ornithine and Ataxia

ornithine has been researched along with Ataxia in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19906 (85.71)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (14.29)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Carrillo, NR; Giulivi, C; Hagerman, RJ; Napoli, E; Rogawski, M; Schneider, A; Tassone, F; Trivedi, A; Wang, JY1
DEHEVESY, G; HAMBRAEUS, L1
Brenton, DP; Cusworth, DC; Hartley, S; Kuzemko, JA; Lumley, S1
Pollitt, R; Wright, T1
Breglia, RJ; Jarowski, CI; Ward, CO1
Greer, M; Sprinkle, T; Williams, CM1
Efron, ML; Moser, HW; Shih, VE1

Trials

1 trial(s) available for ornithine and Ataxia

ArticleYear
Allopregnanolone Treatment Improves Plasma Metabolomic Profile Associated with GABA Metabolism in Fragile X-Associated Tremor/Ataxia Syndrome: a Pilot Study.
    Molecular neurobiology, 2019, Volume: 56, Issue:5

    Topics: Aged; Anxiety; Ataxia; Depression; Energy Metabolism; Fragile X Syndrome; gamma-Aminobutyric Acid; Humans; Male; Metabolomics; Middle Aged; Mitochondria; Ornithine; Oxidative Stress; Pilot Projects; Pregnanolone; Tremor

2019

Other Studies

6 other study(ies) available for ornithine and Ataxia

ArticleYear
CYSTINURIA IN SWEDEN. VIII. A CASE OF COELIAC DISEASE ASSOCIATED WITH CYSTINE-LYSINURIA.
    Acta paediatrica, 1964, Volume: 53

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Ataxia; Celiac Disease; Chromatography; Creatine; Creatinine; Cystinuria; Electrophoresis; Glucose Tolerance Test; Humans; Infant; Intestine, Small; Intestines; Lysine; Muscle Spasticity; Ornithine; Proteins; Psychomotor Disorders; Renal Aminoacidurias; Sweden; Urine; Vitamin A; Xylose

1964
Argininosuccinicaciduria: clinical, metabolic and dietary study.
    Journal of mental deficiency research, 1974, Volume: 18, Issue:0

    Topics: Affective Symptoms; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Ataxia; Child; Citrulline; Dietary Proteins; Electroencephalography; Epilepsy; Female; Humans; Intellectual Disability; Intelligence Tests; Male; Ornithine; Phenobarbital; Seizures; Succinates; Tremor

1974
Psychomotor retardation, epileptic and stuporous attacks, irritability and ataxia associated with ammonia intoxication, high blood ornithine levels and increased homocitruline in the urine.
    Proceedings of the Royal Society of Medicine, 1973, Volume: 66, Issue:3

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Ataxia; Citrulline; Epilepsy; Female; Humans; Ornithine; Paralysis; Psychomotor Disorders

1973
Effect of selected amino acids on ethanol toxicity in rats.
    Journal of pharmaceutical sciences, 1973, Volume: 62, Issue:1

    Topics: Administration, Oral; Alcoholic Intoxication; Amino Acids; Animals; Arginine; Ataxia; Central Nervous System; Drug Interactions; Ethanol; Female; Glycine; Humans; Hydrogen-Ion Concentration; Lethal Dose 50; Lysine; Male; Ornithine; Rats; Sleep; Time Factors

1973
Detection of argininosuccinic aciduria by gas chromatography.
    Clinica chimica acta; international journal of clinical chemistry, 1969, Volume: 23, Issue:1

    Topics: Arginine; Aspartic Acid; Ataxia; Chemical Precipitation; Chromatography, Gas; Epilepsy; Esters; Humans; Hydrogen-Ion Concentration; Intellectual Disability; Liver Diseases; Metabolism, Inborn Errors; Methods; Ornithine; Spectrum Analysis; Succinates

1969
Hyperornithinemia, hyperammonemia, and homocitrullinuria. A new disorder of amino acid metabolism associated with myoclonic seizures and mental retardation.
    American journal of diseases of children (1960), 1969, Volume: 117, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ataxia; Child, Preschool; Citrulline; Diet Therapy; Humans; Intellectual Disability; Lysine; Male; Myoclonus; Ornithine; Ornithine Carbamoyltransferase; Seizures

1969