Page last updated: 2024-08-22

molybdenum and Hepatolenticular Degeneration

molybdenum has been researched along with Hepatolenticular Degeneration in 83 studies

Research

Studies (83)

Timeframe	Studies, this research(%)	All Research%
pre-1990	9 (10.84)	18.7374
1990's	23 (27.71)	18.2507
2000's	31 (37.35)	29.6817
2010's	18 (21.69)	24.3611
2020's	2 (2.41)	2.80

Authors

Authors	Studies
Auger, C; Cardona, I; De Fabregues, O; Palasí, A; Quintana, M; Vargas, V; Viñas, J	1
Aggarwal, A; Bhatt, M	1
Członkowska, A; Litwin, T	1
Rupp, C; Stremmel, W; Weiss, KH	1
Houwen, R	1
Pfister, ED	1
Boyling, L; Plitz, T	1
Członkowska, A; Ferenci, P; Hedera, P; Weiss, KH	1
Stremmel, W	1
Członkowska, A; Dusek, P; Ferenci, P; Litwin, T; Lutsenko, S; Medici, V; Rybakowski, JK; Schilsky, ML; Weiss, KH	1
Appenzeller-Herzog, C; Ewald, H; Heeres, MLS; Houwen, RHJ; Mathes, T; Weiss, KH	1
Purchase, R	1
Brůha, R; Mareček, Z	1
Stremmel, W; Weiss, KH	1
Chen, DB; Feng, L; Hou, HM; Li, XH; Liu, JX; Wei, LT; Wu, C; Zhang, JW	1
Chen, C; Li, WJ; Wang, XP; Yang, RM; You, ZF	1
Buszewski, B; Jurowska, A; Jurowski, K; Kalenik, T; Piekoszewski, W; Szklarzewicz, J	1
Brewer, GJ	6
George, GN; Lichtmannegger, J; Pickering, IJ; Summer, KH; Webb, S; Zhang, L	1
Brewer, GJ; Dick, R; Hou, G	1
Khan, G; Merajver, S	1
Gilman, S; Pestana Knight, EM; Selwa, L	1
Askari, F; Brewer, GJ; Carlson, M; Dick, RB; Fink, JK; Kluin, KJ; Lorincz, MT; Sitterly, J	1
Anan, Y; Miyayama, T; Ogra, Y	1
Askari, F; Brewer, GJ; Burke, JF; Dayalu, P; Lorincz, MT; Nan, B	1
Suttle, NF	1
Pérez-Aguilar, F	1
Gailer, J; George, GN; Harris, HH; Klein, D; Lichtmannegger, J; Pickering, IJ; Summer, KH	1
Askari, F; Brewer, GJ; Carlson, M; Dick, RB; Fink, JK; Hedera, P; Kluin, KJ; Sitterly, J	1
Brechbiel, M; Camphausen, K; Sproull, M	1
El-Youssef, M	1
Al-Mateen, M; Brewer, GJ; Carlson, MD	1
Szalay, F	1
Arora, U; Finckh, M; Heinzmann, U; Klein, D; Lichtmannegger, J; Summer, KH	1
Hayashi, H; Suzuki, R; Wakusawa, S	1
Crone, NE; Jinnah, HA; Reich, SG	1
Algayres, JP; Amezyane, T; Béchade, D; Coutant, G; Desramé, J; Le Berre, JP; Lecoules, S	1
Askari, F; Brewer, GJ; Carlson, M; Dick, RB; Fink, JK; Hedera, P; Kluin, KJ; Lorincz, MT; Moretti, P; Schilsky, M; Sitterly, J; Tankanow, R	1
Bigotto, MA; D'Incà, R; Dal Pont, E; Martines, D; Medici, V; Sturniolo, GC; Trevisan, CP	1
Medici, V; Rossaro, L; Sturniolo, GC	1
Scheinberg, IH; Sternlieb, I	1
Aisen, A; Brewer, GJ; Dick, RD; Fink, JK; Johnson, V; Kluin, K; Wang, Y; Yuzbasiyan-Gurkan, V	1
Ogra, Y; Ohmichi, M; Suzuki, KT	3
Schilsky, ML	2
Brewer, GJ; Brunberg, JA; Dick, RD; Fink, JK; Johnson, V; Kluin, KJ	1
Brewer, GJ; Burnstine, MA; Esmaeli, B; Johnson, V; Martonyi, CL; Sugar, A	1
Lyndon, B; Walter, G	1
Grigg, A; Karunajeewa, H; Metz, J; Wall, A	1
Aoki, T	1
Ogra, Y; Suzuki, KT	1
Ikeda, T; Lai, YR; Sugawara, C; Sugawara, N	1
Lai, YR; Sugawara, C; Sugawara, N	1
Komada, Y; Ogra, Y; Suzuki, KT	1
Chikusa, H; Ogra, Y; Suzuki, KT	1
Ogura, Y; Suzuki, KT	1
Cherian, MG; Czachor, JD; Koropatnick, J	1
Brewer, GJ; Cohen, EJ; Laibson, PR; Liu, M	1
Bronstein, JM; Subramanian, I; Vanek, ZF	1
Reinhold, JG	1
Cramarossa, L; D'Angelo, D; D'Ascanio, I; Ferri, GB; Piane, E	1
Lamand, M; Mason, J; McQuaid, A	1
Walshe, JM	1
Brewer, GJ; Dick, RD; Kluin, KJ; Tankanow, R; Young, AB; Yuzbasiyan-Gurkin, V	1
Mason, J; McQuaid, A	1
Danks, DM	2
Bartsch, R; Klein, D; Summer, KH	1
Mason, J; McQuaid, A; Pheiffer, H	1
Brewer, GJ; Yuzbasiyan-Gurkan, V	1
Mason, J	1
Harper, PL; Walshe, JM	1
Seelig, MS	1
Oberleas, D; Prasad, AS; Rajasekaran, G	1
Loĭko, EA	1

