ornithine has been researched along with Retinal Degeneration in 53 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 40 (75.47) | 18.7374 |
1990's | 6 (11.32) | 18.2507 |
2000's | 3 (5.66) | 29.6817 |
2010's | 3 (5.66) | 24.3611 |
2020's | 1 (1.89) | 2.80 |
Authors | Studies |
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Audano, M; Auricchio, A; Bellezza, I; Boffa, I; Brunetti-Pierri, N; Caterino, M; Cellini, B; De Stefano, L; Dell'Aquila, F; Marrocco, E; Mitro, N; Nusco, E; Pedretti, S; Polishchuk, E; Ruoppolo, M | 1 |
Black, G; Jasani, KM; Kelly, SP; Parry, NRA | 1 |
Agarwal, A; Chandani, N; Dhawan, A; Kumar, K; Raj, P | 1 |
Boenzi, S; Capozzi, P; Dionisi-Vici, C; Morini, C; Rizzo, C; Santorelli, FM | 1 |
Hayasaka, S; Kodama, T; Ohira, A | 1 |
Costagliola, C; D'Aloia, A; D'Avanzo, A; del Giudice, EM; Perrone, L; Prisco, F; Santinelli, R; Tolone, C | 1 |
Bohijn, W; François, J; Vannas-Sulonen, K; Victoria-Troncoso, V | 1 |
Berson, EL | 1 |
Arshinoff, SA; Bell, L; Marliss, EB; McCulloch, JC; McInnes, RR | 1 |
Hiraiwa, N; Inagaki, E; Ishiguro, I; Iwasaki, K; Matsuzawa, T | 1 |
Akiya, S; Baba, S; Choshi, K; Fukuda, K; Hirata, H; Mishima, H; Nishi, Y; Tanaka, Y; Usui, T | 1 |
Hollyfield, JG | 1 |
Heckenlively, J | 1 |
Merin, S; Shapira, Y; Statter, M; Yarom, R; Yatziv, S | 1 |
Kennaway, NG; Weleber, RG | 1 |
Hayasaka, S; Mizuno, K; Omura, K; Saito, T; Tada, K | 1 |
Behrens-Baumann, W; Hansmann, I; König, U; Langenbeck, U; Schröder, K | 1 |
Chen, CJ; Furr, P | 1 |
Buist, NR; Kennaway, NG; Weleber, RG | 1 |
Kaiser-Kupfer, M; Valle, D | 1 |
Matsuzawa, T | 1 |
Milton, RC; Takki, KK | 1 |
Askanas, V; Brody, L; Dvoretzky, I; Engel, WK; Kaiser-Kupfer, MI; Kuwabara, T; Takki, K | 1 |
Berson, EL; Shih, VE; Sullivan, PL | 1 |
Brusilow, S; Kaiser-Kupfer, MI; Takki, K; Valle, D; Walser, M | 1 |
Ishikawa, Y; Kaiser-Kupfer, MI; Kuwabara, T | 1 |
Berson, EL; Gargiulo, M; Shih, VE | 1 |
O'Donnell, JJ; Sandman, R; Sipilä, I; Vannas, A; Vannas-Sulonen, K | 1 |
Bron, AJ; Kaiser-Kupfer, MI; Valle, D | 1 |
Brusilow, SW; Kaiser-Kupfer, M; Valle, D; Walser, M | 1 |
Sipilä, I | 1 |
Brusilow, S; de Monasterio, FM; Kaiser-Kupfer, MI; Valle, D; Walser, M | 1 |
Aguirre, G; Boison, AP; Jezyk, P; Valle, DL | 1 |
Lawler, AM; Milam, AH; Sipila, I; Steel, G; Valle, D; Wang, T | 1 |
Itagaki, T; Ohkuma, H; Takahashi, K; Takeuchi, M; Uyama, M | 1 |
Milam, AH; Steel, G; Valle, D; Wang, T | 2 |
Rodriguez Caballero, ML | 1 |
Arshinoff, SA; Gordon, BA; Marliss, EB; Matuk, Y; McCulloch, JC; Phillips, MJ | 1 |
François, J | 2 |
Martin, SR; O'Donnell, JJ; Sandman, RP | 1 |
Berson, EL; Mandell, R; Schmidt, SY; Shih, VE | 1 |
Arshinoff, SA; Marliss, EB; McCulloch, JC; Parker, JA | 1 |
Berson, EL; Schmidt, SY; Shih, VE | 1 |
Marliss, EB; McCulloch, C | 1 |
Berson, EL; Rabin, AR; Schmidt, SY | 1 |
Itagaki, T; Okuma, H; Takahashi, K; Takeuchi, M; Uyama, M | 1 |
Caruso, RC; Kaiser-Kupfer, MI; Valle, D | 1 |
Itagaki, T; Takahashi, K; Takeuchi, M; Uyama, M | 1 |
Jones, ME | 1 |
Akiya, S; Hayakawa, M; Hayasaka, S; Miyake, Y; Mizuno, K; Ohba, N; Sasayama, C; Shiono, T; Tanaka, Y | 1 |
Simell, O; Takki, K | 1 |
4 review(s) available for ornithine and Retinal Degeneration
Article | Year |
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Retinal risks of high-dose ornithine supplements: a review.
