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penicillamine and Amino Acid Metabolism Disorders, Inborn

penicillamine has been researched along with Amino Acid Metabolism Disorders, Inborn in 8 studies

Penicillamine: 3-Mercapto-D-valine. The most characteristic degradation product of the penicillin antibiotics. It is used as an antirheumatic and as a chelating agent in Wilson's disease.
penicillamine : An alpha-amino acid having the structure of valine substituted at the beta position with a sulfanyl group.

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19907 (87.50)18.7374
1990's1 (12.50)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
MILNE, MD1
ROSSIER, A1
CALDERA, R1
ODIEVRE, M1
Rees, MM1
Rodgers, GM1
Ozog, LS1
Tomskey, GC1
Bell, GE1
Slivka, DC1
Huston, JR1
Seegmiller, JE2
Friedmann, T1
Harrison, HE1
Wong, V1
Schneider, JA2
Crawhall, JC1
Lietman, PS1
Kelly, S1
Copeland, W1

Reviews

1 review available for penicillamine and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Homocysteinemia: association of a metabolic disorder with vascular disease and thrombosis.
    Thrombosis research, 1993, Sep-01, Volume: 71, Issue:5

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Blood Coagulation Factors; Blood Platelets; Child; Cyst

1993

Other Studies

7 other studies available for penicillamine and Amino Acid Metabolism Disorders, Inborn

ArticleYear
DISORDERS OF AMINO-ACID TRANSPORT.
    British medical journal, 1964, Feb-08, Volume: 1, Issue:5379

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Cystinosis; Cystinuria; Dog Diseases; Dogs; Kidney Di

1964
[RECENT IDEAS ON CYSTINOSIS].
    Bulletins et memoires de la Societe medicale des hopitaux de Paris, 1963, Nov-15, Volume: 114

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Chemical Analysis; Citric Acid Cycle; Cystinosis; Dimerc

1963
Diagnosis and treatment of cystinuria.
    Urology, 1974, Volume: 3, Issue:2

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biological Transport; Colorin

1974
The renal clearance of amino acids in a patient with Wilson's disease during penicillamine treatment.
    The Journal of laboratory and clinical medicine, 1968, Volume: 71, Issue:1

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Copper; Creatinine; Hepatolenticular

1968
Cystinosis. Combined clinical staff conference at the National Institutes of Health.
    Annals of internal medicine, 1968, Volume: 68, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Biopsy; Bone Marrow; Child; Chronic Kidney Disease-Mineral and

1968
Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment.
    The American journal of medicine, 1968, Volume: 44, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Blood Chemical Analysis; Cysteine; Cystine; Cysti

1968
A hypothesis on the homocystinuric's response to pyridoxine.
    Metabolism: clinical and experimental, 1968, Volume: 17, Issue:9

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Chemistry, Clinical; Cysteine; Homocystinuria; Hum

1968