Page last updated: 2024-08-26

pregnanetriol and Congenital Adrenal Hyperplasia

pregnanetriol has been researched along with Congenital Adrenal Hyperplasia in 161 studies

Research

Studies (161)

TimeframeStudies, this research(%)All Research%
pre-1990141 (87.58)18.7374
1990's7 (4.35)18.2507
2000's4 (2.48)29.6817
2010's8 (4.97)24.3611
2020's1 (0.62)2.80

Authors

AuthorsStudies
Hamajima, T; Hasegawa, Y; Itonaga, T; Izawa, M1
Beuschlein, F; Greifenstein, A; Krone, N; Reincke, M; Reisch, N; Rottenkolber, M; Schmidt, H; Schwarz, HP1
Fukami, M; Hasegawa, T; Hayashi, M; Homma, K; Kataoka, Y; Kato, F; Ogata, T; Oiso, Y; Sasano, H; Sugimura, Y; Tanaka, H1
Boettcher, C; Hartmann, MF; Kamrath, C; Wudy, SA1
Boettcher, C; Hartmann, MF; Kamrath, C; Wudy, SA; Zimmer, KP1
Arlt, W; Hughes, BA; Jones, CM; Krone, N; Mallappa, A; Merke, DP; Nikolaou, N; O'Neil, DM; Reisch, N; Ross, RJ; Storbeck, KH; Tomlinson, JW; Whitaker, MJ1
Dörr, HG; Kiess, W; Körner, A; Kratzsch, J; Rascher, W; Simm, D; Völkl, TM1
Dörr, HG; Kiess, W; Körner, A; Kratzsch, J; Simm, D; Völkl, TM1
Dauber, A; Kellogg, M; Majzoub, JA1
Fukami, M; Hasegawa, T; Homma, K; Ikeda, K; Koyama, Y; Miwa, M; Murata, M; Ogata, T1
Chan, AO; Taylor, NF1
BELL, M; VARLEY, H1
BONGIOVANNI, A1
DION, FR; HAYLES, AB; MATTOX, VR; SALASSA, RM1
DAVID, MA; FAREDIN, I; JULESZ, M; SZARVAS, F; TOTH, I1
BONGIOVANNI, AM; EBERLEIN, WR; ROOT, AW1
CONCOLINO, G; RASCIO, L; SCIARRA, F; SORCINI, G1
BROSSWITZ, E; LOHMEYER, H1
Anzo, M; Hamajima, T; Hasegawa, T; Homma, K; Jinno, K; Matsuo, N; Ohashi, T; Takahashi, T; Takahashi, Y; Takeshita, E; Toyoura, T; Watanabe, K1
Toma, Y; Yanaihara, T1
Aceto, T; Caprano, VJ; MacGILLIVRAY, MH; Munschauer, RW; Raiti, S1
Bacchus, H1
Finkelstein, M; Halperin, G1
Kusunoki, T; Matsumoto, K; Mizutani, S; Seki, T1
Faredin, I; Tóth, I1
Lacroix, A; McKenna, TJ; Moore, GW; Rabin, D1
LaFranchi, S1
Prader, A; Tassinari, D; Zachmann, M1
Levine, LS; Mininberg, DT; New, MI1
Joannou, GE1
Drayer, NM; Nagel, GT; van der Ploeg, KR; Volmer, M; Wolthers, BG1
Czira, G; Kecskés, L1
Bougneres, P; Couzinet, B; Elkik, F; Gourmelen, M; Schaison, G1
Jansen, M; van den Brande, JL; Wit, JM1
Ishida, H; Kinoshita, K; Minowada, S; Niijima, T1
Hendricks, SA; Kaplan, SA; Lavin, N; Lippe, BM; Mayes, DM1
Gutai, JP; Lee, PA; Migeon, CJ; Urban, MD1
Frisch, H; Parth, K; Schober, E; Swoboda, W1
Granoff, AB1
Lim, YJ; Montalto, J; Warne, GL; Yong, AB1
Fardella, CE; Lin, D; Mahachoklertwattana, P; Miller, WL; Zhang, LH1
Joannou, GE; Reeder, AY1
Saisho, S; Shimozawa, K; Toyoura, T; Yang, Y; Yata, J1
Phillipov, G1
Dörr, HG; Frenzel, S1
Bierich, JR; Gupta, D1
Ferrante, L1
Barrett, GN; Clayton, GW; Holcombe, JH; Keenan, BS; Kirkland, RT; McNeel, R1
Hammond, CB; Riddick, DH2
Brandt-Erichsen, D; Donelan, L; Schoen, EJ; Solomon, IL1
Bongiovanni, AM; Genel, M; Goldman, AS; Rosenfield, RL; Schneider, G1
David, R; Youssefnejadian, E1
Burr, IM; Jennings, AS; Liddle, GW; McKenna, TJ1
Baron, MC; Girard, F; Gourmelen, M; Pham-Huu-Trung, MT; Raux, MC1
Bohrn, E; Brunel, R; Parth, K; Swoboda, W; Zimprich, H1
Christensen, T; Petersen, KE1
Brown, DR; Steffes, MW; Ulstrom, RA; Wong, ET1
Chowers, I; Finkelstein, M; Maschler, I; Muller, A; Shaefer, J; Slavin, S; Weidenfeld, J1
Prader, A; Zachmann, M1
Bailey, CC; Komrower, GM; Palmer, M1
Blizzard, RM; Huseman, CA; Johanson, A; Varma, MM1
Manouguian, G; Stubbe, P1
Hansen, JW; Loriaux, DL1
Juricskay, Z; Kecskés, L; Németh, M; Temesi, M; Tényi, I1
Hughes, IA; Winter, JS1
Shibata, Y1
Franceschetti, F; Magini, A; Messeri, G; Pazzagli, M; Pinzani, P1
Goldsmith, MA; Miller, WL; Solish, SB; Voutilainen, R1
Itoh, N; Kumamoto, Y; Maruta, H; Mikuma, N; Nanbu, A; Tachiki, H; Takagi, Y; Tsunekawa, T1
Homoki, J; Solyom, J; Teller, WM1
Connelly, JF; Davies, HE; Montalto, J; Pitt, JJ; Warne, GL; Yong, AB1
Chrousos, GP; Cutler, GB; Loriaux, DL; Winterer, J1
Hikita, Y1
Fuse, H; Ito, H; Kataumi, Z; Kawamura, K; Shimazaki, J; Sumiya, H1
Frisch, H; Nowotny, P; Vierhapper, H; Waldhäusl, W1
Kellie, AE; Samarajeewa, P1
Canlorbe, P; Chaussain, JL; Job, JC; Munck, A1
Davis, JC; Fliegner, JR; Jeffcoate, TN; Russell, SH; Wade, AP1
Bertrand, J; Cathro, DM; Coyle, MG1
Nichols, J1
Prlpva, VG1
Gson, GG; Nichols, J1
Dorfman, RI; Forchielli, E; Rivera, R1
Cyran, J; Göbel, P1
Cacciari, E; Cicognani, A; Dallera, L; Miano, A; Tassoni, P1
Schindler, H1
Gabrilove, JL; Garmendia, F; Nicolis, GL1
Golubev, VA1
Berger, H; Glatzl, J; Gleispach, H; Rössler, H2
Balachandran, R; Sanghvi, A; Serenko, A; Wight, C1
Metcalf, MG1
Hall, K; Hökfelt, B1
Nagano, T1
Brough, AJ; Camacho, AM; Kowarski, A; Migeon, CJ1
Drayer, NM; Galal, OM; Rudd, BT1
Steinbeck, AW; Thomas, FJ2
Dingman, JF; Lim, NY; Mimica, N1
Acerbi, L; Faglia, G; Farrari, C; Gattinoni, L; Neri, V; Travaglini, P1
New, MI; Seaman, MP1
Cohen, MM; Edwards, JA; Schussler, GC; Vance, VK1
Curtius, HC; Murset, G; Prader, A; Vollmin, JA; Zachmann, M1
Brimblecombe, FS; Eades, SM; Rossiter, MA1
Matsumoto, Y1
Bode, HH; Crawford, JD; Hayek, A1
Curtius, HC; New, MI; Prader, A; Völlmin, JA; Zachmann, M1
Gregorová, I; Horký, K; Kuchel, O; Stárka, L1
Levine, LS; New, MI; Peterson, RE; Pitt, P1
Atherden, SM; Barnes, ND1
Grychtolik, H; Gudowski, G; Ijaiya, K; Tacke, A1
Bayard, F; Beitins, IZ; Kowarski, A; Migeon, CJ1
Newns, GH1
Bailey, CC; Komrower, GM1
Berger, H; Glatzl, J; Gleispach, H; Rössler, H; Tschager, E1
Coyotupa, J; Kaplan, SA; LaFranchi, SH; Lavin, N; Lippe, BM; Parlow, A1
Gleispach, H1
Bidlingmaier, F; Knorr, D1
Bongiovanni, AM; Kirkland, R; Parks, JS; Ranke, M; Tenore, A; Vaidya, V1
Mallin, SR; Walker, FA1
Bergadá, C; Dahl, V; Rivarola, MA1
Knorr, D2
Bergier, G; Varette-Dauvergne, Y; Zakarian, S; Zographos, G1
Bierich, JR; Gupta, D; Huenges, R; Rager, K1
Basmaciogullari, A; Bouthreuil, E; Marti-Henneberg, C; Rappaport, R1
Gabrilove, JL; Nicolis, GL; Sohval, AR1
Frasier, SD; Horton, R; Weiss, BA1
Serrera Contreras, JL1
Holzmann, K; Mickan, H; Wittenbecher, G1
New, MI1
Teller, WM1
Farquhar, JW; Mitchell, FL; Shackleton, CH1
Bicknell, EJ1
Kotchen, TA; Strickland, AL1
Hrnciar, J; Izakovic, V; Stárka, L1
Bongiovanni, AM; Eberlein, WR; Moshang, T1
Herrera Pombo, JL; Ramos, F; Rodríguez Miñón, JL; Vivanco, F1
Merkatz, IR; New, MI; Peterson, RE; Seaman, MP1
Christy, NP; Janoski, AH; Kelly, WG; Roginsky, MS1
Torigoe, T1
Bertrand, J; Haour, F; Loras, B1
Lohmeyer, H1
Miyakawa, I; Mori, N1
Hill, JG; Qazi, QH; Thompson, MW1
Riley, WJ1
Bardin, CW; Lipsett, MB; Strott, CA; Yoshimi, T1
Karl, HJ; Raith, L; Rauhut, D1
Cornu, G; Rappaport, R; Royer, P1
Addy, D; Littlewood, J1
Kelley, VC; Limbeck, GA; Ruvalcaba, RH1
Frasier, SD; Horton, R; Ulstrom, RA1
Szamatowicz, M1
Kogut, MD1
Brachfeldová, J; Hostomská, L1
Isurugi, K; Kinoshita, K; Kumamoto, Y; Takayasu, H1
Rosenbloom, AL; Smith, DW1
Degenhart, HJ; Visser, HK1
Curtius, HC1