Reviews

38 review(s) available for molybdenum and Hepatolenticular Degeneration

Article	Year
Wilson disease. Current opinion in neurology, 2020, Volume: 33, Issue:4 Topics: Clinical Trials as Topic; Copper; Copper-Transporting ATPases; Hepatolenticular Degeneration; Humans; Molybdenum; Phenotype	2020
Wilson disease - currently used anticopper therapy. Handbook of clinical neurology, 2017, Volume: 142 Topics: Chelating Agents; Copper; Enzyme Inhibitors; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Prospective Studies; Trientine	2017
Novel perspectives on Wilson disease treatment. Handbook of clinical neurology, 2017, Volume: 142 Topics: Animals; Chelating Agents; Copper; Genetic Therapy; Hepatolenticular Degeneration; Humans; Molybdenum	2017
[Wilson's disease : What has been confirmed in diagnostic and therapy?] Der Internist, 2017, Volume: 58, Issue:12 Topics: Chelating Agents; Chromosome Aberrations; Copper; Diet Therapy; Genes, Recessive; Hepatolenticular Degeneration; Humans; Liver Transplantation; Molybdenum; Penicillamine; Phenotype; Zinc	2017
WTX101 - an investigational drug for the treatment of Wilson disease. Expert opinion on investigational drugs, 2018, Volume: 27, Issue:6 Topics: Administration, Oral; Animals; Chelating Agents; Copper; Drug Design; Drugs, Investigational; Hepatolenticular Degeneration; Humans; Molybdenum	2018
Wilson disease. Nature reviews. Disease primers, 2018, 09-06, Volume: 4, Issue:1 Topics: Chelating Agents; Copper; Dietary Supplements; Hepatolenticular Degeneration; Humans; Molybdenum; Quality of Life	2018
Comparative effectiveness of common therapies for Wilson disease: A systematic review and meta-analysis of controlled studies. Liver international : official journal of the International Association for the Study of the Liver, 2019, Volume: 39, Issue:11 Topics: Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Liver; Molybdenum; Penicillamine; Randomized Controlled Trials as Topic; Trientine; Zinc	2019
The treatment of Wilson's disease, a rare genetic disorder of copper metabolism. Science progress, 2013, Volume: 96, Issue:Pt 1 Topics: Brain; Chelating Agents; Copper; Cornea; Dimercaprol; Drug Discovery; Hepatolenticular Degeneration; History, 20th Century; Humans; Liver; Molybdenum; Penicillamine; Rare Diseases; Trientine; Zinc Sulfate	2013
[Wilsons disease]. Vnitrni lekarstvi, 2013, Volume: 59, Issue:7 Topics: Adenosine Triphosphatases; Adult; Cation Transport Proteins; Chelating Agents; Copper; Copper-Transporting ATPases; Czech Republic; Female; Hepatolenticular Degeneration; Humans; Liver Cirrhosis; Liver Transplantation; Male; Molybdenum; Mutation; Penicillamine; Trientine; Zinc	2013
Clinical considerations for an effective medical therapy in Wilson's disease. Annals of the New York Academy of Sciences, 2014, Volume: 1315 Topics: Ceruloplasmin; Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Trientine; Zinc	2014
Current Drug Managements of Wilson's Disease: From West to East. Current neuropharmacology, 2016, Volume: 14, Issue:4 Topics: Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Medicine, Chinese Traditional; Molybdenum; Penicillamine; Succimer; Treatment Outcome; Trientine; Zinc	2016
Molybdenum Metallopharmaceuticals Candidate Compounds - The "Renaissance" of Molybdenum Metallodrugs? Current medicinal chemistry, 2016, Volume: 23, Issue:29 Topics: Animals; Atherosclerosis; Cell Cycle Checkpoints; Coordination Complexes; Hepatolenticular Degeneration; Humans; Huntington Disease; Molybdenum; Tungsten Compounds	2016
The risks of free copper in the body and the development of useful anticopper drugs. Current opinion in clinical nutrition and metabolic care, 2008, Volume: 11, Issue:6 Topics: Alzheimer Disease; Angiogenesis Inhibitors; Autoimmunity; Copper; Fibrosis; Hepatolenticular Degeneration; Humans; Inflammation; Molybdenum; Neurodegenerative Diseases; Penicillamine; Trientine	2008
Copper chelation in cancer therapy using tetrathiomolybdate: an evolving paradigm. Expert opinion on investigational drugs, 2009, Volume: 18, Issue:4 Topics: Animals; Antineoplastic Agents; Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Molybdenum; Neoplasms	2009
