Page last updated: 2024-08-21

lignoceric acid and Lipid Metabolism, Inborn Error

lignoceric acid has been researched along with Lipid Metabolism, Inborn Error in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19904 (80.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (20.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Imanaka, T; Kawaguchi, K; Matsumoto, S; Matsuya, Y; Minato, D; Morita, M; Okazaki, A; Shimozawa, N; Tomita, K; Watanabe, S1
Baymann, NA; Bourre, JM; Daudu, OL1
Baumann, NA; Bourre, JM; Daudu, OL; Paturneau-Jouas, MY1
Heikoop, J; Poll-Thé, BT; Saudubray, JM; Schram, AW; Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; van Wijland, MJ; Wanders, RJ1
Poulos, A; Singh, H1

Other Studies

5 other study(ies) available for lignoceric acid and Lipid Metabolism, Inborn Error

ArticleYear
A novel method for determining peroxisomal fatty acid β-oxidation.
    Journal of inherited metabolic disease, 2016, Volume: 39, Issue:5

    Topics: Adrenoleukodystrophy; Carnitine Acyltransferases; Cells, Cultured; Fatty Acids; Fibroblasts; Humans; Lauric Acids; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction; Peroxisomal Disorders; Peroxisomes; Pyrenes; Skin; Zellweger Syndrome

2016
Biosynthesis of lignoceric acid from behenyl0COA in mouse brain microsomes. Comparison between normal and Quaking mutant.
    Biochemical and biophysical research communications, 1975, Apr-21, Volume: 63, Issue:4

    Topics: Animals; Brain; Chromatography, Gas; Chromatography, Thin Layer; Coenzyme A; Fatty Acids; Kinetics; Lipid Metabolism, Inborn Errors; Malonates; Mice; Microsomes; Mutation; Myelin Sheath; NADP; Oxidation-Reduction; Phospholipids; Time Factors

1975
Lignoceric acid biosynthesis in the developing brain. Activities of mitochondrial acetyl-CoA-dependent synthesis and microsomal malonyl-CoA chain-elongating system in relation to myelination. Comparison between normal mouse and dysmyelinating mutants (qua
    European journal of biochemistry, 1977, Jan-03, Volume: 72, Issue:1

    Topics: Aging; Animals; Brain; Coenzyme A; Fatty Acid Synthases; Fatty Acids; Kinetics; Lipid Metabolism, Inborn Errors; Male; Malonates; Mice; Mice, Inbred C57BL; Microsomes; Mitochondria; Mutation; Myelin Sheath; Species Specificity

1977
Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
    Clinica chimica acta; international journal of clinical chemistry, 1987, Jul-15, Volume: 166, Issue:2-3

    Topics: Adrenoleukodystrophy; Adult; Brain Diseases; Cells, Cultured; Fatty Acids; Female; Fibroblasts; Humans; Kidney Diseases; Lipid Metabolism, Inborn Errors; Liver Diseases; Microbodies; Oxidation-Reduction; Refsum Disease; Skin; Syndrome

1987
A comparative study of stearic and lignoceric acid oxidation by human skin fibroblasts.
    Archives of biochemistry and biophysics, 1986, Volume: 250, Issue:1

    Topics: Autoradiography; Fatty Acids; Fibroblasts; Humans; Lipid Metabolism, Inborn Errors; Oxidation-Reduction; Skin; Stearic Acids

1986