palmitic acid has been researched along with Zellweger Syndrome in 5 studies
Palmitic Acid: A common saturated fatty acid found in fats and waxes including olive oil, palm oil, and body lipids.
hexadecanoic acid : A straight-chain, sixteen-carbon, saturated long-chain fatty acid.
Zellweger Syndrome: An autosomal recessive disorder due to defects in PEROXISOME biogenesis which involves more than 13 genes encoding peroxin proteins of the peroxisomal membrane and matrix. Zellweger syndrome is typically seen in the neonatal period with features such as dysmorphic skull; MUSCLE HYPOTONIA; SENSORINEURAL HEARING LOSS; visual compromise; SEIZURES; progressive degeneration of the KIDNEYS and the LIVER. Zellweger-like syndrome refers to phenotypes resembling the neonatal Zellweger syndrome but seen in children or adults with apparently intact peroxisome biogenesis.
| Excerpt | Relevance | Reference |
|---|---|---|
| " Although plasma very-long-chain fatty acid profile suggested X-linked adrenoleukodystrophy, marked reduction in fibroblast lignoceric acid oxidation and the presence of cytosolic catalase were consistent with Zellweger syndrome (ZS)." | 3.69 | Late-onset generalized disorder of peroxisomes. ( Burdette, DE; Fink, JK; Kremser, K; Pahan, K; Singh, I; Stanley, W, 1996) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 5 (100.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Singh, I | 4 |
| Lazo, O | 3 |
| Kremser, K | 2 |
| Pahan, K | 2 |
| Dhaunsi, GS | 1 |
| Ozand, P | 1 |
| Burdette, DE | 1 |
| Fink, JK | 1 |
| Stanley, W | 2 |
| Reubsaet, FA | 1 |
| Veerkamp, JH | 1 |
| Brückwilder, ML | 1 |
| Trijbels, JM | 1 |
| Hashimoto, T | 1 |
| Monnens, LA | 1 |
| Contreras, M | 1 |
| Yoshida, Y | 1 |
| Singh, AK | 1 |
| Weise, M | 1 |
5 other studies available for palmitic acid and Zellweger Syndrome
| Article | Year |
|---|---|
Purification of peroxisomes and subcellular distribution of enzyme activities for activation and oxidation of very-long-chain fatty acids in rat brain.
Topics: Adrenoleukodystrophy; Animals; Antibodies; Brain Chemistry; Coenzyme A Ligases; Fatty Acids; Liver; | 1993 |
Phytanic acid alpha-oxidation. Differential subcellular localization in rat and human tissues and its inhibition by nycodenz.
Topics: Adrenoleukodystrophy; Animals; Cell Fractionation; Cells, Cultured; Centrifugation, Density Gradient | 1993 |
Late-onset generalized disorder of peroxisomes.
Topics: Adrenoleukodystrophy; Adult; Catalase; Fatty Acids; Genetic Linkage; Humans; Male; Microbodies; Oxid | 1996 |
Immunochemical and biochemical studies of fatty acid oxidation in fibroblasts of Zellweger and X-linked adrenoleukodystrophy patients.
Topics: Acetyl-CoA C-Acyltransferase; Acyl-CoA Oxidase; Adrenoleukodystrophy; Fatty Acids; Fibroblasts; Huma | 1991 |
Cellular oxidation of lignoceric acid is regulated by the subcellular localization of lignoceroyl-CoA ligases.
Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis | 1990 |