Zinc and tetrathiomolybdate for the treatment of Wilson's disease and the potential efficacy of anticopper therapy in a wide variety of diseases. Metallomics : integrated biometal science, 2009, Volume: 1, Issue:3 Topics: Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Molybdenum; Zinc	2009
Copper imbalances in ruminants and humans: unexpected common ground. Advances in nutrition (Bethesda, Md.), 2012, Sep-01, Volume: 3, Issue:5 Topics: Alzheimer Disease; Animals; Chelating Agents; Copper; Deficiency Diseases; Enzyme Inhibitors; Hepatolenticular Degeneration; Humans; Infections; Inflammation; Molybdenum; Neoplasms; Nutritional Requirements; Ruminants	2012
[Wilson's disease: physiopathological, clinical and therapeutic considerations]. Gastroenterologia y hepatologia, 2003, Volume: 26, Issue:1 Topics: Adenosine Triphosphatases; Adolescent; Adult; Basal Ganglia Diseases; Brain; Cation Transport Proteins; Ceruloplasmin; Chelating Agents; Chelation Therapy; Copper; Copper-Transporting ATPases; Descemet Membrane; Female; Genes, Recessive; Hepatitis, Chronic; Hepatolenticular Degeneration; Humans; Liver Transplantation; Male; Mental Disorders; Middle Aged; Molybdenum; Penicillamine; Pregnancy; Pregnancy Complications; Prognosis; Recombinant Fusion Proteins; Trientine; Zinc	2003
Antiangiogenic therapy through copper chelation. Expert opinion on therapeutic targets, 2003, Volume: 7, Issue:3 Topics: Angiogenesis Inhibitors; Animals; Chelating Agents; Chelation Therapy; Copper; Corneal Neovascularization; Cyclohexylamines; Hepatolenticular Degeneration; Humans; Molybdenum; Neoplasms; Neovascularization, Pathologic; Penicillamine; Pyridines; Rabbits; Trientine	2003
Wilson disease. Mayo Clinic proceedings, 2003, Volume: 78, Issue:9 Topics: Adenosine Triphosphatases; Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Liver Transplantation; Molybdenum; Penicillamine; Trientine; Zinc	2003
[Wilson disease in 2003]. Orvosi hetilap, 2003, Dec-14, Volume: 144, Issue:50 Topics: Adenosine Triphosphatases; Cation Transport Proteins; Chelating Agents; Copper; Copper-Transporting ATPases; Diagnosis, Differential; Family Planning Services; Genetic Counseling; Genotype; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Phenotype; Trientine; Zinc Acetate; Zinc Sulfate	2003
[Wilson's disease and its pharmacological treatment]. Yakugaku zasshi : Journal of the Pharmaceutical Society of Japan, 2004, Volume: 124, Issue:11 Topics: Adenosine Triphosphatases; Biomarkers; Cation Transport Proteins; Ceruloplasmin; Chelating Agents; Chelation Therapy; Copper; Copper-Transporting ATPases; Female; Hepatolenticular Degeneration; Humans; Iron; Male; Molecular Diagnostic Techniques; Molybdenum; Mutation; Penicillamine; Pregnancy; Pregnancy Outcome; Zinc Acetate	2004
Neurologically presenting Wilson's disease: epidemiology, pathophysiology and treatment. CNS drugs, 2005, Volume: 19, Issue:3 Topics: Behavior; Chelating Agents; Enzyme Inhibitors; Hepatolenticular Degeneration; Humans; Molybdenum; Nervous System Diseases; Penicillamine; Trientine; Zinc	2005
Novel therapeutic approaches to the treatment of Wilson's disease. Expert opinion on pharmacotherapy, 2006, Volume: 7, Issue:3 Topics: Chelating Agents; Child; Child, Preschool; Clinical Trials as Topic; Copper; Female; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Pregnancy; Pregnancy Complications; Zinc	2006
Wilson disease--a practical approach to diagnosis, treatment and follow-up. Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver, 2007, Volume: 39, Issue:7 Topics: Ceruloplasmin; Chelating Agents; Copper; Hepatolenticular Degeneration; Humans; Liver Transplantation; Molybdenum; Mutation; Penicillamine; Trace Elements; Treatment Outcome; Trientine; Zinc	2007
Practical recommendations and new therapies for Wilson's disease. Drugs, 1995, Volume: 50, Issue:2 Topics: Chelating Agents; Copper; Female; Hepatolenticular Degeneration; Humans; Liver; Metallothionein; Molybdenum; Penicillamine; Pregnancy; Trientine; Zinc	1995
Wilson disease: genetic basis of copper toxicity and natural history. Seminars in liver disease, 1996, Volume: 16, Issue:1 Topics: Adenosine Triphosphatases; Carrier Proteins; Cation Transport Proteins; Chelating Agents; Chelation Therapy; Chromosome Mapping; Copper; Copper-Transporting ATPases; Environment; Genetic Therapy; Genome, Human; Hepatitis; Hepatolenticular Degeneration; Humans; Liver Transplantation; Molybdenum; Mutation; Penicillamine; Risk Factors; Trientine; Zinc	1996