Reviews

6 review(s) available for pregnanetriol and Congenital Adrenal Hyperplasia

ArticleYear
Monitoring of therapy in congenital adrenal hyperplasia.
    Clinical chemistry, 2010, Volume: 56, Issue:8

    Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Bone Development; Catecholamines; Glucocorticoids; Humans; Mineralocorticoids; Monitoring, Physiologic; Pregnanetriol; Saliva; Testosterone

2010
[Pregnanediol (P2), pregnanetriol (P3)].
    Nihon rinsho. Japanese journal of clinical medicine, 2005, Volume: 63 Suppl 8

    Topics: Adrenal Hyperplasia, Congenital; Biomarkers; Chromatography, Gas; Cushing Syndrome; Female; Humans; Hypertension; Luteinization; Male; Ovarian Function Tests; Ovulation Detection; Placental Function Tests; Pregnancy; Pregnanediol; Pregnanetriol; Reference Values; Specimen Handling

2005
[The clinical value of amniotic fluid studies (literature review)].
    Akusherstvo i ginekologiia, 1971, Volume: 47, Issue:10

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Carbon Dioxide; Chromosome Aberrations; Chromosome Disorders; Congenital Abnormalities; Down Syndrome; Embryonic and Fetal Development; Erythroblastosis, Fetal; Estriol; Female; Fetal Diseases; Humans; Mucopolysaccharidoses; Oxygen; Pregnancy; Pregnanetriol; Rh-Hr Blood-Group System; Sex Chromatin; Sex Determination Analysis

1971
Congenital adrenal hyperplasia.
    Archives of disease in childhood, 1974, Volume: 49, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Bone Development; Child; Cortisone; Female; Glucocorticoids; Growth; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Menstruation; Mixed Function Oxygenases; Pregnanetriol; Sodium Chloride; Spermatogenesis; Virilism

1974
[Intersexuality in childhood].
    Medizinische Klinik, 1974, Nov-01, Volume: 69, Issue:44

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Androgen-Insensitivity Syndrome; Child; Child, Preschool; Chorionic Gonadotropin; Diagnosis, Differential; Disorders of Sex Development; Female; Genetic Counseling; Genitalia, Female; Genitalia, Male; Humans; Hypospadias; Infant; Klinefelter Syndrome; Male; Mosaicism; Pregnanetriol; Progesterone; Psychosexual Development; Sex Chromosome Aberrations; Transsexualism; Turner Syndrome; Virilism

1974
Congenital adrenal hyperplasia.
    Pediatric clinics of North America, 1968, Volume: 15, Issue:2

    Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Glucocorticoids; Gonadal Steroid Hormones; Humans; Metabolism, Inborn Errors; Mineralocorticoids; Pregnanetriol

1968

Trials

4 trial(s) available for pregnanetriol and Congenital Adrenal Hyperplasia

ArticleYear
Pregnenolone, 17-OH-pregnenolone, and testosterone in plasma of patients with congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1976, Volume: 42, Issue:5

    Topics: 17-alpha-Hydroxypregnenolone; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Clinical Trials as Topic; Female; Humans; Hydrocortisone; Hyperplasia; Infant; Male; Pregnanetriol; Pregnenolone; Progesterone Reductase; Steroid Hydroxylases; Testosterone

1976
Effect of hydrocortisone dose schedule on adrenal steroid secretion in congenital adrenal hyperplasia.
    The Journal of pediatrics, 1985, Volume: 106, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Child; Cortodoxone; Drug Administration Schedule; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pregnanetriol

1985
Single dose dexamethasone in treatment of congenital adrenocortical hyperplasia.
    Metabolism: clinical and experimental, 1971, Volume: 20, Issue:9

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Circadian Rhythm; Clinical Trials as Topic; Cortisone; Dexamethasone; Female; Humans; Hydrocortisone; Hyperplasia; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol

1971
Effect of aminoglutethimide on urinary steroid excretion in patients with congenital adrenal hyperplasia due to incomplete 21-hydroxylase deficiency.
    Metabolism: clinical and experimental, 1972, Volume: 21, Issue:4

    Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropic Hormone; Adult; Aminoglutethimide; Androsterone; Aniline Compounds; Anticonvulsants; Chemistry, Clinical; Clinical Trials as Topic; Dehydroepiandrosterone; Depression, Chemical; Dexamethasone; Etiocholanolone; Female; Humans; Metabolism, Inborn Errors; Metyrapone; Mixed Function Oxygenases; Pregnanetriol; Pyridones

1972

Other Studies

151 other study(ies) available for pregnanetriol and Congenital Adrenal Hyperplasia

ArticleYear
First Morning Pregnanetriol and 17-Hydroxyprogesterone Correlated Significantly in 21-Hydroxylase Deficiency.
    Frontiers in endocrinology, 2021, Volume: 12

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Humans; Pregnanetriol; Prospective Studies; Young Adult

2021
Testicular adrenal rest tumors develop independently of long-term disease control: a longitudinal analysis of 50 adult men with congenital adrenal hyperplasia due to classic 21-hydroxylase deficiency.
    The Journal of clinical endocrinology and metabolism, 2013, Volume: 98, Issue:11

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Child; Child, Preschool; Cross-Sectional Studies; Follow-Up Studies; Glucocorticoids; Humans; Infant; Infertility, Male; Longitudinal Studies; Male; Pregnanetriol; Retrospective Studies; Testicular Neoplasms; Ultrasonography

2013
A 68-year-old phenotypically male patient with 21-hydroxylase deficiency and concomitant adrenocortical neoplasm producing testosterone and cortisol.
    The Tohoku journal of experimental medicine, 2013, Volume: 231, Issue:2

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Aged; Androstenedione; Base Sequence; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydrocortisone; Immunohistochemistry; Japan; Magnetic Resonance Imaging; Male; Molecular Sequence Data; Pregnanetriol; Sequence Analysis, DNA; Testosterone

2013
Reduced activity of 11β-hydroxylase accounts for elevated 17α-hydroxyprogesterone in preterms.
    The Journal of pediatrics, 2014, Volume: 165, Issue:2

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Chromatography, Gas; Cortodoxone; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Infant, Premature; Male; Mass Spectrometry; Metabolome; Pregnanetriol; Retrospective Studies; Steroid 11-beta-Hydroxylase; Steroid 17-alpha-Hydroxylase

2014
Diagnosis of 21-hydroxylase deficiency by urinary metabolite ratios using gas chromatography-mass spectrometry analysis: Reference values for neonates and infants.
    The Journal of steroid biochemistry and molecular biology, 2016, Volume: 156

    Topics: Adrenal Hyperplasia, Congenital; Cohort Studies; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Male; Metabolomics; Pregnanetriol; Reference Values; Steroids; Tetrahydrocortisone

2016
Modified-Release and Conventional Glucocorticoids and Diurnal Androgen Excretion in Congenital Adrenal Hyperplasia.
    The Journal of clinical endocrinology and metabolism, 2017, 06-01, Volume: 102, Issue:6

    Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androsterone; Circadian Rhythm; Cortodoxone; Delayed-Action Preparations; Dexamethasone; Female; Gas Chromatography-Mass Spectrometry; Glucocorticoids; Humans; Hydrocortisone; Male; Middle Aged; Prednisolone; Pregnanetriol; Young Adult

2017
Does an altered leptin axis play a role in obesity among children and adolescents with classical congenital adrenal hyperplasia due to 21-hydroxylase deficiency?
    European journal of endocrinology, 2009, Volume: 160, Issue:2

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Cross-Sectional Studies; Female; Humans; Insulin Resistance; Leptin; Male; Models, Statistical; Obesity; Overweight; Pregnanetriol; Prospective Studies; Receptors, Leptin; Risk Factors; Steroid 21-Hydroxylase; Testosterone; Young Adult

2009
Adiponectin levels are high in children with classic congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency.
    Acta paediatrica (Oslo, Norway : 1992), 2009, Volume: 98, Issue:5

    Topics: 17-alpha-Hydroxyprogesterone; Adiponectin; Adolescent; Adrenal Hyperplasia, Congenital; Body Mass Index; Bone Development; Child; Child, Preschool; Cross-Sectional Studies; Dehydroepiandrosterone Sulfate; Female; Glucocorticoids; Humans; Male; Mineralocorticoids; Obesity; Pregnanetriol; Prospective Studies; Saliva; Skinfold Thickness; Steroid 21-Hydroxylase; Testosterone; Young Adult

2009
Two-step biochemical differential diagnosis of classic 21-hydroxylase deficiency and cytochrome P450 oxidoreductase deficiency in Japanese infants by GC-MS measurement of urinary pregnanetriolone/ tetrahydroxycortisone ratio and 11β-hydroxyandrosterone.
    Clinical chemistry, 2012, Volume: 58, Issue:4

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androsterone; Biomarkers; Case-Control Studies; Diagnosis, Differential; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Male; NADPH-Ferrihemoprotein Reductase; Pregnanetriol; Steroid 17-alpha-Hydroxylase; Steroid 21-Hydroxylase; Tetrahydrocortisone

2012
New strategies for detecting steroid metabolic disorders--paneling vs profiling.
    Clinical chemistry, 2012, Volume: 58, Issue:8

    Topics: Adrenal Hyperplasia, Congenital; Androsterone; Female; Humans; Male; NADPH-Ferrihemoprotein Reductase; Pregnanetriol; Steroid 21-Hydroxylase; Tetrahydrocortisone

2012
The estimation of pregnanetriol and 17-hydroxypregnanolone in urine in congenital adrenal hyperplasia.
    Clinica chimica acta; international journal of clinical chemistry, 1960, Volume: 5

    Topics: Adrenal Cortex; Adrenal Hyperplasia, Congenital; Humans; Pregnanediol; Pregnanetriol; Pregnanolone

1960
The value of urinary pregnanetriol levels in the diagnosis and treatment of the adrenogenital syndrome.
    Laval medical, 1959, Volume: 28

    Topics: Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Body Fluids; Pregnanediol; Pregnanetriol

1959
URINARY STEROID PATTERNS AND LOSS OF SALT IN CONGENITAL ADRENAL HYPERPLASIA.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Aldosterone; Biomedical Research; Blood; Child; Creatine; Creatinine; Diet, Sodium-Restricted; Humans; Infant; Infant, Newborn; Natriuresis; Pregnanediol; Pregnanetriol; Sodium; Sodium, Dietary; Steroids

1964
PREGNANETRIOL STUDIES IN HIRSUTISM AND OTHER ENDOCRINE DISEASES.
    Acta medica Academiae Scientiarum Hungaricae, 1964, Volume: 20

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenogenital Syndrome; Cushing Syndrome; Endocrine System Diseases; Hirsutism; Hypertrichosis; Metabolism; Obesity; Pregnanetriol; Progestins; Urine

1964
MEASUREMENT OF PREGNANETRIOL IN PLASMA.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Blood; Body Fluids; Child; Cortisone; Drug Therapy; Humans; Hydrocortisone; Infant; Infant, Newborn; Pregnanetriol; Progestins; Urine

1964
[PLASMATIC ESTROGENS IN BILATERAL HYPERPLASIA OF THE ADRENAL CORTEX. COMPARATIVE STUDY IN CONGENITAL ADRENOGENITAL SYNDROME AND CUSHING'S SYNDROME].
    Folia endocrinologica, 1964, Volume: 17

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adrenogenital Syndrome; Blood; Cushing Syndrome; Estrogens; Humans; Hyperplasia; Pharmacology; Pregnanetriol; Triamcinolone; Urine

1964
[PREGNANETRIOLONE. SYNTHESIS, QUANTITATIVE DETERMINATION AND ITS IMPORTANCE IN ADRENOGENITAL SYNDROME AND IN FEMALE STERILITY].
    Zeitschrift fur Geburtshilfe und Gynakologie, 1964, Volume: 162

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Chromatography; Cortisone; Female; Humans; Infertility, Female; Metabolism; Pregnanetriol

1964
Elevated urine pregnanetriolone definitively establishes the diagnosis of classical 21-hydroxylase deficiency in term and preterm neonates.
    The Journal of clinical endocrinology and metabolism, 2004, Volume: 89, Issue:12

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Case-Control Studies; Diagnosis, Differential; Female; Gestational Age; Humans; Infant, Newborn; Infant, Premature; Male; Pregnanetriol; Sensitivity and Specificity

2004
Congenital virilizing adrenal hyperplasia without acceleration of growth or bone maturation.
    JAMA, 1966, Dec-26, Volume: 198, Issue:13

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Infant; Pregnanetriol

1966
A method for measurement of total 17-OH, 21-methyl steroids in the urine and its application to clinical problems.
    Metabolism: clinical and experimental, 1967, Volume: 16, Issue:2

    Topics: 17-Hydroxycorticosteroids; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Carbon Tetrachloride; Chemistry Techniques, Analytical; Chromatography, Paper; Corticosterone; Cortisone; Glucuronidase; Humans; Pregnanetriol

1967
Biosynthesis of pregnanetriolone and pregnanetetrol in congenital adrenal hyperplasia.
    Acta endocrinologica, 1967, Volume: 54, Issue:3

    Topics: 17-alpha-Hydroxypregnenolone; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Carbon Isotopes; Chromatography, Thin Layer; Female; Humans; Hydroxyprogesterones; Hyperplasia; Pregnanediol; Pregnanetriol; Tritium

1967
Urinary steroids in fifteen cases of congenital virilizing adrenal hyperplasia.
    Endocrinologia japonica, 1967, Volume: 14, Issue:2

    Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Estrogens; Female; Gonadotropins; Humans; Hydroxyprogesterones; Hyperplasia; Male; Pregnanetriol; Virilism

1967
Metabolism and concentration of androgenic steroids in abdominal skin of hirsute women with androgenital syndrome.
    Acta medica Hungarica, 1984, Volume: 41, Issue:1

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Abdominal Muscles; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenediol; Androstenedione; Dehydroepiandrosterone; Female; Hirsutism; Humans; Male; Middle Aged; Pregnanetriol; Skin; Sulfates; Testosterone

1984
Gonadal dysfunction in adult men with congenital adrenal hyperplasia.
    Acta endocrinologica, 1980, Volume: 95, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Dexamethasone; Follicle Stimulating Hormone; Humans; Leydig Cells; Luteinizing Hormone; Male; Pregnanetriol; Pregnenolone; Progesterone; Testis; Testosterone

1980
Plasma adrenocorticotrophic hormone in congenital adrenal hyperplasia. Importance in long-term management.
    American journal of diseases of children (1960), 1980, Volume: 134, Issue:11

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Female; Fludrocortisone; Glucocorticoids; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Long-Term Care; Male; Natriuresis; Pregnanetriol

1980
Clinical and biochemical variability of congenital adrenal hyperplasia due to 11 beta-hydroxylase deficiency. A study of 25 patients.
    The Journal of clinical endocrinology and metabolism, 1983, Volume: 56, Issue:2

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Cortodoxone; Female; Humans; Hydrocortisone; Infant, Newborn; Male; Pregnanediones; Pregnanetriol; Steroid Hydroxylases

1983
Current concepts in congenital adrenal hyperplasia.
    Pathology annual, 1982, Volume: 17 Pt 2

    Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Cholesterol Side-Chain Cleavage Enzyme; Corticosterone; Female; Humans; Hydroxyprogesterones; Infant, Newborn; Male; Pregnanetriol; Progesterone Reductase; Steroid Hydroxylases

1982
Identification of 15 beta-hydroxylated C21 steroids in the neo-natal period: the role of 3 alpha,15 beta,17 alpha-trihydroxy-5 beta-pregnan-20-one in the perinatal diagnosis of congenital adrenal hyperplasia (CAH) due to a 21-hydroxylase deficiency.
    Journal of steroid biochemistry, 1981, Volume: 14, Issue:9

    Topics: 17-alpha-Hydroxypregnenolone; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Penicillium; Pregnancy; Pregnanetriol; Pregnenes; Steroid Hydroxylases

