Page last updated: 2024-08-17

nadp and Luft Disease

nadp has been researched along with Luft Disease in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (20.00)29.6817
2010's4 (80.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Amaral, AU; Busanello, EN; Gasparotto, J; Gelain, DP; Gregersen, N; Tonin, AM; Wajner, M1
Li, F; Meng, R; Sun, X; Wang, J; Yang, Z; Zhang, A1
Amaral, AU; Cecatto, C; Hickmann, FH; Rodrigues, MD; Wajner, M1
Amaral, AU; Cecatto, C; da Silva, JC; Godoy, KDS; Wajner, M1
Amiel, J; Chrétien, D; Christoph von Kleist-Retzow, J; Cormier-Daire, V; Dommergues, M; Dumez, Y; Faivre, L; Munnich, A; Rötig, A; Rustin, P; Saudubray, JM1

Other Studies

5 other study(ies) available for nadp and Luft Disease

ArticleYear
Mitochondrial bioenergetics deregulation caused by long-chain 3-hydroxy fatty acids accumulating in LCHAD and MTP deficiencies in rat brain: a possible role of mPTP opening as a pathomechanism in these disorders?
    Biochimica et biophysica acta, 2014, Volume: 1842, Issue:9

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acyl-CoA Dehydrogenase, Long-Chain; Adenosine Triphosphate; Animals; Calcium; Cardiomyopathies; Cerebral Cortex; Cytochromes c; Energy Metabolism; Homeostasis; Hydrogen Peroxide; Lauric Acids; Lipid Metabolism, Inborn Errors; Membrane Potential, Mitochondrial; Mitochondria; Mitochondrial Membrane Transport Proteins; Mitochondrial Myopathies; Mitochondrial Permeability Transition Pore; Mitochondrial Swelling; Mitochondrial Trifunctional Protein; Myristic Acids; NADP; Nervous System Diseases; Oxidants; Palmitic Acids; Rats; Rats, Wistar; Rhabdomyolysis

2014
[The changes of LCHAD in preeclampsia with different clinical features and the correlation with NADPH P47-phox, p38MAPK-α, COX-2 and serum FFA and TG].
    Zhonghua fu chan ke za zhi, 2015, Volume: 50, Issue:2

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Cardiomyopathies; Cohort Studies; Cyclooxygenase 2; Fatty Acids; Female; Humans; Hypertension; Lipid Metabolism, Inborn Errors; Mitochondrial Myopathies; Mitochondrial Trifunctional Protein; NADP; NADPH Oxidases; Nervous System Diseases; Oxidation-Reduction; Oxidative Stress; p38 Mitogen-Activated Protein Kinases; Placenta; Pre-Eclampsia; Pregnancy; Pregnancy Trimester, Third; Prospective Studies; Rhabdomyolysis; RNA, Messenger; Triglycerides

2015
Deregulation of mitochondrial functions provoked by long-chain fatty acid accumulating in long-chain 3-hydroxyacyl-CoA dehydrogenase and mitochondrial permeability transition deficiencies in rat heart--mitochondrial permeability transition pore opening as
    The FEBS journal, 2015, Volume: 282, Issue:24

    Topics: Adenosine Triphosphate; Animals; Calcium Channel Blockers; Calcium Signaling; Cardiomyopathies; Cell Membrane Permeability; Enzyme Inhibitors; Humans; Lipid Metabolism, Inborn Errors; Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase; Membrane Potential, Mitochondrial; Mitochondria, Heart; Mitochondrial Membrane Transport Proteins; Mitochondrial Membranes; Mitochondrial Myopathies; Mitochondrial Permeability Transition Pore; Mitochondrial Swelling; Mitochondrial Trifunctional Protein; Myristic Acids; NADP; Nervous System Diseases; Organ Specificity; Oxidative Phosphorylation; Palmitic Acids; Rats, Wistar; Rhabdomyolysis

2015
Disturbance of mitochondrial functions provoked by the major long-chain 3-hydroxylated fatty acids accumulating in MTP and LCHAD deficiencies in skeletal muscle.
    Toxicology in vitro : an international journal published in association with BIBRA, 2016, Volume: 36

    Topics: Animals; Calcium; Cardiomyopathies; Lipid Metabolism, Inborn Errors; Membrane Potential, Mitochondrial; Mitochondria, Muscle; Mitochondrial Myopathies; Mitochondrial Trifunctional Protein; Muscle, Skeletal; Myristic Acids; NADP; Nervous System Diseases; Oxygen Consumption; Palmitic Acids; Rats, Wistar; Rhabdomyolysis

2016
Determination of enzyme activities for prenatal diagnosis of respiratory chain deficiency.
    Prenatal diagnosis, 2000, Volume: 20, Issue:9

    Topics: Adult; Amniocentesis; Chorionic Villi Sampling; Consanguinity; Electron Transport; Female; Fetal Diseases; Fibroblasts; Humans; Male; Mitochondria; Mitochondrial Myopathies; NADP; Pedigree; Pregnancy; Prenatal Diagnosis; Skin

2000