Page last updated: 2024-08-17

methionine and Cystic Fibrosis

methionine has been researched along with Cystic Fibrosis in 27 studies

Research

Studies (27)

TimeframeStudies, this research(%)All Research%
pre-199010 (37.04)18.7374
1990's8 (29.63)18.2507
2000's4 (14.81)29.6817
2010's5 (18.52)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Chandler, JD; Go, YM; Guglani, L; Horati, H; Janssens, HM; Jones, DP; Kilgore, MB; Liu, HK; Margaroli, C; Peng, L; Scholte, BJ; Taurone, AJ; Tiddens, HAWM; Tirouvanziam, R; Uppal, K; Veltman, M1
Laguna, TA; Reilly, CS; Welchlin, C; Wendt, CH; Williams, CB1
Campbell, KC; Cooper, MD; Fox, DJ; Hargrove, TL; Meech, RP; Roberts, MH; Rybak, LP; Speil, CA; Verhulst, SJ; Yanik, SC1
Alshaikh, B; Bennett, MJ; Maqbool, A; Mascarenhas, M; Schall, JI; Stallings, VA1
Bay, BN; Davidson, AG; Hasman, D; Innis, SM; Slack, PJ1
FINKELSTEIN, JD; IRREVERRE, F; LASTER, L; MUDD, SH1
Chen, A; Davidson, AG; Dyer, R; Innis, SM; James, SJ; Melnyk, S1
Darling, T; Driscoll, WJ; Eidelman, O; Guggino, WB; Huang, W; Jacobowitz, DM; Ji, XD; Jozwik, C; McGowan, B; Metcalf, E; Mogayzel, PJ; Mueller, G; Norris, CF; Paweletz, C; Pollard, HB; Srivastava, M; Todo, T; Wright, J; Zeitlin, PL1
Davidson, AG; Innis, SM; James, SJ; Melynk, S1
Joske, RA; Quinlan, MF; Way, NJ1
Funder, JW; Gyorki, S; Khalid, BA; Warne, GL1
Amara, JF; Fang, S; Ferrara, D; Hoppe, H; Marshall, J; O'Riordan, CR; Ostedgaard, LS; Scheule, RK; Smith, AE; Welsh, MJ1
Berger, HA; Cheng, SH; Rich, DP; Saxena, M; Smith, AE; Travis, SM; Welsh, MJ1
Al-Awqati, Q; Barasch, J; Imundo, L; Prince, A1
Hodson, ME; Pitt, TL; Taylor, RF2
Bardet, J; Delacourt, C; Descamps-Latscha, B; Nguyen, AT; Rabier, D; Witko-Sarsat, V1
Barth, AL; Pitt, TL; Woodford, N1
Akcakaya, N; Apak, M; Camcioglu, Y; Cokugras, H; Gokgoz, N; Kayserili, H; Kirdar, B; Onay, T; Topaloglu, O; Tsui, LC; Zielenski, J1
Eto, Y; Iizuka, S; Katsube, A; Morokawa, N; Muraji, T; Tanano, A; Yoshimura, K1
DeBusk, AG; Kelly, JC; Roess, WB; Sullivan, JL1
Khaw, KT; Lebenthal, E; Shwachman, H1
Baran, D; Dedobeleer, G; Defleur, V; Dumont, JE; Kirkpatrick, C; Lamy, F; Lecocq, R; Rodesch, F1
Agnew, JE; Bouchier, IA; Melmed, RN1
Farrell, PM; Klagsbrun, M1
Böhme, B1
Lowman, JT; Ulstrom, RA; Walker, WA1

Trials

2 trial(s) available for methionine and Cystic Fibrosis

ArticleYear
Choline supplementation alters some amino acid concentrations with no change in homocysteine in children with cystic fibrosis and pancreatic insufficiency.
    Nutrition research (New York, N.Y.), 2016, Volume: 36, Issue:5

    Topics: Adolescent; Amino Acids; Amino Acids, Branched-Chain; Child; Child, Preschool; Choline; Cystic Fibrosis; Dietary Supplements; Exocrine Pancreatic Insufficiency; Female; Homocysteine; Humans; Male; Methionine; Placebos

2016
Plasma choline depletion is associated with decreased peripheral blood leukocyte acetylcholine in children with cystic fibrosis.
    The American journal of clinical nutrition, 2011, Volume: 93, Issue:3