[Inborn errors of trace metals]. Ryoikibetsu shokogun shirizu, 1998, Issue:19 Pt 2 Topics: Copper; Hemochromatosis; Hepatolenticular Degeneration; Humans; Iron; Menkes Kinky Hair Syndrome; Metal Metabolism, Inborn Errors; Molybdenum; Zinc	1998
[Biological regulation of copper and selective removal of copper: therapy for Wilson disease and its molecular mechanism]. Yakugaku zasshi : Journal of the Pharmaceutical Society of Japan, 2000, Volume: 120, Issue:10 Topics: Adenosine Triphosphatases; Animals; Carrier Proteins; Cation Transport Proteins; Chelating Agents; Copper; Copper-Transporting ATPases; Disease Models, Animal; Hepatolenticular Degeneration; Humans; Liver; Metallothionein; Molybdenum; Rats; Rats, Inbred LEC; Recombinant Fusion Proteins	2000
Treatment of Wilson's disease: what are the relative roles of penicillamine, trientine, and zinc supplementation? Current gastroenterology reports, 2001, Volume: 3, Issue:1 Topics: Adenosine Triphosphatases; Chelating Agents; Drug Therapy, Combination; Female; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Pregnancy; Trientine; Zinc	2001
Copper control as an antiangiogenic anticancer therapy: lessons from treating Wilson's disease. Experimental biology and medicine (Maywood, N.J.), 2001, Volume: 226, Issue:7 Topics: Angiogenesis Inhibitors; Animals; Antineoplastic Agents; Copper; Hepatolenticular Degeneration; Humans; Molybdenum; Neoplasms; Zinc	2001
Diagnosis and treatment of Wilson's disease. Current neurology and neuroscience reports, 2002, Volume: 2, Issue:4 Topics: Chelating Agents; Copper; Dimercaprol; Enzyme Inhibitors; Female; Hepatolenticular Degeneration; Humans; Liver Transplantation; Male; Molybdenum; Penicillamine; Trientine; Zinc	2002
Trace elements--a selective survey. Clinical chemistry, 1975, Volume: 21, Issue:4 Topics: Adult; Child; Chromium; Cobalt; Copper; Erythrocytes; Fluorine; Hepatolenticular Degeneration; Humans; Iodine; Iron; Magnesium; Microchemistry; Molybdenum; Nickel; Nutritional Physiological Phenomena; Protein Binding; Selenium; Silicon; Tin; Trace Elements; Vanadium; Zinc	1975
[Wilson's disease]. Recenti progressi in medicina, 1992, Volume: 83, Issue:5 Topics: Acetates; Acetic Acid; Adult; Diagnosis, Differential; Diet; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Penicillamine; Pyridoxine; Sulfates; Trientine; Zinc; Zinc Sulfate	1992
Copper and liver disease. European journal of pediatrics, 1991, Volume: 150, Issue:3 Topics: Adult; Chelating Agents; Child; Cholestasis; Copper; Hepatolenticular Degeneration; Humans; Infant; Infant, Newborn; Liver Diseases; Molybdenum; Penicillamine; Zinc	1991
Wilson's disease: an update, with emphasis on new approaches to treatment. Digestive diseases (Basel, Switzerland), 1989, Volume: 7, Issue:4 Topics: Copper; Female; Hepatolenticular Degeneration; Humans; Molybdenum; Penicillamine; Pregnancy; Trientine; Zinc	1989
Thiomolybdates: mediators of molybdenum toxicity and enzyme inhibitors. Toxicology, 1986, Dec-15, Volume: 42, Issue:2-3 Topics: Animals; Copper; Enzyme Inhibitors; Hepatolenticular Degeneration; Humans; Liver; Molybdenum	1986
Inborn errors of trace element metabolism. Clinics in endocrinology and metabolism, 1985, Volume: 14, Issue:3 Topics: Acrodermatitis; Animals; Breast Feeding; Copper; Cutis Laxa; Disease Models, Animal; Female; Hepatolenticular Degeneration; Humans; Infant, Newborn; Infant, Premature, Diseases; Liver; Manganese; Menkes Kinky Hair Syndrome; Metabolism, Inborn Errors; Molybdenum; Pregnancy; Prenatal Diagnosis; Trace Elements; Zinc	1985
Proposed role of copper-molybdenum interaction in iron-deficiency and iron -storage diseases. The American journal of clinical nutrition, 1973, Volume: 26, Issue:6 Topics: Adult; Anemia; Anemia, Hemolytic; Anemia, Hypochromic; Anemia, Sickle Cell; Animals; Copper; Deficiency Diseases; Female; Hemoglobins; Hepatolenticular Degeneration; Humans; Infant; Infant Nutrition Disorders; Infant, Newborn; Infant, Premature, Diseases; Iron; Liver; Metabolic Diseases; Molybdenum; Pregnancy; Pregnancy Complications, Hematologic	1973

