Page last updated: 2024-08-17

nadp and Adult Refsum Disease

nadp has been researched along with Adult Refsum Disease in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19902 (40.00)18.7374
1990's0 (0.00)18.2507
2000's2 (40.00)29.6817
2010's1 (20.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Filho, CS; Grings, M; Knebel, LA; Leipnitz, G; Moura, AP; Tonin, AM; Wajner, M; Zanatta, A1
Duran, M; Komen, JC; Wanders, RJ2
Stumpf, PK1
Avigan, J; Steinberg, D; Tsai, SC1

Reviews

1 review(s) available for nadp and Adult Refsum Disease

ArticleYear
Phytoenzyme systems as models for an understanding of general metabolic pathways.
    The Journal of experimental zoology, 1975, Volume: 194, Issue:1

    Topics: Acetyl Coenzyme A; Alanine; Animals; Biotin; Carboxy-Lyases; Carrier Proteins; Chloroplasts; Coenzyme A; Fatty Acid Desaturases; Fatty Acids; Fatty Acids, Nonesterified; Humans; Linolenic Acids; Lipids; NADP; Oleic Acids; Oxidation-Reduction; Photosynthesis; Plants; Propionates; Refsum Disease; Stearic Acids

1975

Other Studies

4 other study(ies) available for nadp and Adult Refsum Disease

ArticleYear
Phytanic acid disturbs mitochondrial homeostasis in heart of young rats: a possible pathomechanism of cardiomyopathy in Refsum disease.
    Molecular and cellular biochemistry, 2012, Volume: 366, Issue:1-2

    Topics: Animals; Antioxidants; Cardiomyopathies; Chromans; Electron Transport Chain Complex Proteins; Glutathione; Homeostasis; In Vitro Techniques; Male; Membrane Potential, Mitochondrial; Mitochondria, Heart; Myocardium; NADP; NG-Nitroarginine Methyl Ester; Nitric Oxide Synthase; Oxidation-Reduction; Oxidative Stress; Phytanic Acid; Protein Carbonylation; Rats; Rats, Wistar; Refsum Disease; Thiobarbituric Acid Reactive Substances

2012
Omega-hydroxylation of phytanic acid in rat liver microsomes: implications for Refsum disease.
    Journal of lipid research, 2004, Volume: 45, Issue:7

    Topics: Animals; Catalysis; Cytochrome P-450 Enzyme System; Hydroxylation; Male; Microsomes, Liver; Mixed Function Oxygenases; NADP; Phytanic Acid; Protein Isoforms; Rats; Rats, Wistar; Refsum Disease

2004
Characterization of phytanic acid omega-hydroxylation in human liver microsomes.
    Molecular genetics and metabolism, 2005, Volume: 85, Issue:3

    Topics: Adult; Aldehyde Oxidoreductases; Animals; Catalysis; Cytochrome P-450 Enzyme System; Humans; Hydroxylation; Microsomes, Liver; NADP; Oxidation-Reduction; Phytanic Acid; Rats; Refsum Disease

2005
Studies on the alpha oxidation of phytanic acid by rat liver mitochondria.
    The Journal of biological chemistry, 1969, May-25, Volume: 244, Issue:10

    Topics: Adenosine Triphosphate; Animals; Ascorbic Acid; Carbon Dioxide; Carbon Isotopes; Chromatography, Gas; Fatty Acids; Iron; Mitochondria, Liver; NAD; NADP; Rats; Refsum Disease; Spectrum Analysis; Stimulation, Chemical

1969