Page last updated: 2024-08-23

pirfenidone and Hermanski-Pudlak Syndrome

pirfenidone has been researched along with Hermanski-Pudlak Syndrome in 9 studies

Research

Studies (9)

Timeframe	Studies, this research(%)	All Research%
pre-1990	0 (0.00)	18.7374
1990's	0 (0.00)	18.2507
2000's	4 (44.44)	29.6817
2010's	5 (55.56)	24.3611
2020's	0 (0.00)	2.80

Authors

Authors	Studies
Akal, O; Akal, T; Barbu, A; Gahl, WA; Gochuico, BR; Introne, WJ; McGowan, MP; Merideth, MA; O'Brien, KJ; Seward, SL	1
Hara, S; Harada, T; Ishimatsu, Y; Kakugawa, T; Kawabata, Y; Kohno, S; Miura, S; Mukae, H; Nakashima, S; Sakamoto, N; Tomonaga, M; Yoshii, C	1
Roman, J; Santiago-Cornier, A; Vergne, Y; Vicary, GW; Young, LR	1
Bernardini, I; Cardona, H; Gahl, WA; Gochuico, BR; Hess, R; Markello, TC; O'Brien, K; Salas, J; Troendle, J; Yao, J	1
Celik, G; Ciledağ, A; Cirit Koçer, B; Kaya, A; Köktürk, N; Numanoğlu, N	1
Avila, NA; Brantly, M; Calis, KA; Cardona, H; Gahl, WA; Gochuico, B; Montalvo, C; Padua, A; Troendle, J	1
Azuma, A	1
Liu, A; Troendle, JF; Wu, C; Yu, KF	1
Antoniu, SA	1

Reviews

4 review(s) available for pirfenidone and Hermanski-Pudlak Syndrome

Article	Year
An autopsy case of Hermansky-Pudlak syndrome: a case report and review of the literature on treatment. Internal medicine (Tokyo, Japan), 2014, Volume: 53, Issue:23 Topics: Adrenal Cortex Hormones; Autopsy; Ceroid; Drug Therapy, Combination; Fatal Outcome; Female; Hemorrhagic Disorders; Hermanski-Pudlak Syndrome; Humans; Immunosuppressive Agents; Lipofuscin; Lung Transplantation; Middle Aged; Pulmonary Fibrosis; Pyridones; Respiratory Insufficiency	2014
Pulmonary Fibrosis in Hermansky-Pudlak Syndrome. Annals of the American Thoracic Society, 2016, Volume: 13, Issue:10 Topics: Animals; Biomarkers; Disease Progression; Hermanski-Pudlak Syndrome; Hispanic or Latino; Humans; Indoles; Lung Transplantation; Membrane Proteins; Mice; Mutation; Puerto Rico; Pulmonary Fibrosis; Pyridones; Randomized Controlled Trials as Topic; Tomography, X-Ray Computed	2016
[Expectation of new treatments for idiopathic interstitial pneumonias]. Nihon Ronen Igakkai zasshi. Japanese journal of geriatrics, 2005, Volume: 42, Issue:1 Topics: Aged; Anti-Inflammatory Agents, Non-Steroidal; Benzamides; Clinical Trials as Topic; Hermanski-Pudlak Syndrome; Humans; Imatinib Mesylate; Interferon-gamma; Lung; Middle Aged; Piperazines; Prognosis; Protein Kinase Inhibitors; Pulmonary Fibrosis; Pyridones; Pyrimidines; Survival Analysis	2005
Pirfenidone for the treatment of idiopathic pulmonary fibrosis. Expert opinion on investigational drugs, 2006, Volume: 15, Issue:7 Topics: Administration, Oral; Amiodarone; Animals; Anti-Inflammatory Agents, Non-Steroidal; Bleomycin; Cell Line; Clinical Trials, Phase II as Topic; Connective Tissue Growth Factor; Cricetinae; Cyclophosphamide; Drug Evaluation, Preclinical; Drugs, Investigational; Fibroblasts; Hermanski-Pudlak Syndrome; Humans; Immediate-Early Proteins; Intercellular Signaling Peptides and Proteins; Lung Transplantation; Mice; Orphan Drug Production; Photosensitivity Disorders; Pulmonary Fibrosis; Pyridones; Randomized Controlled Trials as Topic; Scleroderma, Systemic; Transforming Growth Factor beta; Treatment Outcome; Tumor Necrosis Factor-alpha	2006

Trials

2 trial(s) available for pirfenidone and Hermanski-Pudlak Syndrome

Article	Year
Pirfenidone for the treatment of Hermansky-Pudlak syndrome pulmonary fibrosis. Molecular genetics and metabolism, 2011, Volume: 103, Issue:2 Topics: Adult; Female; Hermanski-Pudlak Syndrome; Humans; Male; Middle Aged; Patient Compliance; Pulmonary Fibrosis; Pyridones; Radiography; Treatment Outcome	2011
Effect of pirfenidone on the pulmonary fibrosis of Hermansky-Pudlak syndrome. Molecular genetics and metabolism, 2002, Volume: 76, Issue:3 Topics: Adult; Double-Blind Method; Female; Hermanski-Pudlak Syndrome; Humans; Male; Middle Aged; Patient Compliance; Placebos; Pulmonary Fibrosis; Pyridones; Tomography, X-Ray Computed; Treatment Outcome	2002

Other Studies

3 other study(ies) available for pirfenidone and Hermanski-Pudlak Syndrome

Article	Year
Prolonged treatment with open-label pirfenidone in Hermansky-Pudlak syndrome pulmonary fibrosis. Molecular genetics and metabolism, 2018, Volume: 125, Issue:1-2 Topics: Adult; Aged; Female; Hermanski-Pudlak Syndrome; Humans; Lung; Male; Middle Aged; Pulmonary Fibrosis; Pyridones; Tomography, X-Ray Computed	2018
A rare cause of interstitial lung disease: Hermansky-Pudlak syndrome. Tuberkuloz ve toraks, 2011, Volume: 59, Issue:1 Topics: Anti-Inflammatory Agents, Non-Steroidal; Dyspnea; Fatal Outcome; Hermanski-Pudlak Syndrome; Humans; Male; Middle Aged; Pulmonary Fibrosis; Pyridones; Radiography, Thoracic; Respiratory Insufficiency; Tomography, X-Ray Computed	2011
Sequential testing for efficacy in clinical trials with non-transient effects. Statistics in medicine, 2005, Nov-15, Volume: 24, Issue:21 Topics: Anti-Inflammatory Agents, Non-Steroidal; Clinical Trials as Topic; Computer Simulation; Data Interpretation, Statistical; Female; Hermanski-Pudlak Syndrome; Humans; Male; Monte Carlo Method; Normal Distribution; Pulmonary Fibrosis; Pyridones; Vital Capacity	2005