Trials

3 trial(s) available for molybdenum and Hepatolenticular Degeneration

Article	Year
Treatment of Wilson disease with ammonium tetrathiomolybdate: III. Initial therapy in a total of 55 neurologically affected patients and follow-up with zinc therapy. Archives of neurology, 2003, Volume: 60, Issue:3 Topics: Adult; Child; Enzyme Inhibitors; Female; Follow-Up Studies; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Nervous System Diseases; Neurologic Examination; Treatment Outcome; Zinc	2003
Treatment of Wilson disease with ammonium tetrathiomolybdate: IV. Comparison of tetrathiomolybdate and trientine in a double-blind study of treatment of the neurologic presentation of Wilson disease. Archives of neurology, 2006, Volume: 63, Issue:4 Topics: Adolescent; Adult; Anemia; Chelating Agents; Copper; Dose-Response Relationship, Drug; Double-Blind Method; Drug Administration Schedule; Female; Hepatolenticular Degeneration; Humans; Length of Stay; Male; Middle Aged; Molybdenum; Serum Albumin; Speech; Speech Disorders; Treatment Outcome; Trientine; Zinc	2006
Treatment of Wilson disease with ammonium tetrathiomolybdate. II. Initial therapy in 33 neurologically affected patients and follow-up with zinc therapy. Archives of neurology, 1996, Volume: 53, Issue:10 Topics: Adolescent; Adult; Female; Follow-Up Studies; Hepatolenticular Degeneration; Humans; Liver; Male; Molybdenum; Nervous System; Neurologic Examination; Speech-Language Pathology; Time Factors; Treatment Outcome; Zinc	1996