Topics: Animals; Dietary Supplements; Dose-Response Relationship, Drug; Haplorhini; Heterozygote; Humans; Hyperammonemia; Mice; Models, Biological; Ornithine; Rats; Rats, Sprague-Dawley; Retina; Retinal Degeneration; Retinal Pigment Epithelium; Urea Cycle Disorders, Inborn | 2011 |
Nutrition and retinal degenerations. Vitamin A, taurine, ornithine, and phytanic acid.
Topics: Animal Nutritional Physiological Phenomena; Animals; Electroretinography; Fluorescein Angiography; Fundus Oculi; Humans; Nutrition Disorders; Nutritional Requirements; Ornithine; Phytanic Acid; Retinal Degeneration; Taurine; Vitamin A Deficiency | 1982 |
Gyrate atrophy of the choroid and retina. Approaches to therapy.
Topics: Adult; Atrophy; Choroid; Female; Humans; Male; Microscopy, Electron; Muscles; Muscular Diseases; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Transaminases; Uveal Diseases | 1981 |
Gyrate atrophy of the choroid and retina.
Topics: Arginine; Choroid; Creatine; Diet; Genes, Recessive; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Pyridoxine; Retinal Degeneration; Uveal Diseases | 1982 |
49 other study(ies) available for ornithine and Retinal Degeneration
Article | Year |
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Liver-directed gene therapy for ornithine aminotransferase deficiency.
Topics: Animals; Genetic Therapy; Gyrate Atrophy; Liver; Mice; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration | 2023 |
Unique case of gyrate atrophy with a well-preserved electroretinogram (ERG).
Topics: Adult; Cataract; Cataract Extraction; Diet, Protein-Restricted; Disease Progression; Electroretinography; Female; Gyrate Atrophy; Humans; Lens Implantation, Intraocular; Ornithine; Pyridoxine; Retinal Degeneration; Treatment Outcome; Visual Fields; Vitamins | 2018 |
Ocular manifestations in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: a rare association.
Topics: Adolescent; Diagnosis, Differential; Fluorescein Angiography; Fovea Centralis; Fundus Oculi; Humans; Hyperammonemia; Male; Myopia; Ornithine; Retinal Degeneration; Tomography, Optical Coherence; Urea Cycle Disorders, Inborn; Vitreous Body | 2015 |
Retinal degeneration.
Topics: Adult; Amino Acid Transport Systems, Basic; Cataract; Citrulline; Consanguinity; Creatine; Diet, Protein-Restricted; Female; Humans; Hyperammonemia; Metabolism, Inborn Errors; Mitochondrial Membrane Transport Proteins; Ornithine; Retinal Degeneration; Syndrome; Vision Disorders | 2009 |
Low-protein diet and progression of retinal degeneration in gyrate atrophy of the choroid and retina: a twenty-six-year follow-up.
Topics: Adult; Child, Preschool; Choroid; Diet, Protein-Restricted; Electrooculography; Female; Follow-Up Studies; Gyrate Atrophy; Homozygote; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Retina; Retinal Degeneration; Visual Fields | 2004 |
Conjunctival biopsies in gyrate atrophy of the choroid and retina.
Topics: Adult; Atrophy; Choroid; Conjunctiva; Epithelium; Female; Fibroblasts; Humans; Inclusion Bodies; Microscopy, Electron; Ornithine; Retina; Retinal Degeneration | 1984 |
Hyperornithinaemia and gyrate atrophy of the retina: improvement of vision during treatment with a low-arginine diet.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Atrophy; Depression, Chemical; Humans; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Visual Acuity | 1981 |
Disease of ornithine-proline pathway: a delta 1-pyrroline-5-carboxylate reductase deficiency in the retina or retinal degeneration mice.