    Topics: Acetylcholine; Adolescent; Betaine; Child; Child, Preschool; Choline; Cross-Sectional Studies; Cystic Fibrosis; Enzyme Replacement Therapy; Female; Humans; Leukocytes; Male; Methionine; Pancreatin; Sarcosine

2011

Other Studies

25 other study(ies) available for methionine and Cystic Fibrosis

ArticleYear
Myeloperoxidase oxidation of methionine associates with early cystic fibrosis lung disease.
    The European respiratory journal, 2018, Volume: 52, Issue:4

    Topics: Bronchiectasis; Bronchoalveolar Lavage Fluid; Bronchoscopy; Child, Preschool; Cystic Fibrosis; Disease Progression; Female; Humans; Infant; Lung; Male; Methionine; Neutrophils; Oxidants; Oxidation-Reduction; Peroxidase; Prospective Studies; Tomography, X-Ray Computed

2018
Metabolomics analysis identifies novel plasma biomarkers of cystic fibrosis pulmonary exacerbation.
    Pediatric pulmonology, 2015, Volume: 50, Issue:9

    Topics: Adolescent; Adult; Biomarkers; Cohort Studies; Cystic Fibrosis; Cytidine; Female; Humans; Hydrocortisone; Hypoxanthine; Male; Mannose; Matched-Pair Analysis; Metabolome; Metabolomics; Methionine; Young Adult

2015
d-Methionine reduces tobramycin-induced ototoxicity without antimicrobial interference in animal models.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2016, Volume: 15, Issue:4

    Topics: Animals; Anti-Infective Agents; Cystic Fibrosis; Drug Monitoring; Ear Diseases; Escherichia coli; Evoked Potentials, Auditory, Brain Stem; Guinea Pigs; Hair Cells, Auditory, Outer; Methionine; Mice; Protective Agents; Tobramycin

2016
HOMOCYSTINURIA: AN ENZYMATIC DEFECT.
    Science (New York, N.Y.), 1964, Mar-27, Volume: 143, Issue:3613

    Topics: Amino Acids; Blood Protein Disorders; Carbon Isotopes; Child; Cystic Fibrosis; Cystinuria; Fatty Liver; Homocystinuria; Humans; Hypoproteinemia; Intellectual Disability; Ligases; Liver; Methionine; Pancreatic Neoplasms; Proteins; Psoriasis

1964
Increased plasma homocysteine and S-adenosylhomocysteine and decreased methionine is associated with altered phosphatidylcholine and phosphatidylethanolamine in cystic fibrosis.
    The Journal of pediatrics, 2003, Volume: 143, Issue:3

    Topics: Child; Cystic Fibrosis; Female; Homocysteine; Humans; Male; Methionine; Phosphatidylcholines; Phosphatidylethanolamines; S-Adenosylhomocysteine; Severity of Illness Index

2003
De novo biosynthetic profiling of high abundance proteins in cystic fibrosis lung epithelial cells.
    Molecular & cellular proteomics : MCP, 2006, Volume: 5, Issue:9

    Topics: Cell Line; Cystic Fibrosis; Electrophoresis, Gel, Two-Dimensional; Epithelial Cells; Humans; Lung; Methionine; Peptide Mapping; Proteome; Silver Staining; Spectrometry, Mass, Matrix-Assisted Laser Desorption-Ionization; Sulfur Radioisotopes

2006
Choline-related supplements improve abnormal plasma methionine-homocysteine metabolites and glutathione status in children with cystic fibrosis.
    The American journal of clinical nutrition, 2007, Volume: 85, Issue:3

    Topics: Adolescent; Child; Child, Preschool; Choline; Cystic Fibrosis; Dietary Supplements; Female; Glutathione; Glutathione Disulfide; Homocysteine; Humans; Male; Methionine; Phosphatidylcholines

2007
Adult cystic fibrosis presenting with meconium ileus equivalent and diagnosed by selenomethionine scanning of the pancreas.
    Australasian annals of medicine, 1967, Volume: 16, Issue:1

    Topics: Adult; Celiac Disease; Cystic Fibrosis; Humans; Intestinal Obstruction; Male; Methionine; Radiography; Radioisotopes; Radiometry; Selenium

1967
Cystic fibrosis and normal fibroblasts have identical glucocorticoid receptor profiles and induced protein responses.
    Clinical endocrinology, 1983, Volume: 18, Issue:4