Other Studies

42 other study(ies) available for molybdenum and Hepatolenticular Degeneration

Article	Year
Ammonium tetrathiomolybdate in the decoppering phase treatment of Wilson's disease with neurological symptoms: A case series. Brain and behavior, 2020, Volume: 10, Issue:5 Topics: Brain; Hepatolenticular Degeneration; Humans; Longitudinal Studies; Magnetic Resonance Imaging; Molybdenum	2020
Bis-choline tetrathiomolybdate for Wilson's disease. The lancet. Gastroenterology & hepatology, 2017, Volume: 2, Issue:12 Topics: Choline; Copper; Hepatolenticular Degeneration; Humans; Molybdenum	2017
Metabolic disposition of WTX101 (bis-choline tetrathiomolybdate) in a rat model of Wilson disease. Xenobiotica; the fate of foreign compounds in biological systems, 2019, Volume: 49, Issue:3 Topics: Animals; Bile; Biological Transport; Chelating Agents; Copper; Feces; Hepatolenticular Degeneration; Molybdenum; Rats; Urine	2019
Bis-choline Tetrathiomolybdate as Old Drug in a New Design for Wilson's Disease: Good for Brain and Liver? Hepatology (Baltimore, Md.), 2019, Volume: 69, Issue:2 Topics: Brain; Choline; Hepatolenticular Degeneration; Humans; Liver; Molybdenum	2019
Effects of tetrathiomolybdate and penicillamine on brain hydroxyl radical and free copper levels: a microdialysis study in vivo. Biochemical and biophysical research communications, 2015, Feb-27, Volume: 458, Issue:1 Topics: Animals; Brain; Chelating Agents; Copper; Corpus Striatum; Disease Models, Animal; Hepatolenticular Degeneration; Hydroxyl Radical; Mice, Inbred C57BL; Mice, Mutant Strains; Microdialysis; Molybdenum; Penicillamine	2015
Tracing copper-thiomolybdate complexes in a prospective treatment for Wilson's disease. Biochemistry, 2009, Feb-10, Volume: 48, Issue:5 Topics: Adenosine Triphosphatases; Animals; Cation Transport Proteins; Chelating Agents; Copper; Copper-Transporting ATPases; Disease Models, Animal; Hepatolenticular Degeneration; Kidney; Liver; Molybdenum; Prospective Studies; Rats; Rats, Inbred LEC; Rats, Mutant Strains	2009
Improvement in dissolution of liver fibrosis in an animal model by tetrathiomolybdate. Experimental biology and medicine (Maywood, N.J.), 2009, Volume: 234, Issue:6 Topics: Animals; Carbon Tetrachloride; Carbon Tetrachloride Poisoning; Copper; Female; Hepatolenticular Degeneration; Humans; Liver Cirrhosis, Experimental; Mice; Mice, Inbred BALB C; Molybdenum; Time Factors	2009
Status epilepticus in Wilson's disease. Epileptic disorders : international epilepsy journal with videotape, 2009, Volume: 11, Issue:2 Topics: Brain; Chelating Agents; Electroencephalography; Functional Laterality; Hepatolenticular Degeneration; Humans; Liver Cirrhosis; Magnetic Resonance Imaging; Male; Middle Aged; Molybdenum; Review Literature as Topic; Seizures; Status Epilepticus; Treatment Outcome	2009
Treatment of Wilson's disease with tetrathiomolybdate: V. Control of free copper by tetrathiomolybdate and a comparison with trientine. Translational research : the journal of laboratory and clinical medicine, 2009, Volume: 154, Issue:2 Topics: Chelating Agents; Clinical Trials as Topic; Copper; Double-Blind Method; Drug Administration Schedule; Hepatolenticular Degeneration; Humans; Molybdenum; Retrospective Studies; Trientine	2009
Effect of glutathione depletion on removal of copper from LEC rat livers by tetrathiomolybdate. Journal of inorganic biochemistry, 2010, Volume: 104, Issue:8 Topics: Animals; Buthionine Sulfoximine; Chelating Agents; Copper; Enzyme Inhibitors; Glutathione; Hepatolenticular Degeneration; Humans; Liver; Male; Metallothionein; Molybdenum; Oxidation-Reduction; Rats; Rats, Inbred LEC; Rats, Wistar; Time Factors	2010
Prognostic significance of neurologic examination findings in Wilson disease. Parkinsonism & related disorders, 2011, Volume: 17, Issue:7 Topics: Adult; Chelating Agents; Dystonia; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Neurologic Examination; Prognosis; Risk Factors; Tremor; Trientine; Zinc	2011
Tetrathiomolybdate causes formation of hepatic copper-molybdenum clusters in an animal model of Wilson's disease. Journal of the American Chemical Society, 2003, Feb-19, Volume: 125, Issue:7 Topics: Animals; Copper; Disease Models, Animal; Fourier Analysis; Hepatolenticular Degeneration; Humans; Liver; Lysosomes; Molecular Structure; Molybdenum; Rats; Rats, Inbred LEC; Spectrometry, X-Ray Emission; Sulfur	2003
Atypical childhood Wilson's disease. Pediatric neurology, 2004, Volume: 30, Issue:1 Topics: Child; Diagnosis, Differential; Female; Hepatolenticular Degeneration; Humans; Molybdenum	2004
Tetrathiomolybdate in the treatment of acute hepatitis in an animal model for Wilson disease. Journal of hepatology, 2004, Volume: 40, Issue:3 Topics: Acute Disease; Animals; Chelating Agents; Copper; Disease Models, Animal; Female; Hepatitis, Animal; Hepatolenticular Degeneration; Liver; Microscopy, Electron; Molybdenum; Rats; Rats, Inbred LEC; Rats, Long-Evans; Subcellular Fractions; Tissue Distribution	2004
