lignoceric acid has been researched along with Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis in 11 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 9 (81.82) | 18.7374 |
| 1990's | 2 (18.18) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Avigan, J; Chemke, J; Rizzo, WB; Schulman, JD | 1 |
| Goldfischer, S; Moser, AE; Moser, HW; Singh, I | 1 |
| Poulos, A; Singh, H; Street, JM | 1 |
| Contreras, M; Lazo, O; Singh, AK; Singh, I; Stanley, W; Weise, M; Yoshida, Y | 1 |
| Derwas, N; Paton, B; Poulos, A; Sharp, P; Singh, H | 1 |
| Bhushan, A; Contreras, M; Lazo, O; Singh, I; Stanley, W | 1 |
| Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; Wanders, RJ | 1 |
| Contreras, M; Hashmi, M; Irazu, C; Lazo, O; Singh, I; Stanley, W | 1 |
| Griffin, J; Moser, AB; Moser, HW; Sacktor, NC | 1 |
| Kodama, S; Nishio, H; Ohno, M; Onaga, A; Saeki, Y; Shimada, M; Tanaka, K; Yamano, T | 1 |
| Ariga, T; Miyatake, T; Sano-Kawamura, T; Tsuji, S | 1 |
11 other study(ies) available for lignoceric acid and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis
| Article | Year |
|---|---|
Adrenoleukodystrophy: very long-chain fatty acid metabolism in fibroblasts.
Topics: Adrenoleukodystrophy; Cells, Cultured; Culture Media; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Palmitates | 1984 |
Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.
Topics: Abnormalities, Multiple; Adrenoleukodystrophy; Animals; Brain Diseases; Catalase; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Kidney Diseases; Liver; Liver Diseases; Male; Microbodies; Mitochondria, Liver; Oxidation-Reduction; Rats; Rats, Inbred Strains; Sex Chromosome Aberrations; Syndrome; Urate Oxidase | 1984 |
Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation.
Topics: Adrenoleukodystrophy; Carbon Dioxide; Carbon Radioisotopes; Cells, Cultured; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Fibroblasts; Glutamates; Humans; Lipid Metabolism; Microbodies; Oxidation-Reduction; Skin | 1990 |
Cellular oxidation of lignoceric acid is regulated by the subcellular localization of lignoceroyl-CoA ligases.
Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Endoplasmic Reticulum; Fatty Acids; Fibroblasts; Genetic Linkage; Histocytochemistry; Humans; Microbodies; Microscopy, Electron; Mitochondria; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Repressor Proteins; Saccharomyces cerevisiae Proteins; X Chromosome; Zellweger Syndrome | 1990 |
Accumulation and defective beta-oxidation of very long chain fatty acids in Zellweger's syndrome, adrenoleukodystrophy and Refsum's disease variants.
Topics: Adrenoleukodystrophy; Carbon Dioxide; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Diseases, Inborn; Humans; Microbodies; Oxidation-Reduction; Refsum Disease; Syndrome | 1986 |
Adrenoleukodystrophy: impaired oxidation of fatty acids due to peroxisomal lignoceroyl-CoA ligase deficiency.
Topics: Adrenoleukodystrophy; Animals; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Liver; Microbodies; Palmitic Acid; Palmitic Acids; Rats; Skin | 1989 |
Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Male; Microbodies | 1988 |
Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy.
Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Linkage; Humans; Microbodies; Microsomes; Mitochondria; Oxidation-Reduction; Palmitic Acids; Palmitoyl Coenzyme A; Skin; X Chromosome | 1988 |
Effects of subperineurial injections of very-long-chain and medium-chain fatty acids into rat sciatic nerve.
Topics: Adrenoleukodystrophy; Animals; Cholesterol Esters; Diffuse Cerebral Sclerosis of Schilder; Disease Models, Animal; Fatty Acids; Lipids; Male; Palmitic Acid; Palmitic Acids; Peripheral Nerves; Rats; Rats, Inbred Strains | 1986 |
Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Male; Microscopy, Electron; Mucous Membrane; Rectum | 1987 |
Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN).
Topics: Adrenoleukodystrophy; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Skin; Solubility | 1985 |