methylmalonic acid has been researched along with Fatty Liver with Encephalopathy in 2 studies
Methylmalonic Acid: A malonic acid derivative which is a vital intermediate in the metabolism of fat and protein. Abnormalities in methylmalonic acid metabolism lead to methylmalonic aciduria. This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl CoA.
methylmalonic acid : A dicarboxylic acid that is malonic acid in which one of the methylene hydrogens is substituted by a methyl group.
| Excerpt | Relevance | Reference |
|---|---|---|
| "In patients diagnosed as Reye syndrome, tissue carnitine deficiency was not always recognized and no decrease in the free/total carnitine ratio was found in the liver or muscle." | 1.28 | Carnitine deficiency in inherited organic acid disorders and Reye syndrome. ( Kidouchi, K; Kobayashi, M; Sugiyama, N; Wada, Y, 1990) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (50.00) | 18.7374 |
| 1990's | 1 (50.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Glasgow, AM | 1 |
| Chase, HP | 1 |
| Sugiyama, N | 1 |
| Kidouchi, K | 1 |
| Kobayashi, M | 1 |
| Wada, Y | 1 |
2 other studies available for methylmalonic acid and Fatty Liver with Encephalopathy
| Article | Year |
|---|---|
Effect of propionic acid on fatty acid oxidation and ureagenesis.
Topics: Ammonia; Animals; Carbon Dioxide; Fatty Acids; Fatty Liver; Fibroblasts; Liver; Methylmalonic Acid; | 1976 |
Carnitine deficiency in inherited organic acid disorders and Reye syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Humans; Infant; Male; Metabolism, | 1990 |