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phosphatidylcholines and Cystic Fibrosis of Pancreas

phosphatidylcholines has been researched along with Cystic Fibrosis of Pancreas in 30 studies

Research

Studies (30)

TimeframeStudies, this research(%)All Research%
pre-199011 (36.67)18.7374
1990's6 (20.00)18.2507
2000's8 (26.67)29.6817
2010's5 (16.67)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Dyer, RA; Innis, SM; Moukarzel, S1
Dow, SW; Hoang, TT; Kang, Y; Norris, MH; Schweizer, HP; Son, MS; Sun, Z; Troyer, RM1
Bernhard, W; Grothe, J; Pynn, CJ; Raith, M; Riethmüller, J; Stoll, D; Tschürtz, SM1
Aït-Slimane, T; Barbu, V; Bruneau, A; Callebaut, I; Delaunay, JL; Durand-Schneider, AM; Hoffmann, B; Housset, C; Jacquemin, E; Maurice, M1
Astarita, G; Edelman, A; Guerrera, IC; Ollero, M; Piomelli, D; Sermet-Gaudelus, I; Trudel, S1
Chen, A; Davidson, AG; Dyer, R; Innis, SM; James, SJ; Melnyk, S1
Bocci, F; Boselli, E; Frega, NG; Malavolta, M; Pacetti, D1
Karmel, J; McGaw, J; Rigby, AS; Taylor, CJ; Threlfall, D1
Chen, AH; Davidson, AG; Innis, SM; James, SJ1
Brown, NE; Clandinin, MT; Goh, YK; Jumpsen, JA; Ma, D; Paul Man, SF; Thomson, AB1
Davidson, AG; Innis, SM; James, SJ; Melynk, S1
Hoang, TT; Kang, Y; Matthews, WJ; Nguyen, DT; Son, MS1
Niessen, KH; Theisen, M1
Crokaert, R; Dab, I; Michotte, Y; Rogiers, V; Vercruysse, A; Vis, HL1
Parsons, HG; Rademaker, AW; Shillabeer, G1
Crokaert, R; Dab, I; Mandelbaum, I; Mozes, N; Rogiers, V; Vertongen, F; Vis, HL1
Brown, NE; Clandinin, MT; Goh, YK; Kielo, ES; Zuberbuhler, P1
Burdge, GC; Goodale, AJ; Halford, PJ; Hill, CM; Lambert, EJ; Postle, AD; Rolles, CJ1
Butler, JD; Hubbard, VS; Miele, L; Peri, A; Ulane, MM; Ulane, RE1
Bernhard, W; Hedrich, HJ; Tschernig, T; Tümmler, B; von der Hardt, H; Wang, JY1
Heeley, E; Mander, A; Petrovic, M; Postle, AD; Warner, JO; Wright, S1
Mander, A; Moustaki, M; Postle, AD; Reid, KB; Wang, JY; Warner, JO; Wright, SM1
Bernhard, W; Bertling, A; Dombrowsky, H; Freihorst, J; Rau, G; Vieten, G; von der Hardt, H1
Allue, X; Rodriguez-Soriano, J; Sanjurjo, P1
Chazalette, JP; Filliat, M; Galabert, C1
Allué, X; Sanjurjo, P1
Barbero, GJ; Feather, MS; Martinez, JR; Mawhinney, TP1
Govan, JR1
Lynn, WS; Sahu, S1
Hill, R; Kuksis, A; Parsons, HG; Pencharz, P1

Trials

4 trial(s) available for phosphatidylcholines and Cystic Fibrosis of Pancreas

ArticleYear
High-performance liquid chromatography/electrospray ionization ion-trap tandem mass spectrometric analysis and quantification of phosphatidylcholine molecular species in the serum of cystic fibrosis subjects supplemented with docosahexaenoic acid.
    Rapid communications in mass spectrometry : RCM, 2004, Volume: 18, Issue:20