Topics: Animals; Arginase; Cattle; Cornea; Female; Glutamates; Glutamic Acid; Male; Mice; Mice, Inbred C3H; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Oxidoreductases Acting on CH-NH Group Donors; Proline; Pyrroline Carboxylate Reductases; Retina; Retinal Degeneration | 1982 |
Free amino acid concentrations in blood cells of two brothers with gyrate atrophy of the choroid and retina with hyperornithinaemia.
Topics: Adult; Amino Acids; Blood Cells; Choroid; Erythrocytes; Granulocytes; Humans; Lymphocytes; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Transaminases; Uveal Diseases | 1983 |
Simulation of the conditions of gyrate atrophy in vitro suppresses retinal protein synthesis.
Topics: Animals; Atrophy; Autoradiography; Eye Proteins; In Vitro Techniques; Leucine; Ornithine; Papio; Retina; Retinal Degeneration; Retinal Diseases | 1983 |
Possible syndrome of high myopia with retinal degeneration, cataract, manic depression, and elevated plasma amino acids.
Topics: Aged; Amino Acids; Bipolar Disorder; Cataract; Female; Humans; Lysine; Male; Middle Aged; Myopia; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Serine; Syndrome | 1980 |
Myopathy in hyperornithinemic gyrate atrophy of choroid and retina.
Topics: Adolescent; Adult; Biopsy; Child; Choroid; Female; Humans; Lysine; Male; Muscular Atrophy; Ornithine; Retinal Degeneration; Uveal Diseases | 1981 |
Clinical trial of vitamin B6 for gyrate atrophy of the choroid and retina.
Topics: Analysis of Variance; Atrophy; Choroid; Dose-Response Relationship, Drug; Electroretinography; Humans; Lysine; Ornithine; Pyridoxine; Retinal Degeneration; Uveal Diseases | 1981 |
Hyperornithinaemia associated with gyrate atrophy of the choroid and retina: in vivo and in vitro response to vitamin B6.
Topics: Adolescent; Child; Child, Preschool; Choroid; Fibroblasts; Humans; Lymphocytes; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Proline; Pyridoxine; Retinal Degeneration; Transaminases; Uveal Diseases | 1981 |
Biochemical and therapeutical studies in a case of atrophia gyrata.
Topics: Adult; Atrophy; Choroid; Humans; Lysine; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Pedigree; Pyridoxine; Retina; Retinal Degeneration; Transaminases | 1982 |
Bilateral keratoconus in a patient with gyrate atrophy and hyperornithinemia.
Topics: Adult; Atrophy; Choroid; Humans; Keratoconus; Male; Ornithine; Retinal Degeneration; Uveal Diseases | 1983 |
Disease of the ornithine-proline pathway: delta 1-pyrroline-5-carboxylate reductase deficiency in the retina of retinal degeneration mice.
Topics: Animals; Cattle; Eye; Liver; Mice; Mice, Inbred Strains; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Proline; Pyrroles; Retinal Degeneration; Weaning | 1982 |
The natural history of gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Age Factors; Aged; Aphakia; Atrophy; Child; Choroid; Dark Adaptation; Female; Follow-Up Studies; Fundus Oculi; Humans; Male; Middle Aged; Ornithine; Retinal Degeneration; Uveal Diseases; Vision Disorders; Visual Acuity; Visual Fields | 1981 |
Systemic manifestations of gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Atrophy; Child; Choroid; Electroencephalography; Female; Hair; Humans; Male; Middle Aged; Muscles; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Uveal Diseases | 1981 |
Ocular findings in patients with gyrate atrophy on pyridoxine and low-protein, low-arginine diets.
Topics: Adolescent; Adult; Arginine; Atrophy; Child; Choroid; Dark Adaptation; Dietary Proteins; Electroretinography; Female; Humans; Male; Ornithine; Pyridoxine; Retinal Degeneration; Uveal Diseases; Vision Disorders; Visual Acuity; Visual Fields | 1981 |
Gyrate atrophy of the choroid and retina. Biochemical considerations and experience with an arginine-restricted diet.
Topics: Adolescent; Adult; Aminoisobutyric Acids; Arginine; Atrophy; Child; Choroid; Female; Humans; Male; Middle Aged; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Uveal Diseases | 1981 |
Experimental model of gyrate atrophy in animals.
