 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Dehydroepiandrosterone; Female; Humans; Middle Aged; Pregnanetriol; Puberty, Precocious; Virilism | 1970 |
The determination of urinary pregnanetriol and the neutral 17-ketosteroids by gas-liquid chromatography.
Topics: 17-Ketosteroids; Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Adult; Aged; Alcohols; Amenorrhea; Androsterone; Carcinoma; Child, Preschool; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Etiocholanolone; Female; Genital Diseases, Male; Hirsutism; Humans; Hyperplasia; Hyperthyroidism; Hypospadias; Infant; Infertility, Male; Klinefelter Syndrome; Lactation Disorders; Male; Middle Aged; Polycystic Ovary Syndrome; Pregnancy; Pregnanetriol | 1971 |
[Congenital adrenal hyperplasia; 21-hydroxylase-deficiency combined with 17-desmolase-deficiency (author's transl)].
Topics: Adrenal Hyperplasia, Congenital; Androsterone; Chemical Phenomena; Chemistry; Dehydroepiandrosterone; Estrogens; Female; Humans; Lyases; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol | 1974 |
Gas-liquid chromatography of underivatized steroids: simultaneous determination of urinary 17-ketosteroids, pregnanediol, pregnanetriol, and pregnanetriolone.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Computers; Dehydroepiandrosterone; Etiocholanolone; Female; Humans; Pregnanediol; Pregnanetriol | 1974 |
Measurement of acetaldehydrogenic steroids in urine.
Topics: Acetaldehyde; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Chemistry Techniques, Analytical; Chemistry, Clinical; Child; Colorimetry; Humans; In Vitro Techniques; Metyrapone; Pregnanetriol; Steroids; Urine | 1965 |
Clinical and steroid metabolic studies in four siblings with congenital virilizing adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Angiotensin II; Child; Dexamethasone; Estrogens; Female; Gonadotropins; Humans; Hydrocortisone; Male; Metyrapone; Pregnanediol; Pregnanetriol; Sodium; Testosterone; Water-Electrolyte Balance | 1966 |
[Urinary excretion of pregnanetriol in various internal diseases].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropic Hormone; Adult; Aged; Child; Child, Preschool; Endocrine System Diseases; Female; Humans; Hypertension; Liver Cirrhosis; Male; Metyrapone; Middle Aged; Paramethasone; Pregnanetriol; Triparanol | 1966 |
Congenital adrenal hyperplasia due to a deficiency of one of the enzymes involved in the biosynthesis of pregnenolone.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Desoxycorticosterone; Disorders of Sex Development; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Hypokalemia; Hyponatremia; Infant; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Pregnenolone; Secretory Rate; Urine; Water-Electrolyte Balance | 1968 |
Evaluation of deficiency of 21-hydroxylation in patients with congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Dexamethasone; Female; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Pregnanetriol | 1968 |
Semiquantitative estimation of urinary pregnanetriol, pregnanetriolone and tetrahydro S in the investigation of adrenocortical function.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adsorption; Adult; Chemistry, Clinical; Child; Child, Preschool; Cushing Syndrome; Disorders of Sex Development; Ethisterone; Female; Glucuronidase; Hirsutism; Humans; Infant; Magnesium; Methods; Pituitary-Adrenal Function Tests; Polycystic Ovary Syndrome; Pregnanetriol; Puberty, Precocious; Silicon Dioxide; Tetrazolium Salts | 1969 |
Hyperaldosteronism in hypertensive congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adrenocorticotropic Hormone; Aldosterone; Chemistry, Clinical; Child; Desoxycorticosterone; Etiocholanolone; Female; Humans; Hyperaldosteronism; Hyperplasia; Hypertension; Metabolism, Inborn Errors; Mixed Function Oxygenases; Ovarian Neoplasms; Pregnanetriol | 1969 |
Occurrence of a virilizing syndrome with 21-hydroxylase deficiency after pregnancy.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Estrogens; Female; Gonadotropins; Humans; Metyrapone; Mixed Function Oxygenases; Pregnancy; Pregnanediol; Pregnanetriol; Testosterone; Triamcinolone; Virilism | 1969 |
Secretion rates of cortisol and aldosterone precursors in various forms of congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Corticosterone; Desoxycorticosterone; Dexamethasone; Diet; Female; Humans; Hydrocortisone; Hyperplasia; Hypertension; Male; Metabolism, Inborn Errors; Metyrapone; Mixed Function Oxygenases; Potassium; Pregnanetriol; Secretory Rate; Sodium | 1970 |
XO-XX-XXX mosaicism with possible congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Disorders of Sex Development; Female; Fibroblasts; Glucocorticoids; Gonadotropins, Pituitary; Humans; Hydrocortisone; Hyperplasia; Karyotyping; Metabolism, Inborn Errors; Middle Aged; Mosaicism; Mouth Mucosa; Pregnanetriol; Sex Chromosome Aberrations; Skin | 1970 |
Unusual type of congenital adrenal hyperplasia probably due to deficiency of 3-beta-hydroxysteroid dehydrogenase. Case report of a surviving girl and steroid studies.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Child; Dehydroepiandrosterone; Female; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Metabolism, Inborn Errors; Pituitary-Adrenal Function Tests; Pregnanes; Pregnanetriol; Steroids | 1970 |
Adrenal insufficiency in two male infants.