Wilson's disease presenting with an unusual cough. Movement disorders : official journal of the Movement Disorder Society, 2005, Volume: 20, Issue:7 Topics: Adult; Chelating Agents; Cough; Hepatolenticular Degeneration; Humans; Magnetic Resonance Imaging; Male; Molybdenum; Putamen	2005
[Corneal and encephalic abnormalities]. La Revue de medecine interne, 2006, Volume: 27, Issue:8 Topics: Adult; Brain; Chelating Agents; Cornea; Enzyme Inhibitors; Forecasting; Hepatolenticular Degeneration; Humans; Magnetic Resonance Imaging; Male; Molybdenum	2006
Molybdenum. Monograph. Alternative medicine review : a journal of clinical therapeutic, 2006, Volume: 11, Issue:2 Topics: Animals; Coenzymes; Drug Hypersensitivity; Hepatolenticular Degeneration; Humans; Metalloproteins; Molybdenum; Molybdenum Cofactors; Neoplasms; Pteridines; Sulfites	2006
Adverse reaction after tetrathiomolybdate treatment for Wilson's disease: a case report. Movement disorders : official journal of the Movement Disorder Society, 2006, Volume: 21, Issue:11 Topics: Adult; Copper; Dose-Response Relationship, Drug; Enzyme Inhibitors; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Zinc	2006
Treatment of the neurologic manifestations of Wilson's disease. Archives of neurology, 1995, Volume: 52, Issue:4 Topics: Dimercaprol; Hepatolenticular Degeneration; Humans; Molybdenum; Nervous System Diseases; Penicillamine	1995
Treatment of Wilson's disease with ammonium tetrathiomolybdate. I. Initial therapy in 17 neurologically affected patients. Archives of neurology, 1994, Volume: 51, Issue:6 Topics: Adolescent; Adult; Copper; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Nervous System Diseases; Trichloroacetic Acid	1994
Mechanisms of selective copper removal by tetrathiomolybdate from metallothionein in LEC rats. Toxicology, 1996, Jan-08, Volume: 106, Issue:1-3 Topics: Animals; Cadmium; Copper; Female; Hepatolenticular Degeneration; Injections, Intraperitoneal; Kidney; Liver; Male; Mass Spectrometry; Metallothionein; Metals; Molybdenum; Rats; Rats, Mutant Strains; Zinc	1996
Systemic dispositions of molybdenum and copper after tetrathiomolybdate injection in LEC rats. Journal of trace elements in medicine and biology : organ of the Society for Minerals and Trace Elements (GMS), 1995, Volume: 9, Issue:3 Topics: Animals; Brain; Chelating Agents; Copper; Disease Models, Animal; Feces; Gastric Mucosa; Half-Life; Hepatolenticular Degeneration; Injections, Intraperitoneal; Intestinal Mucosa; Intestines; Kidney; Liver; Lung; Male; Mass Spectrometry; Molybdenum; Rats; Rats, Mutant Strains; Rats, Wistar; Spleen; Stomach; Testis; Tissue Distribution	1995
Molybdenum and copper kinetics after tetrathiomolybdate injection in LEC rats: specific role of serum albumin. Journal of trace elements in medicine and biology : organ of the Society for Minerals and Trace Elements (GMS), 1995, Volume: 9, Issue:3 Topics: Animals; Chelating Agents; Chromatography, High Pressure Liquid; Copper; Disease Models, Animal; Dose-Response Relationship, Drug; Half-Life; Hepatolenticular Degeneration; Injections, Intraperitoneal; Liver; Male; Mass Spectrometry; Molybdenum; Protein Binding; Rats; Rats, Mutant Strains; Rats, Wistar; Serum Albumin; Tissue Distribution	1995
Regression of Kayser-Fleischer rings during oral zinc therapy: correlation with systemic manifestations of Wilson's disease. Cornea, 1996, Volume: 15, Issue:6 Topics: Administration, Oral; Adolescent; Adult; Brain Diseases; Copper; Cornea; Corneal Diseases; Female; Hepatolenticular Degeneration; Humans; Magnetic Resonance Imaging; Male; Molybdenum; Prospective Studies; Zinc	1996
Depression in hepatolenticular degeneration (Wilson's disease). The Australian and New Zealand journal of psychiatry, 1997, Volume: 31, Issue:6 Topics: Adult; Antidepressive Agents, Tricyclic; Chelating Agents; Comorbidity; Depressive Disorder; Drug Therapy, Combination; Follow-Up Studies; Hepatolenticular Degeneration; Humans; Male; Mianserin; Molybdenum; Psychomotor Disorders; Sleep Initiation and Maintenance Disorders	1997
Cytopenias secondary to copper depletion complicating ammonium tetrathiomolybdate therapy for Wilson's disease. Australian and New Zealand journal of medicine, 1998, Volume: 28, Issue:2 Topics: Adult; Chelation Therapy; Copper; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Neutropenia; Thrombocytopenia	1998
Targeting of tetrathiomolybdate on the copper accumulating in the liver of LEC rats. Journal of inorganic biochemistry, 1998, Volume: 70, Issue:1 Topics: Animals; Biological Transport, Active; Ceruloplasmin; Copper; Disease Models, Animal; Female; Hepatolenticular Degeneration; Liver; Metallothionein; Molybdenum; Protein Binding; Rats; Rats, Mutant Strains	1998
The effect of subcutaneous tetrathiomolybdate administration on copper and iron metabolism, including their regional redistribution in the brain, in the Long-Evans Cinnamon rat, a bona fide animal model for Wilson's disease. Pharmacology & toxicology, 1999, Volume: 84, Issue:5 Topics: Animals; Brain; Ceruloplasmin; Copper; Disease Models, Animal; Enzyme-Linked Immunosorbent Assay; Ferritins; Hepatolenticular Degeneration; Injections, Subcutaneous; Iron; Kidney; Liver; Male; Metallothionein; Molybdenum; Rats; Rats, Inbred LEC	1999