    Topics: Adolescent; Autoradiography; Cell Division; Cell Line; Cells, Cultured; Child; Child, Preschool; Cystic Fibrosis; Dexamethasone; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Humans; Infant; Methionine; Protein Biosynthesis; Receptors, Glucocorticoid; Receptors, Steroid; Skin

1983
Stoichiometry of recombinant cystic fibrosis transmembrane conductance regulator in epithelial cells and its functional reconstitution into cells in vitro.
    The Journal of biological chemistry, 1994, Jan-28, Volume: 269, Issue:4

    Topics: Adenosine Triphosphate; Animals; Cell Line; CHO Cells; Cricetinae; Cyclic AMP-Dependent Protein Kinases; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Electrophoresis, Polyacrylamide Gel; Epithelium; Genetic Vectors; Humans; Kidney; Kinetics; Membrane Fusion; Membrane Proteins; Methionine; Mice; Mutagenesis, Site-Directed; Phosphorylation; Rats; Recombinant Proteins; Restriction Mapping; Sulfur Radioisotopes; Swine; Thyroid Gland; Time Factors; Transfection

1994
Regulation of the cystic fibrosis transmembrane conductance regulator Cl- channel by negative charge in the R domain.
    The Journal of biological chemistry, 1993, Sep-25, Volume: 268, Issue:27

    Topics: Alanine; Amino Acid Sequence; Animals; Autoradiography; Cell Line; Chloride Channels; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; HeLa Cells; Humans; Ion Channel Gating; Ion Channels; Kinetics; Membrane Proteins; Methionine; Mutagenesis, Site-Directed; Peptide Mapping; Phosphopeptides; Phosphorylation; Protein Kinases; Serine; Sulfur Radioisotopes; Transfection

1993
Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface.
    Proceedings of the National Academy of Sciences of the United States of America, 1995, Mar-28, Volume: 92, Issue:7

    Topics: Bacterial Adhesion; Binding, Competitive; Carbohydrate Sequence; Carbohydrates; Cell Line; Cystic Fibrosis; Epithelium; G(M1) Ganglioside; Humans; Lung; Methionine; Molecular Sequence Data; Oligosaccharides; Pancreas; Pseudomonas aeruginosa; Reference Values; Staphylococcus aureus; Sulfur Radioisotopes

1995
Adult cystic fibrosis: association of acute pulmonary exacerbations and increasing severity of lung disease with auxotrophic mutants of Pseudomonas aeruginosa.
    Thorax, 1993, Volume: 48, Issue:10

    Topics: Acute Disease; Adolescent; Adult; Aged; Cystic Fibrosis; Female; Growth Substances; Humans; Male; Methionine; Middle Aged; Mutation; Pseudomonas aeruginosa; Pseudomonas Infections; Sputum; Time Factors

1993
Neutrophil-derived long-lived oxidants in cystic fibrosis sputum.
    American journal of respiratory and critical care medicine, 1995, Volume: 152, Issue:6 Pt 1

    Topics: Adolescent; Adult; Asthma; Child; Child, Preschool; Chloramines; Cystic Fibrosis; Forced Expiratory Volume; Humans; Methionine; Neutrophils; Oxidants; Peroxidase; Proteins; Pseudomonas aeruginosa; Pseudomonas Infections; Sputum; Staphylococcus aureus; Taurine; Vital Capacity

1995
Complementation of methionine auxotrophs of Pseudomonas aeruginosa from cystic fibrosis.
    Current microbiology, 1998, Volume: 36, Issue:4

    Topics: Cystic Fibrosis; Humans; Methionine; Mutation; Plasmids; Pseudomonas aeruginosa; Pseudomonas Infections

1998
Analysis of the CFTR gene in Turkish cystic fibrosis patients: identification of three novel mutations (3172delAC, P1013L and M1028I).
    Human genetics, 1998, Volume: 102, Issue:2

    Topics: Adenine; Amino Acid Substitution; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytosine; Frameshift Mutation; Humans; Isoleucine; Leucine; Methionine; Mutation; Polymorphism, Genetic; Proline; Sequence Deletion; Turkey

1998
Severe cystic fibrosis in a Japanese girl caused by two novel CFTR (ABCC7) gene mutations: M152R and 1540del10.
    Human mutation, 2000, Volume: 15, Issue:5