Topics: Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Adrenocorticotropic Hormone; Body Weight; Cortisone; Fludrocortisone; Humans; Hydrocortisone; Hyperplasia; Infant, Newborn; Male; Pigmentation Disorders; Pituitary-Adrenal Function Tests; Pregnanetriol; Sodium Chloride; Vomiting | 1970 |
[Gas chromatographic estimation of urinary delta5 pregnenetriol and pregnanetriol in adrenocortical disease and male hypogonadism].
Topics: Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aged; Carcinoma; Child; Child, Preschool; Chorionic Gonadotropin; Chromatography, Gas; Cushing Syndrome; Female; Humans; Hyperaldosteronism; Hypogonadism; Male; Middle Aged; Pregnanes; Pregnanetriol | 1971 |
Congenital adrenal hyperplasia due to deficiency of 11 -hydroxylation of 17 -hydroxylated steroids.
Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Chromatography, Gas; Female; Humans; Hydroxysteroid Dehydrogenases; Hyperplasia; Infant; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Secretory Rate | 1971 |
Androgen production in boys with sexual precocity and congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Chorionic Gonadotropin; Dexamethasone; Ethinyl Estradiol; Humans; Male; Medroxyprogesterone; Norethindrone; Prednisone; Pregnanetriol; Psychosexual Development; Puberty, Precocious; Testosterone | 1972 |
Diagnosis of congenital adrenal hyperplasia by measurement of plasma 17-hydroxyprogesterone.
Topics: 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Biological Assay; Child, Preschool; Cortisone; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Methods; Mixed Function Oxygenases; Pregnanetriol; Protein Binding | 1972 |
[Diagnostic and clinical problems in the congenital adrenogenital syndrome].
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Diagnosis, Differential; Disorders of Sex Development; Female; Humans; Infant; Infant, Newborn; Male; Prednisone; Pregnancy; Pregnanetriol; Prognosis; Virilism | 1972 |
The effect of ACTH administration on aldosterone production in non salt-losing congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Body Weight; Female; Humans; Hydrocortisone; Male; Middle Aged; Natriuresis; Potassium; Pregnanetriol; Radioimmunoassay; Secretory Rate; Stimulation, Chemical; Tritium | 1972 |
Growth and skeletal maturation in congenital adrenal hyperplasia. Review of 20 cases.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Age Factors; Body Height; Bone Development; Child; Child, Preschool; Female; Fludrocortisone; Glucocorticoids; Growth; Humans; Hydrocortisone; Infant; Male; Prednisone; Pregnanetriol; Puberty; Sodium; Sodium Chloride | 1974 |
[Pregnantriolon excretion after ACTH-stimulation in possible heterocygotes of 21-hydroxylase deficiency (author's transl)].
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Female; Heterozygote; Humans; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol; Stimulation, Chemical | 1971 |
[Pregnanetriolone excretion after stimulation with ACTH as a test on presumably heterozygous carriers of a 21-hydroxylase-deficiency (author's transl)].
Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androsterone; Female; Humans; Male; Metabolic Clearance Rate; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Stimulation, Chemical | 1974 |
Serum 17-alpha-hydroxyprogesterone, progesterone, estradiol, and testosterone in the diagnosis and management of congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Child; Child, Preschool; Estradiol; Female; Glucocorticoids; Growth; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Pregnanetriol; Progesterone; Puberty; Radioimmunoassay; Testosterone | 1974 |
[A contribution to the therapy of the congenital adrenal hyperplasia (author's transl)].
Topics: 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Chromatography, Gas; Desoxycorticosterone; Female; Humans; Hydrocortisone; Male; Mixed Function Oxygenases; Prednisolone; Prednisone; Pregnanediol; Pregnanetriol | 1974 |
Diagnosis of congenital adrenal hyperplasia with 11-hydroxylase deficiency by determination of tetrahydro-11-desoxycortisol in urine.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Chromatography, Gas; Disorders of Sex Development; Female; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Pregnanetriol; Radioimmunoassay; Tetrahydrocortisol | 1974 |
Gas-liquid chromatography in the diagnosis of congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Methods; Middle Aged; Pregnanes; Pregnanetriol | 1974 |
Effects of the XYY karyotype in one of two brothers with congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Autistic Disorder; Cells, Cultured; Child; Child, Preschool; Humans; Karyotyping; Lymphocytes; Male; Osteosarcoma; Pregnanetriol; Sex Chromosome Aberrations | 1972 |
Aldosterone secretion rate in the simple virilizing form of congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Carbon Isotopes; Child; Child, Preschool; Chromatography, Paper; Diet, Sodium-Restricted; Female; Humans; Hyperplasia; Male; Potassium; Pregnanetriol; Radioisotope Dilution Technique; Secretory Rate; Sodium; Spectrophotometry; Tritium | 1972 |
Problems in the interpretation of ovarian biopsies in functional gynecologic disorders and sterility of ovarian origin.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Biopsy; Chorionic Gonadotropin; Corpus Luteum; Dexamethasone; Dose-Response Relationship, Drug; Female; Humans; Infertility, Female; Injections, Intramuscular; Ovarian Diseases; Ovary; Ovulation; Pregnanediol; Pregnanetriol | 1973 |
[Hydrocortisone therapy of the AGS (adrenogenital syndrome)].
Topics: Adrenal Hyperplasia, Congenital; Androgens; Body Height; Body Weight; Bone Development; Child; Female; Humans; Hydrocortisone; Male; Prednisone; Pregnanetriol | 1973 |
Linear growth rate, bone maturation and growth hormone secretion in prepubertal children with congenital adrenal hyperplasia.
Topics: Administration, Oral; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Body Height; Bone Development; Child; Child, Preschool; Depression, Chemical; Female; Follow-Up Studies; Growth; Growth Hormone; Humans; Hydrocortisone; Hyperplasia; Male; Pregnanetriol; Time Factors | 1973 |
Non-tumorous feminizing adrenogenital syndrome in the male subject.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androstenedione; Androsterone; Estrogens; Feminization; Gynecomastia; Humans; Hydrocortisone; Male; Pituitary-Adrenal Function Tests; Pregnanetriol; Sex Chromatin; Spermatogenesis; Testis; Testosterone | 1973 |
Amniotic fluid testosterone: implications for the prenatal diagnosis of congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Age Factors; Amniocentesis; Amniotic Fluid; Erythroblastosis, Fetal; Female; Gestational Age; Humans; Male; Mixed Function Oxygenases; Pregnancy; Pregnanetriol; Prenatal Diagnosis; Sex Factors; Sodium; Testosterone | 1974 |
[Metabolism of estrogens in the adrenogenital syndrome].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Estradiol; Estriol; Estrogens; Estrone; Female; Humans; Male; Pregnanetriol | 1974 |
[Pregnanetriol in the amniotic fluid: prenatal diagnosis of adrenogenital syndrome by amniocentesis (author's transl)].
Topics: Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Estriol; Female; Humans; Hydrocortisone; Infant, Newborn; Pregnancy; Pregnanetriol; Prenatal Diagnosis; Sulfates; Twins | 1974 |
[Prenatal diagnosis of adrenogenital syndrome].