1981
The diagnosis of 21-hydroxylase deficiency in a prematurely born infant on the basis of the urinary steroid excretion pattern.
    Clinica chimica acta; international journal of clinical chemistry, 1982, Apr-23, Volume: 120, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Aging; Androstanes; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydrocortisone; Infant, Newborn; Infant, Premature; Male; Pregnanes; Pregnanetriol; Pregnanolone; Pregnenes; Steroid Hydroxylases; Steroids; Tetrahydrocortisone

1982
Steroid spectrum in human urine as revealed by gas chromatography V. Identification and quantitation of 3 alpha, 20 alpha-dihydroxy-5-beta pregnan-11-one (11-keto-pregnanediol) during different stages of development in children with C/21 hydroxylase defic
    Acta biochimica et biophysica; Academiae Scientiarum Hungaricae, 1981, Volume: 16, Issue:3-4

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Aging; Child; Child, Preschool; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Male; Pregnanediol; Pregnanetriol; Puberty; Steroid Hydroxylases

1981
Angiotensin and adrenal steroidogenesis: study of 21-hydroxylase-deficient congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1980, Volume: 51, Issue:6

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Angiotensin II; Diet, Sodium-Restricted; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pregnanetriol; Renin; Steroid Hydroxylases

1980
Reinstitution of mineralocorticoid therapy in congenital adrenal hyperplasia. Effects on control and growth.
    Acta paediatrica Scandinavica, 1981, Volume: 70, Issue:2

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Growth; Humans; Hydrocortisone; Male; Mineralocorticoids; Pregnanetriol; Renin

1981
Dissociation of plasma renin activity and plasma aldosterone level during dexamethasone suppression test in non-salt-losers with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
    Endocrinologia japonica, 1980, Volume: 27, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Dexamethasone; Female; Humans; Male; Pregnanetriol; Renin

1980
Urinary and serum steroid concentrations in the management of congenital adrenal hyperplasia. Lack of physiologic correlations.
    American journal of diseases of children (1960), 1982, Volume: 136, Issue:3

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Child; Child, Preschool; Dose-Response Relationship, Drug; Female; Hormones; Humans; Infant; Male; Pregnanetriol

1982
Plasma progesterone, 17-hydroxyprogesterone, androstenedione and testosterone in prepubertal, pubertal and adult subjects with congenital virilizing adrenal hyperplasia as indicators of adrenal suppression.
    Hormone research, 1980, Volume: 13, Issue:6

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydroxyprogesterones; Infant; Male; Pregnanetriol; Progesterone; Puberty; Sex Factors; Testosterone

1980
Circadian patterns of plasma cortisol, 17-hydroxyprogesterone, and testosterone in congenital adrenal hyperplasia.
    Archives of disease in childhood, 1981, Volume: 56, Issue:3

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Prednisone; Pregnanetriol; Testosterone

1981
Treatment of menstrual irregularities with dexamethasone in congenital adrenal hyperplasia.
    Journal of adolescent health care : official publication of the Society for Adolescent Medicine, 1981, Volume: 2, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Dexamethasone; Female; Gonadal Steroid Hormones; Humans; Hydroxyprogesterones; Menstruation Disturbances; Pregnanetriol; Testosterone

1981
Urinary 17 alpha-hydroxyprogesterone in management of 21-hydroxylase deficiency.
    Journal of paediatrics and child health, 1995, Volume: 31, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Case-Control Studies; Child; Child, Preschool; Chromatography, Gas; Circadian Rhythm; Enzyme-Linked Immunosorbent Assay; Female; Glucocorticoids; Humans; Hydroxyprogesterones; Infant; Male; Predictive Value of Tests; Pregnanetriol; Radioimmunoassay

1995
Deletion of amino acids Asp487-Ser488-Phe489 in human cytochrome P450c17 causes severe 17 alpha-hydroxylase deficiency.
    The Journal of clinical endocrinology and metabolism, 1993, Volume: 77, Issue:2

    Topics: 17-Hydroxycorticosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Aldehyde-Lyases; Amino Acid Sequence; Base Sequence; Blotting, Southern; Blotting, Western; Cytochrome P-450 Enzyme System; DNA; Female; Homozygote; Humans; Hypertension; Hypokalemia; Molecular Sequence Data; Mutagenesis, Site-Directed; Polymerase Chain Reaction; Pregnanediol; Pregnanetriol; Sequence Deletion

1993
15 beta-hydroxysteroids (Part IV). Steroids of the human perinatal period: the synthesis of 3 alpha,15 beta,17 alpha-trihydroxy-5 alpha-pregnan-20-one and its A/B-ring configurational isomers.
    Steroids, 1995, Volume: 60, Issue:12

    Topics: Adrenal Hyperplasia, Congenital; Gas Chromatography-Mass Spectrometry; Humans; Hydroxysteroids; Infant, Newborn; Magnetic Resonance Spectroscopy; Molecular Structure; Pregnanetriol; Stereoisomerism

1995
Urinary pregnanetriol-3-glucuronide in children: age-related change and application to the management of 21-hydroxylase deficiency.
    Acta paediatrica Japonica : Overseas edition, 1996, Volume: 38, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Child; Child, Preschool; Enzyme-Linked Immunosorbent Assay; Female; Humans; Infant; Infant, Newborn; Male; Pregnanetriol; Reference Values

1996
Effect of hypercortisolism and ACTH on the metabolism of cortisol.
    Experimental and clinical endocrinology & diabetes : official journal, German Society of Endocrinology [and] German Diabetes Association, 1998, Volume: 106, Issue:1

    Topics: ACTH Syndrome, Ectopic; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Cushing Syndrome; Female; Humans; Hydrocortisone; Male; Middle Aged; Pregnanetriol

1998
[Problems of delayed diagnosis of an uncomplicated adrenogenital syndrome (AGS) with 21-hydroxylase defect in a 7-year-old boy].
    Deutsche medizinische Wochenschrift (1946), 1998, Jul-03, Volume: 123, Issue:27

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Anti-Inflammatory Agents; Child; Follicle Stimulating Hormone; Gonadotropin-Releasing Hormone; Humans; Hydrocortisone; Luteinizing Hormone; Luteolytic Agents; Male; Pregnanetriol; Puberty, Precocious; Testosterone; Time Factors; Triptorelin Pamoate

1998
[Prenatal diagnosis of the congenital adrenogenital syndrome].
    Monatsschrift fur Kinderheilkunde, 1975, Volume: 123, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Dehydroepiandrosterone; Estriol; Female; Humans; Hydroxyprogesterones; Pregnancy; Pregnanetriol; Prenatal Diagnosis

1975
[Complex biochemical aspects in virilizing adrenal gland syndromes].
    Minerva pediatrica, 1976, Jun-23, Volume: 28, Issue:22

    Topics: Adrenal Hyperplasia, Congenital; Androsterone; Dehydroepiandrosterone; Etiocholanolone; Female; Humans; Male; Pregnanetriol; Pregnatrienes; Virilism

1976
Plasma androgens in congenital adrenal hyperplasia: androstenedione concentration as an index of adrenal androgen suppression.
    The Journal of laboratory and clinical medicine, 1979, Volume: 94, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; Glucocorticoids; Humans; Male; Pregnanetriol; Testosterone

1979
Long-term steroid therapy in patients with adrenogenital syndrome.
    Obstetrics and gynecology, 1975, Volume: 45, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Age Determination by Skeleton; Age Factors; Body Height; Child; Child, Preschool; Cortisone; Dexamethasone; Female; Fertility; Genitalia, Female; Humans; Karyotyping; Male; Menarche; Methylprednisolone; Pregnanetriol; Seizures; Sex Determination Analysis; Time Factors

1975
Adrenal virilism due to 21-hydroxylase deficiency in the postmenarchial female.
    Obstetrics and gynecology, 1975, Volume: 45, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Dexamethasone; Female; Hirsutism; Humans; Hydroxysteroids; Menarche; Metabolism, Inborn Errors; Mixed Function Oxygenases; Prednisone; Pregnancy; Pregnanetriol; Time Factors; Virilism

1975
Blood testosterone values in patients with congenital virilizing adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1975, Volume: 40, Issue:3

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Age Determination by Skeleton; Body Height; Child; Child, Preschool; Female; Glucocorticoids; Humans; Male; Pregnanetriol; Testosterone; Virilism

1975
Persistent testicular delta5-isomerase-3beta-hydroxysteroid dehydrogenase (delta5-3beta-HSD) deficiency in the delta5-3beta-HSD form of congenital adrenal hyperplasia.
    The Journal of clinical investigation, 1975, Volume: 55, Issue:4

    Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Chorionic Gonadotropin; Dexamethasone; Gonadotropins, Pituitary; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Isomerases; Male; Pregnanetriol; Puberty; Sodium; Testis; Testosterone

1975
Early diagnosis of congenital adrenal hyperplasia by measurement of 17-hydroxyprogesterone.
    Clinical endocrinology, 1975, Volume: 4, Issue:4

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Female; Fetal Blood; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Pregnanetriol; Umbilical Veins

