piperidines has been researched along with Metabolism--Inborn-Errors* in 3 studies
3 other study(ies) available for piperidines and Metabolism--Inborn-Errors
| Article | Year |
|---|---|
Early recovery from anesthesia and extubation in an infant with very long chain acyl-CoA dehydrogenase deficiency using midazolam, mivacurium, and high dose remifentanil.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Adjuvants, Anesthesia; Anesthesia Recovery Period; Anesthesia, Intravenous; Anesthetics, Intravenous; Endoscopy; Gastrostomy; Humans; Infant; Isoquinolines; Male; Metabolism, Inborn Errors; Midazolam; Mivacurium; Monitoring, Intraoperative; Neuromuscular Nondepolarizing Agents; Piperidines; Remifentanil | 2009 |
Perioperative recommendations in a child with Fish Odor syndrome.
Topics: Adenoidectomy; Anesthesia, Intravenous; Anesthetics, Intravenous; Child; Humans; Male; Metabolism, Inborn Errors; Methylamines; Odorants; Perioperative Care; Piperidines; Propofol; Remifentanil; Tonsillectomy | 2009 |
Anesthetic management in two siblings with glutaric aciduria type 1.
Glutaric aciduria type 1 (GA-1) is an inborn error of metabolism that results from a deficiency of glutaryl-CoA dehydrogenase. This disorder mainly manifests in early childhood and most patients with this condition develop a dystonic-dyskinetic syndrome. We report the anesthetic management of two sisters with GA-1, aged 30 and 17 months respectively at the time of surgery, who presented with macrocephaly and psychomotor delay. The children required CSF shunting procedures for hydrocephalus and subdural fluid collections, which were performed under total intravenous anesthesia with propofol and remifentanil. Topics: Anesthesia; Anesthetics, Intravenous; Cerebrospinal Fluid Shunts; Child, Preschool; Dystonic Disorders; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Head; Humans; Hydrocephalus; Infant; Metabolism, Inborn Errors; Piperidines; Propofol; Psychomotor Disorders; Remifentanil; Siblings | 2006 |