malonyl-coenzyme-a and Methemoglobinemia

malonyl-coenzyme-a has been researched along with Methemoglobinemia* in 1 studies

Other Studies

1 other study(ies) available for malonyl-coenzyme-a and Methemoglobinemia

Article	Year
Decrease of palmitoyl-CoA elongation in platelets and leukocytes in the patient of hereditary methemoglobinemia associated with mental retardation. Biochemical and biophysical research communications, 1987, Oct-14, Volume: 148, Issue:1 Effect of the deficiency of NADH-cytochrome b5 reductase on fatty acid elongation was studied in the platelets and leukocytes taken from a patient of hereditary methemoglobinemia associated with mental retardation. The activity of fatty acid elongation was determined by measuring the incorporation of [2-14C]malonyl-CoA into palmitoyl-CoA. The de novo biosynthesis of fatty acids was blocked by the addition of phosphotransacetylase, and the elongation system could be assayed in the homogenates separated from de novo biosynthesis. As compared to normal subjects approximately 40% decrease of fatty acid elongation was observed both in the platelets and leukocytes from the patient. Topics: Acyl Coenzyme A; Blood Platelets; Humans; In Vitro Techniques; Intellectual Disability; Kinetics; Leukocytes; Malonyl Coenzyme A; Methemoglobinemia; Palmitoyl Coenzyme A	1987

Article

Year

Decrease of palmitoyl-CoA elongation in platelets and leukocytes in the patient of hereditary methemoglobinemia associated with mental retardation.

Biochemical and biophysical research communications, 1987, Oct-14, Volume: 148, Issue:1

Effect of the deficiency of NADH-cytochrome b5 reductase on fatty acid elongation was studied in the platelets and leukocytes taken from a patient of hereditary methemoglobinemia associated with mental retardation. The activity of fatty acid elongation was determined by measuring the incorporation of [2-14C]malonyl-CoA into palmitoyl-CoA. The de novo biosynthesis of fatty acids was blocked by the addition of phosphotransacetylase, and the elongation system could be assayed in the homogenates separated from de novo biosynthesis. As compared to normal subjects approximately 40% decrease of fatty acid elongation was observed both in the platelets and leukocytes from the patient.

Topics: Acyl Coenzyme A; Blood Platelets; Humans; In Vitro Techniques; Intellectual Disability; Kinetics; Leukocytes; Malonyl Coenzyme A; Methemoglobinemia; Palmitoyl Coenzyme A

1987