Page last updated: 2024-08-22

mannose and Adult Neuronal Ceroid Lipofuscinosis

mannose has been researched along with Adult Neuronal Ceroid Lipofuscinosis in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19903 (42.86)18.7374
1990's4 (57.14)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hellsten, E; Jalanko, A; Olkkonen, VM; Peltonen, L; Vesa, J1
Junaid, MA; Pullarkat, RK1
Heaney-Kieras, J; Kieras, FJ; Wisniewski, KE1
Dell, A; Hall, NA; Haltia, M; Lake, BD; Patrick, AD; Thomas-Oates, JE1
Elleder, M1
Hall, NA; Haltia, M; Patrick, AD1
Krusius, T; Maury, CP; Palo, J; Viitala, J1

Other Studies

7 other study(ies) available for mannose and Adult Neuronal Ceroid Lipofuscinosis

ArticleYear
Human palmitoyl protein thioesterase: evidence for lysosomal targeting of the enzyme and disturbed cellular routing in infantile neuronal ceroid lipofuscinosis.
    The EMBO journal, 1996, Oct-01, Volume: 15, Issue:19

    Topics: Amidohydrolases; Animals; Biological Transport; COS Cells; Endocytosis; Endoplasmic Reticulum; Glycosylation; Hexosaminidases; Humans; Lysosomal Storage Diseases; Lysosomes; Mannose; Molecular Weight; Mutation; Neuronal Ceroid-Lipofuscinoses; Peptide-N4-(N-acetyl-beta-glucosaminyl) Asparagine Amidase; Peptides; Phosphorylation; Receptor, IGF Type 2; Thiolester Hydrolases

1996
Increased brain lysosomal pepstatin-insensitive proteinase activity in patients with neurodegenerative diseases.
    Neuroscience letters, 1999, Apr-02, Volume: 264, Issue:1-3

    Topics: Adult; Aged; Aged, 80 and over; Aging; Alzheimer Disease; Aminopeptidases; Animals; Brain; Child; Dipeptidyl-Peptidases and Tripeptidyl-Peptidases; Dog Diseases; Dogs; Endopeptidases; Female; Humans; Leukodystrophy, Globoid Cell; Male; Mannose; Middle Aged; Neurodegenerative Diseases; Neuronal Ceroid-Lipofuscinoses; Pepstatins; Peptide Hydrolases; Reference Values; Serine Proteases; Tripeptidyl-Peptidase 1

1999
Glycoprotein metabolism in neuronal ceroid lipofuscinosis fibroblasts.
    Biochemical medicine and metabolic biology, 1992, Volume: 48, Issue:2

    Topics: Adolescent; Adult; Age Factors; Cell Line; Child; Child, Preschool; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Glucosamine; Glycoproteins; Humans; Infant; Mannose; Methionine; Neuronal Ceroid-Lipofuscinoses; Skin; Sulfur Radioisotopes; Tritium

1992
Stored dolichyl pyrophosphoryl oligosaccharides in Batten disease.
    American journal of medical genetics, 1992, Feb-15, Volume: 42, Issue:4

    Topics: Carbohydrate Sequence; Cells, Cultured; Chromatography; Dolichol Phosphates; Humans; Lysosomes; Mannose; Mannosidases; Molecular Sequence Data; Neuronal Ceroid-Lipofuscinoses; Polyisoprenyl Phosphate Oligosaccharides

1992
Lectin histochemical study of lipopigments with special regard to neuronal ceroid-lipofuscinosis. Results with concanavalin A.
    Histochemistry, 1989, Volume: 93, Issue:2

    Topics: Adolescent; Adult; Animals; Ceroid; Child; Child, Preschool; Concanavalin A; Gangliosidoses; Humans; Lipofuscin; Mannose; Mucopolysaccharidoses; Neuronal Ceroid-Lipofuscinoses; Neurons; Olivary Nucleus; Pigments, Biological; Staining and Labeling

1989
High-mannose dolichol-linked oligosaccharides in infantile ceroid-lipofuscinosis.
    Biochemical Society transactions, 1989, Volume: 17, Issue:6

    Topics: Brain; Dolichols; Humans; Infant; Mannose; Neuronal Ceroid-Lipofuscinoses; Oligosaccharides

1989
Enrichment of high mannose-type glycans in nervous tissue glycoproteins in neuronal ceroid-lipofuscinosis.
    Journal of the neurological sciences, 1986, Volume: 72, Issue:1

    Topics: Adolescent; Aged; Animals; Brain; Brain Chemistry; Cell Line; Child; Chromatography, Affinity; Glycopeptides; Glycoproteins; Humans; Hydrazines; Mannose; Methylation; Nerve Tissue Proteins; Neuronal Ceroid-Lipofuscinoses; Oligosaccharides; Rats

1986