Page last updated: 2024-11-07

prednisone and Camurati-Engelmann Disease

prednisone has been researched along with Camurati-Engelmann Disease in 8 studies

Prednisone: A synthetic anti-inflammatory glucocorticoid derived from CORTISONE. It is biologically inert and converted to PREDNISOLONE in the liver.
prednisone : A synthetic glucocorticoid drug that is particularly effective as an immunosuppressant, and affects virtually all of the immune system. Prednisone is a prodrug that is converted by the liver into prednisolone (a beta-hydroxy group instead of the oxo group at position 11), which is the active drug and also a steroid.

Research Excerpts

ExcerptRelevanceReference
"Camurati-Engelmann disease (CED) is a rare form of progressive bone dysplasia due to mutations in the transforming factor gene TGFB1 on chromosome 19q13."1.39A family with Camurati-Engelman disease. The role of the missense p.R218C mutation in TGFB1 in bones and endocrine glands. ( Allgrove, J; Anastasiadou, V; Neocleous, V; Phylactou, LA; Shammas, C; Skordis, N; Toumba, M, 2013)
"We suggest that the progressive diaphyseal dysplasia gene has a function in endochondral bone formation and that its mutation is a dynamic one with repeat expansion enhanced in father-to-son transmission."1.30Progressive diaphyseal dysplasia: a three-generation family with markedly variable expressivity. ( Saraiva, JM, 1997)
"The authors have studied two cases of progressive diaphyseal dysplasia (Camurati Engelmann's disease)."1.27Progressive diaphyseal dysplasia: Camurati-Engelmann's disease. ( Calorio, D; Cartesegna, M; Crova, M; Lazzarone, C, 1983)
"Progressive diaphyseal dysplasia is characterized clinically by crippling leg pain, fatigue, headache, poor appetite, muscle weakness, and waddling gait."1.27Progressive diaphyseal dysplasia: evaluation of corticosteroid therapy. ( Alon, U; Berant, M; Kaftori, JK; Naveh, Y, 1985)

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19903 (37.50)18.7374
1990's1 (12.50)18.2507
2000's0 (0.00)29.6817
2010's4 (50.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Pijls, BG1
Steentjes, K1
Schoones, JW1
Dijkstra, SP1
Combier, A1
Palazzo, E1
Forien, M1
Gardette, A1
Dieudé, P1
Ottaviani, S1
Toumba, M1
Neocleous, V1
Shammas, C1
Anastasiadou, V1
Allgrove, J1
Phylactou, LA1
Skordis, N1
Mazaheri, P1
Nadkarni, G1
Lowe, E1
Hines, P1
Vuica, M1
Griffin, M1
Resar, LM1
Lazzarone, C1
Cartesegna, M1
Crova, M1
Calorio, D1
Saraiva, JM1
Naveh, Y1
Alon, U1
Kaftori, JK1
Berant, M1
Lindstrom, JA1

Reviews

2 reviews available for prednisone and Camurati-Engelmann Disease

ArticleYear
Ribbing disease: a systematic review.
    Acta radiologica (Stockholm, Sweden : 1987), 2018, Volume: 59, Issue:4

    Topics: Adult; Anti-Inflammatory Agents, Non-Steroidal; Camurati-Engelmann Syndrome; Female; Glucocorticoids

2018
Failure of conventional treatment and losartan in Camurati-Engelmann disease: A case report.
    Joint bone spine, 2018, Volume: 85, Issue:5

    Topics: Adult; Analgesics; Anti-Inflammatory Agents, Non-Steroidal; Camurati-Engelmann Syndrome; Drug Therap

2018

Other Studies

6 other studies available for prednisone and Camurati-Engelmann Disease

ArticleYear
A family with Camurati-Engelman disease. The role of the missense p.R218C mutation in TGFB1 in bones and endocrine glands.
    Journal of pediatric endocrinology & metabolism : JPEM, 2013, Volume: 26, Issue:9-10

    Topics: Amino Acid Substitution; Anti-Inflammatory Agents; Bone and Bones; Calcium, Dietary; Camurati-Engelm

2013
Ghosal hematodiaphyseal dysplasia: a rare cause of a myelophthisic anemia.
    Pediatric blood & cancer, 2010, Dec-01, Volume: 55, Issue:6

    Topics: Adult; Anemia, Myelophthisic; Anti-Inflammatory Agents; Camurati-Engelmann Syndrome; Female; Humans;

2010
Progressive diaphyseal dysplasia: Camurati-Engelmann's disease.
    Italian journal of orthopaedics and traumatology, 1983, Volume: 9, Issue:1

    Topics: Bone Diseases, Developmental; Camurati-Engelmann Syndrome; Humans; Male; Middle Aged; Prednisone; Ti

1983
Progressive diaphyseal dysplasia: a three-generation family with markedly variable expressivity.
    American journal of medical genetics, 1997, Aug-22, Volume: 71, Issue:3

    Topics: Adolescent; Adult; Camurati-Engelmann Syndrome; Child; Female; Genomic Imprinting; Humans; Male; Mic

1997
Progressive diaphyseal dysplasia: evaluation of corticosteroid therapy.
    Pediatrics, 1985, Volume: 75, Issue:2

    Topics: Adolescent; Adult; Camurati-Engelmann Syndrome; Child; Child, Preschool; Drug Administration Schedul

1985
Diaphyseal dysplasia (Engelmann) treated with corticosteroids.
    Birth defects original article series, 1974, Volume: 10, Issue:12

    Topics: Adolescent; Bone Diseases, Developmental; Camurati-Engelmann Syndrome; Child; Child, Preschool; Huma

1974