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Female; Fetal Diseases; Humans; Methods; Pregnancy; Pregnanetriol | 1972 |
Difficulties in the diagnosis of the adrenogenital syndrome in infancy.
Topics: Adrenal Hyperplasia, Congenital; Age Factors; Androstanes; Chromatography, Gas; Chromatography, Thin Layer; Humans; Infant, Newborn; Ketosteroids; Lipid Metabolism, Inborn Errors; Male; Mixed Function Oxygenases; Pregnanes; Pregnanetriol | 1972 |
Congenital adrenal hyperplasia and diabetes mellitus in a woman aged 71 years.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Age Factors; Aged; Diabetes Complications; Female; Glucose Tolerance Test; Humans; Prednisone; Pregnanetriol | 1972 |
A study of the renin-aldosterone system in congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Blood Pressure; Child; Clitoris; Female; Humans; Hyperplasia; Hyponatremia; Infant, Newborn; Male; Metabolism, Inborn Errors; Pregnanetriol; Renin; Sodium; Sodium Chloride; Steroid Hydroxylases; Water-Electrolyte Balance | 1972 |
An unusual form of adrenogenital syndrome.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Humans; Hydroxysteroid Dehydrogenases; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol | 1971 |
Urinary excretion of pregnanetriol and 5 -pregnenetriol in two forms of congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Administration, Oral; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Glucocorticoids; Humans; Hydrolysis; Hydroxysteroid Dehydrogenases; Infant; Infant, Newborn; Ketosteroids; Male; Methods; Mixed Function Oxygenases; Pregnanetriol | 1971 |
[Adrenogenital syndrome of the adult male. 3 cases].
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Estrogens; Humans; Infertility, Male; Male; Middle Aged; Pregnanetriol; Spermatogenesis | 1971 |
[Evaluation of neutral urinary steroid analysis by gas liquid chromatography using OV-210].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Cushing Syndrome; Etiocholanolone; Humans; Hydrocortisone; Hyperthyroidism; Male; Pregnanetriol | 1971 |
Prenatal diagnosis of adrenogenital syndrome by amniocentesis.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Amniotic Fluid; Chromatography; Female; Fetal Diseases; Gestational Age; Humans; Hyperplasia; Infant, Newborn; Pregnancy; Pregnanetriol; Tritium | 1969 |
On the metabolism of 16-alpha-hydroxy-C21-steroids. 3. Evidence for high rates of production of 16-alpha-hydroxyprogesterone and 16-alpha-hydroxypregnenolone in the salt-losing form of congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Chromatography; Female; Humans; Male; Photometry; Pregnanes; Pregnanetriol; Triamcinolone | 1969 |
[Adrenogenital syndrome in sisters].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Pregnanetriol; Sex Chromosomes | 1969 |
Exchangeable sodium and aldosterone secretion in children with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone; Child; Child, Preschool; Humans; Hydrocortisone; Infant; Infant, Newborn; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol; Sodium | 1970 |
[Pregnanetriolone and the adrenogenital syndrome].
Topics: 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Amenorrhea; Chromatography, Thin Layer; Female; Glucocorticoids; Humans; Hydroxysteroid Dehydrogenases; Ketones; Menstruation Disturbances; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Progesterone | 1970 |
Congenital adrenogenital syndrome and successful pregnancy. Report of a case.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Cesarean Section; Clitoris; Corticosterone; Dexamethasone; Female; Humans; Hydrocortisone; Pregnancy; Pregnancy Complications; Pregnanediol; Pregnanetriol | 1970 |
Steroid studies in parents of patients with congenital virilizing adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Androstanes; Body Height; Body Surface Area; Body Weight; Chromatography, Gas; Creatinine; Female; Heterozygote; Humans; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Steroids; Urine | 1971 |
Urinary excretion of glucuronides and sulfates of acetaldehydogenic steroids.