1975
Plasma aldosterone concentrations related to 17alpha-hydroxyprogesterone in congenital adrenal hyperplasia.
    Acta endocrinologica, 1976, Volume: 82, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Child; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Ketosteroids; Male; Pregnanetriol

1976
Congenital adrenal hyperplasia: simultaneous determination of plasma aldosterone and 17-hydroxyprogesterone.
    Acta endocrinologica, 1978, Volume: 87, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Child; Child, Preschool; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Male; Prednisolone; Pregnanetriol; Radioimmunoassay

1978
17-Hydroxyprogesterone in normal children and congenital adrenal hyperplasia. Measurement in serum by radioimmunoassay after thin-layer chromatography.
    Acta paediatrica Scandinavica, 1979, Volume: 68, Issue:2

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Child; Child, Preschool; Chromatography, Thin Layer; Female; Humans; Hydroxyprogesterones; Infant; Male; Pregnanetriol; Radioimmunoassay; Reference Values

1979
Urinary 17 alpha-hydroxyprogesterone in diagnosis and management of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1979, Volume: 49, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Child, Preschool; Creatinine; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Infant, Newborn, Diseases; Male; Middle Aged; Pregnanetriol

1979
A case of adrenogenital syndrome with aberrant 11beta-hydroxylation.
    Acta endocrinologica, 1977, Volume: 85, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Amenorrhea; Corticosterone; Female; Hirsutism; Humans; Hydrocortisone; Hydroxyprogesterones; Hypertension; Pregnanetriol; Pregnenediones; Steroid Hydroxylases; Syndrome; Testosterone; Thyrotropin; Transcortin

1977
Unusual heterozygotes of congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
    Acta endocrinologica, 1978, Volume: 87, Issue:3

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Female; Heterozygote; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Mixed Function Oxygenases; Pedigree; Pregnanes; Pregnanetriol; Testosterone

1978
Management of congenital adrenal hyperplasia. Urinary steroid estimations--review of their value.
    Archives of disease in childhood, 1978, Volume: 53, Issue:2

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Body Height; Child; Child, Preschool; Female; Fludrocortisone; Humans; Infant; Male; Prednisone; Pregnanetriol; Retrospective Studies

1978
Treatment of congenital virilizing adrenal hyperplasia patients with single and multiple daily doses of prednisone.
    The Journal of pediatrics, 1977, Volume: 90, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Child; Child, Preschool; Drug Administration Schedule; Female; Humans; Hydroxyprogesterones; Male; Prednisone; Pregnanetriol; Progesterone; Testosterone

1977
[Pseudohypoaldsteronism. A further case report (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1977, Volume: 125, Issue:4

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Diagnosis, Differential; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium Chloride

1977
Variable efficacy of glucocorticoids in congenital adrenal hyperplasia.
    Pediatrics, 1976, Volume: 57, Issue:6

    Topics: 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Child; Cortisone; Depression, Chemical; Dexamethasone; Female; Glucocorticoids; Humans; Hydrocortisone; Male; Prednisone; Pregnanetriol; Steroid Hydroxylases

1976
Significance of 3alpha, 17 alpha-dihydroxy-5beta-pregnane-20-one in the diagnosis of congenital adrenal hyperplasia.
    Endokrinologie, 1975, Volume: 66, Issue:1

    Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adult; Cholestanes; Chromatography, Gas; Female; Humans; Hydrolysis; Male; Pregnanediol; Pregnanetriol

1975
The application of a serum 17OH-progesterone radioimmunoassay to the diagnosis and management of congenital adrenal hyperplasia.
    The Journal of pediatrics, 1976, Volume: 88, Issue:5

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Fetal Blood; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Pregnanetriol; Radioimmunoassay; Renin; Sodium Chloride; Steroid Hydroxylases

1976
[Determination of urinary 17 alpha-hydroxyprogesterone excretion using ELISA--evaluation of normal subjects and patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency].
    Nihon Naibunpi Gakkai zasshi, 1991, Aug-20, Volume: 67, Issue:8

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Child; Child, Preschool; Circadian Rhythm; Enzyme-Linked Immunosorbent Assay; Female; Humans; Hydroxyprogesterones; Infant; Infant, Low Birth Weight; Infant, Newborn; Male; Pregnanetriol; Reference Values

1991
A chemiluminescent method for the measurement of pregnanetriol-3 alpha-glucuronide in human diluted urine.
    Journal of bioluminescence and chemiluminescence, 1989, Volume: 4, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Female; Humans; Hydroxyprogesterones; Immunoassay; Luminescent Measurements; Male; Middle Aged; Pregnanetriol; Quality Control

1989
Molecular characterization of a Leydig cell tumor presenting as congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1989, Volume: 69, Issue:6

    Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child, Preschool; Cosyntropin; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Humans; Hydrocortisone; Hydroxyprogesterones; Leydig Cell Tumor; Male; Pregnanetriol; Testicular Neoplasms; Testosterone

1989
[A clinical study of congenital adrenal hyperplasia].
    Hinyokika kiyo. Acta urologica Japonica, 1989, Volume: 35, Issue:11

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Body Height; Bone Development; Child, Preschool; Cyproterone; Cyproterone Acetate; Dexamethasone; Female; Follicle Stimulating Hormone; Humans; Hydrocortisone; Infant; Infant, Newborn; Luteinizing Hormone; Male; Obesity; Pregnanetriol

1989
Detection of late onset steroid 21-hydroxylase deficiency by capillary gas chromatographic profiling of urinary steroids in children and adolescents.
    European journal of pediatrics, 1988, Volume: 147, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Infant; Male; Pregnanes; Pregnanetriol; Pregnanolone; Puberty, Precocious; Steroid Hydroxylases; Tetrahydrocortisol; Virilism

1988
Diagnosis of 21-hydroxylase deficiency in newborn infants by GC-MS of urinary steroids.
    Australian paediatric journal, 1988, Volume: 24, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant, Newborn; Male; Pregnanetriol; Progestins; Steroid Hydroxylases

1988
[Reevaluation of recalled infants by neonatal mass screening for congenital adrenal hyperplasia due to 21-hydroxylase deficiency. Diagnostic value of pregnanetriolone in a single urine specimen using glass capillary gas chromatography].
    Nihon Naibunpi Gakkai zasshi, 1985, Mar-20, Volume: 61, Issue:3

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Chromatography, Gas; Cortodoxone; Female; Follow-Up Studies; Humans; Hydroxyprogesterones; Male; Mass Screening; Pregnancy; Pregnanetriol; Steroid Hydroxylases

1985
[A case of congenital adrenogenital syndrome].
    Hinyokika kiyo. Acta urologica Japonica, 1985, Volume: 31, Issue:8

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Middle Aged; Pregnanetriol; Steroid Hydroxylases

1985
Capillary gas chromatography as a tool for characterization of urinary steroid excretion in patients with congenital adrenal hyperplasia.
    Journal of steroid biochemistry, 1985, Volume: 22, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Male; Middle Aged; Pregnanetriol; Steroids; Tetrahydrocortisone

1985
The radioimmunoassay of pregnanetriol 3 alpha-glucuronide.
    Journal of steroid biochemistry, 1985, Volume: 22, Issue:6

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Antibody Specificity; Child; Female; Haptens; Humans; Hydrocortisone; Immune Sera; Male; Menstruation; Pregnanetriol; Radioimmunoassay; Serum Albumin, Bovine

1985
[Treatment of virilizing adrenal hyperplasia in adolescents. Use and side-effects of dexamethasone].
    Archives francaises de pediatrie, 1985, Volume: 42, Issue:9

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androgens; Child; Dexamethasone; Female; Humans; Hydroxyprogesterones; Male; Pregnanetriol; Virilism

1985
Diagnosis of the adrenogenital syndrome before birth.
    Lancet (London, England), 1965, Sep-18, Volume: 2, Issue:7412

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Female; Fetal Diseases; Humans; Infant, Newborn; Pregnancy; Pregnanetriol

1965
Antenatal diagnosis of adrenocortical hyperplasia.
    Lancet (London, England), 1969, Apr-05, Volume: 1, Issue:7597

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Estriol; Female; Fetal Diseases; Gestational Age; Humans; Infant, Newborn; Pregnancy; Pregnanetriol

1969
Antenatal diagnosis of adrenocortical hyperplasia.
    Lancet (London, England), 1969, Jun-07, Volume: 1, Issue:7606

    Topics: Adrenal Hyperplasia, Congenital; Adult; Amniotic Fluid; Estradiol; Estriol; Estrogens; Estrone; Female; Fetal Diseases; Humans; Pregnancy; Pregnanetriol

1969
[On the method of determination of pregnanetriol].
    Laboratornoe delo, 1969, Volume: 6

    Topics: Abortion, Habitual; Adrenal Gland Diseases; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Female; Humans; Methods; Microchemistry; Pregnancy; Pregnanetriol

1969
Antenatal diagnosis of the adrenogenital syndrome.
    Lancet (London, England), 1969, Nov-15, Volume: 2, Issue:7629

    Topics: Adrenal Hyperplasia, Congenital; Amniotic Fluid; Estriol; Female; Fetal Diseases; Humans; Infant, Newborn; Infant, Newborn, Diseases; Pregnancy; Pregnanetriol