    Topics: Administration, Oral; Biomarkers; Blood Chemical Analysis; Child; Chromatography, High Pressure Liquid; Cystic Fibrosis; Dietary Supplements; Docosahexaenoic Acids; Humans; Phosphatidylcholines; Reproducibility of Results; Sensitivity and Specificity; Spectrometry, Mass, Electrospray Ionization

2004
Pilot safety study of liposomal prostaglandin (PGE1) in respiratory exacerbations in cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2002, Volume: 1, Issue:2

    Topics: Adolescent; Alprostadil; Anti-Bacterial Agents; Anti-Inflammatory Agents; Cystic Fibrosis; Double-Blind Method; Humans; Infusions, Intravenous; Liposomes; Lung Diseases; Phosphatidylcholines; Pilot Projects; Pseudomonas Infections; Respiratory Function Tests; Sputum; Treatment Outcome

2002
Fatty acids in blood and intestine following docosahexaenoic acid supplementation in adults with cystic fibrosis.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2006, Volume: 5, Issue:2

    Topics: Administration, Oral; Adolescent; Adult; Capsules; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Dietary Supplements; Docosahexaenoic Acids; Duodenum; Erythrocytes; Fatty Acids; Female; Genotype; Humans; Intestinal Mucosa; Male; Mutation; Phosphatidylcholines; Phosphatidylethanolamines

2006
Cystic fibrosis and phosphatidylcholine biosynthesis.
    Clinica chimica acta; international journal of clinical chemistry, 1994, Oct-31, Volume: 230, Issue:2

    Topics: Base Sequence; Blood Platelets; Cells, Cultured; Choline; Cyclic AMP; Cystic Fibrosis; Dinoprostone; DNA Primers; Fibroblasts; Heterozygote; Humans; Molecular Sequence Data; Phosphatidylcholines; Polymerase Chain Reaction; Reference Values; Skin

1994

Other Studies

26 other study(ies) available for phosphatidylcholines and Cystic Fibrosis of Pancreas

ArticleYear
Complex Relation Between Diet and Phospholipid Fatty Acids in Children With Cystic Fibrosis.
    Journal of pediatric gastroenterology and nutrition, 2017, Volume: 64, Issue:4

    Topics: Adolescent; Biomarkers; Case-Control Studies; Child; Child, Preschool; Cross-Sectional Studies; Cystic Fibrosis; Diet; Diet Surveys; Dietary Fats; Female; Humans; Male; Phosphatidylcholines; Phosphatidylethanolamines

2017
Blocking phosphatidylcholine utilization in Pseudomonas aeruginosa, via mutagenesis of fatty acid, glycerol and choline degradation pathways, confirms the importance of this nutrient source in vivo.
    PloS one, 2014, Volume: 9, Issue:7

    Topics: 3-Hydroxyacyl-CoA Dehydrogenase; Amino Acid Sequence; Animals; Bacterial Proteins; Choline; Cystic Fibrosis; Fatty Acids; Glycerol; Host-Pathogen Interactions; Lung; Mice, Inbred BALB C; Molecular Sequence Data; Mutagenesis; Mutation; Operon; Phosphatidylcholines; Pseudomonas aeruginosa; Pseudomonas Infections; Sequence Homology, Amino Acid; Signal Transduction

2014
Plasma phosphatidylcholine alterations in cystic fibrosis patients: impaired metabolism and correlation with lung function and inflammation.
    Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology, 2015, Volume: 35, Issue:4

    Topics: Adult; Arachidonic Acid; Betaine; Choline; Cystic Fibrosis; Deuterium; Docosahexaenoic Acids; Female; Forced Expiratory Volume; Humans; Inflammation; Interleukin-6; Isotope Labeling; Kinetics; Liver; Lung; Male; Phosphatidylcholines; Phosphatidylethanolamine N-Methyltransferase; Young Adult

2015
Functional defect of variants in the adenosine triphosphate-binding sites of ABCB4 and their rescue by the cystic fibrosis transmembrane conductance regulator potentiator, ivacaftor (VX-770).
    Hepatology (Baltimore, Md.), 2017, Volume: 65, Issue:2