    Topics: Amino Acid Substitution; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Frameshift Mutation; Gene Deletion; Humans; Methionine; Mutation, Missense

2000
Membrane function in cystic fibrosis. II. Methionine transport in normal and cystic fibrosis fibroblasts.
    Biochemical genetics, 1977, Volume: 15, Issue:11-12

    Topics: Biological Transport, Active; Cell Line; Cells, Cultured; Cystic Fibrosis; Fibroblasts; Humans; Kinetics; Methionine; Skin

1977
Recurrent acute pancreatitis in patients with cystic fibrosis with normal pancreatic enzymes.
    Pediatrics, 1975, Volume: 55, Issue:1

    Topics: Acute Disease; Adolescent; Adult; Amylases; Chlorides; Cholecystokinin; Chymotrypsin; Cystic Fibrosis; Female; Glucose Tolerance Test; Humans; Intubation, Gastrointestinal; Lipase; Magnesium; Male; Methionine; Pain; Pancreas; Pancreatitis; Potassium; Recurrence; Secretin; Selenium; Sodium; Trypsin

1975
Auxotrophy of Pseudomonas aeruginosa in cystic fibrosis.
    FEMS microbiology letters, 1992, May-01, Volume: 71, Issue:3

    Topics: Amino Acids; Arginine; Bronchiectasis; Cystic Fibrosis; Humans; Methionine; Proline; Pseudomonas aeruginosa; Sputum; Thiamine

1992
Analysis of proteins synthesized by fibroblasts from patients with cystic fibrosis by two-dimensional gel electrophoresis and double label autoradiography.
    Pediatric research, 1985, Volume: 19, Issue:12

    Topics: Adolescent; Adult; Autoradiography; Cells, Cultured; Child; Child, Preschool; Cystic Fibrosis; Electrophoresis, Polyacrylamide Gel; Female; Fibroblasts; Humans; Male; Methionine; Mutation; Protein Biosynthesis; Proteins; Selenomethionine; Skin

1985
The normal and abnormal pancreatic scan.
    The Quarterly journal of medicine, 1968, Volume: 37, Issue:148

    Topics: Adenoma, Islet Cell; Adult; Aged; Amyloidosis; Aneurysm; Cholelithiasis; Cystic Fibrosis; Diabetes Mellitus; Female; Gold Isotopes; Humans; Injections, Intravenous; Liver Function Tests; Male; Methionine; Middle Aged; Neoplasm Metastasis; Pancreas; Pancreatectomy; Pancreatic Diseases; Pancreatic Neoplasms; Pancreatitis; Peptic Ulcer; Radioisotopes; Radionuclide Imaging; Selenium

1968
The methylation of transfer and ribosomal ribonucleic acid in human fibroblasts: normal methylation of ribonucleic acid in cystic fibrosis.
    Pediatric research, 1974, Volume: 8, Issue:3

    Topics: Adolescent; Adult; Autoradiography; Carbon Radioisotopes; Cells, Cultured; Child; Chromatography; Cystic Fibrosis; Fibroblasts; Humans; Methionine; Methylation; Ribonucleosides; RNA, Ribosomal; RNA, Transfer; Skin; Tritium; Uridine

1974
[Current concepts on the pathogenesis of mucoviscidosis].
    Zeitschrift fur arztliche Fortbildung, 1974, Feb-15, Volume: 68, Issue:4

    Topics: Calcium; Cell Membrane Permeability; Chlorides; Cystic Fibrosis; Heterozygote; Homozygote; Humans; Immunoglobulin Fragments; Methionine; Salivary Glands; Sodium

1974
Albumin synthesis rates in patients with hypoproteinemia.
    The Journal of pediatrics, 1971, Volume: 78, Issue:5

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Anaphylaxis; Anorexia Nervosa; Bile Ducts; Child; Child, Preschool; Chromatography, Gel; Colitis, Ulcerative; Cystic Fibrosis; Female; Glomerulonephritis; Humans; Hypoproteinemia; Infant; Injections, Intravenous; Intellectual Disability; Kinetics; Liver; Liver Cirrhosis; Liver Cirrhosis, Biliary; Liver Diseases; Male; Methionine; Nephrotic Syndrome; Psychomotor Disorders; Purpura; Radioisotopes; Selenium; Serum Albumin; Spectrophotometry; Tyrosine

1971