Page last updated: 2024-08-21

lignoceric acid and Cerebro-Hepato-Renal Syndrome

lignoceric acid has been researched along with Cerebro-Hepato-Renal Syndrome in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's10 (90.91)18.2507
2000's0 (0.00)29.6817
2010's1 (9.09)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Imanaka, T; Kawaguchi, K; Matsumoto, S; Matsuya, Y; Minato, D; Morita, M; Okazaki, A; Shimozawa, N; Tomita, K; Watanabe, S1
Kremser, K; Lazo, O; Singh, I1
Dhaunsi, GS; Lazo, O; Ozand, P; Pahan, K; Singh, I1
Burdette, DE; Fink, JK; Kremser, K; Pahan, K; Singh, I; Stanley, W1
Fujiki, Y; Hashimoto, T; Kamijo, K; Kondo, N; Orii, T; Osumi, T; Shimozawa, N; Suzuki, Y; Tomatsu, S; Tsukamoto, T1
Chahal, A; Khan, M; Sandhir, R; Singh, I1
Beckman, K; Johnson, DW; Paton, BC; Poulos, A; Singh, H; Stockham, PC1
Ashcraft, J; Kremser, K; Singh, AK; Singh, I; Stanczak, H; Stanley, W1
Masuno, M; Okamoto, H; Orii, T; Shimozawa, N; Suzuki, Y; Yajima, S1
Brückwilder, ML; Hashimoto, T; Monnens, LA; Reubsaet, FA; Trijbels, JM; Veerkamp, JH1
Contreras, M; Lazo, O; Singh, AK; Singh, I; Stanley, W; Weise, M; Yoshida, Y1

Other Studies

11 other study(ies) available for lignoceric acid and Cerebro-Hepato-Renal Syndrome

ArticleYear
A novel method for determining peroxisomal fatty acid β-oxidation.
    Journal of inherited metabolic disease, 2016, Volume: 39, Issue:5

    Topics: Adrenoleukodystrophy; Carnitine Acyltransferases; Cells, Cultured; Fatty Acids; Fibroblasts; Humans; Lauric Acids; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction; Peroxisomal Disorders; Peroxisomes; Pyrenes; Skin; Zellweger Syndrome

2016
Purification of peroxisomes and subcellular distribution of enzyme activities for activation and oxidation of very-long-chain fatty acids in rat brain.
    Biochimica et biophysica acta, 1993, Sep-29, Volume: 1170, Issue:1

    Topics: Adrenoleukodystrophy; Animals; Antibodies; Brain Chemistry; Coenzyme A Ligases; Fatty Acids; Liver; Microbodies; Mitochondria; Palmitic Acid; Palmitic Acids; Rats; Repressor Proteins; Saccharomyces cerevisiae Proteins; Subcellular Fractions; Zellweger Syndrome

1993
Phytanic acid alpha-oxidation. Differential subcellular localization in rat and human tissues and its inhibition by nycodenz.
    The Journal of biological chemistry, 1993, May-15, Volume: 268, Issue:14

    Topics: Adrenoleukodystrophy; Animals; Cell Fractionation; Cells, Cultured; Centrifugation, Density Gradient; Chlorides; Chondrodysplasia Punctata; Epoxy Compounds; Fatty Acids; Ferric Compounds; Fibroblasts; Humans; Hypoglycemic Agents; Iohexol; Kinetics; Liver; Microbodies; Mitochondria; Organelles; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Phytanic Acid; Rats; Rats, Sprague-Dawley; Skin; Subcellular Fractions; Zellweger Syndrome

1993
Late-onset generalized disorder of peroxisomes.
    Neurology, 1996, Volume: 46, Issue:3

    Topics: Adrenoleukodystrophy; Adult; Catalase; Fatty Acids; Genetic Linkage; Humans; Male; Microbodies; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; X Chromosome; Zellweger Syndrome

1996
Correction by gene expression of biochemical abnormalities in fibroblasts from Zellweger patients.
    Pediatric research, 1996, Volume: 39, Issue:5

    Topics: Acyltransferases; ATP-Binding Cassette Transporters; Cell Line; DNA, Complementary; Fatty Acids; Fibroblasts; Gene Expression; Genetic Complementation Test; Genetic Therapy; Humans; Membrane Proteins; Microbodies; Oxidation-Reduction; Peroxisomal Biogenesis Factor 2; Transfection; Zellweger Syndrome

1996
Localization of nervonic acid beta-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy.
    Journal of lipid research, 1998, Volume: 39, Issue:11

    Topics: Adrenoleukodystrophy; Animals; Cell Line; Coenzyme A Ligases; Fatty Acids; Fatty Acids, Monounsaturated; Fibroblasts; Genetic Linkage; Humans; Microbodies; Neuroglia; Oxidation-Reduction; Rats; Rats, Sprague-Dawley; Repressor Proteins; Saccharomyces cerevisiae Proteins; X Chromosome; Zellweger Syndrome

1998
Metabolism of trideuterated iso-lignoceric acid in rats in vivo and in human fibroblasts in culture.
    Lipids, 1999, Volume: 34, Issue:9

    Topics: Animals; Blood-Brain Barrier; Brain; Cells, Cultured; Chromatography, Gas; Deuterium; Fatty Acids; Fibroblasts; Humans; Liver; Oxidation-Reduction; Peroxisomes; Rats; Rats, Sprague-Dawley; Zellweger Syndrome

1999
Complementation in Zellweger syndrome: biochemical analysis of newly generated peroxisomes.
    Human heredity, 1992, Volume: 42, Issue:3

    Topics: Acyltransferases; Cell Line; Fatty Acids; Genetic Complementation Test; Humans; Microbodies; Oxidation-Reduction; Zellweger Syndrome

1992
Transformation and characterization of mutant human fibroblasts defective in peroxisome assembly.
    Experimental cell research, 1992, Volume: 201, Issue:2

    Topics: Acyltransferases; Adrenoleukodystrophy; Cell Line, Transformed; Dihydroxyacetone Phosphate; Fatty Acids; Fibroblasts; Humans; Microbodies; Mutation; Transformation, Genetic; Zellweger Syndrome

1992
Immunochemical and biochemical studies of fatty acid oxidation in fibroblasts of Zellweger and X-linked adrenoleukodystrophy patients.
    Biochimica et biophysica acta, 1991, Jun-03, Volume: 1083, Issue:3

    Topics: Acetyl-CoA C-Acyltransferase; Acyl-CoA Oxidase; Adrenoleukodystrophy; Fatty Acids; Fibroblasts; Humans; Immunoblotting; Microbodies; Oxidation-Reduction; Oxidoreductases; Palmitic Acid; Palmitic Acids; X Chromosome; Zellweger Syndrome

1991
Cellular oxidation of lignoceric acid is regulated by the subcellular localization of lignoceroyl-CoA ligases.
    Journal of lipid research, 1990, Volume: 31, Issue:4

    Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Endoplasmic Reticulum; Fatty Acids; Fibroblasts; Genetic Linkage; Histocytochemistry; Humans; Microbodies; Microscopy, Electron; Mitochondria; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Repressor Proteins; Saccharomyces cerevisiae Proteins; X Chromosome; Zellweger Syndrome

1990