Therapeutic effects of tetrathiomolybdate on hepatic dysfunction occurring naturally in Long-Evans Cinnamon (LEC) rats: a bona fide animal model for Wilson's disease. Research communications in molecular pathology and pharmacology, 1999, Volume: 103, Issue:2 Topics: Animals; Bile; Body Weight; Chelating Agents; Copper; Disease Models, Animal; Hepatolenticular Degeneration; Jaundice; Liver; Male; Molybdenum; Rats; Rats, Inbred F344; Rats, Long-Evans; Tissue Distribution	1999
Comparative mechanism and toxicity of tetra- and dithiomolybdates in the removal of copper. Journal of inorganic biochemistry, 1999, Jun-30, Volume: 75, Issue:3 Topics: Animals; Ceruloplasmin; Chelating Agents; Copper; Drug Stability; Hepatolenticular Degeneration; Humans; Liver; Molybdenum; Rats; Rats, Long-Evans	1999
Metabolic fate of the insoluble copper/tetrathiomolybdate complex formed in the liver of LEC rats with excess tetrathiomolybdate. Journal of inorganic biochemistry, 2000, Jan-30, Volume: 78, Issue:2 Topics: Animals; Copper; Disease Models, Animal; Feces; Half-Life; Hepatolenticular Degeneration; Liver; Molybdenum; Rats; Rats, Long-Evans	2000
Reduction of copper and metallothionein in toxic milk mice by tetrathiomolybdate, but not deferiprone. Journal of inorganic biochemistry, 2002, Jan-15, Volume: 88, Issue:2 Topics: Animals; Copper; Deferiprone; Disease Models, Animal; Hepatolenticular Degeneration; Metallothionein; Mice; Mice, Mutant Strains; Molybdenum; Phenotype; Pyridones	2002
Kayser-Fleischer ring as the presenting sign of Wilson disease. American journal of ophthalmology, 2002, Volume: 133, Issue:6 Topics: Adolescent; Biopsy; Ceruloplasmin; Copper; Corneal Diseases; Descemet Membrane; Drug Therapy, Combination; Female; Hepatolenticular Degeneration; Humans; Liver Function Tests; Molybdenum; Zinc Acetate	2002
The interactions of penicillamine with copper in vivo and the effect on hepatic metallothionein levels and copper/zinc distribution: the implications for Wilson's disease and arthritis therapy. The Journal of laboratory and clinical medicine, 1992, Volume: 119, Issue:6 Topics: Animals; Arthritis; Copper; Cytosol; Hepatolenticular Degeneration; Humans; Injections, Intramuscular; Liver; Male; Metallothionein; Methionine; Molybdenum; Organometallic Compounds; Penicillamine; Rats; Rats, Inbred Strains; Reference Values; Zinc	1992
Thiomolybdates in the treatment of Wilson's disease. Archives of neurology, 1992, Volume: 49, Issue:2 Topics: Hepatolenticular Degeneration; Humans; Molybdenum	1992
Initial therapy of patients with Wilson's disease with tetrathiomolybdate. Archives of neurology, 1991, Volume: 48, Issue:1 Topics: Adolescent; Adult; Ceruloplasmin; Copper; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum	1991
A comparison of the effects of penicillamine, trientine, and trithiomolybdate on [35S]-labeled metallothionein in vitro; implications for Wilson's disease therapy. Journal of inorganic biochemistry, 1991, Feb-01, Volume: 41, Issue:2 Topics: Animals; Copper; Cytosol; Hepatolenticular Degeneration; Liver; Male; Metallothionein; Molybdenum; Penicillamine; Rats; Rats, Inbred Strains; Sulfur Radioisotopes; Trientine	1991
Quantitation of Cu-containing metallothionein by a Cd-saturation method. Analytical biochemistry, 1990, Aug-15, Volume: 189, Issue:1 Topics: Animals; Cadmium; Cadmium Radioisotopes; Cells, Cultured; Chemistry Techniques, Analytical; Child; Child, Preschool; Chromatography, Gel; Copper; Cysteine; Ethanolamines; Fibroblasts; Glutathione; Hepatolenticular Degeneration; Humans; Male; Metallothionein; Molybdenum; Rats; Rats, Inbred Strains	1990
Can Wilson's disease patients be decoppered? Lancet (London, England), 1989, Jun-24, Volume: 1, Issue:8652 Topics: Animals; Copper; Drug Evaluation, Preclinical; Hepatolenticular Degeneration; Liver; Molybdenum; Rats	1989
Reversible pancytopenia secondary to treatment with tetrathiomolybdate. British journal of haematology, 1986, Volume: 64, Issue:4 Topics: Adult; Female; Hepatolenticular Degeneration; Humans; Male; Molybdenum; Pancytopenia	1986
Essential micronutrient elements. Biochemistry and changes in liver disorders. The American journal of clinical nutrition, 1970, Volume: 23, Issue:5 Topics: Alcohol Oxidoreductases; Cadmium; Copper; Hair; Hepatolenticular Degeneration; Humans; Iron; Liver Cirrhosis; Liver Diseases; Manganese; Molybdenum; Selenium; Trace Elements; Zinc	1970
[Changes in the content of several microelements (copper, iron, zinc, manganese and molybdenum) in the blood and urine in hepato-cerebral dystrophy]. Zhurnal nevropatologii i psikhiatrii imeni S.S. Korsakova (Moscow, Russia : 1952), 1968, Volume: 68, Issue:2 Topics: Adolescent; Adult; Copper; Female; Hepatolenticular Degeneration; Humans; Iron; Male; Manganese; Molybdenum; Trace Elements; Zinc	1968