Page last updated: 2024-08-24

nojirimycin and Gaucher Disease

nojirimycin has been researched along with Gaucher Disease in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (50.00)29.6817
2010's1 (50.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Aguilar-Moncayo, M; García Fernández, JM; García-Moreno, MI; Higaki, K; Luan, Z; Ninomiya, H; Ohno, K; Ortiz Mellet, C; Suzuki, Y1
Aguilar-Moncayo, M; García Fernández, JM; García-Moreno, MI; Higaki, K; Li, L; Luan, Z; Nanba, E; Ninomiya, H; Ohno, K; Ortiz Mellet, C; Suzuki, Y1

Other Studies

2 other study(ies) available for nojirimycin and Gaucher Disease

ArticleYear
Chaperone activity of bicyclic nojirimycin analogues for Gaucher mutations in comparison with N-(n-nonyl)deoxynojirimycin.
    Chembiochem : a European journal of chemical biology, 2009, Nov-23, Volume: 10, Issue:17

    Topics: 1-Deoxynojirimycin; Animals; Cells, Cultured; Enzyme Inhibitors; Fibroblasts; Gaucher Disease; Glucosylceramidase; Humans; Imino Sugars; Molecular Chaperones; Molecular Structure; Mutation; Protein Conformation; Protein Folding

2009
A Fluorescent sp2-iminosugar with pharmacological chaperone activity for gaucher disease: synthesis and intracellular distribution studies.
    Chembiochem : a European journal of chemical biology, 2010, Nov-22, Volume: 11, Issue:17

    Topics: 1-Deoxynojirimycin; Animals; Cell Line, Tumor; Cells, Cultured; Enzyme Stability; Fibroblasts; Fluorescence; Gaucher Disease; Glucosylceramidase; Hot Temperature; Humans; Hydrogen-Ion Concentration; Immunoblotting; Intracellular Space; Lysosomes; Microscopy, Confocal; Models, Chemical; Molecular Chaperones; Molecular Structure; Mutation

2010