Topics: Acetaldehyde; Acetates; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Chromatography, Paper; Cushing Syndrome; Glucuronates; Glucuronidase; Humans; Pregnanediol; Pregnanes; Pregnanetriol; Pregnenolone; Sulfates | 1968 |
Blood progesterone and 17-hydroxyprogesterone levels and production rates in a boy with virilizing congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Carbon Isotopes; Chemistry, Clinical; Child, Preschool; Chromatography, Gas; Chromatography, Thin Layer; Humans; Hydroxyprogesterones; Hyperplasia; Male; Metabolic Clearance Rate; Pregnanetriol; Progesterone; Tritium | 1968 |
[Studies of the enzymatic determination of pregnane-3 alpha, 17 alpha, 20 alpha-triol in the urine].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Chromatography, Paper; Cushing Syndrome; Female; Glucuronidase; Humans; Hydroxysteroid Dehydrogenases; Male; Methods; Middle Aged; Pregnanetriol; Pseudomonas | 1968 |
Statural growth in congenital adrenal hyperplasia treated with hydrocortisone.
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Body Height; Bone Development; Child, Preschool; Corticosterone; Female; Growth; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium | 1968 |
[Steroid chemical studies on heterozygote trait carriers of congenital virilizing adrenal cortex hyperplasia].
Topics: Adrenal Hyperplasia, Congenital; Adult; Chromatography, Gas; Female; Heterozygote; Humans; Male; Methods; Pregnanetriol; Testosterone | 1968 |
Ventricular tachycardia associated with hyperkalemia. Occurrence in an infant aged 13 days with adrenogenital syndrome.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Electrocardiography; Humans; Hyperkalemia; Infant, Newborn; Infant, Newborn, Diseases; Male; Pregnanetriol; Tachycardia | 1969 |
Simulated congenital adrenal hyperplasia in a male neonate associated with medroxyprogesterone therapy during pregnancy.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Diagnosis, Differential; Female; Humans; Infant, Newborn; Infant, Newborn, Diseases; Male; Maternal-Fetal Exchange; Medroxyprogesterone; Pregnancy; Pregnancy Complications; Pregnanetriol | 1969 |
Androgen metabolism in congenital adrenal hyperplasia due to 11 beta-hydroxylase deficiency.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androgens; Androstanes; Child, Preschool; Female; Humans; Hyperplasia; Mixed Function Oxygenases; Pregnanetriol; Testosterone | 1969 |
[Diagnosis and therapeutic results in cases of hirsutism in women].
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Androsterone; Cushing Syndrome; Diagnosis, Differential; Female; Hirsutism; Humans; Polycystic Ovary Syndrome; Pregnanetriol | 1969 |
Quantitative estimation of urinary pregnanetriol, pregnanetriolone, tetrahydro S and delta-5-pregnenetriol in the investigation of adrenocortical function.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Paper; Clitoris; Cushing Syndrome; Female; Hirsutism; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors; Methods; Mixed Function Oxygenases; Pituitary-Adrenal Function Tests; Pregnanetriol; Sex Chromosome Aberrations; Urogenital Abnormalities | 1969 |
Adrenogenital syndrome. Association with 3-beta-hydroxysteroid dehydrogenase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Chloramphenicol; Desoxycorticosterone; Female; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Infant, Newborn; Mestranol; Metabolic Diseases; Norethynodrel; Penicillins; Pregnanetriol; Pyelonephritis; Sepsis; Streptomycin; Urine | 1965 |
[Problems of congenital adrenogenital syndrom in childhood].
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol | 1965 |
Gas chromatographic estimation of urinary pregnanetriol, pregnanetriolone and pregnanetetrol in congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aged; Chromatography, Gas; Female; Humans; Male; Middle Aged; Pregnanediol; Pregnanetriol | 1966 |
Varying expression for salt losing in related patients with congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium Chloride | 1966 |
Excretion of six individual 17-ketosteroids and testosterone in four girls with precocious sexual hair (premature adrenarche).
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Body Height; Child; Chromatography, Paper; Electroencephalography; Female; Growth; Hair; Humans; Pregnanetriol; Puberty, Precocious; Testosterone | 1966 |
[Gas chromatography determination of pregnanediol, pregnanetriol and pregnanetriolone in urine].
Topics: Adrenal Hyperplasia, Congenital; Androsterone; Chemistry, Clinical; Chromatography, Gas; Glucuronidase; Pregnanediol; Pregnanes; Pregnanetriol | 1966 |