Topics: Animals; Atrophy; Choroid; Disease Models, Animal; Injections; Macaca fascicularis; Macaca mulatta; Ornithine; Pigment Epithelium of Eye; Rats; Rats, Inbred Strains; Retinal Degeneration; Uveal Diseases; Vitreous Body | 1981 |
Reduction of hyperornithinemia with a low protein, low arginine diet and pyridoxine in patients with a deficiency of ornithine-ketoacid transaminase (OKT) activity and gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Amino Acids, Essential; Arginine; Child; Choroid; Dietary Proteins; Female; Humans; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Pyridoxine; Retinal Degeneration; Transaminases; Uveal Diseases | 1981 |
Gyrate atrophy of the retina and choroid. Two methods for prenatal diagnosis.
Topics: Amniotic Fluid; Atrophy; Child; Choroid; Chromatography, High Pressure Liquid; Female; Humans; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Pregnancy; Prenatal Diagnosis; Retinal Degeneration; Transaminases; Uveal Diseases | 1981 |
Clinical and biochemical heterogeneity in gyrate atrophy.
Topics: Adolescent; Adult; Atrophy; Cataract; Child; Choroid; Female; Genes; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Pyridoxine; Retinal Degeneration; Uveal Diseases | 1980 |
Gyrate atrophy of the choroid and retina: amino acid metabolism and correction of hyperornithinemia with an arginine-deficient diet.
Topics: Adult; Amino Acids; Arginine; Choroid; Diet; Female; Humans; Male; Middle Aged; Ornithine; Retinal Degeneration; Retinal Detachment; Time Factors; Uveal Diseases | 1980 |
Inhibition of arginine-glycine amidinotransferase by ornithine. A possible mechanism for the muscular and chorioretinal atrophies in gyrate atrophy of the choroid and retina with hyperornithinemia.
Topics: Amidinotransferases; Animals; Arginase; Atrophy; Choroid; Creatine; Glycine; Humans; Kidney; Kinetics; Male; Muscles; Ornithine; Ornithine-Oxo-Acid Transaminase; Rats; Retina; Retinal Degeneration; Uveal Diseases | 1980 |
Gyrate atrophy of the choroid and retina: improved visual function following reduction of plasma ornithine by diet.
Topics: Adult; Arginine; Choroid; Color Perception; Dark Adaptation; Dietary Proteins; Female; Humans; Ornithine; Photoreceptor Cells; Retinal Degeneration; Uveal Diseases; Vision, Ocular | 1980 |
Gyrate atrophy of the choroid and retina in a cat.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Cats; Choroid; Disease Models, Animal; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Retina; Retinal Degeneration; Transaminases; Uveal Diseases | 1981 |
Mice lacking ornithine-delta-aminotransferase have paradoxical neonatal hypoornithinaemia and retinal degeneration.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Animals; Animals, Newborn; Arginine; Base Sequence; DNA Primers; Food, Fortified; Genotype; Gyrate Atrophy; Humans; Infant; Lysine; Mammals; Mice; Mice, Mutant Strains; Molecular Sequence Data; Ornithine; Ornithine-Oxo-Acid Transaminase; Phenotype; Polymerase Chain Reaction; Retina; Retinal Degeneration | 1995 |
[Changes in the intermediate stage of retinal degeneration after intravitreal injection of ornithine].
Topics: Animals; Atrophy; Fluorescein Angiography; Injections; Macaca fascicularis; Ornithine; Photoreceptor Cells; Pigment Epithelium of Eye; Retinal Degeneration; Vitreous Body | 1993 |
A mouse model of gyrate atrophy of the choroid and retina. Early retinal pigment epithelium damage and progressive retinal degeneration.
Topics: Animals; Atrophy; Choroid; Disease Models, Animal; Electroretinography; Female; Mice; Mice, Inbred C57BL; Ornithine; Ornithine-Oxo-Acid Transaminase; Pigment Epithelium of Eye; Retinal Degeneration | 1996 |
Correction of ornithine accumulation prevents retinal degeneration in a mouse model of gyrate atrophy of the choroid and retina.
Topics: Amino Acids; Animals; Arginine; Choroid; Disease Models, Animal; Electroretinography; Gyrate Atrophy; Mice; Mice, Knockout; Ornithine; Ornithine-Oxo-Acid Transaminase; Retina; Retinal Degeneration | 2000 |
[Chorio-retinal degenerations and aminoaciduria. III. Atrophia gyrata].
