Page last updated: 2024-11-07

penicillamine and Cruveilhier-Baumgarten Syndrome

penicillamine has been researched along with Cruveilhier-Baumgarten Syndrome in 7 studies

Penicillamine: 3-Mercapto-D-valine. The most characteristic degradation product of the penicillin antibiotics. It is used as an antirheumatic and as a chelating agent in Wilson's disease.
penicillamine : An alpha-amino acid having the structure of valine substituted at the beta position with a sulfanyl group.

Cruveilhier-Baumgarten Syndrome: Liver cirrhosis with intrahepatic portal obstruction, HYPERTENSION, and patent UMBILICAL VEINS.

Research Excerpts

ExcerptRelevanceReference
"Fifty-eight patients with Wilson's disease are reviewed, of whom 25 symptomatic patients experienced liver disease first and 28, brain disease."1.26Clinical spectrum of Wilson's disease (hepatolenticular degeneration). ( Dobyns, WB; Goldstein, NP; Gordon, H, 1979)

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19904 (57.14)18.7374
1990's1 (14.29)18.2507
2000's0 (0.00)29.6817
2010's2 (28.57)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Idrissi, ML1
Babakhoya, A1
Khabbache, K1
Souilmi, F1
Benmiloud, S1
Abourrazak, S1
Chaouki, S1
Atmani, S1
Bouharrou, A1
Hida, M1
Moores, A1
Fox, S1
Lang, A1
Hirschfield, GM1
Martínez-Cuesta, MA1
Moreno, L1
Piqué, JM1
Bosch, J1
Rodrigo, J1
Esplugues, JV1
Grand, RJ1
Dobyns, WB1
Goldstein, NP1
Gordon, H1
Warnes, TW1
Slovis, TL1
Dubois, RS1
Rodgerson, DO1
Silverman, A1

Reviews

2 reviews available for penicillamine and Cruveilhier-Baumgarten Syndrome

ArticleYear
[Wilson's disease in the child: apropos of 20 cases].
    The Pan African medical journal, 2013, Volume: 14

    Topics: Adolescent; Anemia, Hemolytic; Ceruloplasmin; Chelation Therapy; Child; Child, Preschool; Consanguin

2013
Treatment of primary biliary cirrhosis.
    Seminars in liver disease, 1985, Volume: 5, Issue:3

    Topics: Adrenal Cortex Hormones; Autoimmune Diseases; Azathioprine; Chlorambucil; Cholelithiasis; Colchicine

1985

Other Studies

5 other studies available for penicillamine and Cruveilhier-Baumgarten Syndrome

ArticleYear
Wilson disease: Canadian perspectives on presentation and outcomes from an adult ambulatory setting.
    Canadian journal of gastroenterology = Journal canadien de gastroenterologie, 2012, Volume: 26, Issue:6

    Topics: Adolescent; Adult; Ambulatory Care; Biopsy; Brain Diseases; Canada; Chelating Agents; Child; Female;

2012
Nitric oxide-mediated beta 2-adrenoceptor relaxation is impaired in mesenteric veins from portal-hypertensive rats.
    Gastroenterology, 1996, Volume: 111, Issue:3

    Topics: Adrenergic beta-Agonists; Albuterol; Animals; Electric Stimulation; Hypertension, Portal; Immunohist

1996
Wilson's disease.
    Mayo Clinic proceedings, 1979, Volume: 54, Issue:4

    Topics: Hepatolenticular Degeneration; Humans; Hypertension, Portal; Penicillamine; Portacaval Shunt, Surgic

1979
Clinical spectrum of Wilson's disease (hepatolenticular degeneration).
    Mayo Clinic proceedings, 1979, Volume: 54, Issue:1

    Topics: Adolescent; Adult; Brain Diseases; Child; Copper; Cornea; Dimercaprol; Female; Hepatolenticular Dege

1979
The varied manifestations of Wilson's disease.
    The Journal of pediatrics, 1971, Volume: 78, Issue:4

    Topics: Adolescent; Anemia, Hemolytic; Ascites; Ceruloplasmin; Child; Copper; Diseases in Twins; Eye Manifes

1971