mocetinostat and Hermanski-Pudlak-Syndrome

mocetinostat has been researched along with Hermanski-Pudlak-Syndrome* in 1 studies

Other Studies

1 other study(ies) available for mocetinostat and Hermanski-Pudlak-Syndrome

Article	Year
Pulmonary and Intestinal Involvement in a Patient with Myeloperoxidase-specific Antineutrophil Cytoplasmic Antibody-positive Hermansky-Pudlak Syndrome. Internal medicine (Tokyo, Japan), 2023, Jan-01, Volume: 62, Issue:1 A 26-year-old Japanese woman was admitted with a 1-month history of diarrhea, a high fever for a few days, and exacerbation of dyspnea. She was treated with an antifibrotic drug and long-term oxygen therapy for Hermansky-Pudlak syndrome-related pulmonary fibrosis. New ground-glass attenuation appeared on chest computed tomography (CT), and a colon biopsy showed an inflammatory cell accumulation with a high titer of myeloperoxidase (MPO)-specific anti-neutrophil cytoplasmic antibodies (ANCA). Systemic inflammation related to MPO-ANCA titer elevation was suspected. Steroid pulse therapy and intravenous cyclophosphamide improved chest CT findings and diarrhea. Therefore, immunosuppressant treatment should be considered for systemic inflammation related to MPO-ANCA. Topics: Adult; Antibodies, Antineutrophil Cytoplasmic; Diarrhea; Female; Hermanski-Pudlak Syndrome; Humans; Inflammation; Peroxidase	2023

Article

Year

Pulmonary and Intestinal Involvement in a Patient with Myeloperoxidase-specific Antineutrophil Cytoplasmic Antibody-positive Hermansky-Pudlak Syndrome.

Internal medicine (Tokyo, Japan), 2023, Jan-01, Volume: 62, Issue:1

A 26-year-old Japanese woman was admitted with a 1-month history of diarrhea, a high fever for a few days, and exacerbation of dyspnea. She was treated with an antifibrotic drug and long-term oxygen therapy for Hermansky-Pudlak syndrome-related pulmonary fibrosis. New ground-glass attenuation appeared on chest computed tomography (CT), and a colon biopsy showed an inflammatory cell accumulation with a high titer of myeloperoxidase (MPO)-specific anti-neutrophil cytoplasmic antibodies (ANCA). Systemic inflammation related to MPO-ANCA titer elevation was suspected. Steroid pulse therapy and intravenous cyclophosphamide improved chest CT findings and diarrhea. Therefore, immunosuppressant treatment should be considered for systemic inflammation related to MPO-ANCA.

Topics: Adult; Antibodies, Antineutrophil Cytoplasmic; Diarrhea; Female; Hermanski-Pudlak Syndrome; Humans; Inflammation; Peroxidase

2023