    Topics: Adenosine Triphosphate; Adolescent; Aminophenols; ATP Binding Cassette Transporter, Subfamily B; Binding Sites; Cells, Cultured; Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Hep G2 Cells; Humans; Male; Mutagenesis; Mutation, Missense; Phosphatidylcholines; Quinolones; Sampling Studies; Transfection; Young Adult

2017
Plasma lipidomics reveals potential prognostic signatures within a cohort of cystic fibrosis patients.
    Journal of lipid research, 2011, Volume: 52, Issue:5

    Topics: Adolescent; Adult; Child; Child, Preschool; Cholesterol; Cholesterol Esters; Chromatography, Liquid; Cystic Fibrosis; Endocannabinoids; Female; Forced Expiratory Volume; Humans; Infant; Lipids; Lysophosphatidylcholines; Male; Mass Spectrometry; Oleic Acids; Phosphatidylcholines; Pseudomonas Infections; Triglycerides; Young Adult

2011
Increased plasma homocysteine and S-adenosylhomocysteine and decreased methionine is associated with altered phosphatidylcholine and phosphatidylethanolamine in cystic fibrosis.
    The Journal of pediatrics, 2003, Volume: 143, Issue:3

    Topics: Child; Cystic Fibrosis; Female; Homocysteine; Humans; Male; Methionine; Phosphatidylcholines; Phosphatidylethanolamines; S-Adenosylhomocysteine; Severity of Illness Index

2003
Phosphatidylcholine and lysophosphatidylcholine excretion is increased in children with cystic fibrosis and is associated with plasma homocysteine, S-adenosylhomocysteine, and S-adenosylmethionine.
    The American journal of clinical nutrition, 2005, Volume: 81, Issue:3

    Topics: Case-Control Studies; Child; Choline Deficiency; Cross-Sectional Studies; Cystic Fibrosis; Diet Records; Dietary Fats; Feces; Female; Homocysteine; Humans; Intestinal Absorption; Lysophosphatidylcholines; Male; Phosphatidylcholines; S-Adenosylhomocysteine; S-Adenosylmethionine

2005
Choline-related supplements improve abnormal plasma methionine-homocysteine metabolites and glutathione status in children with cystic fibrosis.
    The American journal of clinical nutrition, 2007, Volume: 85, Issue:3

    Topics: Adolescent; Child; Child, Preschool; Choline; Cystic Fibrosis; Dietary Supplements; Female; Glutathione; Glutathione Disulfide; Homocysteine; Humans; Male; Methionine; Phosphatidylcholines

2007
In vivo evidence of Pseudomonas aeruginosa nutrient acquisition and pathogenesis in the lungs of cystic fibrosis patients.
    Infection and immunity, 2007, Volume: 75, Issue:11

    Topics: Adolescent; Adult; Cystic Fibrosis; Drug Resistance, Bacterial; Food; Gene Expression Profiling; Gene Expression Regulation, Bacterial; Humans; Lung; Metabolic Networks and Pathways; Oligonucleotide Array Sequence Analysis; Phosphatidylcholines; Pseudomonas aeruginosa; Pseudomonas Infections; Reverse Transcriptase Polymerase Chain Reaction; RNA, Bacterial; RNA, Messenger; Virulence

2007
[Why do children rarely have gallstones? Examinations of the lithoindices and the bile acid pattern in infants and children in health and disease (author's transl)].
    Monatsschrift Kinderheilkunde : Organ der Deutschen Gesellschaft fur Kinderheilkunde, 1980, Volume: 128, Issue:8

    Topics: Adolescent; Age Factors; Bile Acids and Salts; Celiac Disease; Child; Child, Preschool; Cholecystokinin; Cholelithiasis; Cholesterol; Cystic Fibrosis; Germany, West; Humans; Infant; Intestinal Secretions; Intestine, Small; Phosphatidylcholines

