palmitoyl coenzyme a has been researched along with Lipid Metabolism, Inborn Error in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 2 (33.33) | 18.7374 |
1990's | 2 (33.33) | 18.2507 |
2000's | 2 (33.33) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Liebig, M; Mayatepek, E; Mueller, M; Ruiter, J; Schymik, I; Spiekerkoetter, U; Strauss, AW; Wanders, RJ; Wendel, U | 1 |
Mayatepek, E; Primassin, S; Spiekerkoetter, U; Ter Veld, F | 1 |
Anderson, VE; Hale, DE; Tamvakopoulos, CS; Willi, S | 1 |
Almeida, IT; Ijlst, L; Ruiter, JP; Ventura, FV; Wanders, RJ | 1 |
de Vries, CT; Schrakamp, G; Schram, AW; Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; Wanders, RJ | 1 |
Amendt, BA; Rhead, WJ | 1 |
6 other study(ies) available for palmitoyl coenzyme a and Lipid Metabolism, Inborn Error
Article | Year |
---|---|
Neonatal screening for very long-chain acyl-coA dehydrogenase deficiency: enzymatic and molecular evaluation of neonates with elevated C14:1-carnitine levels.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Biomarkers; Carnitine; Cohort Studies; Fatty Acids; Humans; Infant, Newborn; Lipid Metabolism, Inborn Errors; Lymphocytes; Neonatal Screening; Oxidation-Reduction; Palmitoyl Coenzyme A; Sequence Analysis, DNA; Spectrometry, Mass, Electrospray Ionization | 2006 |
Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Betaine; Carnitine; Cell Line, Tumor; Cell Proliferation; Cell Survival; Dietary Supplements; Humans; Lipid Metabolism, Inborn Errors; Liver; Mice; Mice, Knockout; Muscle, Skeletal; Palmitoyl Coenzyme A; Palmitoylcarnitine; Physical Exertion; Time Factors | 2008 |
Long-chain acyl-CoA profiles in cultured fibroblasts from patients with defects in fatty acid oxidation.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenase, Long-Chain; Carnitine O-Palmitoyltransferase; Cell Line; Fatty Acids; Fibroblasts; Humans; Lipid Metabolism, Inborn Errors; Oxidation-Reduction; Palmitoyl Coenzyme A | 1995 |
Inhibition of oxidative phosphorylation by palmitoyl-CoA in digitonin permeabilized fibroblasts: implications for long-chain fatty acid beta-oxidation disorders.
Topics: 2,4-Dinitrophenol; Acyl Coenzyme A; Adenosine Triphosphate; Cell Membrane Permeability; Cells, Cultured; Citrate (si)-Synthase; Digitonin; Dinitrophenols; Fatty Acids; Fibroblasts; Humans; Lipid Metabolism, Inborn Errors; Octoxynol; Oxidation-Reduction; Oxidative Phosphorylation; Palmitoyl Coenzyme A; Succinates; Succinic Acid; Uncoupling Agents | 1995 |
Peroxisomal beta-oxidation of palmitoyl-CoA in human liver homogenates and its deficiency in the cerebro-hepato-renal (Zellweger) syndrome.
Topics: Acyl Coenzyme A; Animals; beta-N-Acetylhexosaminidases; Centrifugation, Density Gradient; Humans; Lipid Metabolism, Inborn Errors; Liver; Microbodies; Oxidation-Reduction; Palmitoyl Coenzyme A; Rats; Subcellular Fractions | 1986 |
The multiple acyl-coenzyme A dehydrogenation disorders, glutaric aciduria type II and ethylmalonic-adipic aciduria. Mitochondrial fatty acid oxidation, acyl-coenzyme A dehydrogenase, and electron transfer flavoprotein activities in fibroblasts.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenases; Adipates; Animals; Caprylates; Electron Transport; Electron-Transferring Flavoproteins; Fatty Acids; Fibroblasts; Flavin-Adenine Dinucleotide; Flavoproteins; Glutarates; Lipid Metabolism, Inborn Errors; Liver; Malonates; Mitochondria; Palmitoyl Coenzyme A; Succinates; Succinic Acid; Swine | 1986 |