1969
A modified method for the analysis of urinary 17-ketosteroids, pregnanediol and pregnanetriol by gas liquid chromatography in normal subjects and subjects with various endocrine disorders.
    Acta endocrinologica, 1967, Volume: 54, Issue:1

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Disorders of Sex Development; Etiocholanolone; Female; Hirsutism; Humans; Klinefelter Syndrome; Male; Polycystic Ovary Syndrome; Pregnanediol; Pregnanetriol; Testicular Neoplasms; Turner Syndrome

1967
[Gas chromatography determination of urinary pregnanediol and -triol and its significance for the differentiation of adrenal hirsutism in women].
    Endokrinologie, 1969, Volume: 54, Issue:5

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Chemistry, Clinical; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Diagnosis, Differential; Female; Glucocorticoids; Hirsutism; Humans; Pregnanediol; Pregnanetriol

1969
[Various aspects of steroidogenesis in congenital adrenogenital syndrome with or without salt loss (determination of the urinary excretion of aldosterone, androsterone, etiocholanolone, dehydroisoandrosterone, 17-hydroxy-11-desoxycorticosterone, pregnaned
    Minerva pediatrica, 1969, May-26, Volume: 21, Issue:21

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Androsterone; Child; Child, Preschool; Dehydroepiandrosterone; Desoxycorticosterone; Etiocholanolone; Female; Humans; Infant; Kidney; Male; Mineralocorticoids; Pregnanediol; Pregnanetriol; Progestins; Sodium; Water-Electrolyte Balance

1969
[Suprarenal virilism].
    Munchener medizinische Wochenschrift (1950), 1970, Oct-16, Volume: 112, Issue:42

    Topics: 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Dehydroepiandrosterone; Female; Humans; Middle Aged; Pregnanetriol; Puberty, Precocious; Virilism

1970
The determination of urinary pregnanetriol and the neutral 17-ketosteroids by gas-liquid chromatography.
    Steroids, 1971, Volume: 18, Issue:2

    Topics: 17-Ketosteroids; Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Adult; Aged; Alcohols; Amenorrhea; Androsterone; Carcinoma; Child, Preschool; Chromatography, Gas; Cushing Syndrome; Dehydroepiandrosterone; Etiocholanolone; Female; Genital Diseases, Male; Hirsutism; Humans; Hyperplasia; Hyperthyroidism; Hypospadias; Infant; Infertility, Male; Klinefelter Syndrome; Lactation Disorders; Male; Middle Aged; Polycystic Ovary Syndrome; Pregnancy; Pregnanetriol

1971
[Congenital adrenal hyperplasia; 21-hydroxylase-deficiency combined with 17-desmolase-deficiency (author's transl)].
    Padiatrie und Padologie, 1974, Volume: 9, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Androsterone; Chemical Phenomena; Chemistry; Dehydroepiandrosterone; Estrogens; Female; Humans; Lyases; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol

1974
Gas-liquid chromatography of underivatized steroids: simultaneous determination of urinary 17-ketosteroids, pregnanediol, pregnanetriol, and pregnanetriolone.
    Clinica chimica acta; international journal of clinical chemistry, 1974, Oct-15, Volume: 56, Issue:1

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Computers; Dehydroepiandrosterone; Etiocholanolone; Female; Humans; Pregnanediol; Pregnanetriol

1974
Measurement of acetaldehydrogenic steroids in urine.
    Analytical biochemistry, 1965, Volume: 13, Issue:3

    Topics: Acetaldehyde; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Chemistry Techniques, Analytical; Chemistry, Clinical; Child; Colorimetry; Humans; In Vitro Techniques; Metyrapone; Pregnanetriol; Steroids; Urine

1965
Clinical and steroid metabolic studies in four siblings with congenital virilizing adrenal hyperplasia.
    Acta endocrinologica, 1966, Volume: 52, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Angiotensin II; Child; Dexamethasone; Estrogens; Female; Gonadotropins; Humans; Hydrocortisone; Male; Metyrapone; Pregnanediol; Pregnanetriol; Sodium; Testosterone; Water-Electrolyte Balance

1966
[Urinary excretion of pregnanetriol in various internal diseases].
    Nihon Naibunpi Gakkai zasshi, 1966, Dec-20, Volume: 42, Issue:9

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropic Hormone; Adult; Aged; Child; Child, Preschool; Endocrine System Diseases; Female; Humans; Hypertension; Liver Cirrhosis; Male; Metyrapone; Middle Aged; Paramethasone; Pregnanetriol; Triparanol

1966
Congenital adrenal hyperplasia due to a deficiency of one of the enzymes involved in the biosynthesis of pregnenolone.
    The Journal of clinical endocrinology and metabolism, 1968, Volume: 28, Issue:2

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Desoxycorticosterone; Disorders of Sex Development; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Hypokalemia; Hyponatremia; Infant; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Pregnenolone; Secretory Rate; Urine; Water-Electrolyte Balance

1968
Evaluation of deficiency of 21-hydroxylation in patients with congenital adrenal hyperplasia.
    Archives of disease in childhood, 1968, Volume: 43, Issue:230

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Dexamethasone; Female; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Pregnanetriol

1968
Semiquantitative estimation of urinary pregnanetriol, pregnanetriolone and tetrahydro S in the investigation of adrenocortical function.
    Acta endocrinologica, 1969, Volume: 60, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adsorption; Adult; Chemistry, Clinical; Child; Child, Preschool; Cushing Syndrome; Disorders of Sex Development; Ethisterone; Female; Glucuronidase; Hirsutism; Humans; Infant; Magnesium; Methods; Pituitary-Adrenal Function Tests; Polycystic Ovary Syndrome; Pregnanetriol; Puberty, Precocious; Silicon Dioxide; Tetrazolium Salts

1969
Hyperaldosteronism in hypertensive congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:12

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adrenocorticotropic Hormone; Aldosterone; Chemistry, Clinical; Child; Desoxycorticosterone; Etiocholanolone; Female; Humans; Hyperaldosteronism; Hyperplasia; Hypertension; Metabolism, Inborn Errors; Mixed Function Oxygenases; Ovarian Neoplasms; Pregnanetriol

1969
Occurrence of a virilizing syndrome with 21-hydroxylase deficiency after pregnancy.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:10

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Estrogens; Female; Gonadotropins; Humans; Metyrapone; Mixed Function Oxygenases; Pregnancy; Pregnanediol; Pregnanetriol; Testosterone; Triamcinolone; Virilism

1969
Secretion rates of cortisol and aldosterone precursors in various forms of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1970, Volume: 30, Issue:3

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Corticosterone; Desoxycorticosterone; Dexamethasone; Diet; Female; Humans; Hydrocortisone; Hyperplasia; Hypertension; Male; Metabolism, Inborn Errors; Metyrapone; Mixed Function Oxygenases; Potassium; Pregnanetriol; Secretory Rate; Sodium

1970
XO-XX-XXX mosaicism with possible congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1970, Volume: 30, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Disorders of Sex Development; Female; Fibroblasts; Glucocorticoids; Gonadotropins, Pituitary; Humans; Hydrocortisone; Hyperplasia; Karyotyping; Metabolism, Inborn Errors; Middle Aged; Mosaicism; Mouth Mucosa; Pregnanetriol; Sex Chromosome Aberrations; Skin

1970
Unusual type of congenital adrenal hyperplasia probably due to deficiency of 3-beta-hydroxysteroid dehydrogenase. Case report of a surviving girl and steroid studies.
    The Journal of clinical endocrinology and metabolism, 1970, Volume: 30, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Child; Dehydroepiandrosterone; Female; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Metabolism, Inborn Errors; Pituitary-Adrenal Function Tests; Pregnanes; Pregnanetriol; Steroids

1970
Adrenal insufficiency in two male infants.
    Proceedings of the Royal Society of Medicine, 1970, Volume: 63, Issue:5

    Topics: Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Adrenocorticotropic Hormone; Body Weight; Cortisone; Fludrocortisone; Humans; Hydrocortisone; Hyperplasia; Infant, Newborn; Male; Pigmentation Disorders; Pituitary-Adrenal Function Tests; Pregnanetriol; Sodium Chloride; Vomiting

1970
[Gas chromatographic estimation of urinary delta5 pregnenetriol and pregnanetriol in adrenocortical disease and male hypogonadism].
    Nihon Hinyokika Gakkai zasshi. The japanese journal of urology, 1971, Volume: 62, Issue:5

    Topics: Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aged; Carcinoma; Child; Child, Preschool; Chorionic Gonadotropin; Chromatography, Gas; Cushing Syndrome; Female; Humans; Hyperaldosteronism; Hypogonadism; Male; Middle Aged; Pregnanes; Pregnanetriol

1971
Congenital adrenal hyperplasia due to deficiency of 11 -hydroxylation of 17 -hydroxylated steroids.
    The Journal of clinical endocrinology and metabolism, 1971, Volume: 33, Issue:3

    Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Chromatography, Gas; Female; Humans; Hydroxysteroid Dehydrogenases; Hyperplasia; Infant; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Secretory Rate