1980
Abnormal fatty acid turnover in the phospholipids of the red blood cell membranes of cystic fibrosis patients (in vitro study).
    Pediatric research, 1984, Volume: 18, Issue:8

    Topics: Adolescent; Adult; Blood Platelets; Cystic Fibrosis; Erythrocyte Membrane; Fatty Acids; Female; Humans; Linoleic Acid; Linoleic Acids; Male; Phosphatidylcholines; Phosphatidylethanolamines; Phospholipids

1984
Early onset of essential fatty acid deficiency in patients with cystic fibrosis receiving a semisynthetic diet.
    The Journal of pediatrics, 1984, Volume: 105, Issue:6

    Topics: Adolescent; Adult; Cystic Fibrosis; Fatty Acids, Essential; Female; Food, Formulated; Humans; Phosphatidylcholines

1984
In vitro study of the incorporation and transport of nonesterified fatty acids into the phospholipids of the red blood cell membranes of cystic fibrosis patients.
    Pediatric research, 1982, Volume: 16, Issue:9

    Topics: Biological Transport; Child; Cystic Fibrosis; Erythrocyte Membrane; Erythrocytes; Fatty Acids, Nonesterified; Female; Humans; In Vitro Techniques; Linoleic Acids; Male; Palmitic Acids; Phosphatidylcholines; Phosphatidylethanolamines; Phospholipids

1982
Fatty acid pool size in plasma lipoprotein fractions of cystic fibrosis patients.
    The American journal of clinical nutrition, 1995, Volume: 62, Issue:6

    Topics: Adolescent; Adult; Aging; Child; Child, Preschool; Cholesterol Esters; Cystic Fibrosis; Fatty Acids; Female; Fish Oils; Food, Fortified; Humans; Lipids; Lipoproteins; Lipoproteins, HDL; Lipoproteins, VLDL; Male; Phosphatidylcholines; Phosphatidylethanolamines; Triglycerides

1995
Plasma lipid concentrations in children with cystic fibrosis: the value of a high-fat diet and pancreatic supplementation.
    The British journal of nutrition, 1994, Volume: 71, Issue:6

    Topics: Adolescent; Adult; Amylases; Child; Child, Preschool; Cholesterol; Chromatography, High Pressure Liquid; Cystic Fibrosis; Dietary Fats; Endopeptidases; Humans; Hydrolases; Intestinal Absorption; Lipase; Lipids; Liver Cirrhosis; Phosphatidylcholines; Triglycerides

1994
Lung surfactant in a cystic fibrosis animal model: increased alveolar phospholipid pool size without altered composition and surface tension function in cftrm1HGU/m1HGU mice.
    Thorax, 1997, Volume: 52, Issue:8

    Topics: Analysis of Variance; Animals; Bronchoalveolar Lavage Fluid; Chromatography, High Pressure Liquid; Cystic Fibrosis; Glycoproteins; Lung; Mice; Mice, Inbred Strains; Mice, Mutant Strains; Phosphatidylcholines; Phospholipids; Proteolipids; Pulmonary Surfactant-Associated Protein A; Pulmonary Surfactant-Associated Proteins; Pulmonary Surfactants; Specific Pathogen-Free Organisms

1997
Neutrophil phosphatidylcholine (PC) composition in cystic fibrosis (CF).
    Biochemical Society transactions, 1997, Volume: 25, Issue:4

    Topics: Adult; Bronchiectasis; Cell Membrane; Cystic Fibrosis; Humans; Membrane Lipids; Neutrophils; Phosphatidylcholines; Reference Values

1997
Deficient hydrophilic lung surfactant proteins A and D with normal surfactant phospholipid molecular species in cystic fibrosis.
    American journal of respiratory cell and molecular biology, 1999, Volume: 20, Issue:1