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Female; Humans; Male; Ornithine; Pedigree; Retinal Degeneration | 1975 |
Amino-acid metabolism and liver ultrastructure in hyperornithinemia with gyrate atrophy of the choroid and retina.
Topics: Adult; Amino Acids; Child; Choroid; Humans; Hypertrophy; Liver; Male; Ornithine; Retinal Degeneration; Syndrome; Uveal Diseases | 1979 |
Gyrate atrophy of the choroid and retina.
Topics: Adolescent; Amino Acids; Atrophy; Child; Choroid; Dark Adaptation; Female; Genes, Recessive; Humans; Ornithine; Pedigree; Retina; Retinal Degeneration; Visual Acuity; Visual Fields | 1979 |
Gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Child; Female; Follow-Up Studies; Heterozygote; Homozygote; Humans; Ornithine; Pedigree; Retinal Degeneration | 1979 |
Gyrate atrophy of the retina: inborn error of L-ornithin:2-oxoacid aminotransferase.
Topics: Adolescent; Female; Heterozygote; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Pedigree; Retinal Degeneration; Transaminases | 1978 |
Ornithine ketoacid transaminase deficiency in gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Atrophy; Cells, Cultured; Child; Choroid; Female; Humans; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Pyridoxal Phosphate; Retinal Degeneration; Skin; Syndrome; Transaminases | 1978 |
Hyperornithinemia and gyrate atrophy of the choroid and retina.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Atrophy; Child; Choroid; Female; Glutamates; Humans; Male; Middle Aged; Mitochondria, Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Pedigree; Retinal Degeneration; Syndrome; Uveal Diseases | 1978 |
Ocular and biochemical abnormalities in gyrate atrophy of the choroid and retina.
Topics: Administration, Oral; Adolescent; Adult; Amino Acids; Atrophy; Child; Choroid; Dark Adaptation; Electroretinography; Fibroblasts; Fluorescein Angiography; Humans; Myopia; Ornithine; Ornithine-Oxo-Acid Transaminase; Pyridoxine; Retina; Retinal Degeneration; Visual Fields | 1978 |
Gyrate atrophy of the choroid and retina with hyperornithinemia.
Topics: Adult; Choroid; Humans; Male; Metabolism, Inborn Errors; Ornithine; Pedigree; Retinal Degeneration; Syndrome | 1975 |
Plasma amino-acids in hereditary retinal disease. Ornithine, lysine, and taurine.
Topics: Adolescent; Adult; Amino Acids; Atrophy; Child; Female; Humans; Lysine; Male; Middle Aged; Ornithine; Retinal Degeneration; Taurine | 1976 |
[Retinal degeneration after intravitreal injection of ornithine. 2. Late change after administration].
Topics: Animals; Atrophy; Choroid; Injections; Macaca fascicularis; Ornithine; Retina; Retinal Degeneration; Time Factors; Vitreous Body | 1992 |
Gyrate atrophy of the choroid and retina. Long-term reduction of ornithine slows retinal degeneration.
Topics: Adult; Arginine; Child; Child, Preschool; Female; Follow-Up Studies; Fundus Oculi; Genetic Variation; Gyrate Atrophy; Humans; Infant; Longitudinal Studies; Male; Middle Aged; Ornithine; Ornithine-Oxo-Acid Transaminase; Retinal Degeneration; Treatment Outcome | 1991 |
[Retinal degeneration after intravitreal injection of ornithine. 1. Early change after administration].
Topics: Animals; Injections; Macaca fascicularis; Ornithine; Pigment Epithelium of Eye; Retinal Degeneration; Vitreous Body | 1990 |
Conversion of glutamate to ornithine and proline: pyrroline-5-carboxylate, a possible modulator of arginine requirements.
Topics: Amino Acids; Animals; Arginine; Biotransformation; Glutamates; Glutamic Acid; Humans; Intestinal Mucosa; Kidney; Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Proline; Proline Oxidase; Pyrroles; Retinal Degeneration; Spleen | 1985 |
Gyrate atrophy of the choroid and retina: 15 Japanese patients.
Topics: Adolescent; Adult; Child; Choroid; Female; Humans; Japan; Male; Middle Aged; Myopia; Ornithine; Refractive Errors; Retinal Degeneration; Uveal Diseases | 1986 |
Raised plasma-ornithine and gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Aqueous Humor; Atrophy; Child; Choroid; Electroretinography; Eye Diseases; Female; Fundus Oculi; Humans; Male; Middle Aged; Ornithine; Retina; Retinal Degeneration; Syndrome; Transaminases | 1973 |