1971
Androgen production in boys with sexual precocity and congenital adrenal hyperplasia.
    Metabolism: clinical and experimental, 1972, Volume: 21, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Chorionic Gonadotropin; Dexamethasone; Ethinyl Estradiol; Humans; Male; Medroxyprogesterone; Norethindrone; Prednisone; Pregnanetriol; Psychosexual Development; Puberty, Precocious; Testosterone

1972
Diagnosis of congenital adrenal hyperplasia by measurement of plasma 17-hydroxyprogesterone.
    Archives of disease in childhood, 1972, Volume: 47, Issue:251

    Topics: 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Biological Assay; Child, Preschool; Cortisone; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Methods; Mixed Function Oxygenases; Pregnanetriol; Protein Binding

1972
[Diagnostic and clinical problems in the congenital adrenogenital syndrome].
    Zeitschrift fur arztliche Fortbildung, 1972, Feb-15, Volume: 66, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Child; Child, Preschool; Diagnosis, Differential; Disorders of Sex Development; Female; Humans; Infant; Infant, Newborn; Male; Prednisone; Pregnancy; Pregnanetriol; Prognosis; Virilism

1972
The effect of ACTH administration on aldosterone production in non salt-losing congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1972, Volume: 35, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Aldosterone; Body Weight; Female; Humans; Hydrocortisone; Male; Middle Aged; Natriuresis; Potassium; Pregnanetriol; Radioimmunoassay; Secretory Rate; Stimulation, Chemical; Tritium

1972
Growth and skeletal maturation in congenital adrenal hyperplasia. Review of 20 cases.
    Archives of disease in childhood, 1974, Volume: 49, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Age Factors; Body Height; Bone Development; Child; Child, Preschool; Female; Fludrocortisone; Glucocorticoids; Growth; Humans; Hydrocortisone; Infant; Male; Prednisone; Pregnanetriol; Puberty; Sodium; Sodium Chloride

1974
[Pregnantriolon excretion after ACTH-stimulation in possible heterocygotes of 21-hydroxylase deficiency (author's transl)].
    Padiatrie und Padologie, 1971, Volume: 6, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Child; Female; Heterozygote; Humans; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol; Stimulation, Chemical

1971
[Pregnanetriolone excretion after stimulation with ACTH as a test on presumably heterozygous carriers of a 21-hydroxylase-deficiency (author's transl)].
    Padiatrie und Padologie, 1974, Volume: 9, Issue:3

    Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androsterone; Female; Humans; Male; Metabolic Clearance Rate; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Stimulation, Chemical

1974
Serum 17-alpha-hydroxyprogesterone, progesterone, estradiol, and testosterone in the diagnosis and management of congenital adrenal hyperplasia.
    The Journal of pediatrics, 1974, Volume: 85, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Child; Child, Preschool; Estradiol; Female; Glucocorticoids; Growth; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Pregnanetriol; Progesterone; Puberty; Radioimmunoassay; Testosterone

1974
[A contribution to the therapy of the congenital adrenal hyperplasia (author's transl)].
    Wiener klinische Wochenschrift, 1974, Sep-20, Volume: 86, Issue:17

    Topics: 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Chromatography, Gas; Desoxycorticosterone; Female; Humans; Hydrocortisone; Male; Mixed Function Oxygenases; Prednisolone; Prednisone; Pregnanediol; Pregnanetriol

1974
Diagnosis of congenital adrenal hyperplasia with 11-hydroxylase deficiency by determination of tetrahydro-11-desoxycortisol in urine.
    Helvetica paediatrica acta, 1974, Volume: Suppl 34

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Chromatography, Gas; Disorders of Sex Development; Female; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Pregnanetriol; Radioimmunoassay; Tetrahydrocortisol

1974
Gas-liquid chromatography in the diagnosis of congenital adrenal hyperplasia.
    Journal of steroid biochemistry, 1974, Volume: 5, Issue:5

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Methods; Middle Aged; Pregnanes; Pregnanetriol

1974
Effects of the XYY karyotype in one of two brothers with congenital adrenal hyperplasia.
    Clinical genetics, 1972, Volume: 3, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Autistic Disorder; Cells, Cultured; Child; Child, Preschool; Humans; Karyotyping; Lymphocytes; Male; Osteosarcoma; Pregnanetriol; Sex Chromosome Aberrations

1972
Aldosterone secretion rate in the simple virilizing form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1972, Volume: 34, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Carbon Isotopes; Child; Child, Preschool; Chromatography, Paper; Diet, Sodium-Restricted; Female; Humans; Hyperplasia; Male; Potassium; Pregnanetriol; Radioisotope Dilution Technique; Secretory Rate; Sodium; Spectrophotometry; Tritium

1972
Problems in the interpretation of ovarian biopsies in functional gynecologic disorders and sterility of ovarian origin.
    The Journal of reproductive medicine, 1973, Volume: 10, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Biopsy; Chorionic Gonadotropin; Corpus Luteum; Dexamethasone; Dose-Response Relationship, Drug; Female; Humans; Infertility, Female; Injections, Intramuscular; Ovarian Diseases; Ovary; Ovulation; Pregnanediol; Pregnanetriol

1973
[Hydrocortisone therapy of the AGS (adrenogenital syndrome)].
    Monatsschrift fur Kinderheilkunde, 1973, Volume: 121, Issue:7

    Topics: Adrenal Hyperplasia, Congenital; Androgens; Body Height; Body Weight; Bone Development; Child; Female; Humans; Hydrocortisone; Male; Prednisone; Pregnanetriol

1973
Linear growth rate, bone maturation and growth hormone secretion in prepubertal children with congenital adrenal hyperplasia.
    Acta paediatrica Scandinavica, 1973, Volume: 62, Issue:5

    Topics: Administration, Oral; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Body Height; Bone Development; Child; Child, Preschool; Depression, Chemical; Female; Follow-Up Studies; Growth; Growth Hormone; Humans; Hydrocortisone; Hyperplasia; Male; Pregnanetriol; Time Factors

1973
Non-tumorous feminizing adrenogenital syndrome in the male subject.
    The Journal of urology, 1973, Volume: 110, Issue:6

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androstenedione; Androsterone; Estrogens; Feminization; Gynecomastia; Humans; Hydrocortisone; Male; Pituitary-Adrenal Function Tests; Pregnanetriol; Sex Chromatin; Spermatogenesis; Testis; Testosterone

1973
Amniotic fluid testosterone: implications for the prenatal diagnosis of congenital adrenal hyperplasia.
    The Journal of pediatrics, 1974, Volume: 84, Issue:5

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Age Factors; Amniocentesis; Amniotic Fluid; Erythroblastosis, Fetal; Female; Gestational Age; Humans; Male; Mixed Function Oxygenases; Pregnancy; Pregnanetriol; Prenatal Diagnosis; Sex Factors; Sodium; Testosterone

1974
[Metabolism of estrogens in the adrenogenital syndrome].
    Revista iberica de endocrinologia, 1974, Volume: 21, Issue:123

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Estradiol; Estriol; Estrogens; Estrone; Female; Humans; Male; Pregnanetriol

1974
[Pregnanetriol in the amniotic fluid: prenatal diagnosis of adrenogenital syndrome by amniocentesis (author's transl)].
    Geburtshilfe und Frauenheilkunde, 1974, Volume: 34, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Estriol; Female; Humans; Hydrocortisone; Infant, Newborn; Pregnancy; Pregnanetriol; Prenatal Diagnosis; Sulfates; Twins

1974
[Prenatal diagnosis of adrenogenital syndrome].
    Deutsche medizinische Wochenschrift (1946), 1972, Jan-21, Volume: 97, Issue:3

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Amniocentesis; Amniotic Fluid; Female; Fetal Diseases; Humans; Methods; Pregnancy; Pregnanetriol

1972
Difficulties in the diagnosis of the adrenogenital syndrome in infancy.
    Pediatrics, 1972, Volume: 49, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Age Factors; Androstanes; Chromatography, Gas; Chromatography, Thin Layer; Humans; Infant, Newborn; Ketosteroids; Lipid Metabolism, Inborn Errors; Male; Mixed Function Oxygenases; Pregnanes; Pregnanetriol

1972
Congenital adrenal hyperplasia and diabetes mellitus in a woman aged 71 years.
    Acta endocrinologica, 1972, Volume: 69, Issue:2

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Age Factors; Aged; Diabetes Complications; Female; Glucose Tolerance Test; Humans; Prednisone; Pregnanetriol

1972
A study of the renin-aldosterone system in congenital adrenal hyperplasia.
    The Journal of pediatrics, 1972, Volume: 81, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Blood Pressure; Child; Clitoris; Female; Humans; Hyperplasia; Hyponatremia; Infant, Newborn; Male; Metabolism, Inborn Errors; Pregnanetriol; Renin; Sodium; Sodium Chloride; Steroid Hydroxylases; Water-Electrolyte Balance

1972
An unusual form of adrenogenital syndrome.
    Endokrinologie, 1971, Volume: 57, Issue:3

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Humans; Hydroxysteroid Dehydrogenases; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol

1971
Urinary excretion of pregnanetriol and 5 -pregnenetriol in two forms of congenital adrenal hyperplasia.
    The Journal of clinical investigation, 1971, Volume: 50, Issue:12

    Topics: 17-alpha-Hydroxypregnenolone; Administration, Oral; Adrenal Hyperplasia, Congenital; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Glucocorticoids; Humans; Hydrolysis; Hydroxysteroid Dehydrogenases; Infant; Infant, Newborn; Ketosteroids; Male; Methods; Mixed Function Oxygenases; Pregnanetriol

1971
[Adrenogenital syndrome of the adult male. 3 cases].
    Revista clinica espanola, 1971, Sep-15, Volume: 122, Issue:5

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Estrogens; Humans; Infertility, Male; Male; Middle Aged; Pregnanetriol; Spermatogenesis

1971
[Evaluation of neutral urinary steroid analysis by gas liquid chromatography using OV-210].
    Horumon to rinsho. Clinical endocrinology, 1971, Volume: 19, Issue:11

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Cushing Syndrome; Etiocholanolone; Humans; Hydrocortisone; Hyperthyroidism; Male; Pregnanetriol

1971
Prenatal diagnosis of adrenogenital syndrome by amniocentesis.
    The Journal of pediatrics, 1969, Volume: 75, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Amniotic Fluid; Chromatography; Female; Fetal Diseases; Gestational Age; Humans; Hyperplasia; Infant, Newborn; Pregnancy; Pregnanetriol; Tritium

1969
On the metabolism of 16-alpha-hydroxy-C21-steroids. 3. Evidence for high rates of production of 16-alpha-hydroxyprogesterone and 16-alpha-hydroxypregnenolone in the salt-losing form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:10

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Child; Chromatography; Female; Humans; Male; Photometry; Pregnanes; Pregnanetriol; Triamcinolone

1969
[Adrenogenital syndrome in sisters].
    Horumon to rinsho. Clinical endocrinology, 1969, Volume: 17, Issue:7

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Pregnanetriol; Sex Chromosomes

1969
Exchangeable sodium and aldosterone secretion in children with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
    Pediatric research, 1970, Volume: 4, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone; Child; Child, Preschool; Humans; Hydrocortisone; Infant; Infant, Newborn; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanetriol; Sodium

1970
[Pregnanetriolone and the adrenogenital syndrome].
    Bibliotheca gynaecologica, 1970, Volume: 53

    Topics: 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Amenorrhea; Chromatography, Thin Layer; Female; Glucocorticoids; Humans; Hydroxysteroid Dehydrogenases; Ketones; Menstruation Disturbances; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Progesterone

1970
Congenital adrenogenital syndrome and successful pregnancy. Report of a case.
    Obstetrics and gynecology, 1970, Volume: 35, Issue:3

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Cesarean Section; Clitoris; Corticosterone; Dexamethasone; Female; Humans; Hydrocortisone; Pregnancy; Pregnancy Complications; Pregnanediol; Pregnanetriol

1970
Steroid studies in parents of patients with congenital virilizing adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1971, Volume: 33, Issue:1

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Androstanes; Body Height; Body Surface Area; Body Weight; Chromatography, Gas; Creatinine; Female; Heterozygote; Humans; Male; Metabolism, Inborn Errors; Mixed Function Oxygenases; Pregnanediol; Pregnanetriol; Steroids; Urine

1971
Urinary excretion of glucuronides and sulfates of acetaldehydogenic steroids.
    The Journal of clinical endocrinology and metabolism, 1968, Volume: 28, Issue:1

    Topics: Acetaldehyde; Acetates; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Chromatography, Paper; Cushing Syndrome; Glucuronates; Glucuronidase; Humans; Pregnanediol; Pregnanes; Pregnanetriol; Pregnenolone; Sulfates

1968
Blood progesterone and 17-hydroxyprogesterone levels and production rates in a boy with virilizing congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1968, Volume: 28, Issue:7

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Carbon Isotopes; Chemistry, Clinical; Child, Preschool; Chromatography, Gas; Chromatography, Thin Layer; Humans; Hydroxyprogesterones; Hyperplasia; Male; Metabolic Clearance Rate; Pregnanetriol; Progesterone; Tritium

1968
[Studies of the enzymatic determination of pregnane-3 alpha, 17 alpha, 20 alpha-triol in the urine].
    Zeitschrift fur die gesamte experimentelle Medizin einschliesslich experimentelle Chirurgie, 1968, Volume: 145, Issue:1

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adult; Child; Chromatography, Paper; Cushing Syndrome; Female; Glucuronidase; Humans; Hydroxysteroid Dehydrogenases; Male; Methods; Middle Aged; Pregnanetriol; Pseudomonas

1968
Statural growth in congenital adrenal hyperplasia treated with hydrocortisone.
    The Journal of pediatrics, 1968, Volume: 73, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Body Height; Bone Development; Child, Preschool; Corticosterone; Female; Growth; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium

1968
[Steroid chemical studies on heterozygote trait carriers of congenital virilizing adrenal cortex hyperplasia].
    Monatsschrift fur Kinderheilkunde, 1968, Volume: 116, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Adult; Chromatography, Gas; Female; Heterozygote; Humans; Male; Methods; Pregnanetriol; Testosterone

1968
Ventricular tachycardia associated with hyperkalemia. Occurrence in an infant aged 13 days with adrenogenital syndrome.
    American journal of diseases of children (1960), 1969, Volume: 117, Issue:6

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Electrocardiography; Humans; Hyperkalemia; Infant, Newborn; Infant, Newborn, Diseases; Male; Pregnanetriol; Tachycardia

1969
Simulated congenital adrenal hyperplasia in a male neonate associated with medroxyprogesterone therapy during pregnancy.
    American journal of obstetrics and gynecology, 1969, Apr-15, Volume: 103, Issue:8

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Diagnosis, Differential; Female; Humans; Infant, Newborn; Infant, Newborn, Diseases; Male; Maternal-Fetal Exchange; Medroxyprogesterone; Pregnancy; Pregnancy Complications; Pregnanetriol

1969
Androgen metabolism in congenital adrenal hyperplasia due to 11 beta-hydroxylase deficiency.
    Pediatrics, 1969, Volume: 44, Issue:2

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androgens; Androstanes; Child, Preschool; Female; Humans; Hyperplasia; Mixed Function Oxygenases; Pregnanetriol; Testosterone

1969
[Diagnosis and therapeutic results in cases of hirsutism in women].
    Ginekologia polska, 1969, Volume: 40, Issue:6

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Androsterone; Cushing Syndrome; Diagnosis, Differential; Female; Hirsutism; Humans; Polycystic Ovary Syndrome; Pregnanetriol

1969
Quantitative estimation of urinary pregnanetriol, pregnanetriolone, tetrahydro S and delta-5-pregnenetriol in the investigation of adrenocortical function.
    Acta endocrinologica, 1969, Volume: 60, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Paper; Clitoris; Cushing Syndrome; Female; Hirsutism; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors; Methods; Mixed Function Oxygenases; Pituitary-Adrenal Function Tests; Pregnanetriol; Sex Chromosome Aberrations; Urogenital Abnormalities

1969
Adrenogenital syndrome. Association with 3-beta-hydroxysteroid dehydrogenase deficiency.
    American journal of diseases of children (1960), 1965, Volume: 110, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Chloramphenicol; Desoxycorticosterone; Female; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Infant, Newborn; Mestranol; Metabolic Diseases; Norethynodrel; Penicillins; Pregnanetriol; Pyelonephritis; Sepsis; Streptomycin; Urine

1965
[Problems of congenital adrenogenital syndrom in childhood].
    Padiatrie und Grenzgebiete, 1965, Volume: 4, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Child; Child, Preschool; Female; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Pregnanetriol

1965
Gas chromatographic estimation of urinary pregnanetriol, pregnanetriolone and pregnanetetrol in congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1966, Volume: 26, Issue:11

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aged; Chromatography, Gas; Female; Humans; Male; Middle Aged; Pregnanediol; Pregnanetriol

1966
Varying expression for salt losing in related patients with congenital adrenal hyperplasia.
    Pediatrics, 1966, Volume: 38, Issue:2

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Child, Preschool; Female; Humans; Infant; Infant, Newborn; Male; Pregnanetriol; Sodium Chloride

1966
Excretion of six individual 17-ketosteroids and testosterone in four girls with precocious sexual hair (premature adrenarche).
    Helvetica paediatrica acta, 1966, Volume: 21, Issue:5

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Body Height; Child; Chromatography, Paper; Electroencephalography; Female; Growth; Hair; Humans; Pregnanetriol; Puberty, Precocious; Testosterone

1966
[Gas chromatography determination of pregnanediol, pregnanetriol and pregnanetriolone in urine].
    Zeitschrift fur klinische Chemie und klinische Biochemie, 1966, Volume: 4, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Androsterone; Chemistry, Clinical; Chromatography, Gas; Glucuronidase; Pregnanediol; Pregnanes; Pregnanetriol

1966