ornithine and Metabolic Diseases

ornithine has been researched along with Metabolic Diseases in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19903 (50.00)18.7374
1990's0 (0.00)18.2507
2000's1 (16.67)29.6817
2010's1 (16.67)24.3611
2020's1 (16.67)2.80

Authors

AuthorsStudies
Hoeks, M; Huigen, M; IJzermans, T; Nijenhuis, T; Rennings, A; van der Meijden, W1
J, J; K N, S; Sivashanmugam, M; V, U1
ROBSON, EB; ROSE, GA1
AVERY, GB; CONE, TE; FLEMING, WH; MORGAN, RI1
Andrade, D; Camacho, JA; Cederbaum, SD; Derbeneva, O; Mardach, R; Qu, Y; Rioseco-Camacho, N; Ruiz-Pesini, E; Zaldivar, F1
Goodwin, JF1

Reviews

1 review(s) available for ornithine and Metabolic Diseases

ArticleYear
Ornithine and its role in metabolic diseases: An appraisal.
    Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie, 2017, Volume: 86

    Topics: Animals; Humans; Metabolic Diseases; Ornithine; Polyamines; Proline; Protein Binding; Protein Structure, Secondary

2017

Other Studies

5 other study(ies) available for ornithine and Metabolic Diseases

ArticleYear
Improving a Rare Metabolic Disorder Through Kidney Transplantation: A Case Report of a Patient With Lysinuric Protein Intolerance.
    American journal of kidney diseases : the official journal of the National Kidney Foundation, 2023, Volume: 81, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Transport System y+L; Arginine; Humans; Kidney Transplantation; Lysine; Metabolic Diseases; Ornithine

2023
The effect of intravenous lysine on the renal clearances of cystine, arginine and ornithine in normal subjects, in patients with cystinuria and Fanconi syndrome and in their relatives.
    Clinical science, 1957, Volume: 16, Issue:1

    Topics: Amino Acids; Arginine; Cystine; Cystinuria; Fanconi Syndrome; Humans; Lysine; Metabolic Diseases; Ornithine

1957
GASTROINTESTINAL MALABSORPTION ASSOCIATED WITH CYSTINURIA. REPORT OF A CASE IN A NEGRO.
    Pediatrics, 1963, Volume: 32

    Topics: Adolescent; Anemia; Anemia, Hypochromic; Arginine; Black People; Celiac Disease; Cystine; Cystinuria; Emaciation; Humans; Lysine; Metabolic Diseases; Ornithine; Phosphorus Metabolism Disorders; Proteins; Rickets

1963
Clinical and functional characterization of a human ORNT1 mutation (T32R) in the hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome.
    Pediatric research, 2006, Volume: 60, Issue:4

    Topics: Adolescent; Adult; Amino Acid Transport Systems, Basic; Child; Citrullinemia; DNA, Mitochondrial; Female; Haplotypes; Humans; Hyperammonemia; Male; Metabolic Diseases; Mitochondrial Membrane Transport Proteins; Mutation; Ornithine; Pedigree; Phenotype; Polymorphism, Genetic; Proteins; RNA, Messenger; Syndrome

2006
Spectrophotometry of proline in plasma and urine.
    Clinical chemistry, 1972, Volume: 18, Issue:5

    Topics: Amino Acids; Benzene; Chemical Phenomena; Chemistry; Creatinine; Evaluation Studies as Topic; Filtration; Humans; Hydrolysis; Hydroxyproline; Indenes; Indicators and Reagents; Infant; Ketones; Malabsorption Syndromes; Metabolic Diseases; Methods; Nitrites; Ornithine; Proline; Proteins; Spectrophotometry; Ultraviolet Rays

1972