penicillamine has been researched along with Congenital Hypocupremia in 5 studies
Penicillamine: 3-Mercapto-D-valine. The most characteristic degradation product of the penicillin antibiotics. It is used as an antirheumatic and as a chelating agent in Wilson's disease.
penicillamine : An alpha-amino acid having the structure of valine substituted at the beta position with a sulfanyl group.
| Excerpt | Relevance | Reference |
|---|---|---|
| "Excellent treatment options exist for Wilson disease, based on copper chelation." | 2.49 | Inborn errors of copper metabolism. ( Kaler, SG, 2013) |
| "Menkes' disease is a rare X-linked recessive inherited disorder of copper metabolism characterized by neurodegeneration, peculiar hair, and early death." | 1.27 | Menkes' disease: long-term treatment with copper and D-penicillamine. ( Baerlocher, K; Nadal, D, 1988) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 3 (60.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 2 (40.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Kaler, SG | 1 |
| Nomura, S | 1 |
| Nozaki, S | 1 |
| Hamazaki, T | 1 |
| Takeda, T | 1 |
| Ninomiya, E | 1 |
| Kudo, S | 1 |
| Hayashinaka, E | 1 |
| Wada, Y | 1 |
| Hiroki, T | 1 |
| Fujisawa, C | 1 |
| Kodama, H | 1 |
| Shintaku, H | 1 |
| Watanabe, Y | 1 |
| Prockop, DJ | 1 |
| Kivirikko, KI | 1 |
| Tuderman, L | 1 |
| Guzman, NA | 1 |
| Siegel, RC | 1 |
| Nadal, D | 1 |
| Baerlocher, K | 1 |
2 reviews available for penicillamine and Congenital Hypocupremia
| Article | Year |
|---|---|
Inborn errors of copper metabolism.
Topics: Chelating Agents; Child; Copper; Cutis Laxa; Ehlers-Danlos Syndrome; Hepatolenticular Degeneration; | 2013 |
Lysyl oxidase.
Topics: Amino Acid Oxidoreductases; Aneurysm; Animals; Chickens; Collagen; Copper; Cutis Laxa; Dogs; Ehlers- | 1979 |
3 other studies available for penicillamine and Congenital Hypocupremia
| Article | Year |
|---|---|
PET imaging analysis with 64Cu in disulfiram treatment for aberrant copper biodistribution in Menkes disease mouse model.
Topics: Animals; Autoradiography; Brain; Chelating Agents; Copper; Copper Radioisotopes; Disease Models, Ani | 2014 |
The biosynthesis of collagen and its disorders (second of two parts).
Topics: Aging; Animals; Colchicine; Collagen; Collagen Diseases; Ehlers-Danlos Syndrome; Glucosyltransferase | 1979 |
Menkes' disease: long-term treatment with copper and D-penicillamine.
Topics: Body Fluids; Brain; Brain Diseases, Metabolic; Copper; Drug Therapy, Combination; Electroencephalogr | 1988 |