    Topics: Bacterial Infections; Bronchoalveolar Lavage Fluid; Child; Cystic Fibrosis; Glycoproteins; Humans; Lung Diseases; Mass Spectrometry; Phosphatidylcholines; Phosphatidylglycerols; Phosphatidylinositols; Phospholipids; Proteolipids; Pseudomonas Infections; Pulmonary Surfactant-Associated Protein A; Pulmonary Surfactant-Associated Protein D; Pulmonary Surfactant-Associated Proteins; Pulmonary Surfactants

1999
Metabolism of surfactant phosphatidylcholine molecular species in cftr(tm1HGU/tm1HGU) mice compared to MF-1 mice.
    Experimental lung research, 2001, Volume: 27, Issue:4

    Topics: Animals; Bronchoalveolar Lavage Fluid; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Disease Models, Animal; Humans; Kinetics; Lung; Mice; Mice, Mutant Strains; Phosphatidylcholines; Pulmonary Surfactants; Tritium

2001
Fatty-acid composition of lecithin fraction of mucus in cystic fibrosis.
    Lancet (London, England), 1977, Apr-02, Volume: 1, Issue:8014

    Topics: Bronchi; Child; Cystic Fibrosis; Fatty Acids, Essential; Humans; Mucus; Phosphatidylcholines

1977
Fatty-acid composition of serum-lecithins in cystic-fibrosis patients without steatorrhoea.
    Lancet (London, England), 1978, Oct-21, Volume: 2, Issue:8095

    Topics: Cystic Fibrosis; Fatty Acids, Unsaturated; Humans; Pancreas; Phosphatidylcholines

1978
Triglyceride levels after Intralipid infusion in children with cystic fibrosis.
    Pediatrics, 1978, Volume: 61, Issue:6

    Topics: Child, Preschool; Cystic Fibrosis; Dietary Fats; Drug Combinations; Fatty Acids, Essential; Fatty Acids, Nonesterified; Female; Glycerol; Humans; Male; Parenteral Nutrition; Phosphatidylcholines; Triglycerides

1978
The chronically reserpinized rat as an animal model for cystic fibrosis: I. Acute effect of isoproterenol and pilocarpine upon pulmonary lavage fluid.
    Pediatric research, 1979, Volume: 13, Issue:6

    Topics: Animals; Carbohydrate Metabolism; Cholesterol; Cystic Fibrosis; Isoproterenol; Lipid Metabolism; Lung; Male; Phosphatidylcholines; Phospholipids; Pilocarpine; Proteins; Rats; Reserpine; Therapeutic Irrigation

1979
Mucoid strains of Pseudomonas aeruginosa: the influence of culture medium on the stability of mucus production.
    Journal of medical microbiology, 1975, Volume: 8, Issue:4

    Topics: Acetylcysteine; Cetrimonium Compounds; Citrates; Culture Media; Cystic Fibrosis; Deoxycholic Acid; Ferric Compounds; Humans; Lactose; Mucus; Neutral Red; Phosphatidylcholines; Polysorbates; Pseudomonas aeruginosa; Sodium Dodecyl Sulfate; Species Specificity; Surface-Active Agents; Thiosulfates

1975
Lipid composition of airway secretions from patients with asthma and patients with cystic fibrosis.
    The American review of respiratory disease, 1977, Volume: 115, Issue:2

    Topics: Adolescent; Adult; Asthma; Ceramides; Child; Cholesterol; Cystic Fibrosis; Diglycerides; Glycolipids; Humans; Lipid Metabolism; Lung; Phosphatidylcholines; Phosphatidylethanolamines; Phospholipids; Therapeutic Irrigation; Triglycerides

1977
Modulation of human erythrocyte shape and fatty acids by diet.
    Biochimica et biophysica acta, 1986, Aug-21, Volume: 860, Issue:2

    Topics: Adolescent; Cystic Fibrosis; Dietary Fats; Erythrocyte Membrane; Erythrocytes; Erythrocytes, Abnormal; Fatty Acids; Fatty Acids, Essential; Food, Formulated; Humans; Linoleic Acid; Linoleic Acids; Lipids; Membrane Lipids; Microscopy, Electron; Phosphatidylcholines; Phosphatidylethanolamines

1986